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Abstracts tagged "Vasculitis"

  • Abstract Number: 0420 • ACR Convergence 2021

    Development and Validation of a Simulation Model for Maintenance Treatment in ANCA-Associated Vasculitis

    Zachary Wallace1, John Stone2, Hyon K. Choi3 and Emily Hyle4, 1Massachusetts General Hospital, Newton, MA, 2Massachusetts General Hospital Rheumatology Unit, Harvard Medical School, Boston, MA, 3Massachusetts General Hospital, Lexington, MA, 4Infectious Diseases, Department of Medicine, Massachusetts General Hospital, Boston, MA

    Background/Purpose: ANCA-associated vasculitis (AAV) care has evolved over the last two decades with several approaches to remission maintenance. However, these approaches have trade-offs regarding the…
  • Abstract Number: 1396 • ACR Convergence 2021

    Baricitinib in Relapsing Giant Cell Arteritis: A Prospective Open-Label Single-Institution Study

    Matthew Koster1, Cynthia Crowson2, Rachel Giblon1, Ali Duarte-Garcia1, Jane Jaquith1, Cornelia M. Weyand1 and Kenneth Warrington3, 1Mayo Clinic, Rochester, MN, 2Mayo Clinic, Eyota, MN, 3Mayo Clinic, Rochester, Minnesota

    Background/Purpose: Pre-clinical giant cell arteritis (GCA) mouse models have demonstrated effective suppression of arterial wall lesional T-cells through inhibition of Janus kinase 3 (JAK3) and…
  • Abstract Number: 1720 • ACR Convergence 2021

    Cervical Dysplasia and HPV Infection in Women with Vasculitis

    Taylor Koenig1, Ambra Burrell2, Hilary Kleppel3, Ashlee Weaver4, Veronica Mruk5, Lynn Fussner1, Salem Almaani6 and Alexa Meara1, 1Ohio State University Wexner Medical Center, Columbus, OH, 2Division of Rheumatology, The Ohio State University Wexner Medical Center, Columbus, OH, 3Wright State University, Blacklick, OH, 4Ohio State University College of Medicine, Columbus, OH, 5Ohio State University / Nationwide Children's Hospital, Columbus, OH, 6Ohio State University Medical Center, Columbus, OH

    Background/Purpose: The most common cause of cervical cancer is persistent human papillomavirus (HPV) infection in the cervical epithelium, causing precancerous cervical dysplasia and ultimately cervical…
  • Abstract Number: 0425 • ACR Convergence 2021

    Diagnostic Accuracy of Muscle MRI for Muscular Vasculitis in Anti-neutrophil Cytoplasmic Antibody-associated Vasculitis: A Pilot Study

    Ryuta Inaba, Daisuke Waki, Keisuke Nishimura, Tomohiro Yoshida, Kaoru Mizukawa, Shintaro Yamamoto, Osamu Iri, Kohei Yo and Hiroyuki Murabe, Department of Endocrinology and Rheumatology, Kurashiki Central Hospital, Kurashiki, Japan

    Background/Purpose: Histopathologic confirmation is the golden standard for diagnosis of anti-neutrophil cytoplasmic antibody-associated vasculitis (AAV), but sometimes can be difficult because of its invasion (e.g.…
  • Abstract Number: 1397 • ACR Convergence 2021

    Treatment of Giant Cell Arteritis with Tocilizumab: A Retrospective Cohort Study of 119 Patients

    jigisha rakholiya1, Matthew Koster1, Hannah Langenfeld1, Cynthia Crowson2, Andy Abril3, Pankaj Bansal4, Lester Mertz5, Alicia Rodriguez Pla6, Rahul Sehgal4, Benjamin Wang7 and Kenneth Warrington8, 1Mayo Clinic, Rochester, MN, 2Mayo Clinic, Eyota, MN, 3Mayo Clinic, Ponte Vedra Beach, FL, 4Mayo Clinic, Eau Claire, WI, 5Mayo Clinic Arizona, Scottsdale, AZ, 6Mayo Clinic in Arizona, Scottsdale, AZ, 7Mayo Clinic, Jacksonville, FL, 8Mayo Clinic, Rochester, Minnesota

