ACR Meeting Abstracts

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Abstracts tagged "takayasu arteritis and vasculitis"

  • Abstract Number: 1778 • 2018 ACR/ARHP Annual Meeting

    Comparison of Clinical and Angiographic Features of Arterial Involvement in Takayasu’s Arteritis and Behcet’s Disease

    Su Jin Choi1, Doo-Ho Lim2, Ji Seon Oh1, Seokchan Hong1, Yong-Gil Kim1, Chang Keun Lee1 and Bin Yoo1, 1Division of Rheumatology, Department of Internal Medicine, University of Ulsan College of Medicine, Asan Medical Center, Seoul, Korea, Republic of (South), 2Division of Rheumatology, Department of Internal Medicine, University of Ulsan College of Medicine, Ulsan University Hospital, Ulsan, Korea, Republic of (South)

    Background/Purpose: Systemic vasculitis is one of the major manifestations of Behcet’s disease (BD). Takayasu’s arteritis (TA) is a chronic vasculitis that primarily affects the aorta…
  • Abstract Number: 1882 • 2018 ACR/ARHP Annual Meeting

    Characteristics and Treatment Outcomes of Takayasu Arteritis in a Nationwide, Retrospective Cohort Study in Japan

    Haruhito A. Uchida1, Yoshikazu Nakaoka2, Hajime Yoshifuji3, Takahiko Sugihara4, Yoshiko Watanabe5, Masayoshi Harigai6, Yoshihiro Arimura7 and Mitsuaki Isobe8, 1Department of Chronic Kidney Disease and Cardiovascular Disease, Okayama University Graduate School of Medicine, Dentistry and Pharmaceutical Sciences, Okayama, Japan, 2Department of Vascular Physiology, National Cerebral and Cardiovascular Center Research Institute, Osaka, Japan, 3Department of Rheumatology and Clinical Immunology, Graduate School of Medicine, Kyoto University, Kyoto, Japan, 4Department of Medicine and Rheumatology, Tokyo Metropolitan Geriatric Hospital, Tokyo, Japan, 5First Department of Physiology, Kawasaki Medical School, Kurashiki, Japan, 6Tokyo Women's Medical University, Division of Epidemiology and Pharmacoepidemiology of Rheumatic Diseases, Institute of Rheumatology, Tokyo, Japan, 7Kyorin University School of Medicine, First Department of Internal Medicine, Tokyo, Japan, 8Sakakibara Heart Institute, Tokyo, Japan

    Background/Purpose: Takayasu arteritis (TAK) typically affects young women under 40 years old, whereas patients with onset age over 40 years are occasionally observed. It still…
  • Abstract Number: 2781 • 2018 ACR/ARHP Annual Meeting

    Long Term Follow-up Results of Takayasu Arteritis Cohort: A Tertiary-Single Center Study

    Sema Kaymaz Tahra1, Fatma Alibaz-Oner1 and Haner Direskeneli2, 1Rheumatology, Marmara University School of Medicine, Istanbul, Turkey, 2Rheumatology, Marmara University, School of Medicine, Istanbul, Turkey

    Background/Purpose: To assess the clinical characteristics and long term follow-up outcomes of patients with Takayasu’s arteritis (TAK) in a tertiary referral center. Methods: In this…
  • Abstract Number: 1734 • 2017 ACR/ARHP Annual Meeting

    CXCR5+ CD4 T Cells Signature Differentiates Takayasu Arteritis from Giant Cell Arteritis

    Anne-Claire Desbois1, Valentin Quiniou2, Patrick Bruneval3, Nicolas Derian2, Anna Maciejewski-Duval2, Marlène Garrido4, Cloé Comarmond5, Jacques Pouchot6, Michelle Rosenzwajg2, David Klatzmann2, Patrice Cacoub7 and David Saadoun8, 1Hôpital Pitié-Salpêtrière, Internal Medicine and Clinical Immunology, Paris, France, 2GHPS, Paris, France, 3HEGP, Paris, France, 4I3 laboratory, Pitié-Salpétrière, Paris, France, 5DHU 2iB Internal Medicine Referal Center for Autoimmune diseases Pitie Hospital, Paris, France, 6Internal Medicine Department, European Hospital Georges Pompidou, Paris, France, 7Department of Internal Medicine and Clinical Immunology, Groupe Hospitalier Pitié-Salpêtrière, Paris, France, 8Sorbonne Universités, UPMC Univ Paris 06, UMR 7211, and Inflammation-Immunopathology-Biotherapy Department (DHU i2B), F-75005, Paris, France; INSERM, UMR_S 959, F-75013, Paris, France; CNRS, FRE3632, F-75005, Paris, France; AP-HP, Groupe Hospitalier, Paris, France

