ACR Meeting Abstracts

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Abstracts tagged "Vasculitis"

  • Abstract Number: 0432 • ACR Convergence 2021

    Anti-IL5 Therapy in Eosinophilic Granulomatosis with Polyangiitis (EGPA): A Longitudinal Follow-up Study ≥ 24months

    Allyson Egan1, Pasupathy Sivasothy2, Lisa Willcocks2, Rachel Jones2, Marcos Martinez Del Pero3 and David R.W. Jayne4, 1Vasculitis and Lupus Centre, Cambridge University Hospital, University of Cambridge, London, United Kingdom, 2Vasculitis and Lupus Centre, Department of Medicine, Cambridge University Hospital, Cambridge, United Kingdom, 3Vasculitis and Lupus Centre, Cambridge University Hospital, Cambridge, United Kingdom, 4University of Cambridge, Cambridge, United Kingdom

    Background/Purpose: In the randomized, placebo-controlled MIRRA trial for relapsing and refractory eosinophilic granulomatosis with polyangiitis (EGPA), adjuvant therapy with 300mg anti-IL5 mAB Mepolizumab [MEPO] for…
  • Abstract Number: 1405 • ACR Convergence 2021

    Effectiveness of Tocilizumab in Cranial and Extracranial Phenotypes of Giant Cell Arteritis: Multicenter Study of 471 Cases