    Background/Purpose: Giant cell arteritis (GCA) is an inflammatory condition of medium- and large-sized arteries. Prospective clinical trials have demonstrated the efficacy of tocilizumab (TCZ) for…
  • Abstract Number: 1728 • ACR Convergence 2021

    Takayasu’s Arteritis and Pregnancy: A Meta-analysis

    Aine Gorman1, Leah Rooney2, Matthew Turk1, Louise Moore3, Jared Bierbrier4, Celine O'Brien5, Anne Clohessy6, Eamonn Molloy7, Lorraine O Neill8, Fionnuala McAuliffe9 and Douglas Veale10, 1St Vincents Hospital, Dublin, Ireland, 2St Vincent's University Hospital, Dublin, Ireland, 3Our Lady's Hospice and Care Services, Harold's Cross, Dublin 6W, Kinnegad, Ireland, 4McMaster University, Hamilton, ON, Canada, 5Perinatal Research Centre, Obstetrics and Gynaecology, School of Medicine, University College Dublin and National Maternity Hospital, Dublin, Dublin, Ireland, 6National Maternity Hopistal, Dublin, Ireland, 7St Vincent's Healthcare Group, Dublin, Ireland, 8St. Vincent's Hospital, Dublin, Ireland, 9National Maternity Hopsital Dublin, Dublin, Ireland, 10University College Dublin, Dublin, Ireland

    Background/Purpose: Takayasu’s arteritis is a systemic autoimmune disease characterised by large vessel vasculitis. It usually affects women of childbearing age, with 90% of patients diagnosed…
  • Abstract Number: 0431 • ACR Convergence 2021

    Clinical Characteristics and Outcomes of ANCA-Associated and Non Immune-Mediated Hypertrophic Pachymeningitis: A Comparative Study

    Eduardo Martin-Nares, Lilian Guadalupe Cano Cruz and Andrea Hinojosa-Azaola, Department of Immunology and Rheumatology, Instituto Nacional de Ciencias Médicas y Nutrición Salvador Zubirán, Mexico City, Mexico

    Background/Purpose: Hypertrophic pachymeningitis (HP) is an infrequent manifestation in autoimmune and non-autoimmune conditions. The differences in clinical characteristics and outcomes of ANCA-associated and non-immune-mediated HP…
  • Abstract Number: 1403 • ACR Convergence 2021

