ACR Meeting Abstracts

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  • Abstract Number: 1357 • 2016 ACR/ARHP Annual Meeting

    Clinical Description of Patients with Cytoplasmic Discrete Speckles on Indirect Immunofluorescence on HEp-2 Cells in a Universitary Hospital

    Martin Brom1, Carolina Eva Carrizo2, Roberto Arana3 and Cecilia N. Pisoni3, 1Hospital Italiano de Buenos Aires, Buenos Aires, Argentina, 2CEMIC, Buenos Aires, Argentina, 3Rheumatology and Immunology, CEMIC, Buenos Aires, Argentina

    Background/Purpose: Indirect Immunofluorescence (IIF) shows different nuclear and cytoplasmic fluorescence patterns depending on the antibodies present in the cell. Cytoplasmic patterns are an unusual finding.…
  • Abstract Number: 1358 • 2016 ACR/ARHP Annual Meeting

    Response of Hidradenitis Suppurativa to Biologic Therapy

    Shaunak Mulani1, Sean McNish2, Sarah Harris1 and Victoria K. Shanmugam2, 1The George Washington University, Washington, DC, 2Division of Rheumatology, The George Washington University, Washington, DC

    Response of Hidradenitis Suppurativa to Biologic Therapy Background/Purpose: Hidradenitis suppurativa (HS) is a chronic, debilitating inflammatory disease of apocrine sweat glands, characterized by recurrent abscessing…
  • Abstract Number: 1359 • 2016 ACR/ARHP Annual Meeting

    New Markers for Celiac Disease: Anti-Neo-Epitope Human and Microbial Transglutaminases

    Torsten Matthias1, Sandra Neidhöfer2, Patricia Jeremias1 and Aaron Lerner3, 1Aesku.Kipp.Institute, Wendelsheim, Germany, 2AESKU.KIPP.Stitute, Wendelsheim, Germany, 3B. Rappaport School of Medicine, Technion-Israel Institute of Technology, Haifa, Israel

    Background/Purpose: Microbial transglutaminase (mTg) and human tissue Tg (tTg) complexed to gliadin peptides present neo-epitopes. Antibodies against these complexes are called tTg neo-epitope and mTg…
  • Abstract Number: 1360 • 2016 ACR/ARHP Annual Meeting

    Discontinuation Causes of Biological Therapies: Over a Five-Year Period. Biobadasar

    Diego Baenas1, Soledad Retamozo2, Alejandro Alvarellos2, Francisco Caeiro3, Maria Jezabel Haye Salinas1, Juan Pablo Pirola3, María Celina de La Vega4, Gustavo Casado5, Gimena Gomez6, Javier Roberti7, Osvaldo Luis Cerda8, Ignacio Javier Gandino9, Ana Quinteros10, Ida Exeni5,11, Belen Barrios12, Carla Gobbi13, Analia Alvarez14, Amelia Granel15, Alejandra Peluzzon16, Ana Capuccio17, Romina Nieto18, Rossana Quintana19,20, Eduardo Mussano21,22, Santiago Scarafia23, Mercedes Argentina García24, Mercedes De La Sota25, Karin Kirmayr26, Edson Javier Velozo27, Santiago Aguero28, Cristina Battagliotti29, Sidney Soares de Souza30, Emilia Cavillon31, Analia Bohr32, Andrea Smichowski33, Alejandro Benitez34, Daniela Vidal35, Dora Pereira36, Liliana Martinez37, Luis Somma38, Marta Zalazar39, Pablo Finucci Curi40, Leandro Carlevaris41, Guillermo Berbotto42 and Veronica Saurit43, 1Hospital Privado Centro Médico de Córdoba, Córdoba, Argentina, 2Rheumatology Unit, Hospital Privado Centro Médico de Córdoba, Postgraduate Career of Rheumatology Catholic University of Córdoba, Fundación para las Ciencias Biomédicas de Córdoba (FUCIBICO), Cordoba, Argentina, 3Rheumatology, Hospital Privado Centro Médico de Córdoba, Córdoba, Argentina, 4Sociedad Argentina de Reumatología, CABA, Argentina, 5Sociedad Argentina de Reumatologia, CABA, Argentina, 6Sociedad Argentina de Reumatología, Buenos Aires, Argentina, 7SAR, CABA, Argentina, 8Rheumatology Section, Instituto de Rehabilitación Psicofísica, Buenos Aires, Argentina, 9Hospital Italiano de Buenos Aires, Buenos Aires, Argentina, 10Centro Integral Reumatológico, Tucuman, Argentina, 11Sanatorio Parque, Cordoba, Argentina, 12Hospital Tornu, CABA, Argentina, 13Rheumatology, Sanatorio Allende de Córdoba, Cordoba, Argentina, 14Hospital Penna, Bahía Blanca, Argentina, 15Centro Platense de Reumatología, La Plata, Argentina, 16Hospital Clínica José de San Martín, CABA, Argentina, 17Hospital Cesar Milstein, CABA, Argentina, 18Hospital Provincial, Rosario, Argentina, 19Sanatorio Parque, Rosario, Argentina, 20SAR, Rosario, Argentina, 21Córdoba, Hospital Nacional de Clínicas, Córdoba, Argentina, 22SAR, Cordoba, Argentina, 23Hospital Bernardino Rivadavia, CABA, Argentina, 24Rheumatology Unit, HIGA San Martín La Plata, La Plata, Argentina, 25Consultorios, Bahia Blanca, Argentina, 26Sociedad Argentina de Reumatologia. Argentina, CABA, Argentina, 27Rheumatology, Sanatorio Adventista del Plata, Entre Rios, Argentina, 28Sanatorio Pasteur, Catamarca, Argentina, 29Hospital de Niños Dr Orlando Alasia, Santa Fé, Argentina, 30Ramallo 1851, REUMAR, CABA, Argentina, 31Consultorio, Cordoba, Argentina, 32Hospital de Rehabilitación Rocca, CABA, Argentina, 33Atención Integral de Reumatología, CABA, Argentina, 34CEIM, CABA, Argentina, 35Hospital de Niños de Córdoba, Córdoba, Argentina, 36Centro Raquis, Buenos Aires, Argentina, 37Hospital Fernandez, CABA, Argentina, 38SOMMA, Buenos Aires, Argentina, 39Hospital Pirovano, CABA, Argentina, 40Centro Médico Mitre, Entre Rios, Argentina, 41IARI, CABA, Argentina, 42Sanatorio Británico, Rosario, Argentina, 43Hospital Privado Centro Médico de Córdoba, Cordoba, Argentina

