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Abstracts tagged "Myopathies"

  • Abstract Number: 0287 • ACR Convergence 2025

    Comprehensive Profiling of Neutrophil Subsets Reveals Functional Signatures Linked to Vasculopathic Features in Patients with Inflammatory Myopathies

    Daniel Alberto Carrillo-Vázquez1, Beatriz Alcalá-Carmona1, Jennifer Tiaré Balderas Miranda2, Yatzil Reyna Juárez3, María José Ostos Prado1, Samuel Govea-Peláez1, Nancy R Mejía Domínguez4, Guillermo Juárez Vega4, Karina Santana-De Anda1, Jiram Torres-Ruiz5 and Diana Gómez-Martín6, 1Instituto Nacional De Ciencias Médicas Y Nutrición Salvador Zubirán, Mexico City, Distrito Federal, Mexico, 2Universidad Nacional Autónoma de México, Coyoacán, Federal District, Mexico, 3Instituto Politècnico Nacional, Tultitlán de Mariano Escobedo, Mexico State, Mexico, 4Universidad Nacional Autónoma de México, Mexico City, Distrito Federal, Mexico, 5INCMNSZ, Ciudad de México, Mexico, 6INCMNSZ, Mexico city, Federal District, Mexico

    Background/Purpose: Vasculopathic manifestations of idiopathic inflammatory myopathies (IIM) such as interstitial lung disease (ILD), calcinosis, skin ulcers, mechanic’s hands, are characterized by immune-mediated vascular damage.…
  • Abstract Number: 2073 • ACR Convergence 2025

    Cell-free DNA as a Potential Marker of Muscle Involvement and Treatment Response in Myositis

    Sabína Oreská1, Kristina Svobodová1, Lucia Vernerová1, Dana Dlouhá2, Hana Wunsch1, Karel Pavelka1, Jiri Vencovsky3, Ladislav Šenolt4, Michal Vrablik5, Jaroslav Alois Hubáček2 and Michal Tomcik1, 1Institute of Rheumatology and Department of Rheumatology, 1st Faculty of Medicine, Charles University, Prague, Czech Republic, Prague, Czech Republic, 2Experimental Medicine Center, Institute for Clinical and Experimental Medicine, Prague, Czech Republic, 3Institute of Rheumatology, Praha 8, Czech Republic, 4Institute of Rheumatology and Department of Rheumatology, First Faculty of Medicine, Charles University, Prague, Czech Republic, 53rd Department of Internal Medicine, General University Hospital and 1st Faculty of Medicine, Charles University, Prague, Czech Republic, Prague, Czech Republic

    Background/Purpose: Idiopathic inflammatory myopathies (IIM) are characterized by inflammatory muscle injury. Circulating cell-free DNA (cfDNA), including nuclear (cfnDNA) and mitochondrial (cfmtDNA) DNA, has been shown…
  • Abstract Number: 1210 • ACR Convergence 2025

    Artificial Intelligence-Based Capillaroscopy and Laboratory Biomarkers to Predict Disease Activity in Idiopathic Inflammatory Myopathies: Preliminary Data from the CapIAMI Cohort