    Background/Purpose: To compare microarray gene analysis of patients with Giant cell arteritis to patients with Takayasu arteritis. Methods: We performed comparative microarray gene analysis of…
  • Abstract Number: 1746 • 2017 ACR/ARHP Annual Meeting

    mTOR Pathway Activation in Takayasu Arteriti

    Cloé Comarmond1, Aurélie Leroyer2, Zeidan Mohamad3, Jean-Pierre Fourez4, Fabien Koskas5, Philippe Cluzel6, Anna Maciejewski-Duval7, Marlène Garrido8, Patrice Cacoub9 and David Saadoun10, 1DHU 2iB Internal Medicine Referal Center for Autoimmune diseases Pitie Hospital, Paris, France, 2Hopital de Marseille, Marseille, France, 3Hopital Necker, Paris, France, 4Groupe Hospitalier Pitié-Salpétrière, Paris, France, 5Department of vascular surgery, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France, 6Department of cardiovascular imagery, Assistance Publique-Hôpitaux de Paris (AP-HP), Groupe Hospitalier Pitié Salpétrière, 83 Boulevard de l'Hôpital, 75013, Paris, France., Paris, France, 7GHPS, Paris, France, 8I3 laboratory, Pitié-Salpétrière, Paris, France, 9Department of Internal Medicine and Clinical Immunology, Groupe Hospitalier Pitié-Salpêtrière, Paris, France, 10Sorbonne Universités, UPMC Univ Paris 06, UMR 7211, and Inflammation-Immunopathology-Biotherapy Department (DHU i2B), F-75005, Paris, France; INSERM, UMR_S 959, F-75013, Paris, France; CNRS, FRE3632, F-75005, Paris, France; AP-HP, Groupe Hospitalier, Paris, France

    Background/Purpose: mTORC1 drives the proinflammatory expansion of T helper (TH) type 1, TH17 cells and controls fibroblast proliferation, typical features of Takayasu arteritis (TA) pathogenesis.…
  • Abstract Number: 2932 • 2017 ACR/ARHP Annual Meeting

    mTOR Pathway Is Activated in Endothelial Cells from Patients with Takayasu Arteritis and Is Modulated By Serum IgG

    Jérôme Hadjadj1, Guillaume Canaud2, Tristan Mirault3, Maxime Samson4, Patrick Bruneval5, Alexis Regent6, Claire Goulvestre7, Veronique Witko-Sarsat8, Nathalie Costedoat-Chalumeau9, Loïc Guillevin for the French Vasculitis Study Group10, Luc Mouthon11 and Benjamin Terrier12, 1Department of Internal Medicine, National Referral Center for Rare Autoimmune and Systemic Diseases, Hospital Cochin, Assistance Publique-Hôpitaux de Paris (AP-HP), Team Neutrophils and Vasculitis, INSERM U1016, Cochin Institute, Paris, France, Paris, France, 2Department of Nephrology and Transplantation, Necker-Enfants Malade, Université Paris Descartes, Sorbonne Paris Cité, INSERM U1151, Necker-Enfants Malades Hospital, Paris, France AP-HP, Paris, France, PARIS, France, 3Department of Vascular Medicine, Georges Pompidou European Hospital, AP-HP, Université Paris Descartes, Sorbonne Paris Cité, Paris, France, Paris, France, 4Dijon University Hospital, Dijon, France, 5HEGP, Paris, France, 6National Referral Center for Rare Systemic Autoimmune Diseases, Hôpital Cochin, AP–HP, Université Paris Descartes, Paris, France, 7Department of Immunology, Hospital Cochin, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France, Paris, France, 8Team Neutrophils and Vasculitis, INSERM U1016, Cochin Institute, LABEX Inflamex, Université Sorbonne Paris Cité, 75013, Paris, France, Paris, France, 9Service de médecine interne Pôle médecine, Hôpital Cochin, Centre de référence maladies auto-immunes et systémiques rares de l’île de France, Paris, France, 10Service de Médecine Interne, Centre de Référence Maladies Auto-Immunes et Auto-Inflammatoires Systémiques Rares, Hôpital Cochin, Paris, France, 11Service de Médecine Interne, Hôpital Cochin, Centre de référence national pour les maladies systémiques autoimmunes rares d’Ile de France, DHU Authors, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France ;Université Paris Descartes Sorbonne Paris, Paris, France, 12Service de Médecine Interne, Hôpital Cochin, Centre de référence national pour les maladies systémiques autoimmunes rares d’Ile de France, DHU Authors, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France, Paris, France

