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Abstracts tagged "dermatomyositis"

  • Abstract Number: 027 • 2023 Pediatric Rheumatology Symposium

    Identifying and Understanding JDM in Africa: A Survey of Rheumatology Care Providers from Africa

    Jessica Perfetto1, Laura Lewandowski2, Dawn Wahezi1, Christiaan Scott3 and Angela Migowa4, 1Children's Hospital at Montefiore, New York, NY, 2NIAMS, NIH, Bethesda, MD, 3Red Cross War Memorial Children's Hospital, 4Aga Khan University, Nairobi, Kenya

    Background/Purpose: There is a paucity of data on pediatric rheumatic disease (PRD) in low and middle-income countries (LMIC), creating a false perception of low prevalence…
  • Abstract Number: 023 • 2023 Pediatric Rheumatology Symposium

    Effect of Type 1 Interferons and JAK Inhibitors on Gene Expression in Bioengineered Pediatric Skeletal Muscle

    Lauren Covert1, Joseph Prinz2, Hailee Patel3, Jeffrey Dvergsten4 and George Truskey3, 1Duke University, Durham, NC, 2Duke University School of Medicine, Department of Biostatistics and Bioinformatics, Durham, NC, 3Duke University, Department of Biomedical Engineering, Durham, NC, 4Duke University Hospital, Durham, NC

    Background/Purpose: Genetic studies of new-onset juvenile dermatomyositis (JDM) exhibit elevation of Type 1 interferons (IFN 1) IFNα and IFNβ in blood, skin, and muscle. To…
  • Abstract Number: 018 • 2023 Pediatric Rheumatology Symposium

    Using the Electronic Health Record to Identify Subjects with Rheumatic Disease

    Alysha Taxter1, Matthew Basiaga2, Rajdeep Pooni3, Caitlan Pinotti4, Lisa Buckley5 and CARRA Registry Investigators6, 1Nationwide Children's Hospital, Columbus, OH, 2Mayo Clinic, Rochester, MN, 3Stanford University, Palo Alto, CA, 4Duke, Durham, NC, 5Vanderbilt University Medical Center, Nashville, TN, 6CARRA, Washington, DC

    Background/Purpose: Research teams spend hours manually searching the electronic health records (EHRs) to identify potential candidates eligible for recruitment to the Childhood Arthritis and Rheumatology…
  • Abstract Number: 008 • 2023 Pediatric Rheumatology Symposium

    Treatment Response and Outcomes of 63 Cases of Juvenile Dermatomyositis-Associated Calcinosis

    Belina Yi1, Dawn Wahezi2, Lauren Covert3, Kaveh Ardalan4, Joyce Hui-Yuen5, Natalia Vasquez Canizares2, Doaa Mosad Mosa6, Madison Jones7, Colleen Correll8, Alexis Begezda9, Susan Shenoi10, Eveline Wu11, Leonard Kovalick12, William Lapin13, Stacey Tarvin14, Melissa Oliver15, Martha Rodriguez14, Itay Marmor16, Kevin Baszis17, Alysha Taxter18, Andrew Hanson19, Cynthia Crowson19 and Amir Orandi19, 1Children's Hospital Los Angeles, Los Angeles, CA, 2Children's Hospital at Montefiore, New York, NY, 3Duke University, Durham, NC, 4Duke University School of Medicine, Durham, NC, 5Cohen Children's Medical Center, Northwell Health, Lake Success, New York; Center for Autoimmune, Musculoskeletal, and Hematopoietic Diseases Research, Feinstein Institutes for Medical Research, Northwell Health, Manhasset, NY, 6Mansoura University Hospitals, Mansoura University Faculty of Medicine, El Mansoura, Egypt, 7Keck School of Medicine at University of Southern California, Los Angeles, CCA, 8University of Minnesota, Minneapolis, MN, 9Penn State, State College, PA, 10Seattle Children's Hospital, Seattle, WA, 11UNC Chapel Hill, Chapel Hill, NC, 12UNC Health Care, Durham, NC, 13Connecticut Children's, Hartford, CT, 14Riley Hospital for Children at Indiana University Health, Indianapolis, IN, 15Indiana University, Indianapolis, IN, 16Dana-Dwek Children's Hospital, Hod Hasharon, Israel, 17Washington University School of Medicine, St Louis, MO, 18Nationwide Children's Hospital, Columbus, OH, 19Mayo Clinic, Rochester, MN

    Background/Purpose: Calcinosis is a poorly understood and morbid complication of juvenile dermatomyositis (JDM). As there is no consensus treatment approach for calcinosis, and limited knowledge…
  • Abstract Number: 004 • 2023 Pediatric Rheumatology Symposium