    Gema María Lledó Ibáñez1, Jorge Álvarez-Troncoso2, Borja del Carmelo Gracia Tello3, Sergio Prieto-Gonzalez4, Elena Martínez Robles5, Diana Cristina-Varela6, Sebastián Molina-Ríos7, Luis Sáez Comet8, Eiman Soliman9, Franklin Uguña10, Miguel Antonio Mesa11, Miguel Martín Cascón12, Tânia Santiago13, Grace-Jimena Santamaría-Peñaloza14, Tsvetoslav Georgiev15, Santiago Bernal-Macias16, Begoña Marí-Alfonso17, Jesus Ballano Rodríguez-Solís18, Sally Patricia Pino Hernández19, Jacek Olas20, Juan Manuel Mosquera Angarita21, Elena García- Guijarro22, Isabel Perales Fraile23, Mayka Freire Dapena24, Iván Pérez de Pedro25, Luis Adrián Viteri Noël26 and Eduardo Ramos ibáñez27, 1Hospital Clínic de Barcelona, Barcelona, Spain, 2Hospital Universitario La Paz, Madrid, Madrid, Spain, 3Hospital Clínico Universitario Lozano Blesa, Zaragoza, Spain, 4Hospital Clinic, Barcelona, Catalonia, Spain, 5Hospital Universitario La Paz, Madrid, Spain, 6Unidad de Reumatología, Hospital General de Medellín, Medellín, Colombia, Medellín, Colombia, 7Hospital Universitario Nacional de Colombia, Bogotá, Colombia, Bogotá, Colombia, 8Hospital Universitario Miguel Servet, Zaragoza, Spain, 9Alexandria Faculty of Medicine, Alexandria, Egypt, 10Sociedad Ecuatoriana de Reumatologia, Quito, Ecuador, 11Universidad Pontificia Bolivariana, Medellin, Colombia, 12Hospital General Universitario Morales Meseguer, Murcia, Spain, 13ULS de Coimbra, Coimbra, Portugal, 14Hospital Metropolitano, Quito, Ecuador, 15Hospital St. Marina, Varna, Varna, Bulgaria, 16Hospital Universitario San Ignacio, Bogotá, Colombia, 17Hospital Universitario Parc Taulí, Barcelona, Spain, 18Hospital Universitario del Henares, Alcalá de Henares, Madrid, Spain, 19Asoreuma, Care for Kids, Bogota, Distrito Capital de Bogota, Colombia, 20MCRIiR, Szpital Specjalistyczny im. J. Dietla w Krakowie, Cracow, Poland, 21Hospital Sant Joan de Déu, Barcelona, Spain, 22Hospital Universitario Infanta Cristina, Madrid, Spain, 23Hospital Universitario Infanta Sofía, Madrid, Spain, 24Hospital Clínico Universitario de Santiago de Compostela, La Coruña, Spain, 25Hospital Regional Universitario de Málaga, Málaga, Spain, 26Hospital Universitario Ramón y Cajal, Madrid, Spain, 27Capillary.io, Zaragoza, Aragon, Spain

    Background/Purpose: Nailfold videocapillaroscopy (NVC) is a valuable non-invasive tool for assessing microvascular damage in autoimmune diseases. However, its application in idiopathic inflammatory myopathies (IIM) remains…
  • Abstract Number: 0285 • ACR Convergence 2025

    Delayed-Onset Myopathy in Dermatomyositis: A Retrospective Cohort Study

    Connor Buechler1, Nawang Singhe2, Lindsey Wanberg2, Cody Rasner2, Joseph McGrath2, Karen Baker-James2, Rebecca Freese2 and David Pearson3, 1University of Minnesota, Mendota Heights, MN, 2University of Minnesota, Minneapolis, MN, 3Department of Dermatology, University of Minnesota, Minneapolis, MN

    Background/Purpose: Amyopathic dermatomyositis (ADM) is a subset of DM in which cutaneous findings occur without muscle disease for >6 months after diagnosis. However, there is…
  • Abstract Number: 2072 • ACR Convergence 2025

    Results of an Integrated Program for Early Cancer Detection in Idiopathic Inflammatory Myopathies

    valeria cantu1, Rebeca L. Polina-Lugo1, Emmanuel Dominguez-Chapa2, Ana Cecilia Bardan Inchaustegui3, Rosa Arvizu-Rivera4, fernanda m. garcia-Carrillo5, Ericka S. Reyna-Hernandez6, Daniela A. Mejia-Rodriguez6, Jesus Alberto Cardenas-de la Garza7 and Miguel Villarreal-Alarcón8, 1Division of Rheumatology, University Hospital "Dr. Jose Eleuterio Gonzalez", Universidad Autonoma de Nuevo Leon, Monterrey, Nuevo León, Mexico, 2Universidad Autonoma de Nuevo Leon, Monterrey, Nuevo León, Mexico, 3Universidad Autónoma de Nuevo Leon, Monterrey, Nuevo León, Mexico, 4Hospital Universitario "Dr. José Eleuterio Gonzalez", Escobedo, Nuevo León, Mexico, 5Hospital Universitario "Dr. José Eleuterio González" UANL, Monterrey, Nuevo Leon, Mexico, 6Rheumatology Service, Hospital Universitario “Dr. Jose Eleuterio Gonzalez”, Universidad Autonoma de Nuevo Leon, Monterrey, Nuevo Leon, Mexico, 7Rheumatology Service, University Hospital “Dr. José Eleuterio González”, Universidad Autónoma de Nuevo León, Monterrey, México, Monterrey, Mexico, 8Hospital Universitario UANL, Monterrey, Nuevo León, Mexico