    Giant Cell Arteritis Subtypes: Data from the ARTESER Registry

    Eugenio De Miguel1, Jesús T. Sánchez-Costa2, Javier Narvaez3, Miguel Ángel gonzalez-Gay4, Noemí Garrido-Puñal5, Paula V. Estrada-Alarcon6, Rafael B. Melero-González7, Elisa Fernández-Fernández8, María T. Silva-Diaz9, Joaquín M. Belzunegui10, Clara Moriano11, Julio Sánchez12, Judit Lluch13, Itziar Calvo14, Vicente Aldasoro15, Leticia León-Mateos16, Javier Loricera García17, Alberto Ruíz-Román5, Cristina Valero-Martínez18, Patricia Moya19, Marina Tortosa-Cabañas20, Vanessa A. Navarro-Angeles6, Carles Galisteo21, Anne Riveros-Frutos22, Jose A. Román-Ivorra23, Selene Labrada-Arrabal24, Margarida Vasques-Rocha25, Carlota L. Iñiguez-Ubiaga26, María García-González27 and Ricardo Blanco28, 1Hospital Universitario La Paz, Madrid, Spain, 2Spanish Society of Rheumatology, Madrid, Spain, 3Division of Rheumatology, Hospital Universitario de Bellvitge, Barcelona, Spain, 4Research group on Genetic Epidemiology and Atherosclerosis in Systemic Diseases and in Metabolic Bone Diseases of the Musculoskeletal System, IDIVAL, Division of Rheumatology, Hospital Universitario Marqués de Valdecilla; School of Medicine, Universidad de Cantabria, Santander, Spain. Cardiovascular Pathophysiology and Genomics Research Unit, School of Physiology, Faculty of Health Sciences, University of the Witwatersrand, Johannesburg, South Africa, 5Hospital Universitario Virgen del Rocío, Sevilla, Spain, 6Hospital de Sant Joan Despí Moisès Broggi. Sant Joan Despí, Barcelona, Spain, 7Complejo Hospitalario Universitario de Vigo, Vigo, Spain, 8Rheumatology department, La Paz University Hospital, Madrid, Spain, 9Complejo Hospitalario Universitario de La Coruña, Coruña, Spain, 10Hospital Universitario Donostia, Donostia-San Sebasti, Spain, 11Hospital Universitario de León, León, Spain, 12Hospital Universitario 12 de Octubre, Madrid, Spain, 13Hospital Universitari Bellvitge, Hospitalet de Llobregat, Spain, 14Basurto University Hospital, Bilbao, Spain, 15Complejo Hospitalario de Navarra, Pamplona, Spain, 16Hospital Clínico San Carlos. Madrid. Spain, Madrid, Spain, 17Hospital Universitario Marqués de Valdecilla, Santander, Spain, 18Hospital Universitario de La Princesa, Madrid, Spain, 19Hospital Sant Pau, Barcelona, Spain, 20Hospital Universitario Ramón y Cajal, Madrid, Spain, 21Hospital Universitari Parc Tauli, Saadell, Spain, 22Hospital Germans Trias i Pujol, Badalona, Spain, 23Hospital Universitari i Politècnic La Fe, Valencia, Spain, 24Hospital del Mar, Barcelona, Spain, 25Hospital Universitario Araba, Vitoria-Gasteiz, Spain, 26Hospital Universitario Lucus Augusti, Lugo, Spain, 27Hospital Universitario de Canarias, La Laguna, Spain, 28Hospital Universitario Marqués de Valdecilla, IDIVAL, Santander, Spain

    Background/Purpose: Giant cell arteritis (GCA) is the most common systemic vasculitis over 50 years of age. Classically, GCA was assimilated with the involvement of the…
  • Abstract Number: 1862 • ACR Convergence 2021

    Clonal Hematopoiesis Across the Age Spectrum in Patients with Systemic Vasculitis

    Kristina Wells1, Fernanda Gutierrez-Rodrigues2, Bhavisha Patel2, Kaitlin Quinn3, Keith Sikora1, Neal Young4 and Peter Grayson5, 1National Institute of Arthritis, Musculoskeletal and Skin Diseases (NIAMS), National Institutes of Health (NIH), Bethesda, MD, 2National Heart, Lung, and Blood Institute (NHLBI), National Institutes of Health (NIH), Bethesda, MD, 3National Institute of Arthritis and Musculoskeletal and Skin Diseases (NIAMS), National Institutes of Health (NIH), Washington, DC, 4National Heart, Lung, and Blood Institute (NHLBI), National Institues of Health, Bethesda, MD, 5National Institutes of Arthritis and Musculoskeletal and Skin Diseases (NIAMS), National Institutes of Health (NIH), Bethesda, MD

    Background/Purpose: Clonal hematopoiesis (CH) is a pre-malignant state characterized by somatic mutations in hematologic precursor cells in genes associated with myeloid malignancies. Incidence of CH…
  • Abstract Number: 0432 • ACR Convergence 2021

    Anti-IL5 Therapy in Eosinophilic Granulomatosis with Polyangiitis (EGPA): A Longitudinal Follow-up Study ≥ 24months

    Allyson Egan1, Pasupathy Sivasothy2, Lisa Willcocks2, Rachel Jones2, Marcos Martinez Del Pero3 and David R.W. Jayne4, 1Vasculitis and Lupus Centre, Cambridge University Hospital, University of Cambridge, London, United Kingdom, 2Vasculitis and Lupus Centre, Department of Medicine, Cambridge University Hospital, Cambridge, United Kingdom, 3Vasculitis and Lupus Centre, Cambridge University Hospital, Cambridge, United Kingdom, 4University of Cambridge, Cambridge, United Kingdom

    Background/Purpose: In the randomized, placebo-controlled MIRRA trial for relapsing and refractory eosinophilic granulomatosis with polyangiitis (EGPA), adjuvant therapy with 300mg anti-IL5 mAB Mepolizumab [MEPO] for…
  • Abstract Number: 1405 • ACR Convergence 2021