    Background/Purpose: To analyze discontinuation causes of biologics therapies (bDMARDs) in patients who are registered in the database BIOBADASAR. Methods: Database included demographics of patients, type…
  • Abstract Number: 1361 • 2016 ACR/ARHP Annual Meeting

    The Role of Von Willebrand Factor Antigen As a Disease Biomarker in the Clinical Assessment of Children with Juvenile Dermatomyositis

    Dawn Wahezi1, Vito Arena2, Jaeun Choi2 and Qi Gao2, 1Pediatric Rheumatology, The Children's Hospital at Montefiore, Bronx, NY, 2Albert Einstein College of Medicine, Bronx, NY

    Background/Purpose:  With the advent of new therapies, outcomes for children with juvenile dermatomyositis (JDM) have significantly improved. Accurate markers of clinically inactivedisease are thus fundamental…
  • Abstract Number: 1362 • 2016 ACR/ARHP Annual Meeting

    Associations Between 25-Hydroxyvitamin D, Parathyroid Hormone, and Cathelicidin Concentrations with Inflammation and Cardiovascular Risk in Subjects with Pediatric Systemic Lupus Erythematosus

    Varsha Gupta1, Vin Tangpricha2, Eric Yow3, Grace McComsey4, Laura E. Schanberg5, Angela B. Robinson6 and APPLE Investigators Group, 1Case Western Reserve University School of Medicine, Cleveland, OH, 2Medicine, Emory University School of Medicine, Atlanta, GA, 3Biostatistics, Duke Clinical Research Institute, Durham, NC, 4Pediatric Infectious Diseases, Rheumatology, and Geographic Medicine, Rainbow Babies and Children's Hospital / Case Medical Center, Cleveland, OH, 5Department of Pediatrics, Duke University Medical Center, Durham, NC, 6Pediatric Rheumatology, Rainbow Babies and Childrens Hospital, Cleveland, OH

    Background/Purpose: Previous studies have shown associations between reduced serum 25-hydroxyvitamin D (25OHD) levels, inflammation, and disease activity in pediatric systemic lupus erythematosus (pSLE). The goal…
  • Abstract Number: 1363 • 2016 ACR/ARHP Annual Meeting

    Serum Adipokines in Juvenile Dermatomyositis Are Associated with Disease Activities and Cardiac Function

    Birgit Nomeland Witczak1, Kristin Godang2, Thomas Schwartz3, Nicoleta Cristina Olarescu4, Berit Flatø5,6, Jens Bollerslev5,7, Ivar Sjaastad5,8,9 and Helga Sanner5,6, 1Oslo University Hospital, Institute for Experimental Medical Research, Oslo University Hospital, Oslo, Norway, Oslo, Norway, 2Department of Specialised Endocrinology, Oslo University Hospital, Section of Specialised Endocrinology, Department of Endocrinology, Oslo University Hospital, Rikshospitalet, Oslo, Norway, Oslo, Norway, 3Department of Infectious Diseases, Department of Infectious Diseases, Oslo University Hospital, Oslo, Norway, Oslo, Norway, 4Department of Endocrinology, Oslo University Hospital, Rikshospitalet, Oslo, Norway., Section of Specialised Endocrinology, Department of Endocrinology, Oslo University Hospital, Rikshospitalet, Oslo, Norway, Oslo, Norway, 5Institute for Clinical Medicine, University of Oslo, Oslo, Norway, Oslo, Norway, 6Department of Rheumatology, Oslo University Hospital, Rikshospitalet, Oslo, Norway, Oslo, Norway, 7Section of Specialised Endocrinology, Department of Endocrinology, Oslo University Hospital, Rikshospitalet, Oslo, Norway, Oslo, Norway, 8Department of Cardiology, Oslo University Hospital, Oslo, Norway, Oslo, Norway, 9Institute for Experimental Medical Research, Oslo University Hospital, Oslo, Norway, Oslo, Norway