    Analysis of Patients with Juvenile Dermatomyositis Compared to Healthy Controls Using CITE-seq Identifies Differences in Cell Composition and Gene and Epitope Expression

    Camilla Wibrand1, Emily Flynn2, Gabrielle Rabadam2, George Hartoularos2, Yang Sun2, Chun Ye2, Susan Kim3, Marina Sirota2 and Jessica Neely1, 1UCSF, San Francisco, CA, 2University of California, San Francisco, San Francisco, CA, 3UCSF Benioff Children's Hospital, San Francisco, CA

    Background/Purpose: Juvenile dermatomyositis (JDM) is a rare and serious systemic autoimmune condition, and much remains unknown about the pathogenesis, the immune cell types and cell-specific…
  • Abstract Number: 064 • 2023 Pediatric Rheumatology Symposium

    Towards the Development of Composite Parent-Centered Disease Activity Scores for Juvenile Dermatomyositis

    Silvia Rosina1, Ana Isabel Rebollo-Giménez2, Letizia Tarantola3, Roberta Naddei4, Alessandro Consolaro2, Angela Pistorio5 and Angelo Ravelli6, 1IRCCS Istituto Giannina Gaslini, Genova, Italy, 2IRCCS Istituto Giannina Gaslini, UOC Reumatologia e Malattie Infiammatorie, Genova, Italy, 3Università degli Studi di Genova, Dipartimento di Neuroscienze, Riabilitazione, Oftalmologia, Genetica e Scienze Materno-Infantili (DiNOGMI), Genova, Italy, 4Università degli Studi di Napoli Federico II, Dipartimento di Scienze Mediche Traslazionali, Napoli, Italy, 5IRCCS Istituto Giannina Gaslini, Direzione Scientifica, Genova, Italy, 6IRRCS Istituto Giannina Gaslini and Università degli Studi di Genova, Genova, Italy

    Background/Purpose: Increasing attention has been recently paid to the development of parent- and child-centered composite DAS for the assessment of health status of children with…
  • Abstract Number: 066 • 2023 Pediatric Rheumatology Symposium

    Telemedicine Use in the Assessment of Juvenile Myositis: A Mixed-Methods Study of an International Healthcare Provider Experience

    Y. Ingrid Goh1, Peter Blier2, Bianca Lang3, Marietta De Guzman4, Julie Fuller5, Kristin Houghton6, Kathryn Cook7, Susan Kim8, Vanessa Carbone1, Heather Tory9, Jo-Anne Marcuz1, Albert Chow10, Liza McCann11, Charalampia Papadopoulou12, Clarissa Pilkington13 and Stacey Tarvin14, 1The Hospital for Sick Children, Toronto, ON, Canada, 2Retired, Amherst, MA, 3Dalhousie University - Halifax, Halifax, NS, Canada, 4Baylor College of Medicine, Texas Children's Hospital, Houston, TX, 5UT Southwestern, Dallas, TX, 6University of British Columbia, Vancouver, BC, Canada, 7Akron Children's Hospital, Akron, OH, 8UCSF Benioff Children's Hospital, San Francisco, CA, 9Connecticut Children's Medical Center, S Glastonbury, CT, 10Loma Linda University, Loma Linda, CA, 11Alder Hey Children's NHS Foundation Trust, Liverpool, United Kingdom, 12UCL Institute of Child Health, and Great Ormond Street Hospital NHS Foundation Trust, Section Head Infection, Immunology, and Rheumatology, London, United Kingdom, 13Great Ormond Street Hospital, London, United Kingdom, 14Riley Hospital for Children at Indiana University Health, Indianapolis, IN

    Background/Purpose: Care of patients with juvenile myositis (JM) involves complex assessments performed by specialized healthcare providers (HCPs). Restrictions during the COVID-19 pandemic required the rapid…
  • Abstract Number: 070 • 2023 Pediatric Rheumatology Symposium

    The Impact of the COVID-19 Pandemic on Patients with Juvenile Idiopathic Inflammatory Myopathies

    Dawn Wahezi1, Dominique Jerome1, Evin Rothschild1, Jeffrey Dvergsten2, Stacey Tarvin3, Susan Kim4 and Tamar Rubinstein1, 1Children's Hospital at Montefiore, New York, NY, 2Duke University Hospital, Durham, NC, 3Riley Hospital for Children at Indiana University Health, Indianapolis, IN, 4UCSF Benioff Children's Hospital, San Francisco, CA