    Background/Purpose: Cancer risk is significantly increased in Idiopathic Inflammatory Myopathies (IIM), particularly within the first 3 to 5 years after diagnosis. Given that cancer represents…
  • Abstract Number: 1211 • ACR Convergence 2025

    Plasma Levels of miR-133a-3p and miR-1-3p as Potential Biomarkers of Muscle Involvement and Initial Treatment Response in Myositis

    Kristina Svobodová1, Sabína Oreská1, Lucia Vernerová2, Dana Dlouhá3, Hana Wunsch2, Karel Pavelka2, Jiri Vencovsky4, Ladislav Šenolt5, Michal Vrablik6, Jaroslav Alois Hubáček3 and Michal Tomcik2, 1Institute of Rheumatology and Department of Rheumatology, 1st Faculty of Medicine, Charles University, Prague, Czech Republic, 2Institute of Rheumatology and Department of Rheumatology, 1st Faculty of Medicine, Charles University, Prague, Czech Republic, Prague, Czech Republic, 3Experimental Medicine Center, Institute for Clinical and Experimental Medicine, Prague, Czech Republic, 4Institute of Rheumatology, Praha 8, Czech Republic, 5Institute of Rheumatology and Department of Rheumatology, First Faculty of Medicine, Charles University, Prague, Czech Republic, 63rd Department of Internal Medicine, General University Hospital and 1st Faculty of Medicine, Charles University, Prague, Czech Republic, Prague, Czech Republic

    Background/Purpose: Idiopathic inflammatory myopathies (IIM) involve muscle inflammation. MicroRNAs (miRNAs), such as miR-133a-3p and miR-1-3p, play a key role in gene regulation and muscle repair.…
  • Abstract Number: 0282 • ACR Convergence 2025

    Clinical Meaningfulness and Improvement Thresholds of Myositis Core Set Measures: Association with Patient-Reported Outcomes

    Shiri Keret1, Raisa Lomanto Silva2, Irada Choudhuri3, Eugenia Gkiaouraki3, Tanya Chandra3, Nantakarn Pongtarakulpanit3, Shreya Sriram3, Niladri Bhowmick3, Vaidehi Kothari3, Kaushik Sreerama Reddy3, Eaman Alhassan4, Anushka Aggarwal5, Maha Almackenzie6, Siamak Moghadam-Kia4, Dana Ascherman7, Chester V. Oddis7 and Rohit Aggarwal8, 1Bnai Zion Medical Center, Atlit, Israel, 2Massachusetts General Hospital, Boston, MA, 3University of Pittsburgh Medical Center, Pittsburgh, 4University of Pittsburgh Medical Center, Pittsburgh, PA, 5Indraprastha Apollo Hospital, New Delhi, India, 6Medical Cities of the Ministry of the Interior, Riyadh, Saudi Arabia, 7University of Pittsburgh, Pittsburgh, PA, 8University of Pittsburgh, Rheumatology and Clinical Immunology, Pittsburgh, United States of America, Pittsburgh, PA

    Background/Purpose: The six myositis core set measures (CSMs) are widely utilized to assess disease activity in idiopathic inflammatory myopathies (IIM). However, their association with how…
  • Abstract Number: 2071 • ACR Convergence 2025

    Impact of Diagnostic Delay on Disease Activity and Cumulative Damage in Patients with Idiopathic Inflammatory Myopathies in a Third-level Hospital in Mexico

    valeria cantu1, Rebeca L. Polina-Lugo1, Emmanuel Dominguez-Chapa2, Ana Cecilia Bardan Inchaustegui3, Fernanda M. Garcia-Carrillo4, Daniela A. Mejia-Rodriguez4, Ericka S. Reyna-Hernandez4, Rosa Arvizu-Rivera5, Jesus Alberto Cardenas-de la Garza6 and Miguel Villarreal-Alarcón7, 1Division of Rheumatology, University Hospital "Dr. Jose Eleuterio Gonzalez", Universidad Autonoma de Nuevo Leon, Monterrey, Nuevo León, Mexico, 2Universidad Autonoma de Nuevo Leon, Monterrey, Nuevo León, Mexico, 3Universidad Autónoma de Nuevo Leon, Monterrey, Nuevo León, Mexico, 4Rheumatology Service, Hospital Universitario “Dr. Jose Eleuterio Gonzalez”, Universidad Autonoma de Nuevo Leon, Monterrey, Nuevo Leon, Mexico, 5Hospital Universitario "Dr. José Eleuterio Gonzalez", Escobedo, Nuevo León, Mexico, 6Rheumatology Service, University Hospital “Dr. José Eleuterio González”, Universidad Autónoma de Nuevo León, Monterrey, México, Monterrey, Mexico, 7Hospital Universitario UANL, Monterrey, Nuevo León, Mexico

