ACR Meeting Abstracts

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Abstracts tagged "Behcet’s syndrome"

  • Abstract Number: 016 • 2020 Pediatric Rheumatology Symposium

    Genetic Susceptibility Loci for Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Adenitis (PFAPA) Syndrome

    Kalpana Manthiram1, Silvia Preite 2, Fatma Dedeoglu 3, Selcan Demir 4, Seza Ozen 5, Kathryn Edwards 6, Sivia Lapidus 7, Alexander Katz 2, Henry Feder 8, Maranda Lawton 3, Greg Licameli 3, Peter Wright 9, Karyl Barron 2, Amanda Ombrello 2, Beverly Barham 2, Tina Romeo 10, Anne Jones 11, Hemalatha Srinivasalu 12, Pamela Mudd 12, Roberta DeBiasi 12, Ahmet Gul 13, Gary Marshall 14, Olcay Jones 15, Yuriy Stepanovskiy 16, Polly Ferguson 17, Pamela Schwartzberg 2, Elaine Remmers 2 and Daniel Kastner 18, 1National Institutes of Health, Bethesda, Maryland, 2National Institutes of Health, Bethesda, 3Boston Children's Hospital, Boston, 4Hacettepe University, Division of Pediatric Rheumatology, Department of Pediatrics, Faculty of Medicine, Ankara, Turkey, 5Hacettepe University, Division of Pediatric Rheumatology, Department of Pediatrics, Faculty of Medicine, 6Vanderbilt University School of Medicine, Nashville, 7The Joseph M. Sanzari Children's Hospital, Hackensack Meridian Health, Maplewood, 8Connecticut Children's Medical Center, Hartford, 9Dartmouth-Hitchcock Medical Center, Lebanon, 10NIH, Bethesda, 11Bethesda, 12Children's National Medical Center, Washington, 13Istanbul University, Istanbul, Turkey, 14University of Louisville School of Medicine, Louisville, 15Walter Reed National Military Medical Center, Bethesda, 16Shupyk National Medical Academy of Postgraduate Education, Kiev, 17University of Iowa Carver College of Medicine, Iowa City, 18National Human Genome Research Institute, Bethesda

    Background/Purpose: Periodic fever, aphthous stomatitis, pharyngitis, cervical adenitis (PFAPA) syndrome is the most common periodic fever syndrome of childhood. Although familial clustering of the disease…
  • Abstract Number: 1691 • 2019 ACR/ARP Annual Meeting

    Efficacy of TNF α Inhibitors for Refractory Vascular Behcet’s Disease: A Multicenter Observational Study of 27 Patients

    Aysun Aksoy 1, Ayten Yazici 2, Ahmet Omma 3, Ayşe Cefle 4, Fatos Onen 5, Unal Tasdemir 6, Tulin Ergun 7, Haner Direskeneli 8 and Fatma Alibaz-Oner9, 1Marmara University Faculty of Medicine, Division of Internal Medicine, Department of Rheumatology, Istanbul, Turkey; University of Manchester, Division of Musculoskeletal and Dermatological Sciences, Manchester, United Kingdom, Istanbul, Istanbul, Turkey, 2Kocaeli University, Faculty of Medicine, Division of Rheumatology, Kocaeli, Kocaeli, Turkey, 3Health Sciences University, Ankara Numune Training and Research Hospital, Department of Rheumatology, Ankara, Turkey, 4Division of Rheumatology, Kocaeli University School of Medicine, Kocaeli, Turkey, Kocaeli, Turkey, 5Dokuz Eylul University School of Medicine, Division of Rheumatology, İzmir, Turkey, 6Dokuz Eylul University, School of Medicine Division of Internal Medicine Rheumatology Department, izmir, Turkey, 7Marmara University School of Medicine Dermatology Department, istanbul, Turkey, 8Marmara University, School of Medicine, Division of Rheumatology, Istanbul, Turkey, 9Marmara University Faculty of Medicine,Department of Rheumatology,Istanbul,Turkey, Istanbul, Turkey

