Abstract Number: 96 • 2017 Pediatric Rheumatology Symposium
Correlation and Responsiveness of Cutaneous Lupus Disease Area and Severity Index and Skindex-29 with Cutaneous Childhood Lupus Erythematous
Background/Purpose: Characteristic inflammatory cutaneous lesions are common manifestations of children with systemic lupus erythematosus (cSLE); however they are among understudied areas of cSLE. The Cutaneous…Abstract Number: 103 • 2017 Pediatric Rheumatology Symposium
The Performance of a New Risk Assessment Scoring System in Detecting IVIG Resistance in Kawasaki Disease as Compared to the Kobayashi and Egami Scores in a Large Single Centre Canadian Cohort
Background/Purpose: We have shown previously that patients with Kawasaki Disease (KD) resistant to IVIG are at risk for the development of coronary artery abnormalities. Prediction…Abstract Number: 58 • 2017 Pediatric Rheumatology Symposium
Analysis and Implications of Non-Invasive Knee Acoustical Emissions in Juvenile Idiopathic Arthritis
Background/Purpose: Juvenile Idiopathic Arthritis (JIA), the most common chronic rheumatic disease occurring in childhood, is an important cause of disability. Despite the persistence of disease…Abstract Number: 93 • 2017 Pediatric Rheumatology Symposium
Corticosteroid Regimen Use in the Pilot Study of Consensus Treatment Plans for Induction Therapy in Childhood Proliferative Lupus Nephritis
Background/Purpose: Comparative data in the pediatric lupus nephritis (LN) population are lacking. To reduce treatment variability and facilitate comparative effectiveness studies, the Childhood Arthritis and…Abstract Number: 12 • 2017 Pediatric Rheumatology Symposium
Use of Ultrasound to Determine Remission Status in Children with Juvenile Idiopathic Arthritis
Background/Purpose: The ultimate goal for clinicians caring for children with Juvenile idiopathic arthritis (JIA) is to attain disease remission off medications. Correct identification of remission…Abstract Number: 83 • 2017 Pediatric Rheumatology Symposium
Feverprints: A Crowdsourcing Study of Temperature in Health and Disease
Background/Purpose: Autoinflammatory diseases (AIDs) are a rare group of illnesses characterized by unprovoked episodes of fever and systemic inflammation. An understanding of their pathophysiology has…Abstract Number: 117 • 2017 Pediatric Rheumatology Symposium
The Effect of Bisphosphonate Use on Bone Density Measurements in Patients with Muscular Dystrophy
Background/Purpose: Individuals with Duchenne muscular dystrophy (DMD) and Becker muscular dystrophy have impaired bone health and increased fracture risk due to several factors including immobility,…Abstract Number: 102 • 2017 Pediatric Rheumatology Symposium
Duration of High-Dose Aspirin Therapy Does Not Affect Coronary Artery Outcomes in Kawasaki Disease
Background/Purpose: Kawasaki Disease (KD) is an acute vasculitis targeting the coronary arteries. Prompt treatment with intravenous immunoglobulin (IVIg) reduces the occurrence and potentially the progression…Abstract Number: 127 • 2017 Pediatric Rheumatology Symposium
Description of first 40 patients from a Rheumatologic Transition Clinic in Chile
Background/Purpose: Transition is the planned, coordinated and continuous process in which an adolescent with chronic rheumatic disease is transferred from the pediatric service to an…Abstract Number: 151 • 2017 Pediatric Rheumatology Symposium
Severe Phenotype of Mevalonate-kinase Deficiency in the Czech Republic
Background/Purpose: Disease phenotype of mevalonate-kinase (MVK) deficiency (MKD) varies in relation to the extent of enzymatic activity reduction. It ranges from multi-organ involvement with fatal…Abstract Number: 79 • 2017 Pediatric Rheumatology Symposium
Predicting Colchicine Response in Patients with Undefined Autoinflammatory Diseases
Background/Purpose: Autoinflammatory diseases (AIDs) are a rare group of illnesses characterized by unprovoked episodes of fever and systemic inflammation. An understanding of their pathophysiology has…Abstract Number: 21 • 2017 Pediatric Rheumatology Symposium
Enhancing Quality of Care in Childhood-Onset Systemic Lupus Erythematosus by Improving Performance on Quality Indicator Measures in Cardiovascular and Bone Health
Background/Purpose: Childhood-onset SLE (cSLE) leads to poor health outcomes, including cardiovascular and bone health, due to high rates of potentially devastating disease complications and medication…Abstract Number: 22 • 2017 Pediatric Rheumatology Symposium
Patient perception of barriers to taking medication in Juvenile Idiopathic Arthritis
Background/Purpose: Juvenile Idiopathic Arthritis (JIA) is the most common rheumatic disease of childhood. Treatments include disease modifying anti-rheumatic drugs, commonly methotrexate (MTX), biologics including Etanercept…Abstract Number: 24 • 2017 Pediatric Rheumatology Symposium
Development and Implementation of a “Data-In-Once” Model for a Pediatric Rheumatology Learning Health System
Background/Purpose: Medical institutions are adopting electronic health records (EHR) in accordance with Meaningful Use. This affords the opportunity for standardizing and capturing patient data to…Abstract Number: 19 • 2017 Pediatric Rheumatology Symposium
The Lymphocyte Repertoire in Juvenile Dermatomyositis
Background/Purpose: In adult dermatomyositis (DM), clonal populations of T and B cells with shared variable (V) gene usage have been identified in affected muscle, suggesting…