    Background/Purpose: Takayasu arteritis (TA) and giant cell arteritis (GCA) are large-vessel vasculitis characterized by vascular remodelling involving endothelial cells (ECs) and vascular smooth muscle cells,…
  • Abstract Number: 71 • 2017 ACR/ARHP Annual Meeting

    The Critical Role of Interleukin-33 in Promoting Angiogenesis and Regulates Inflammation through Mast Cells in Takayasu Arteritis

    Anne-Claire Desbois1, Patrice Cacoub2, Aurélie LEROYER3, Edwige Tellier4, Marlène Garrido5, Anna Maciejewski-Duval6, Cloé Comarmond7, Stéphane Barete6, Michel Arock6, Patrick Bruneval8, Jean-Marie Launay9, Pierre Fouret10, Ulrich Blank11, Michelle Rosenzwajg6, David Klatzman12, Mohamed Jarraya13, Philippe Cluzel14, Fabien Koskas15, Gilles Kaplanski16 and David Saadoun17, 1Hôpital Pitié-Salpêtrière, Internal Medicine and Clinical Immunology, Paris, France, 2Department of Internal Medicine and Clinical Immunology, Groupe Hospitalier Pitié-Salpêtrière, Paris, France, 3Faculté de Pharmacie, Marseille, France, 4Université Marseille, Marseille, France, 5I3 laboratory, Pitié-Salpétrière, Paris, France, 6GHPS, Paris, France, 7DHU 2iB Internal Medicine Referal Center for Autoimmune diseases Pitie Hospital, Paris, France, 8HEGP, Paris, France, 9Hôpital lariboisière, Paris, France, 10Hôpital La Pitié Salpétrière, Paris, France, 11Hôpital Bichat, Paris, France, 12UPMC Université Paris 06, UMR 7211, Paris, France, 13Hôpital Saint Louis, Paris, France, 14Department of cardiovascular imagery, Assistance Publique-Hôpitaux de Paris (AP-HP), Groupe Hospitalier Pitié Salpétrière, 83 Boulevard de l'Hôpital, 75013, Paris, France., Paris, France, 15Department of vascular surgery, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France, 16Aix-Marseille Université - Internal Medicine hopital conception - F-13000 Marseilles, Marseille, France, 17Sorbonne Universités, UPMC Univ Paris 06, UMR 7211, and Inflammation-Immunopathology-Biotherapy Department (DHU i2B), F-75005, Paris, France; INSERM, UMR_S 959, F-75013, Paris, France; CNRS, FRE3632, F-75005, Paris, France; AP-HP, Groupe Hospitalier, Paris, France

    Background/Purpose: Large vessel vasculitis (LVV) include Takayasu arteritis (TA) and giant cell arteritis (GCA). Arterial lesions in LVV result from chronic inflammation and neoangiogenesis. IL-33,…
  • Abstract Number: 784 • 2017 ACR/ARHP Annual Meeting