    Lara Sánchez-Bilbao1, Javier Loricera1, Santos Castañeda2, Clara Moriano3, Javier Narvaez4, Vicente Aldasoro5, Olga Maíz6, Rafael Melero7, Juan Ignacio Villa8, Paloma Vela9, Susana Romero-Yuste10, José Luis Callejas11, Eugenio De Miguel12, Eva Galindez-Agirregoikoa13, Francisca Sivera14, Jesús Carlos Fernández-López15, Carles Galisteo16, Iván Ferraz-Amaro17, Juan Carlos Nieto18, Juan Ramón de Dios19, Julio Sánchez20, Esther Fernández21, Isabel de la Morena22, Patricia Moya23, Roser Solans-Laqué24, Jose Luis Andreu25, Marcelino Revenga26, Eztizen Labrador27, Andrea García-Valle28, Adela Gallego29, Carlota Iñíguez30, Cristina Hidalgo31, Noemí Garrido-Puñal32, Ruth López-González33, José Andrés Román-Ivorra34, Sara Manrique Arija35, Paz Collado36, Enrique Raya11, Francisco Navarro37, Antoni Juan Mas38, Carmen Ordas39, Maria Dolors Boquet40, Noelia Álvarez-Rivas41, Maria Luisa Velloso-Feijoo42, Cristina Campos-Fernández43, Íñigo Rúa-Figueroa44, Arantxa Conesa45, Eva Salgado46, Miguel Ángel gonzalez-Gay47 and Ricardo Blanco48, 1Hospital Universitario Marqués de Valdecilla, Santander, Spain, 2Hospital Universitario de la Princesa, Madrid, Spain, 3Hospital Universitario de León, León, Spain, 4Division of Rheumatology, Hospital Universitario de Bellvitge, Barcelona, Spain, 5Complejo Hospitalario de Navarra, Pamplona, Spain, 6Hospital Universitario de Donostia, San Sebastián, Spain, 7Complexo Hospitalario Universitario de Vigo, Vigo, Galicia, Spain, 8Hospital Sierrallana, Torrelavega, Spain, 9Hospital General Universitario de Alicante, Alicante, Spain, 10Complejo Hospitalario Universitario de Pontevedra, Pontevedra, Spain, 11Hospital San Cecilio, Granada, Spain, 12Hospital Universitario La Paz, Madrid, Spain, 13Hospital Universitario de Basurto, Bilbao, Spain, 14Hospital Universitario de Elda, Alicante, Spain, 15Hospital Universitario Juan Canalejo, A Coruña, Spain, 16Hospital Universitari Parc Tauli, Saadell, Spain, 17Hospital Universitario de Canarias, Santa Cruz de Tenerife, Spain, 18Hospital General Universitario Gregorio Marañón, Madrid, Spain, 19Hospital Universitario de Araba, Mondragón, Spain, 20Hospital Universitario 12 de Octubre, Madrid, Spain, 21Hospital Clínico Universitario Virgen de la Arrixaca, Murcia, Spain, 22Hospital Clínico Universitario de Valencia, Valencia, Spain, 23Hospital Sant Pau, Barcelona, Spain, 24Hospital Vall d'Hebron, Barcelona, Spain, 25Hospital Universitario Puerta de Hierro, Madrid, Spain, 26Hospital Universitario Ramón y Cajal, Madrid, Spain, 27Hospital San Pedro, Logroño, La Rioja, Spain, 28Complejo Asistencial Universitario de Palencia, Palencia. Spain, Palencia, Spain, 29Complejo Hospitalario Universitario de Badajoz, Badajoz, Spain, 30Hospital Universitario Lucus Augusti, Lugo, Galicia, Spain, 31Hospital Universitario Salamanca, Salamanca, Spain, 32Hospital Universitario Virgen del Rocío, Sevilla, Spain, 33Complejo Hospitalario de Zamora, Zamora, Spain, 34Hospital Universitario y Politécnico La Fe, Valencia, Spain, 35Hospital Regional de Málaga, Málaga. Spain., Malaga, Spain, 36Hospital Universitario Severo Ochoa, Madrid, Spain, 37Hospital General Universitario de Elche, Elche, Spain, 38Hospital Universitario Son Llàtzer, Palma de Mallorca, Spain, 39Hospital de Cabueñes, Gijón, Spain, 40Hospital Arnau de Vilanova, Lleida. Spain., Lleida, Spain, 41Hospital San Agustín, Aviles, Spain, 42Hospital Universitario de Valme, Sevilla, Spain, 43Consorci Hospital General Universitari de Valencia, Valencia, Spain, 44Hospital Universitario Doctor Negrín, Gran Canaria, Spain, 45Hospital Universitario de Castellón, Castellón, Spain, 46Complejo Hospitalario Universitario de Ourense, Ourense, Spain, 47Research group on Genetic Epidemiology and Atherosclerosis in Systemic Diseases and in Metabolic Bone Diseases of the Musculoskeletal System, IDIVAL, Division of Rheumatology, Hospital Universitario Marqués de Valdecilla; School of Medicine, Universidad de Cantabria, Santander, Spain. Cardiovascular Pathophysiology and Genomics Research Unit, School of Physiology, Faculty of Health Sciences, University of the Witwatersrand, Johannesburg, South Africa, 48Hospital Universitario Marqués de Valdecilla, IDIVAL, Santander, Spain

    Background/Purpose: Giant cell arteritis (GCA) may be divided into cranial, and extracranial GCA phenotypes. Tocilizumab (TCZ) has shown efficacy and safety in GCA.Our aim was…
  • Abstract Number: 1865 • ACR Convergence 2021

    Incidence, Prevalence, and Mortality of Chronic Periaortitis: A Population-based Study

    Umar Ghaffar1, Kenneth Warrington2, Stephanie Duong1, Cynthia Crowson3, Michelle Burke1, Boyd Viers1, Aaron Potretzke1, Haraldur Bjarnason1 and Matthew Koster1, 1Mayo Clinic, Rochester, MN, 2Mayo Clinic, Rochester, Minnesota, 3Mayo Clinic, Eyota, MN

    Background/Purpose: Chronic periaortitis is an inflammatory condition that typically involves the infrarenal portion of the abdominal aorta. To date, no epidemiologic studies have been performed…
  • Abstract Number: 0502 • ACR Convergence 2021

    Global Transcriptomic Profiling Identifies Differential Gene Expression Signatures Between Inflammatory and Non-inflammatory Aortic Aneurysms