    Background/Purpose: Vascular involvement is one of the major causes of morbidity and mortality in Behcet’s Disease (BD) patients. Immunosuppressive (IS) agents are the mainstay of…
  • Abstract Number: 1694 • 2019 ACR/ARP Annual Meeting

    Pharmacogenetics and Pharmacodynamics of Response to Apremilast in a Phase 3 Clinical Study in Subjects with Active Behçet’s Disease

    Joseph Maranville1, Irina Medvedeva 1, Robert Yang 1, Mindy Chen 2, Lorraine (Ruoying) Fang 2, Sandra Collazo 3, Shannon McCue 3, Marla Hochfeld 3 and Peter Schafer 3, 1Celgene Corporation, Cambridge, MA, 2Celgene Corporation, Berkeley Heights, NJ, 3Celgene Corporation, Summit, NJ

    Background/Purpose: This was an exploratory analysis of genetic polymorphisms, plasma biomarkers, and blood leukocytes with clinical response in the phase 3 clinical study CC-10004-BCT-002 (NCT02307513).Methods:…
  • Abstract Number: 1695 • 2019 ACR/ARP Annual Meeting

    Apremilast in Combination vs Monotherapy for Refractory Oral And/or Genital Ulcers in Behçet’s Disease: National Multicenter Study of 51 Cases

    Belén Atienza-Mateo1, Mónica Calderón-Goercke 2, DIANA PRIETO- PENA 3, Iñigo Gonzalez-Mazon 3, Lara Sanchez-Bilbao 1, Jose Luis Martín-Varillas 1, Javier Loricera 4, Vanesa Calvo Río 1, Jenaro Graña 5, Gerard Espinosa 6, Clara Moriano 7, Trinidad Pérez-Sandoval 7, Manuel Martín-Martínez 7, Elvira Díez 7, María Dolores García-Armario 8, Esperanza Martínez 8, Ivan Castellvi 9, Patricia Moya Alvarado 10, Francisca Sivera 11, Jaime Calvo-Alen 12, Isabel de la Morena 13, Francisco Ortiz-Sanjuán 14, José Andrés Román-Ivorra 14, Ana Pérez-Gómez 15, Sergi Heredia 16, Alejandro Olivé-Marqués 16, Águeda Prior-Español 17, Carolina Díez 18, Juan José Alegre-Sancho 19, Amparo Ybáñez 19, Ángels Martínez-Ferrer 19, Javier Narváez 20, Ignasi Figeras 21, Ana Turrión 22, Susana Romero-Yuste 23, Pilar Trénor 24, Soledad Ojeda 25, Miguel Á. González-Gay 26 and Ricardo Blanco 26, 1Rheumatology, Hospital Universitario Marques de Valdecilla, Santander, Spain, 2Hospital Marqués de Valdecilla, Santander, Cantabria, Spain, 3Rheumatology, Hospital Universitario Marques de Valdecilla, Santander, Cantabria, Spain, 4Rheumatology Department. Hospital Marqués de Valdecilla, Santander, Cantabria, Spain, 5Centro Médico Quirón A Coruña, A Coruña, Galicia, Spain, 6Department of Autoimmune Diseases, Hospital Clínic, Barcelona, Barcelona, Catalonia, Spain, 7Complejo Asistencial Universitario de León, León, Castilla y Leon, Spain, 8Hospital Lluís Alcanyís, Xàtiva, Comunidad Valenciana, Spain, 9Hospital de la Santa Creu i Sant Pau, Barcelona, Spain, 10Hospital de la Santa Creu i Sant Pau, Barcelona, Catalonia, Spain, 11Hospital General Universitario de Elda, Elda, Spain, 12Hospital Universitario Araba, Vitoria-Gasteiz, Spain, 13Hospital General Universitario de Valencia, Valencia, Comunidad Valenciana, Spain, 14Hospital Universitario y Politécnico La Fe, Valencia, Comunidad Valenciana, Spain, 15Hospital Universitario Príncipe de Asturias, Alcalá de Henares, Madrid, Spain, 16Hospital Universitari Germans Trias i Pujol, Badalona, Catalonia, Spain, 17Hospital Universitari Germans Trias i Pujol, Badalona, Spain, 18Hospital de El Bierzo, León, Castilla y Leon, Spain, 19Hospital Universitario Doctor Peset, Valencia, Comunidad Valenciana, Spain, 20Rheumatology Department, Hospital Universitari de Bellvitge, Barcelona, Catalonia, Spain, 21Hospital Bellvitge, Barcelona, Catalonia, Spain, 22Hospital Clínico Universitario de Salamanca, Salamanca, Spain, 23Complejo Hospitalario Universitario Pontevedra, Pontevedra, Galicia, Spain, 24Hospital Clínico Universitario de Valencia, Valencia, Comunidad Valenciana, Spain, 25Hospital Doctor Negrín, Las Palmas de Gran Canaria, Canarias, Spain, 26Hospital Universitario Marqués de Valdecilla, Santander, Cantabria, Spain