    Background/Purpose: Idiopathic inflammatory myopathies (IIM) are a rare and heterogeneous group of autoimmune diseases marked by inflammation of muscle tissue and extramuscular manifestations. Their atypical…
  • Abstract Number: 1201 • ACR Convergence 2025

    Prognostic Significance of 1-Year Pulmonary Function Changes in Myositis-Associated Interstitial Lung Disease

    Shiri Keret1, Silvia Martinez Laverde2, Irada Choudhuri2, Raisa Lomanto Silva3, Eugenia Gkiaouraki2, Tanya Chandra2, Nantakarn Pongtarakulpanit4, Shreya Sriram2, Niladri Bhowmick2, Vaidehi Kothari2, Kaushik Sreerama Reddy2, Eaman Alhassan5, Anushka Aggarwal6, Maha Almackenzie7, Daniel Sullivan2, Sara Faghihi-Kashani8, Koichi Yamaguchi2, Daniel Kass2, Kevin Gibson2, Dana Ascherman9, Siamak Moghadam-Kia5, Chester V. Oddis9 and Rohit Aggarwal10, 1Bnai Zion Medical Center, Atlit, Israel, 2University of Pittsburgh Medical Center, Pittsburgh, 3Massachusetts General Hospital, Boston, MA, 4Mahidol University, University of Pittsburgh, Bangkok, Thailand, 5University of Pittsburgh Medical Center, Pittsburgh, PA, 6Indraprastha Apollo Hospital, New Delhi, India, 7Medical Cities of the Ministry of the Interior, Riyadh, Saudi Arabia, 8UCSF, Mountain View, CA, 9University of Pittsburgh, Pittsburgh, PA, 10University of Pittsburgh, Rheumatology and Clinical Immunology, Pittsburgh, United States of America, Pittsburgh, PA

    Background/Purpose: Lung involvement is the most frequent and severe extramuscular complication of Idiopathic Inflammatory Myopathy (IIM). The utility of pulmonary function test (PFT) monitoring for…
  • Abstract Number: 0281 • ACR Convergence 2025

    Anti-IL-6 Autoantibodies and IL-6 Signalling in Idiopathic Inflammatory Myopathies

    Anja Srpcic1, Manca Ogric1, Sasa Cucnik1, Sergej Pirkmajer2, Katja Lakota1 and Katja Perdan Pirkmajer1, 1University Medical Centre Ljubljana, Ljubljana, Slovenia, 2Faculty of Medicine, University of Ljubljana, Ljubljana, Slovenia

    Background/Purpose: Idiopathic inflammatory myopathies (IIM) are a heterogeneous group of systemic autoinflammatory diseases that affect muscle tissue, often leading to muscle atrophy, weakness and myalgia.…
  • Abstract Number: 2068 • ACR Convergence 2025

    Comparing characteristics, diagnostics, and treatment in people with different idiopathic inflammatory myopathies using a large representative cohort

    Michael George1, Thomas Riley1, Ellen Romich2, Emily Holladay3, Tim Beukelman4, Shanette Daigle5, Amy Mudano5, Fenglong Xie6, Xiang Guo7, Nicole Kulisek8, Arne Yndestad9, Ashraf Chaudhary8 and Jeffrey Curtis10, 1University of Pennsylvania, Philadelphia, PA, 2University of Pennsylvania, Media, PA, 3University of Alabama at Birmingham, Birmingham, AL, 4Foundation for Advancing Science Technology Education and Research, Hoover, AL, 5Foundation for Advancing Science, Technology, Education and Research (FASTER), Hoover, AL, 6The University of Alabama at Birmingham, Birmingham, AL, 7Pfizer, Inc, New York, NY, 8Pfizer, Inc, Collegeville, PA, 9Pfizer Inc, Oslo, Norway, Oslo, Norway, 10Foundation for Advancing Science, Technology, Education and Research, Birmingham, AL