    Damage and Predictors of Damage in Takayasu’s Arteritis

    Antoine G. Sreih1, Tanaz A. Kermani2, David Cuthbertson3, Simon Carette4, Nader A. Khalidi5, Curry L. Koening6, Carol A. Langford7, Carol A. McAlear8, Paul A. Monach9, Larry W. Moreland10, Christian Pagnoux11, Philip Seo12, Kenneth J. Warrington13, Steven R. Ytterberg13 and Peter A. Merkel1,14, 1Division of Rheumatology, University of Pennsylvania, Philadelphia, PA, 2Division of Rheumatology, University of California, Los Angeles, CA, 3Biostatistics and Informatics, Department of Pediatrics, University of South Florida, Tampa, FL, 4Mount Sinai Hospital, University of Toronto, Toronto, ON, Canada, 5Rheumatology, McMaster University, Hamilton, ON, Canada, 6Rheumatology, University of Utah, Salt Lake City, UT, 7Rheumatic and Immunologic Diseases, Cleveland Clinic, Cleveland, OH, 8University of Pennsylvania, Philadelphia, PA, 9Boston University School of Medicine, Boston, MA, 10Rheumatology & Clinical Immunology, University of Pittsburgh, Pittsburgh, PA, 11Rheumatology-Vasculitis clinic, Mount Sinai Hospital, University of Toronto, Toronto, ON, Canada, 12Medicine, Johns Hopkins University, Baltimore, MD, 13Rheumatology, Mayo Clinic, Rochester, MN, 14Biostatistics, Epidemiology, and Bioinformatics, University of Pennsylvania, Philadelphia, PA

    Background/Purpose: Information regarding the degree and the predictors of damage in patients with Takayasu’s arteritis (TAK) is limited. This study aimed to characterize damage and…
  • Abstract Number: 785 • 2017 ACR/ARHP Annual Meeting

    Longitudinal Angiographic Findings in Patients with Takayasu’s Arteritis

    Antoine G. Sreih1, Tanaz A. Kermani2, David Cuthbertson3, Simon Carette4, Lindsy J. Forbess5, Nader A. Khalidi6, Curry L. Koening7, Carol A. McAlear8, Paul A. Monach9, Larry W. Moreland10, Christian Pagnoux11, Philip Seo12, Robert F. Spiera13, Kenneth J. Warrington14, Steven R. Ytterberg14, Carol A. Langford15 and Peter A. Merkel16,17, 1Rheumatology, University of Pennsylvania, Philadelphia, PA, 2Division of Rheumatology, University of California, Los Angeles, CA, 3Biostatistics and Informatics, Department of Pediatrics, University of South Florida, Tampa, FL, 4Mount Sinai Hospital, University of Toronto, Toronto, ON, Canada, 5Medicine, Division of Rheumatology, Cedars-Sinai Medical Center, Los Angeles, CA, 6Rheumatology, McMaster University, Hamilton, ON, Canada, 7Rheumatology, University of Utah, Salt Lake City, UT, 8University of Pennsylvania, Philadelphia, PA, 9Boston University School of Medicine, Boston, MA, 10Rheumatology & Clinical Immunology, University of Pittsburgh, Pittsburgh, PA, 11Rheumatology-Vasculitis clinic, Mount Sinai Hospital, University of Toronto, Toronto, ON, Canada, 12Medicine, Johns Hopkins University, Baltimore, MD, 13Rheumatology, Hospital for Special Surgery, New York, NY, 14Rheumatology, Mayo Clinic, Rochester, MN, 15Rheumatic and Immunologic Diseases, Cleveland Clinic, Cleveland, OH, 16Biostatistics, Epidemiology, and Bioinformatics, University of Pennsylvania, Philadelphia, PA, 17Division of Rheumatology, University of Pennsylvania, Philadelphia, PA

    Background/Purpose : Longitudinal data on the type, progression, and predictors of arterial lesions in patients with Takayasu’s arteritis (TAK) is limited. This study aimed to…
  • Abstract Number: 796 • 2017 ACR/ARHP Annual Meeting

    Presentation and Outcome of Large-Vessel Vasculitis Diagnosed between 50 and 60 Years: Case-Control Study Based on 183 Cases