    Background/Purpose: Oral and/or genital aphthous ulcers are the most common symptoms of Behçet´s disease (BD), and are often refractory to conventional treatment. The inhibitor of…
  • Abstract Number: 1696 • 2019 ACR/ARP Annual Meeting

    Is the Risk of Tuberculosis Increased in Behçet’s Disease Compared to Other Rheumatological Disorders After Anti-TNF-α Treatment?

    Ummugulsum Gazel 1, Derya Kocakaya 2, Irem Topcu 3, Hakan Karatas 4, Murat Karabacak 5, Pamir Atagunduz 6, Nevsun Inanc 7, Fatma Alibaz-Oner 5 and Haner Direskeneli8, 1Marmara University, Faculty of Medicine, Department of Rheumatology, Istanbul, Turkey, Istanbul, Turkey, 2Marmara University Faculty of Medicine Department of Chest Diseases, Istanbul, Turkey, Istanbul, Istanbul, Turkey, 3Marmara University, School of Medicine, Istanbul,Turkey, ıstanvul, Turkey, 4Marmara University ,School of Medicine, Istanbul,Turkey, Istanbul, Turkey, 5Marmara University Faculty of Medicine,Department of Rheumatology,Istanbul,Turkey, Istanbul, Turkey, 6Marmara University Faculty of Medicine,Department of Rheumatology, Istanbul, Turkey, Istanbul, Turkey, 7Marmara University, Faculty of Medicine, Division of Rheumatology, Istanbul, Turkey, ISTANBUL, Turkey, 8Marmara University, School of Medicine, Division of Rheumatology, Istanbul, Turkey

    Background/Purpose: Tumor necrosis factor (TNF)-α inhibitors are extensively utilized in the treatment of inflammatory rheumatic diseases. These agents increase the risk of tuberculosis (TB), especially…
  • Abstract Number: 1697 • 2019 ACR/ARP Annual Meeting

    Efficacy of Apremilast for Oral Ulcers Associated with Active Behçet’s Syndrome over 64 Weeks: Long-term Results from the Japanese Subgroup in a Phase III Study

    Mitsuhiro Takeno1, Yoshiya Tanaka 2, Hajime Kono 3, Shoji Sugii 4, Mitsumasa Kishimoto 5, Sue Cheng 6, Shannon McCue 7, Mindy Chen 8, Maria Paris 6 and Hiroaki Dobashi 9, 1Nippon Medical School, Tokyo, Japan, 2University of Occupational and Environmental Health Japan, Kitakyushu, Japan, 3Teikyo University School of Medicine, Tokyo, Japan, 4Department of Rheumatic Diseases, Tokyo Metropoitan Tama Medica Center, Fuchu, Japan, 5Immuno-Rheumatology Center, St. Luke’s International Hospital, Tokyo, Japan, 6Celgene Corporation, Summit, 7Celgene Corporation, Summit, NJ, 8Celgene Corporation, Berkeley Heights, NJ, 9Kagawa University, Kagawa, Japan