    Benjamin Hur1, Matthew Koster1, Jin Sung Jang1, Kenneth Warrington2 and Jaeyun Sung1, 1Mayo Clinic, Rochester, MN, 2Mayo Clinic, Rochester, Minnesota

    Background/Purpose: Non-infectious aortitis may be a manifestation of systemic large vessel vasculitis such as giant cell arteritis (GCA) or may be a form of single…
  • Abstract Number: 1406 • ACR Convergence 2021

    Incidence and General Clinical Features of Giant Cell Arteritis in the ARTESER Multicenter Study

    Jesús T. Sánchez-Costa1, Rafael B. Melero-González2, Elisa Fernández-Fernández3, María T. Silva-Diaz4, Joaquín M. Belzunegui5, Clara Moriano6, Julio Sánchez7, Judit Lluch8, Itziar Calvo9, Vicente Aldasoro10, Lydia Abasolo11, Javier Loricera12, Alberto Ruíz-Román13, Santos Castañeda14, Patricia Moya15, María J. Garcia-Villanueva16, Vanessa A. Navarro-Angeles17, Carles Galisteo18, Anne Riveros-Frutos19, Jose A. Román-Ivorra20, Selene Labrada-Arrabal21, Margarida Vasques-Rocha22, Carlota L. Iñiguez-Ubiaga23, María García-González24, Clara Molina-Almela25, María Alcalde-Villar26, Antonio Juan Mas27, Eugenio De Miguel28, Javier Narvaez29, Miguel Ángel gonzalez-Gay30, Noemí Garrido-Puñal13, Paula V. Estrada-Alarcon17 and Ricardo Blanco31, 1Research unit, Spanish Society of Rheumatology, Madrid, Spain, 2Complejo Hospitalario Universitario de Vigo, Vigo, Spain, 3Rheumatology department, La Paz University Hospital, Madrid, Spain, 4Complejo Hospitalario Universitario de La Coruña, Coruña, Spain, 5Hospital Universitario Donostia, Donostia-San Sebasti, Spain, 6Hospital Universitario de León, León, Spain, 7Hospital Universitario 12 de Octubre, Madrid, Spain, 8Hospital Universitari Bellvitge, Hospitalet de Llobregat, Spain, 9Basurto University Hospital, Bilbao, Spain, 10Complejo Hospitalario de Navarra, Pamplona, Spain, 11Rheumatology Department, Hospital Clínico San Carlos, Madrid, Spain, 12Hospital Universitario Marqués de Valdecilla, Santander, Spain, 13Hospital Universitario Virgen del Rocío, Sevilla, Spain, 14Hospital Universitario de la Princesa, Madrid, Spain, 15Hospital Sant Pau, Barcelona, Spain, 16Rheumatology Department, Hospital Universitario Ramón y Cajal, Madrid, Spain, 17Hospital de Sant Joan Despí Moisès Broggi. Sant Joan Despí, Barcelona, Spain, 18Hospital Universitari Parc Tauli, Saadell, Spain, 19Hospital Germans Trias i Pujol, Badalona, Spain, 20Hospital Universitari i Politècnic La Fe, Valencia, Spain, 21Hospital del Mar, Barcelona, Spain, 22Hospital Universitario Araba, Vitoria-Gasteiz, Spain, 23Hospital Universitario Lucus Augusti, Lugo, Spain, 24Hospital Universitario de Canarias, La Laguna, Spain, 25Rheumatology Department, Consorci Hospital General Universitari de Valencia, Valencia, Spain, 26Hospital Universitario Severo Ochoa, Leganés, Spain, 27Rheumatology Department, Hospital Universitario Son Llàtzer, Palma de Mallorca, Spain, 28Hospital Universitario La Paz, Madrid, Spain, 29Division of Rheumatology, Hospital Universitario de Bellvitge, Barcelona, Spain, 30Research group on Genetic Epidemiology and Atherosclerosis in Systemic Diseases and in Metabolic Bone Diseases of the Musculoskeletal System, IDIVAL, Division of Rheumatology, Hospital Universitario Marqués de Valdecilla; School of Medicine, Universidad de Cantabria, Santander, Spain. Cardiovascular Pathophysiology and Genomics Research Unit, School of Physiology, Faculty of Health Sciences, University of the Witwatersrand, Johannesburg, South Africa, 31Hospital Universitario Marqués de Valdecilla, IDIVAL, Santander, Spain

