Abstract Number: 1162 • 2017 ACR/ARHP Annual Meeting
Impact of Bone Localization on the Prognostic of Langerhans Cell Histiocytosis: A Monocentric Retrospective Study
Background/Purpose: Langerhans cell histiocytosis (LCH) is a rare condition, and mostly affects children. Bone is the most commonly involved organ, with bone lesions in 50%…Abstract Number: 1163 • 2017 ACR/ARHP Annual Meeting
A First-in-Human Phase I Study to Evaluate the Safety, Tolerability, Pharmacokinetics and Pharmacodynamics of a Novel Anti-Interleukin 1 Biologic Agent, Rph-104, in Healthy Subjects
Background/Purpose: Interleukin-1 (IL-1) is highly active pro-inflammatory cytokine, which is responsible for clinical and laboratory findings in hereditary and acquired auto-inflammatory disorders. Blocking IL-1 activity…Abstract Number: 1164 • 2017 ACR/ARHP Annual Meeting
Spectrum of Skin Eruption and Histological Findings in Adult-Onset Still’s Disease and Significance of Atypical Persistent Skin Eruptions
Background/Purpose: Adult-onset Still disease (AOSD) is a rare systemic inflammatory disorder characterized by spiking fevers, polyarthritis and an evanescent salmon-pink maculopapular eruption. Several cases of…Abstract Number: 1165 • 2017 ACR/ARHP Annual Meeting
Clinical Characteristics of Patients with Late-Onset Familial Mediterranean Fever in Japan
Background/Purpose: Familial Mediterranean fever (FMF) is an auto-inflammatory disease characterized by recurrent episodes of fever and polyserositis. Most patients have their first febrile attack before…Abstract Number: 1166 • 2017 ACR/ARHP Annual Meeting
Systemic Degos Disease: Long Term Survival on Combined Therapy with Eculizumab and Treprostinil
Background/Purpose: Degos disease (Malignant Atrophic Papulosis) is a thrombotic microvasculopathy of complement activation, endothelial cell injury and progressive microvascular obliteration. Lesions are marked by vascular…Abstract Number: 1167 • 2017 ACR/ARHP Annual Meeting
Phenotypical Features of Patients with Rheumatologic Manifestations of Common Variable Immunodeficiency
Background/Purpose: Patients with common variable immunodeficiency (CVID) have a higher incidence of rheumatologic disorders. To delineate this clinical association, we investigated the phenotypical features of…Abstract Number: 1168 • 2017 ACR/ARHP Annual Meeting
Eosinophilic Fasciitis: Baseline Retrospective Evaluation of Clinical Characteristics and Prognosis in a Cohort of 83 Patients
Background/Purpose: Eosinophilic fasciitis (EF) is a rare disease and there have been few published series that include clinical, pathological and serological data. These studies have…Abstract Number: 1169 • 2017 ACR/ARHP Annual Meeting
Rapid Improvement with Tocilizumab in Refractory and Severe Uveitic Cystoid Macular Edema
Background/Purpose: In uveitis, remission-inducing therapy with even more vigor than does rheumatology is mandatory. Since the eye is so much less forgiving of chronic inflammation…Abstract Number: 1170 • 2017 ACR/ARHP Annual Meeting
High Output Flow Cytometry Array Classifies Subjects with Uveitis Due to Behcet’s Disease and Sarcoidosis
Background/Purpose: The information content of multi-parametric flow cytometry-based immune-phenotyping experiments is routinely underexploited given the paucity of adequate tools and strategies for large-scale unbiased data…Abstract Number: 1171 • 2017 ACR/ARHP Annual Meeting
Mycophenolate Mofetil May Improve Interstitial Pneumonia with Autoimmune Features
Background/Purpose: To assess the efficacy of mycophenolate mofetil (MMF) in treatment of adult patients with interstitial pneumonia with autoimmune features (IPAF). Methods: A retrospective medical…Abstract Number: 1172 • 2017 ACR/ARHP Annual Meeting
Utility of Interstitial Pneumonia with Autoimmune Features (IPAF) Proposed Criteria in the Classification of Patients with CTD-Associated Interstitial Lung Disease in a Single Centre
Background/Purpose: The term interstitial pneumonia with autoimmune features (IPAF) has recently been proposed to identify those patients with ILD and clinical and/or serological autoimmune manifestations…Abstract Number: 1173 • 2017 ACR/ARHP Annual Meeting
Rheumatic Immune Related Adverse Events Due to Programmed Cell Death Protein 1 (PD-1) Inhibition for Cancer: Comprehensive Analysis of a Whole Cancer Cohort
Background/Purpose: Immune checkpoint therapy with programmed cell death protein 1 (PD-1) inhibitors has led to significant survival benefits in the treatment of multiple cancers. This…Abstract Number: 1174 • 2017 ACR/ARHP Annual Meeting
Which Definition Should be Used to Determine Colchicine Resistance in Patients with Familial Mediterranean Fever?
Background/Purpose: Colchicine is the main therapy for familial Mediterranean fever (FMF); however, around 5-10% of FMF patients are colchicine-resistant. Currently there is no standard and…Abstract Number: 1175 • 2017 ACR/ARHP Annual Meeting
Rituximab for Idiopathic and IgG4-Related Retroperitoneal Fibrosis
Rituximab for Idiopathic and IgG4-Related Retroperitoneal FibrosisBackground/Purpose: Untreated retroperitoneal fibrosis (RPF) can lead to chronic back and flank pain and/or renal failure. The mainstay of…Abstract Number: 1176 • 2017 ACR/ARHP Annual Meeting
A Randomized, Open-Label, Dose-Ranging Study of Oral Delayed Release Prednisone in Patients with Untreated Polymyalgia Rheumatica
Background/Purpose: Polymyalgia rheumatica (PMR) is a common condition of unknown etiology with a lifetime risk of 2.43% in women and 1.66% in men.1 PMR is…
ACR Meeting Abstracts