    Background/Purpose: Behçet’s syndrome is a chronic, multi-system, variable vessel vasculitis characterized by painful, recurrent oral ulcers (OU) that can be disabling and may impair quality…
  • Abstract Number: 1698 • 2019 ACR/ARP Annual Meeting

    Development of Machine Learning Models (Artificial Neural Networks) for Prediction of Vision Threatening Behçet’s Disease

    Nevin Hammam1, Eiman Abd El-Latif 2, Iman I El-Gazzar 3, Nermeen Samy 4, Rasha A Abdel Noor 5, Emad El-Shebeiny 6, Amany R El-Najjar 7, Nahla N Eesa 8, Mohamed N Salem 9, Soha E Ibrahim 10, Dina F El-Essawi 11, Ahmed M Elsaman 12, Hanan M Fathi 13, Rehab A Sallam 14, Rawhya R El-Shereef 15, Mervat I Abd-Elazeem 16, Emtethal A Said 17, Noha M Khalil 18, Dina Shahin 19, Hanan M El-Saadany 20, Marwa S ElKhalifa 21, Samah I Nasef 22, Ahmed M Abdalla 23, Nermeen Noshy 4, Rasha M Fawzy 24, Ehab Saad 25, Abdel-Hafeez Moshrif 26, Amira T El-Shanawany 27, Yousra H Abdel-Fattah 28, Hossam M Khalil 29 and Tamer A Gheita 30, 1University of Alberta, Edmonton, AB, Canada, 2Ophthalmology Department, Faculty of Medicine, Alexandria University, Alexandria, Egypt, Alexandria, Egypt, 3Rheumatology Department, Faculty of Medicine, Cairo University, Cairo, Egypt, Cairo, Egypt, 4Internal Medicine Department, Rheumatology Unit, Faculty of Medicine, Ain-Shams University, Cairo, Egypt, Cairo, Egypt, 5Internal Medicine Department, Rheumatology Unit, Tanta University, Gharbia, Egypt, Gharbia, Egypt, 6Internal Medicine Department, Rheumatology Unit, Menoufia University, Menoufia, Egypt, Menoufia, Egypt, 7Rheumatology Department, Faculty of Medicine, Zagazig University, Sharkia, Egypt, Sharkia, Egypt, 8Rheumatology Department, Faculty of Medicine, Cairo University, Cairo, Egypt., Cairo, Egypt, 9Internal Medicine Department, Rheumatology Unit, Faculty of Medicine, Beni-Suef University, Beni-Suef, Egypt, Beni-Suef, Egypt, 10Rheumatology Department, Faculty of Medicine, Ain Shams University, Cairo, Egypt, Cairo, Egypt, 11Internal Medicine Department, Rheumatology Unit (NCRRT), Atomic Energy Authority (AEA), Cairo, Egypt, Cairo, Egypt, 12Rheumatology Department, Faculty of Medicine, Sohag University, Sohag, Egypt., Sohag, Egypt, 13Rheumatology Department, Faculty of Medicine, Fayoum University, Fayoum, Egypt, Fayoum, Egypt, 14Rheumatology Department, Faculty of Medicine, Mansoura University, Dakahlia, Egypt, Dakahlia, Egypt, 15Rheumatology Department, Faculty of Medicine, Minia University, Minia, Egypt., Minia, Egypt, 16Rheumatology Department, Faculty of Medicine, Beni-Suef University, Beni-Suef, Egypt, Beni-Suef, Egypt, 17Rheumatology Department, Faculty of Medicine, Benha University, Kalubia, Egypt, Benha, Egypt, 18Internal Medicine Department, Rheumatology Unit, Faculty of Medicine, Cairo University, Cairo, Egypt, Cairo, Egypt, 19Internal Medicine Department, Rheumatology Unit, Faculty of Medicine, Mansoura University, Dakahlia, Egypt, Dakahlia, Egypt, 20Rheumatology Department, Faculty of Medicine, Tanta University, Tanta, Egypt, Tanta, Egypt, 21Internal Medicine Department, Rheumatology Unit, Faculty of Medicine, Alexandria University, Alexandria, Egypt, Alexandria, Egypt, 22Rheumatology Department, Faculty of Medicine, Suez-Canal University, Ismailia, Egypt, Ismailia, Egypt, 23Rheumatology Department, Faculty of Medicine, Aswan University, Aswan, Egypt, Aswan, Egypt, 24Rheumatology Department, Faculty of Medicine, Benha University, Kalubia, Egypt, Kalubia, Egypt, 25Rheumatology Department, Faculty of Medicine, South Valley University, Qena, Egypt, Qena, Egypt, 26Rheumatology Department, Faculty of Medicine, Al-Azhar University, Assuit, Egypt, Assiut, Egypt, 27Rheumatology Department, Faculty of Medicine, Menoufia University, Menoufia, Egypt, Menoufia, Egypt, 28Rheumatology Department, Faculty of Medicine, Alexandria University, Alexandria, Egypt, Alexandria, Egypt, 29Ophthalmology Department, Faculty of Medicine, Beni-Suef University, Beni-Suef, Egypt., Beni-Suef, Egypt, 30Rheumatology Department, Kasr Al Ainy School of Medicine, Cairo University, Cairo, Egypt., Cairo, Egypt