    Background/Purpose: Epidemiological information on Giant Cell Arteritis (GCA) comes mainly from the Scandinavian countries of northern Europe, which show a higher incidence than the countries…
  • Abstract Number: 1866 • ACR Convergence 2021

    Vasculitis in Patients with Sarcoidosis: A Single-Institution Case Series of 17 Patients

    Bradly Kimbrough1, Kenneth Warrington2, Hannah Langenfeld3, Cynthia Crowson4, Eva Carmona3, Andrew Virata3 and Matthew Koster3, 1Mayo Clinic Rochester, Rochester, MN, 2Mayo Clinic, Rochester, Minnesota, 3Mayo Clinic, Rochester, MN, 4Mayo Clinic, Eyota, MN

    Background/Purpose: Vasculitis in patients with sarcoidosis is rare and can affect blood vessels of any size. Limited information describing this association is available. The purpose…
  • Abstract Number: 0504 • ACR Convergence 2021

    Longitudinal Patterns of Vascular Inflammation in Large-vessel Vasculitis

    Hugh Alessi1, Kaitlin Quinn2, Mark A. Ahlman3, Yiming Luo3, Elaine Novakovich3 and Peter Grayson4, 1National Institutes of Health, Bethesda, Maryland, 2National Institute of Arthritis and Musculoskeletal and Skin Diseases (NIAMS), National Institutes of Health (NIH), Washington, DC, 3National Institutes of Health, Bethesda, MD, 4National Institutes of Arthritis and Musculoskeletal and Skin Diseases (NIAMS), National Institutes of Health (NIH), Bethesda, MD

    Background/Purpose: The two main forms of large vessel vasculitis (LVV), giant cell arteritis (GCA) and Takayasu’s arteritis (TAK), are clinically heterogenous diseases with variable disease…
  • Abstract Number: 1408 • ACR Convergence 2021

    Treatment of Giant Cell Arteritis in the ARTESER Multicenter Study of 1675 Patients