    Effectiveness of Tocilizumab in Cranial and Extracranial Phenotypes of Giant Cell Arteritis: Multicenter Study of 471 Cases

    Lara Sánchez-Bilbao1, Javier Loricera1, Santos Castañeda2, Clara Moriano3, Javier Narvaez4, Vicente Aldasoro5, Olga Maíz6, Rafael Melero7, Juan Ignacio Villa8, Paloma Vela9, Susana Romero-Yuste10, José Luis Callejas11, Eugenio De Miguel12, Eva Galindez-Agirregoikoa13, Francisca Sivera14, Jesús Carlos Fernández-López15, Carles Galisteo16, Iván Ferraz-Amaro17, Juan Carlos Nieto18, Juan Ramón de Dios19, Julio Sánchez20, Esther Fernández21, Isabel de la Morena22, Patricia Moya23, Roser Solans-Laqué24, Jose Luis Andreu25, Marcelino Revenga26, Eztizen Labrador27, Andrea García-Valle28, Adela Gallego29, Carlota Iñíguez30, Cristina Hidalgo31, Noemí Garrido-Puñal32, Ruth López-González33, José Andrés Román-Ivorra34, Sara Manrique Arija35, Paz Collado36, Enrique Raya11, Francisco Navarro37, Antoni Juan Mas38, Carmen Ordas39, Maria Dolors Boquet40, Noelia Álvarez-Rivas41, Maria Luisa Velloso-Feijoo42, Cristina Campos-Fernández43, Íñigo Rúa-Figueroa44, Arantxa Conesa45, Eva Salgado46, Miguel Ángel gonzalez-Gay47 and Ricardo Blanco48, 1Hospital Universitario Marqués de Valdecilla, Santander, Spain, 2Hospital Universitario de la Princesa, Madrid, Spain, 3Hospital Universitario de León, León, Spain, 4Division of Rheumatology, Hospital Universitario de Bellvitge, Barcelona, Spain, 5Complejo Hospitalario de Navarra, Pamplona, Spain, 6Hospital Universitario de Donostia, San Sebastián, Spain, 7Complexo Hospitalario Universitario de Vigo, Vigo, Galicia, Spain, 8Hospital Sierrallana, Torrelavega, Spain, 9Hospital General Universitario de Alicante, Alicante, Spain, 10Complejo Hospitalario Universitario de Pontevedra, Pontevedra, Spain, 11Hospital San Cecilio, Granada, Spain, 12Hospital Universitario La Paz, Madrid, Spain, 13Hospital Universitario de Basurto, Bilbao, Spain, 14Hospital Universitario de Elda, Alicante, Spain, 15Hospital Universitario Juan Canalejo, A Coruña, Spain, 16Hospital Universitari Parc Tauli, Saadell, Spain, 17Hospital Universitario de Canarias, Santa Cruz de Tenerife, Spain, 18Hospital General Universitario Gregorio Marañón, Madrid, Spain, 19Hospital Universitario de Araba, Mondragón, Spain, 20Hospital Universitario 12 de Octubre, Madrid, Spain, 21Hospital Clínico Universitario Virgen de la Arrixaca, Murcia, Spain, 22Hospital Clínico Universitario de Valencia, Valencia, Spain, 23Hospital Sant Pau, Barcelona, Spain, 24Hospital Vall d'Hebron, Barcelona, Spain, 25Hospital Universitario Puerta de Hierro, Madrid, Spain, 26Hospital Universitario Ramón y Cajal, Madrid, Spain, 27Hospital San Pedro, Logroño, La Rioja, Spain, 28Complejo Asistencial Universitario de Palencia, Palencia. Spain, Palencia, Spain, 29Complejo Hospitalario Universitario de Badajoz, Badajoz, Spain, 30Hospital Universitario Lucus Augusti, Lugo, Galicia, Spain, 31Hospital Universitario Salamanca, Salamanca, Spain, 32Hospital Universitario Virgen del Rocío, Sevilla, Spain, 33Complejo Hospitalario de Zamora, Zamora, Spain, 34Hospital Universitario y Politécnico La Fe, Valencia, Spain, 35Hospital Regional de Málaga, Málaga. Spain., Malaga, Spain, 36Hospital Universitario Severo Ochoa, Madrid, Spain, 37Hospital General Universitario de Elche, Elche, Spain, 38Hospital Universitario Son Llàtzer, Palma de Mallorca, Spain, 39Hospital de Cabueñes, Gijón, Spain, 40Hospital Arnau de Vilanova, Lleida. Spain., Lleida, Spain, 41Hospital San Agustín, Aviles, Spain, 42Hospital Universitario de Valme, Sevilla, Spain, 43Consorci Hospital General Universitari de Valencia, Valencia, Spain, 44Hospital Universitario Doctor Negrín, Gran Canaria, Spain, 45Hospital Universitario de Castellón, Castellón, Spain, 46Complejo Hospitalario Universitario de Ourense, Ourense, Spain, 47Research group on Genetic Epidemiology and Atherosclerosis in Systemic Diseases and in Metabolic Bone Diseases of the Musculoskeletal System, IDIVAL, Division of Rheumatology, Hospital Universitario Marqués de Valdecilla; School of Medicine, Universidad de Cantabria, Santander, Spain. Cardiovascular Pathophysiology and Genomics Research Unit, School of Physiology, Faculty of Health Sciences, University of the Witwatersrand, Johannesburg, South Africa, 48Hospital Universitario Marqués de Valdecilla, IDIVAL, Santander, Spain