    Background/Purpose: Ocular involvement in Behçet’s Disease (BD) is associated with chronic damage and high morbidity; however, limited evidence is available on risk factors to recognize…
  • Abstract Number: 1699 • 2019 ACR/ARP Annual Meeting

    Disease Course of Behçet’s Syndrome Patients Not Fulfilling International Study Group Criteria at Presentation

    Sinem Nihal Esatoglu1, Seyda Bilgin 2, Cem Sulu 2, Vedat Hamuryudan 3, Zekayi Kutlubay 4, Melike Melikoglu 3, Izzet Fresko 5, Hasan Yazici 6 and Gulen Hatemi 7, 1Istanbul University-Cerrahpasa, Cerrahpasa Medical Faculty, Department of Internal Medicine, Division of Rheumatology, Istanbul, Turkey, 2Istanbul University-Cerrahpasa, Cerrahpasa Medical Faculty, Department of Internal Medicine, Istanbul, Turkey, 3Istanbul University-Cerrahpasa, Cerrahpasa Medical Faculty, Department of Internal Medicine, Division of Rheumatology, Istanbul University – Cerrahpasa, Behçet’s Disease Research Center, Istanbul, Turkey, Istanbul, Turkey, 4Istanbul University-Cerrahpasa, Cerrahpasa Medical Faculty, Department of Dermatology, Istanbul University – Cerrahpasa, Behçet’s Disease Research Center, Istanbul, Turkey, Istanbul, Turkey, 5Istanbul University-Cerrahpasa, Cerrahpasa Medical Faculty, Department of Internal Medicine, Division of Rheumatology, Istanbul University – Cerrahpasa, Behçet’s Disease Research Center, Istanbul, Turkey, 6Academic Hospital, Istanbul, Turkey, Istanbul, Turkey, 7Istanbul University-Cerrahpasa, Cerrahpasa Medical Faculty, Department of Internal Medicine, Division of Rheumatology, Istanbul University-Cerrahpasa, Behcet's Disease Research Center, Istanbul, Turkey, Istanbul, Turkey

    Background/Purpose: Behçet’s syndrome (BS) shows a heterogeneous phenotype involving many organ systems and is diagnosed by recognizing the coexisting manifestations. Patients may have major organ…
  • Abstract Number: 1700 • 2019 ACR/ARP Annual Meeting

    Clinical Characteristics and the Level Disease Activity of Behcet´s Disease in China: A Study Based on Smart System of Disease Management (SSDM)