    Jesús T. Sánchez-Costa1, Iñigo Hernández-Rodríguez2, Elisa Fernández-Fernández3, María T. Silva-Diaz4, Jesús A. Valero-Jaimes5, Ismael González-Fernández6, Julio Sánchez7, Judit Lluch8, Eva Galindez-Agirregoikoa9, Javier Mendizábal-Mateos10, Pia M. Lois Bermejo11, Javier Loricera12, Alejandro Muñoz13, Cristina Valero-Martínez14, Patricia Moya15, Carmen Larena-Grijalba16, Vanessa A. Navarro-Angeles17, Joan Calvet-Fontova18, Ivette Casafont19, Francisco Ortiz-Sanjuán20, Selene Labrada-Arrabal21, Jaime Calvo-Alén22, Carlota L. Iñiguez-Ubiaga23, Vanesa Hernández24, Cristina Campos-Fernández25, María Alcalde-Villar26, Antonio Juan-Mas27, Eugenio De Miguel28, Javier Narvaez29, Miguel Ángel gonzalez-Gay30, Noemí Garrido-Puñal31, Paula V. Estrada-Alarcon17 and Ricardo Blanco32, 1Spanish Society of Rheumatology, Madrid, Spain, 2Complejo Hospitalario Universitario de Vigo, Vigo, Spain, 3Rheumatology department, La Paz University Hospital, Madrid, Spain, 4Complejo Hospitalario Universitario de La Coruña, Coruña, Spain, 5Hospital Universitario Donostia, Donostia-San Sebasti, Spain, 6Hospital Universitario de León, León, Spain, 7Hospital Universitario 12 de Octubre, Madrid, Spain, 8Hospital Universitari Bellvitge, Hospitalet de Llobregat, Spain, 9Hospital Universitario de Basurto, Bilbao, Spain, 10H. Navarra, Navarra, Spain, 11Rheumatology Department, Hospital Clínico San Carlos, Madrid, Spain, 12Hospital Universitario Marqués de Valdecilla, Santander, Spain, 13Hospital Universitario Virgen del Rocío, Sevial, Spain, 14Hospital Universitario de La Princesa, Madrid, Spain, 15Hospital Sant Pau, Barcelona, Spain, 16Rheumatology Department, Hospital Universitario Ramón y Cajal, Madrid, Spain, 17Hospital de Sant Joan Despí Moisès Broggi. Sant Joan Despí, Barcelona, Spain, 18Hospital Universitari Parc Tauli, Sabadell, Spain, 19Hospital Universitari Germans Trias i Pujol, Barcelona, Badalona, Spain, 20H. La Fe, Valencia, Spain, 21Hospital del Mar, Barcelona, Spain, 22Rheumatology Department, Hospital Universitario Araba, Vitoria-Gasteiz, Spain, 23Hospital Universitario Lucus Augusti, Lugo, Spain, 24Rheumatology Department, Hospital Universitario de Canarias, La Laguna, Spain, 25Consorci Hospital General Universitari de Valencia, Valencia, Spain, 26Hospital Universitario Severo Ochoa, Leganés, Spain, 27Hospital Universitario Son Llàtzer, Palma de Mallorca, Spain, 28Hospital Universitario La Paz, Madrid, Spain, 29Division of Rheumatology, Hospital Universitario de Bellvitge, Barcelona, Spain, 30Research group on Genetic Epidemiology and Atherosclerosis in Systemic Diseases and in Metabolic Bone Diseases of the Musculoskeletal System, IDIVAL, Division of Rheumatology, Hospital Universitario Marqués de Valdecilla; School of Medicine, Universidad de Cantabria, Santander, Spain. Cardiovascular Pathophysiology and Genomics Research Unit, School of Physiology, Faculty of Health Sciences, University of the Witwatersrand, Johannesburg, South Africa, 31Hospital Universitario Virgen del Rocío, Sevilla, Spain, 32Hospital Universitario Marqués de Valdecilla, IDIVAL, Santander, Spain

    Background/Purpose: Glucocorticoids (GC) are the mainstay therapy in Giant Cell Arteritis (GCA), initially at high doses (40-60 mg/day) followed by gradual glucocorticoid tapering. This treatment,…
  • Abstract Number: 1867 • ACR Convergence 2021

    Investigating Adenosine Deaminase 2 Activity in Large Vessel Vasculitis

    Andrew Porter1, Robert Maughan1, Charis Pericleous1, Allan Kiprianos1, Hyuk Jee2, Pui Lee2, Taryn Youngstein1 and Justin Mason1, 1Imperial College London, London, United Kingdom, 2Boston Children's Hospital, Newton, MA

    Background/Purpose: Deficiency of adenosine deaminase 2 (DADA2) leads to a broad phenotype that in some resembles polyarteritis nodosa with fever and rash, but in others…
  • Abstract Number: 0525 • ACR Convergence 2021

    STEAP3, FZD2 and EGFLAM Are Novel Genetic Risk Loci for Granulomatosis with Polyangitis: A Genome Wide Association Study from UK Biobank

    Mehmet Hocaoglu1, Jamal Mikdashi2, Yi-Ju Chen2, James Perry2 and Charles Hong2, 1University of Maryland Medical Center, Midtown Campus, Baltimore, MD, 2University of Maryland School of Medicine, Baltimore, MD

    Background/Purpose: Granulomatosis with Polyangitis (GPA) is a systemic ANCA associated small vessel vasculitis. Prior genetic studies demonstrated a strong association of HLA Class II region…
  • Abstract Number: 1409 • ACR Convergence 2021

    Clinical Features at Disease Onset of Different Subsets of Large-vessel-giant Cell Arteritis in a Monocentric Cohort of 100 Patients