    Background/Purpose: Studies of idiopathic inflammatory myopathies (IIM) are often based on the analysis of single cohorts at academic centers. We aimed to identify potential gaps…
  • Abstract Number: 1199 • ACR Convergence 2025

    Interstitial Lung Disease in Systemic Autoimmune Rheumatic Diseases (SARDs): Radiologic and Histologic Correlations

    Darya S. Jalaledin1, Aidan pye2, Angela Chang2, Navid Saleh2, Saud AlHajeri3, Beatrice Daviault4, Arusa Shah5, Sabrina Hoa6, Océane Landon-Cardinal7, Alec Yu2, Robert Levy8, Jennifer Wilson9, Charles Poirier4, James Choi2, John Yee2, Hyein Kim2 and Kun Huang10, 1Université de Montréal, Saint-Lambert, QC, Canada, 2University of British Columbia, VANCOUVER, BC, Canada, 3University of British Columbia, Vancouver, Canada, 4University of Montreal, Montreal, QC, Canada, 5University of Montreal, Montreal, BC, Canada, 6University of Montreal, Brossard, QC, Canada, 7Centre hospitalier de l'Université de Montréal, Montréal, QC, Canada, 8University of British Columbia, Deerfield, IL, 9UBC, Vancouver, BC, Canada, 10University of British Columbia, Vancouver, Surrey, BC, Canada

    Background/Purpose: Systemic autoimmune rheumatic diseases (SARDs) are a major cause of interstitial lung disease (ILD), with high prevalence in inflammatory idiopathic myopathy (IIM), systemic sclerosis…
  • Abstract Number: 2067 • ACR Convergence 2025

    Patterns of Comorbidity in Idiopathic Inflammatory Myopathies: A Cross-sectional Analysis of Disease Burden and Risk Factors

    Ilke Coskun Benlidayi1, Meghna Lama2, Oladipo Kunle Afolayan2, Meera Shah3, Manali Sarkar4, Tamar Rubinstein5, Aleksandra Opinc-Rosiak6, Rada Miskovic7, Marcin Milchert8, Dimitri Luz Felipe da Silva9, Samuel Katsuyuki Shinjo10, Elena Nikiphorou11, Ioannis Parodis12, Vincenzo Venerito13, Vikas Agarwal14 and Latika Gupta15, 1Cukurova University, Adana, Turkey, 2The University of Texas Health Science Centre at Houston School of Public Health: Houston, Texas, Houston, 3Indraprastha Apollo Hospital, New Delhi, Mumbai, Maharashtra, India, 4Sir H. N. Reliance Foundation Hospital and Research Centre, Mumbai, Maharashtra, India., Mumbai, Maharashtra, India, 5Albert Einstein College of Medicine, White Plains, NY, 6Medical University of Lodz, Zeromskiego 113, 90-549 Lodz, Poland., Lodz, Poland, 7University of Belgrade; Clinic of Allergy and Immunology, University Clinical Centre of Serbia, Belgrade, Serbia, 8Pomeranian Medical University in Szczecin, Szczecin, Poland, 9University Santo Amaro, São Paulo, Brazil, Sao Paulo, Brazil, 10Faculdade de Medicina FMUSP, Universidade de Sao Paulo, Sao Paulo, SP, Brazil, Sao Paulo, Brazil, 11King's College London, London, United Kingdom, 12Karolinska Institutet and Karolinska University Hospital, Department of Medicine Solna, Division of Rheumatology, Stockholm, Sweden, 13Univeristy of Bari "Aldo Moro", Italy, Bari, Bari, Italy, 14Sanjay Gandhi Postgraduate Institute of Medical Sciences, Lucknow, Uttar Pradesh, India, 15School of Infection, Inflammation and Immunology, College of Medicine and Health, University of Birmingham; Royal Wolverhampton NHS Trust; Centre for Musculoskeletal Research, School of Biological Sciences, The University of Manchester, Manchester; Francis Crick Institute, London, Birmingham, UK, United Kingdom