    Lingli Dong1, Shouxin Li 1, Fen Wang 2, Zhenbiao Wu 3, Shengtao Zhang 1, Qin Li 4, Henglian Wu 5, Zhengang Wang 6, Huifang Guo 7, Yikai Yu 1, LingXun Shen 8, Yasong Li 9, Yang Liu 10, Tian Wang 11, Peng Ji 12, Zongwen Shuai 2, Hongbin Li 13, Li Luo 12, Hui Xiao 14, Yuhua Jia 15, Bing Wu 16, Shengsong Jia 15, Fei Xiao 17 and Lijun Wu 18, 1Tongji Hospital,Tongji Medical Colllege,Huazhong University of Science and Technology, Wuhan, Hubei, China (People's Republic), 2First Affiliated Hospital of Medical University Of Anhui, Hefei, Anhui, China (People's Republic), 3The First Affiliated Hospital of The Fourth Military Medical University, Xian, Shanxi, China (People's Republic), 4The First People's Hospital of Yunnan Province, Kunming, Yunnan, China (People's Republic), 5Dongguan donghua hospital, Dongguan, Guangdong, China (People's Republic), 6TongRen hospital,Capital University, Bei Jing, China (People's Republic), 7The Second Hospital of Hebei Medical University, Shijiazhuang, Hebei, China (People's Republic), 8Union Hospital Affiliated Tongji Medical College of Huazhong University of Science and Technology, Wuhan, China (People's Republic), 9Zhejiang provincial people's hospital, Hangzhou, Zhejiang, China (People's Republic), 10Affiliated Hospital of Inner Mongolia Medical University, Huhehaote, Nei Mongol, China (People's Republic), 11Beijing Anzhen Hospital, Capital Medical University, Beijing, Beijing, China (People's Republic), 12The first affiliated hospital of xinjiang medical university, Urumchi, China (People's Republic), 13The Affiliated Hospital of Inner Mongolia Medical University, Huhhot, Nei Mongol, China (People's Republic), 14Shanghai Gothic Internet Technology Co., Ltd, shanghai, Shanghai, China (People's Republic), 15Shanghai Gothic Internet Technology Co., Ltd., Shanghai, Shanghai, China (People's Republic), 16Shanghai Gothic Internet Technology Co., Ltd, Shanghai, China (People's Republic), 17Shanghai Gothic Internet Technology Co., Ltd., shanghai, China (People's Republic), 18People's Hospital of Xinjiang Uygur Autonomous region, Wulumuqi, Xinjiang, China (People's Republic)

    Background/Purpose: Behcet´s disease (BD) is a systemic autoimmune disease that affects multiple organ systems with recurrent oral ulcers, genital ulcers and skin lesions, which might…
  • Abstract Number: 1701 • 2019 ACR/ARP Annual Meeting

    Amyloidosis in Behcet’s Disease: Experience of a Vasculitis Centre at Silk Road

    Ertugrul Cagri Bolek 1, Enes Erul 1, Gozde Kubra Yardımcı 1, Levent Kilic 2, Ali Akdoğan 1 and Omer Karadag3, 1Hacettepe University Vasculitis Centre, Ankara, Turkey, ankara, Turkey, 2Hacettepe University, Faculty of Medicine, Department of Internal Medicine, Division of Rheumatology, Ankara, Turkey, 3Hacettepe University Vasculitis Centre, Ankara, Turkey / Vasculitis and Lupus Clinic, Addenbrooke’s Hospital, University of Cambridge, UK, Ankara, Turkey

    Background/Purpose: Bechet’s disease (BD) is a vasculitis characterized by oral aphtae, genital ulcers, skin lesions, uveitis and with less frequent involvement of the neurological, vascular…
  • Abstract Number: 1705 • 2019 ACR/ARP Annual Meeting

    Cyclophosphamide Therapy for the Neurologic Involvement of Behçet’s Disease – Is It Superior to Azathioprine in Preventing Relapses?