    Background/Purpose: Since the onset of the COVID-19 pandemic, there have been concerns regarding the risks of SARS-CoV-2 infection in patients with juvenile idiopathic inflammatory myopathies…
  • Abstract Number: 086 • 2023 Pediatric Rheumatology Symposium

    Systemic Sclerosis Overlap Syndrome: A Case Series from a Single Large Pediatric Center

    Jessica Nguyen1, Miriah Gillispie-Taylor1, Eyal Muscal1 and Marietta Deguzman2, 1Baylor College of Medicine, Houston, TX, 2Baylor College of Medicine, Texas Children's Hospital, Houston, TX

    Background/Purpose: Childhood-onset systemic sclerosis (SSc) is a rare but potentially life-threatening autoimmune condition with features including immune, fibrotic, and vascular manifestations affecting the skin and…
  • Abstract Number: 099 • 2023 Pediatric Rheumatology Symposium

    The Impact of the COVID-19 Pandemic on Juvenile Dermatomyositis

    Tresa Ambooken1, Sangati Kadakia1, Tara Lozy1, Brianna Bulbin2, Suhas Ganguli3, Dawn Wahezi4 and Sivia Lapidus1, 1Department of Pediatrics, Joseph M. Sanzari Children's Hospital, Hackensack University Medical Center, Hackensack, NJ, 2Hackensack Meridian School of Medicine, Hackensack, NJ, 3Department of Pediatrics, K. Hovnanian Children's Hospital, Jersey Shore University Medical Center, Neptune City, NJ, 4Children's Hospital at Montefiore, New York, NY

    Background/Purpose: Juvenile Dermatomyositis (JDM) is theorized to occur in a genetically susceptible individual as a response to an environmental trigger, leading to autoimmunity and inflammation.…
  • Abstract Number: 100 • 2023 Pediatric Rheumatology Symposium

    The Brazilian Registry of Juvenile Dermatomyositis (JDM): II – A Longitudinal Assessment of Muscle Strength by Manual Muscle Test (MMT) and Childhood Myositis Assessment Scale (CMAS) Tools

    Darcisio Antonio1, Taciana Fernandes1, Adriana Elias2, Teresa Robazzi3, Ana Julia Moraes4, Sheila Oliveira5, Flavio Sztajnbok6, Luciana Carvalho7, Luciana Marques8, Silvana Sacchetti9, Maria Teresa Terreri10, Simone Appenzelle11, Roberto Marini12, Carlos Rabello Jr13, Cristina Magalhaes14, Melissa Fraga15, Marcia Bandeira16, Iloite Scheibel17, Isabela Daud2, Beatriz Carneiro2, Claudio Len18, Clovis Silva19 and Claudia Magalhaes20, 1Universidade Estadual Paulista (UNESP) Botucatu, Brazil, 2Instituto da Criança - Universidade de São Paulo (USP), São Paulo, Brazil, 3Universidade Federal da Bahia, Brazil, 4Universidade Federal do Para, Brazil, 5Universidade Federal do Rio de janeiro, Rio de Janeiro, 6Universidade Estadual do Rio de Janeiro, Rio de Janeiro, Brazil, 7Universidade de Sao Paulo- Ribeirao Preto, São Paulo, Brazil, 8Hospital Albert Sabin, Brazil, 9Santa Casa de Sao Paulo, Brazil, 10UNIFESP, São Paulo, Brazil, 11University of Campinas, Campinas, Sao Paulo, Brazil, 12UNICAMP, São Paulo, Brazil, 13Hospital Geral de Fortaleza, Brazil, 14Hospital Jose de Alencar - Brasilia, Brazil, 15Hospital Darcy Vargas, Brazil, 16Hospital Pequeno Principe- Curitiba, Brazil, 17Hospital Conceição de Porto Alegre, Brazil, 18Universidade Federal de São Paulo - Unifesp, São Paulo, Brazil, 19Universidade de São Paulo, São Paulo, Brazil, 20São Paulo State University, Pediatric Rheumatology Division, Botucatu, Brazil

    Background/Purpose: Muscle weakness is often progressive and persistent in Juvenile Dermatomyositis (JDM). Muscle strength testing is useful for evaluating severity of muscle weakness. There is…
  • Abstract Number: 101 • 2023 Pediatric Rheumatology Symposium

    Differences in Clinical and Patient-reported Outcomes in Juvenile Dermatomyositis by Race and Ethnicity

    Susan Kim1, Rebecca Olveda2 and Jessica Neely2, 1UCSF Benioff Children's Hospital, San Francisco, CA, 2UCSF, San Francisco, CA