    Background/Purpose: Giant cell arteritis (GCA) may be divided into cranial, and extracranial GCA phenotypes. Tocilizumab (TCZ) has shown efficacy and safety in GCA.Our aim was…
  • Abstract Number: 1865 • ACR Convergence 2021

    Incidence, Prevalence, and Mortality of Chronic Periaortitis: A Population-based Study

    Umar Ghaffar1, Kenneth Warrington2, Stephanie Duong1, Cynthia Crowson3, Michelle Burke1, Boyd Viers1, Aaron Potretzke1, Haraldur Bjarnason1 and Matthew Koster1, 1Mayo Clinic, Rochester, MN, 2Mayo Clinic, Rochester, Minnesota, 3Mayo Clinic, Eyota, MN

    Background/Purpose: Chronic periaortitis is an inflammatory condition that typically involves the infrarenal portion of the abdominal aorta. To date, no epidemiologic studies have been performed…
  • Abstract Number: 0502 • ACR Convergence 2021

    Global Transcriptomic Profiling Identifies Differential Gene Expression Signatures Between Inflammatory and Non-inflammatory Aortic Aneurysms

    Benjamin Hur1, Matthew Koster1, Jin Sung Jang1, Kenneth Warrington2 and Jaeyun Sung1, 1Mayo Clinic, Rochester, MN, 2Mayo Clinic, Rochester, Minnesota

    Background/Purpose: Non-infectious aortitis may be a manifestation of systemic large vessel vasculitis such as giant cell arteritis (GCA) or may be a form of single…
  • Abstract Number: 1406 • ACR Convergence 2021

    Incidence and General Clinical Features of Giant Cell Arteritis in the ARTESER Multicenter Study