    Background/Purpose: Comorbidities contribute to the disease burden in idiopathic inflammatory myopathies (IIMs). Understanding their distribution and predictors across IIM subtypes can guide tailored strategies. This…
  • Abstract Number: 1196 • ACR Convergence 2025

    Prevalence of and Factors Associated with Chronic Opioid Use among Individuals with Inflammatory Myopathies

    Anuya Natu1, Haley Zimmerman2, Kristin Wipfler3, Kaleb Michaud4, Yvonne Lee5 and Didem Saygin2, 1John H. Stroger, Jr. Hospital of Cook County, Chicago, IL, 2Rush University Medical Center, Chicago, IL, 3FORWARD, The National Databank for Rheumatic Diseases, Omaha, NE, 4University of Nebraska Medical Center, Omaha, NE, 5Northwestern University, Chicago, IL

    Background/Purpose: Idiopathic inflammatory myopathies (IIM) can be associated with significant pain and functional impairment. While the use of opioids has been documented in other inflammatory…
  • Abstract Number: 2066 • ACR Convergence 2025

    Psychosocial Factors Strongly Influence Subjective Well-being in Patients with Idiopathic Inflammatory Myopathies

    Meera Shah1, Emilia Naseva2, Tsvetelina Velikova3, Tamar Rubinstein4, Manali Sarkar5, Lavanya Mangla6, Oliver Distler7, Ingrid de Groot8, Lisa Christ9, Carlo Vinicio Caballero Uribe10, Ai Lyn Tan11, Abraham Edgar Gracia Ramos12, Vincenzo Venerito13, Vikas Agarwal14 and Latika Gupta15, 1Indraprastha Apollo Hospital, New Delhi, Mumbai, Maharashtra, India, 2Faculty of Public Health, Medical University of Sofia, 15 Acad. Ivan Evstratiev Geshov, 1606 Sofia; Medical Faculty, Sofia University St. Kliment Ohridski, Sofia, Bulgaria, 3Medical Faculty, Sofia University St. Kliment Ohridski, Sofia, Bulgaria, 4Albert Einstein College of Medicine, White Plains, NY, 5Sir H. N. Reliance Foundation Hospital and Research Centre, Mumbai, Maharashtra, India., Mumbai, Maharashtra, India, 6Maulana Azad Medical College, 2-Bahadurshah Zafar Marg, New Delhi, New Delhi, India, 7Department of Rheumatology, University Hospital Zurich, University of Zurich, Switzerland, Zurich, Switzerland, 8The Myositis Association, Rotterdam, Netherlands, 9Department of Rheumatology and Immunology, Inselspital, Bern University Hospital, University of Bern, Bern, Switzerland., Bern, Switzerland, 10Department of Medicine, Hospital Universidad del Norte, Barranquilla, Atlantico, Colombi, Barranquilla, Colombia, 11NIHR Leeds Biomedical Research Centre, Leeds Teaching Hospitals Trust, Leeds; Leeds Institute of Rheumatic and Musculoskeletal Medicine, University of Leeds, Leeds, England, United Kingdom, 12Department of Internal Medicine, General Hospital, National Medical Center “La Raza”, Instituto Mexicano del Seguro Social, Av. Jacaranda S/N, Col. La Raza, Del. Azcapotzalco, C.P. 02990 Mexico City, Mexico., Mexico City, Mexico, 13Univeristy of Bari "Aldo Moro", Italy, Bari, Bari, Italy, 14Sanjay Gandhi Postgraduate Institute of Medical Sciences, Lucknow, Uttar Pradesh, India, 15School of Infection, Inflammation and Immunology, College of Medicine and Health, University of Birmingham; Royal Wolverhampton NHS Trust; Centre for Musculoskeletal Research, School of Biological Sciences, The University of Manchester, Manchester; Francis Crick Institute, London, Birmingham, UK, United Kingdom

    Background/Purpose: Traditional clinical measures are well established in idiopathic inflammatory myopathies (IIM), yet exploration of subjective well-being (SWB) remains limited. SWB assessment facilitates holistic patient…
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All abstracts accepted to ACR Convergence are under media embargo once the ACR has notified presenters of their abstract’s acceptance. They may be presented at other meetings or published as manuscripts after this time but should not be discussed in non-scholarly venues or outlets. The following embargo policies are strictly enforced by the ACR.

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