    Background/Purpose: Previous studies in juvenile dermatomyositis (JDM) have shown that patients from minoritized ethnicities and those with lower family income are more likely to have…
  • Abstract Number: 120 • 2023 Pediatric Rheumatology Symposium

    The Brazilian Registry of Juvenile Dermatomyositis (JDM): I- Onset Clinical Features and Disease Activity Scores by DAS-20 over 2-Years-Follow Up

    Beatriz Carneiro1, Adriana Elias1, Teresa Robazzi2, Ana Julia Moraes3, Sheila Oliveira4, Flavio Sztajnbok5, Luciana Carvalho6, Luciana Marques7, Silvana Sacchetti8, Maria Teresa Terreri9, Simone Appenzelle10, Roberto Marini11, Andre Cavalcante12, Marcia Bandeira13, Cristina Magalhaes14, Melissa Fraga15, Iloite Scheibel16, Isabela Daud1, Darcisio Antonio17, Claudio Len18, Clovis Silva19, Taciana Fernandes17 and Claudia Magalhaes20, 1Instituto da Criança - Universidade de São Paulo (USP), São Paulo, Brazil, 2Universidade Federal da Bahia, Brazil, 3Universidade Federal do Para, Brazil, 4Universidade Federal do Rio de janeiro, Rio de Janeiro, 5Universidade Estadual do Rio de Janeiro, Rio de Janeiro, Brazil, 6Universidade de Sao Paulo- Ribeirao Preto, São Paulo, Brazil, 7Hospital Albert Sabin, Brazil, 8Santa Casa de Sao Paulo, Brazil, 9UNIFESP, São Paulo, Brazil, 10University of Campinas, Campinas, Sao Paulo, Brazil, 11UNICAMP, São Paulo, Brazil, 12Hospital Materno-Infantil de Goiania, Brazil, 13Hospital Pequeno Principe- Curitiba, Brazil, 14Hospital Jose de Alencar - Brasilia, Brazil, 15Hospital Darcy Vargas, Brazil, 16Hospital Conceição de Porto Alegre, Brazil, 17Universidade Estadual Paulista (UNESP) Botucatu, Brazil, 18Universidade Federal de São Paulo - Unifesp, São Paulo, Brazil, 19Universidade de São Paulo, São Paulo, Brazil, 20São Paulo State University, Pediatric Rheumatology Division, Botucatu, Brazil

    Background/Purpose: A national registry was set up, enrolling new onset JDM cases in 18 hospitals, during 3-years (2015-2018) with 2-years follow up, in a low…
  • Abstract Number: 028 • 2023 Pediatric Rheumatology Symposium

    Achieving Medication-Free Remission in Juvenile Dermatomyositis

    Harneet Ghumman1, Ilaria Maccora2, Hermine Brunner1, Amy Cassedy3, Mekibib Altaye2, Asra Firdous1, Alexei Grom1, Daniel Lovell1, Angela Merritt1, Megan Quinlan-Waters1 and Sheila Angeles-Han2, 1Cincinnati Children's Hospital Medical Center, Cincinnati, OH, 2Cincinnati Children's Hospital, Cincinnati, OH, 3Cincinnati Children's Hospital Medical Center, Cincinnati, OH

    Background/Purpose: Juvenile dermatomyositis (JDM) is characterized by symmetric proximal muscle weakness, distinct rash, and a risk for calcinosis. Systemic immunosuppression is needed. Evidence is limited…
  • Abstract Number: 0173 • ACR Convergence 2022

    Cutaneous Manifestations, Clinical Trials, Safety Efficacy and Safety of Lenabasum in the Phase 3 DeterMine Trial in Dermatomyositis

    Victoria Werth1, Barbara White2, Josef Concha3, Josh Dan1, Nancy Dgetluck2, Kathleen Hally2, Scott Constantine2, Rohit Aggarwal4, David Fiorentino5, Ingrid Lundberg6 and Chester Oddis7, 1Philadelphia VAMC, Philadelphia, PA, USA and Department of Dermatology, Perelman School of Medicine at the University of Pennsylvania, Philadelphia, 2Corbus Pharmaceuticals, Norwood, MA, 3Universiity of Pennsylvania/Dermatology, Philadelphia, PA, 4University of Pittsburgh, Division of Rheumatology, Pittsburgh, PA, 5Stanford university/Department of Dermatology, Palo Alto, CA, 6Karolinska Institute, Stockholm, Sweden, 7University of Pittsburgh, Pittsburgh, PA

    Background/Purpose: Safe and effective treatments are of significant unmet need in DM. Lenabasum, a CB2 agonist that activates resolution of inflammation, improved skin disease, patient-reported…
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