    Jesús T. Sánchez-Costa1, Rafael B. Melero-González2, Elisa Fernández-Fernández3, María T. Silva-Diaz4, Joaquín M. Belzunegui5, Clara Moriano6, Julio Sánchez7, Judit Lluch8, Itziar Calvo9, Vicente Aldasoro10, Lydia Abasolo11, Javier Loricera12, Alberto Ruíz-Román13, Santos Castañeda14, Patricia Moya15, María J. Garcia-Villanueva16, Vanessa A. Navarro-Angeles17, Carles Galisteo18, Anne Riveros-Frutos19, Jose A. Román-Ivorra20, Selene Labrada-Arrabal21, Margarida Vasques-Rocha22, Carlota L. Iñiguez-Ubiaga23, María García-González24, Clara Molina-Almela25, María Alcalde-Villar26, Antonio Juan Mas27, Eugenio De Miguel28, Javier Narvaez29, Miguel Ángel gonzalez-Gay30, Noemí Garrido-Puñal13, Paula V. Estrada-Alarcon17 and Ricardo Blanco31, 1Research unit, Spanish Society of Rheumatology, Madrid, Spain, 2Complejo Hospitalario Universitario de Vigo, Vigo, Spain, 3Rheumatology department, La Paz University Hospital, Madrid, Spain, 4Complejo Hospitalario Universitario de La Coruña, Coruña, Spain, 5Hospital Universitario Donostia, Donostia-San Sebasti, Spain, 6Hospital Universitario de León, León, Spain, 7Hospital Universitario 12 de Octubre, Madrid, Spain, 8Hospital Universitari Bellvitge, Hospitalet de Llobregat, Spain, 9Basurto University Hospital, Bilbao, Spain, 10Complejo Hospitalario de Navarra, Pamplona, Spain, 11Rheumatology Department, Hospital Clínico San Carlos, Madrid, Spain, 12Hospital Universitario Marqués de Valdecilla, Santander, Spain, 13Hospital Universitario Virgen del Rocío, Sevilla, Spain, 14Hospital Universitario de la Princesa, Madrid, Spain, 15Hospital Sant Pau, Barcelona, Spain, 16Rheumatology Department, Hospital Universitario Ramón y Cajal, Madrid, Spain, 17Hospital de Sant Joan Despí Moisès Broggi. Sant Joan Despí, Barcelona, Spain, 18Hospital Universitari Parc Tauli, Saadell, Spain, 19Hospital Germans Trias i Pujol, Badalona, Spain, 20Hospital Universitari i Politècnic La Fe, Valencia, Spain, 21Hospital del Mar, Barcelona, Spain, 22Hospital Universitario Araba, Vitoria-Gasteiz, Spain, 23Hospital Universitario Lucus Augusti, Lugo, Spain, 24Hospital Universitario de Canarias, La Laguna, Spain, 25Rheumatology Department, Consorci Hospital General Universitari de Valencia, Valencia, Spain, 26Hospital Universitario Severo Ochoa, Leganés, Spain, 27Rheumatology Department, Hospital Universitario Son Llàtzer, Palma de Mallorca, Spain, 28Hospital Universitario La Paz, Madrid, Spain, 29Division of Rheumatology, Hospital Universitario de Bellvitge, Barcelona, Spain, 30Research group on Genetic Epidemiology and Atherosclerosis in Systemic Diseases and in Metabolic Bone Diseases of the Musculoskeletal System, IDIVAL, Division of Rheumatology, Hospital Universitario Marqués de Valdecilla; School of Medicine, Universidad de Cantabria, Santander, Spain. Cardiovascular Pathophysiology and Genomics Research Unit, School of Physiology, Faculty of Health Sciences, University of the Witwatersrand, Johannesburg, South Africa, 31Hospital Universitario Marqués de Valdecilla, IDIVAL, Santander, Spain

    Background/Purpose: Epidemiological information on Giant Cell Arteritis (GCA) comes mainly from the Scandinavian countries of northern Europe, which show a higher incidence than the countries…
  • Abstract Number: 1866 • ACR Convergence 2021

    Vasculitis in Patients with Sarcoidosis: A Single-Institution Case Series of 17 Patients

    Bradly Kimbrough1, Kenneth Warrington2, Hannah Langenfeld3, Cynthia Crowson4, Eva Carmona3, Andrew Virata3 and Matthew Koster3, 1Mayo Clinic Rochester, Rochester, MN, 2Mayo Clinic, Rochester, Minnesota, 3Mayo Clinic, Rochester, MN, 4Mayo Clinic, Eyota, MN

    Background/Purpose: Vasculitis in patients with sarcoidosis is rare and can affect blood vessels of any size. Limited information describing this association is available. The purpose…
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All abstracts accepted to ACR Convergence are under media embargo once the ACR has notified presenters of their abstract’s acceptance. They may be presented at other meetings or published as manuscripts after this time but should not be discussed in non-scholarly venues or outlets. The following embargo policies are strictly enforced by the ACR.

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