    Priscila Dias Cardoso Ribeiro 1, Eduarda Bonelli Zarur 1, Flávia Maria Matos Melo Campos Peixoto 1, Pedro Matos 1, Pedro Paulo de Alcantara Pedro 1, Rywka Tenenbaum Medeiros Golebiovsk 1, Livia Dutra 2 and Alexandre Wagner de Souza3, 1UNIFESP-EPM, Sao Paulo, Sao Paulo, Brazil, 2Escola Paulista de Medicina (EPM), Brazil, São Paulo, Brazil, 3UNIFESP-EPM, São Paulo, Sao Paulo, Brazil

    Background/Purpose: Neurologic involvement is one of the most serious cause of long-term morbidity and mortality in Behçet’s disease (BD). To date, no controlled trials have…
  • Abstract Number: 1706 • 2019 ACR/ARP Annual Meeting

    HLA-B*51 and Its Subtypes in Brazilian Patients with Behçet’s Disease

    Joice Belem 1, Ana Maria Fraga 2, Luís Eduardo Coelho Andrade 1 and Alexandre Wagner de Souza1, 1UNIFESP-EPM, São Paulo, Sao Paulo, Brazil, 2Fleury Group, São Paulo, Sao Paulo, Brazil

    Background/Purpose: HLA-B*51 is considered the genetic marker mostly associated with Behçet's disease (BD), mainly in countries of the silk route, where its prevalence ranges from…
  • Abstract Number: 1720 • 2019 ACR/ARP Annual Meeting

    Pentoxifylline Gel for Oral Ulcers in Patients with Behçet’s Syndrome

    Gulen Hatemi1, Berna Yurttas 2, Zekayi Kutlubay 3, Tim Cote 4, Semsi Burak Derkunt 4, Yusuf Yazici 5 and Hasan Yazici 6, 1Istanbul University-Cerrahpasa, Cerrahpasa Medical Faculty, Department of Internal Medicine, Division of Rheumatology, Istanbul University-Cerrahpasa, Behcet's Disease Research Center, Istanbul, Turkey, Istanbul, Turkey, 2Istanbul University-Cerrahpasa, Cerrahpasa Medical Faculty, Department of Internal Medicine, Division of Rheumatology, Istanbul University- Cerrahpasa, Behçet's Disease Research Center, Istanbul, Turkey, Istanbul, 3Istanbul University-Cerrahpasa, Cerrahpasa Medical Faculty, Department of Dermatology, Istanbul University – Cerrahpasa, Behçet’s Disease Research Center, Istanbul, Turkey, Istanbul, Turkey, 4Silk Road Therapeutics, Washington, DC, USA, Washington, WA, 5New York University School of Medicine, New York, NY, USA, New York, NY, 6Academic Hospital, Istanbul, Turkey, Istanbul, Turkey

    Background/Purpose: Oral ulcers, the hallmark lesion of Behçet’s syndrome (BS) can be disabling and impair eating, drinking and speaking. Despite recent advances in systemic medications…
  • Abstract Number: 440 • 2019 ACR/ARP Annual Meeting

    Disease Activity and Quality of Life in Behçet’s Syndrome: The Role of Patient Reported Outcome

    Antonio Figliomeni1, Alice Parma 1, Viola Signorini 2, Emanuele Calabresi 1, Rosaria Talarico 1 and Marta Mosca 3, 1Università di Pisa, PISA, Italy, 2Rheumatology Unit, Department of clinical and experimental medicine, University of Pisa, pisa, Toscana, Italy, 3Rheumatology Unit, Department of clinical and experimental medicine, University of Pisa, Pisa, Italy

    Background/Purpose: Behçet’s syndrome (BS) is a systemic vasculitis, characterised by recurrent oro-genital ulcers, ocular inflammation and skin manifestations; articular, vascular, gastro-enteric and neurological involvement may…
  • Abstract Number: 1932 • 2019 ACR/ARP Annual Meeting

    Genetic Evidence for Recent Positive Selection of the HLA-B*51:01 Allele in the Turkish Population, a Population with a High Prevalence of HLA-B*51-Associated Behçet’s Disease

    Elaine Remmers1, Ahmet Gül 2 and Daniel Kastner 1, 1National Human Genome Research Institute, Bethesda, MD, 2Istanbul University, Istanbul Faculty of Medicine, Department of Internal Medicine, Division of Rheumatology, Istanbul, Turkey

    Background/Purpose: The Turkish population has one of the highest world-wide prevalence’s of the genetically complex inflammatory Behçet’s disease (BD), estimated as 4 affected per 1000…
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