    Francesca Regola1, Giovanni Bosio2, Laura Andreoli3, Franco Franceschini1 and Paola Toniati1, 1Rheumatology and Clinical Immunology Unit, ASST Spedali Civili and University of Brescia, Brescia, Italy, 2Nuclear Medicine Unit, ASST Spedali Civili of Brescia, Brescia, Italy, 3University of Brescia, Brescia, Italy

    Background/Purpose: Giant Cell Arteritis (GCA) is the most frequent systemic vasculitis in patients older than 50 years involving medium-sized and large arteries. Inflammation of the…
  • Abstract Number: 1872 • ACR Convergence 2021

    Differentiating Primary Central Nervous System Vasculitis from Non-inflammatory Intracranial Vasculopathy

    Moein Amin1, Takashi Shimoyama2, Ken Uchino1, Leonard Calabrese1 and Rula Hajj-Ali3, 1Cleveland Clinic, Cleveland, OH, 2Nippon Medical School, Tokyo, Japan, 3Cleveland Clinic, Hunting Valley, OH

    Background/Purpose: Establishing the diagnosis of Primary central nervous system vasculitis CNSV is challenging. In this study we aimed to investigate distinguishing primary CNSV compared to…
  • Abstract Number: 0622 • ACR Convergence 2021

    Ethnic Disparities in Giant-Cell Arteritis: A Clinical Comparison Among Caucasian and Hispanic Patients in the Inland Empire of Southern California

    Kathleena D'Anna and Mehrnaz Hojjati, Loma Linda University Health, Loma Linda, CA

    Background/Purpose: Giant-Cell Arteritis (GCA) is the most common systemic vasculitis among North Americans, historically described in Caucasian populations, with limited clinical data in other ethnic…
  • Abstract Number: 1410 • ACR Convergence 2021

    Predictors of Relapse in Giant-Cell Arteritis: A Retrospective Single Center Analysis

    Kathleena D'Anna1, David Lim2, Lorena Salto1 and Mehrnaz Hojjati1, 1Loma Linda University Health, Loma Linda, CA, 2Loma Linda University Health, Redlands, CA

    Background/Purpose: Giant Cell Arteritis (GCA) is the most common systemic vasculitis in North America, typically affecting Caucasian female adults over 50 years of age. Flares…
  • Abstract Number: 1874 • ACR Convergence 2021

    Using 18F-fluorodeoxyglucose Positron Emission Tomography to Standardize Clinical Trial Recruitment in Takayasu’s Arteritis

    Kaitlin Quinn1, Hugh Alessi2, Emily Rose3, Mark A. Ahlman4, Christopher Redmond4, Yiming Luo4, Ertugrul Cagri bolek5, Carol Langford6, Cristina Ponte7, Peter Merkel8 and Peter Grayson9, 1National Institute of Arthritis and Musculoskeletal and Skin Diseases (NIAMS), National Institutes of Health (NIH), Washington, DC, 2National Institutes of Health, Bethesda, Maryland, 3Case Western, Cleveland Heights, OH, 4National Institutes of Health, Bethesda, MD, 5Vasculitis Translational Research Program, NIAMS, NIH, US, Lanham, MD, 6Cleveland Clinic, Moreland Hills, OH, 7Hospital de Santa Maria, Lisbon, Portugal, 8University of Pennsylvania, Philadelphia, PA, 9National Institutes of Arthritis and Musculoskeletal and Skin Diseases (NIAMS), National Institutes of Health (NIH), Bethesda, MD

    Background/Purpose: Disease activity assessment can be challenging in Takayasu’s arteritis (TAK), which can lead to difficulty in determining eligibility for enrollment into randomized clinical trials…
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All abstracts accepted to ACR Convergence are under media embargo once the ACR has notified presenters of their abstract’s acceptance. They may be presented at other meetings or published as manuscripts after this time but should not be discussed in non-scholarly venues or outlets. The following embargo policies are strictly enforced by the ACR.

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