    Laure Delaval1,2, Aurélie Daumas3, Maxime Samson4, Mikael Ebbo5, Hubert de Boysson6, Eric Liozon7, Henry Dupuy8, Alexis Regent9, Mathieu Puyade10, Daniel Blockmans11, Estibaliz Lazaro12, Ygal Benhamou13, Karim Sacre14, Alice Bérezné15, Loïc Guillevin2,9,16 and Benjamin Terrier17,18,19, 1National Referral Center for Rare Systemic Autoimmune Diseases, Hôpital Cochin, AP–HP, Université Paris Descartes, paris, France, 2Internal medicine, Cochin University Hospital, paris, France, 3Department of Internal Medicine, Aix-Marseille Université, La Timone University Hospital, AP-HM, Marseille, France, 4Department of Internal Medicine and Clinical Immunology, Hôpital François Mitterrand, CHU de Dijon, Dijon, France, 5internal medicine, Aix-Marseille Université, La Timone University Hospital, AP-HM, Paris, France, 6Department of Internal Medicine, Caen University Hospital, Caen, France, 7Departement of Internal Medicine, Limoges University Hospital, Limoges, France, 8Department of Internal Medicine, Haut-Lévêque Hospital, Pessac, France, 9National Referral Center for Rare Systemic Autoimmune Diseases, Hôpital Cochin, AP–HP, Université Paris Descartes, Paris, France, 10Department of Internal Medicine, University Hospital of Poitiers, Poitiers, France, 11General Internal Medicine, University Hospital Gasthuisberg, Leuven, Belgium, 12Department of Internal Medecine and Clinical Immunology, Bordeaux University Hospital, Pessac, France, 13Department of internal medicine, University Hospital of Rouen, Rouen, France, 14Department of Internal Medicine, Bichat Hospital, Paris, France, 15Department of internal medicine, CHR Annecy-Genevois, Metz-Tessy, France, 16French Vasculitis Study Group (FVSG), Paris, France, 17Service de Médecine Interne, Hôpital Cochin, Centre de référence national pour les maladies systémiques autoimmunes rares d’Ile de France, DHU Authors, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France, Paris, France, 18Internal Medicine, Cochin University Hospital, Paris, France, 19French Vasculitis Study Group (FVSG), paris, France

    Background/Purpose: Primary large-vessel vasculitis (LVV) include giant cell arteritis (GCA) and Takayasu arteritis (TA). Age at onset is commonly used to distinguish GCA and TA.…
  • Abstract Number: 820 • 2017 ACR/ARHP Annual Meeting

    Prognostic Value of Positron Emission Tomography in a Prospective, Longitudinal Cohort of Patients with Large Vessel Vasculitis

    Peter C. Grayson1, Sara Alehashemi2, Armin Bagheri3, Ali Cahid Civelek4, Thomas Cupps5, Mariana J. Kaplan6, Ashkan Malayeri4, Peter A. Merkel7, Elaine Novakovich8, David A. Bluemke4 and Mark Ahlman4, 1National Institute of Arthritis, Musculoskeletal and Skin Disease (NIAMS), Bethesda, MD, 2Rheumatology, National Institutes of Health, Bethesda, MD, 3Vasculitis Translational Research Program, NIAMS, NIH, Bethesda, MD, 4Radiology and Imaging Sciences, National Institutes of Health, Bethesda, MD, 5Rheumatology, Georgetown University, Bethesda, MD, 6NIAMS/NIH, Bethesda, MD, 7University of Pennsylvania, Philadelphia, MN, 8Systemic Autoimmunity Branch, NIAMS, National Institutes of Health, Bethesda, MD

    Background/Purpose: While several studies have examined the potential of 18F-flurodeoxyglucose (FDG) positron emission tomography (PET) to help establish a diagnosis of large vessel vasculitis (LVV),…
  • Abstract Number: 821 • 2017 ACR/ARHP Annual Meeting

    Discrepancies between Clinical- and Imaging-Based Assessments of Disease Activity in Takayasu’s Arteritis

    Peter C. Grayson1, Mark Ahlman2, Kathleen Marinelli3, Renee Borchin4, Simon Carette5, Nader A. Khalidi6, Carol A. Langford7, Carol A. McAlear8, Paul A. Monach9, Christian Pagnoux5, Kenneth J. Warrington10, Steven R. Ytterberg10 and Peter A. Merkel11, 1National Institute of Arthritis, Musculoskeletal and Skin Disease (NIAMS), Bethesda, MD, 2Radiology and Imaging Sciences, National Institutes of Health, Bethesda, MD, 3NIAMS, National Institutes of Health, Bethesda, MD, 4University of South Florida, Tampa, FL, 5Division of Rheumatology, Mount Sinai Hospital, University of Toronto, Toronto, ON, Canada, 6Rheumatology, McMaster University, Hamilton, ON, Canada, 7Rheumatic and Immunologic Diseases, Cleveland Clinic, Cleveland, OH, 8University of Pennsylvania, Philadelphia, PA, 9Boston University School of Medicine, Boston, MA, 10Rheumatology, Mayo Clinic, Rochester, MN, 11Biostatistics, Epidemiology, and Informatics, University of Pennsylvania, Philadelphia, PA

    Background/Purpose: To study the relationship between clinically-determined disease activity and vascular inflammation assessed by positron emission tomography (PET) in patients with TakayasuÕs arteritis (TAK). Methods:…
  • Abstract Number: 859 • 2016 ACR/ARHP Annual Meeting

    Long-Term Outcomes of Renal Artery Involvement in Takayasu Arteritis

    Seokchan Hong1, Oh Chan Kwon2, Byeongzu Ghang3, Yong-Gil Kim1, Chang-Keun Lee1 and Bin Yoo1, 1Division of Rheumatology, Department of Internal Medicine, University of Ulsan College of Medicine, Asan Medical Center, Seoul, South Korea, 2Division of Rheumatology, Department of Internal Medicine, University of Ulsan College of Medicine, Asan Medical Center, Seoul, Korea, The Republic of, 3Division of Rheumatology, Department of Internal Medicine, Univerisy of Ulsan College of Medicine, Asan Medical Center, Seoul, South Korea

    Long-term Outcomes of Renal Artery Involvement in Takayasu Arteritis Background/Purpose: Takayasu arteritis (TA) involving the renal artery can result in hypertension, renal dysfunction, and premature…
  • Abstract Number: 860 • 2016 ACR/ARHP Annual Meeting

    Assessment of the Frequency of Cardiovascular Risk Factors in Patients with Takayasu’s Arteritis

    Fatma Alibaz-Oner1, Matthew J. Koster2, Ali Ugur Unal3, Hale Gulcin Yildirim4, Ceylan Cikikci4, Cynthia S. Crowson5, Ashima Makol6, Steven R. Ytterberg6, Eric L. Matteson6, Haner Direskeneli7 and Kenneth J. Warrington6, 1Department of Rheumatology, Marmara University Faculty of Medicine, Istanbul, Turkey, 2Rheumatology, University of California Los Angeles, CA, USA Mayo Clinic, Rochester, MN, 3Marmara University, School of Medicine, Rheumatology, Istanbul, Turkey, 4Marmara University Faculty of Medicine, Istanbul, Turkey, 5Health Sciences Research, Mayo Clinic, Rochester, MN, 6Rheumatology, Mayo Clinic, Rochester, MN, 7Rheumatology, Marmara University, School of Medicine, Istanbul, Turkey

    Background/Purpose: Accelerated atherosclerosis associated with chronic inflammation is one of the major complications of systemic inflammatory diseases. Takayasu arteritis (TAK) is a rare, systemic large-vessel…
  • Abstract Number: 881 • 2016 ACR/ARHP Annual Meeting

    Cardiopulmonary Involvement in Takayasu Arteritis

    David Brennan1, Kenneth J. Warrington2, Jean Schmidt3, Cynthia S. Crowson4 and Matthew J. Koster5, 1Internal Medicine, Mayo Clinic, Rochester, MN, 2Rheumatology, Mayo Clinic, Rochester, MN, 3Department of Internal Medicine and RECIF, Amiens University Hospital, Amiens, France, 4Health Sciences Research, Mayo Clinic, Rochester, MN, 5Rheumatology, University of California Los Angeles, CA, USA Mayo Clinic, Rochester, MN

    Background/Purpose:  Takayasu arteritis (TAK) is an inflammatory large-vessel vasculitis of unknown etiology affecting the proximal aorta and its primary branches. Heart disease is a major…
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