    Background/Purpose: We have earlier demonstrated redistribution of adipose tissue in JDM patients. There is an increase in visceral adipose tissue (VAT), a highly active metabolic…
  • Abstract Number: 1364 • 2016 ACR/ARHP Annual Meeting

    Efficacy and Safety of Tumour Necrosis Factor Antagonists in a Large Cohort of Juvenile Dermatomyositis Patients

    Raquel Campanilho-Marques1,2,3,4, Claire Deakin5, Stephanie Simou6, Lucy R Wedderburn2,7,8, Clarissa Pilkington7,9 and on behalf of Juvenile Dermatomyositis Research Group (JDRG), 1Infection, Inflammation and Rheumatology Section, UCL Institute of Child Health, London, Portugal, 2Rheumatology, Great Ormond Street Hospital for Children NHS Trust, London, United Kingdom, 3Rheumatology, Santa Maria Hospital, CHLN, Lisbon, Portugal, 4Rheumatology, Instituto Português de Reumatologia, Lisbon, Portugal, 5Infection, Inflammation and Rheumatology Section,, UCL Institute of Child Health, London, United Kingdom, 6Infection, Inflammation and Rheumatology, UCL Institute of Child Health, London, United Kingdom, 7Infection, Inflammation and Rheumatology Section, UCL Institute of Child Health, London, United Kingdom, 8Rheumatology Unit, Arthritis Research UK Centre for Adolescent Rheumatology, University College London, London, United Kingdom, 9Paediatric Rheumatology, Great Ormond Street Hospital for Children NHS Trust, London, United Kingdom

    Background/Purpose:  Some patients with juvenile dermatomyositis (JDM) have a disease course which is refractory to multiple drug treatments. There is evidence that prolonged disease activity…
  • Abstract Number: 1365 • 2016 ACR/ARHP Annual Meeting

    Trends in Medication Usage in Patients with Juvenile Dermatomyositis

    Takayuki Kishi1, Nastaran Bayat2, Michael Ward3, Adam Huber4, Lan Wu1, Gulnara Mamyrova5, Ira Targoff6, William Warren-Hicks7, Frederick W. Miller2, Lisa G. Rider8 and the Childhood Myositis Heterogeneity Study Group, 1Environmental Autoimmunity Group, National Institute of Environmental Health Sciences, NIH, Bethesda, MD, 2Environmental Autoimmunity Group, National Institute of Environmental Health Sciences, National Institutes of Health, Bethesda, MD, 3National Institute of Arthritis and Musculoskeletal and Skin Diseases, National Institutes of Health, Bethesda, MD, 4IWK Health Centre, Halifax, NS, Canada, 5Department of Medicine, Division of Rheumatology, The George Washington University, Washington, DC, 6VA Medical Center, University of Oklahoma Health Sciences Center, Oklahoma Medical Research Foundation, Oklahoma City, OK, 7Social and Scientific Systems, Inc., Durham, NC, 8Environmental Autoimmunity Grp, National Institute of Environmental Health Sciences, National Institutes of Health, Bethesda, MD

    Background/Purpose:  Juvenile dermatomyositis (JDM) is a systemic autoimmune disease with characteristic rashes and chronic muscle inflammation. Because of its rarity, most therapeutic choices are based…
  • Abstract Number: 1366 • 2016 ACR/ARHP Annual Meeting

    Evidence Based Criteria for Corticosteroid Tapering/Discontinuation. an Analysis of the Paediatric Rheumatology International Trials Organization (PRINTO) Trial in New Onset Juvenile Dermatomyositis

    Gabriella Giancane1, Claudio Lavarello1, Angela Pistorio1, Francesco Zulian2, Bo Magnusson2, Tadej Avcin2, Fabrizia Corona2, Valeria Gerloni2, Serena Pastore2, Roberto Marini Sr.2, Silvana Martino2, Anne Pagnier2, Michel Rodiere2, Christine Soler2, Valda Stanevicha2, Rebecca ten Cate2, Yosef Uziel2, Jelena Vojinovic2, Angelo Ravelli2, Alberto Martini2 and Nicolino Ruperto2, 1Pediatria II, Reumatologia, PRINTO, Istituto Giannina Gaslini, Genoa, Italy, 2Istituto Giannina Gaslini, Genoa, Italy

    Background/Purpose:  Corticosteroids in juvenile dermatomyositis (JDM) alone or in association with other immunosuppressive drugs, namely methotrexate (MTX) and cyclosporine (CSA), represent the first-line treatment option for…
  • Abstract Number: 1367 • 2016 ACR/ARHP Annual Meeting

    Long-Term Outcomes and Their Predictors in Patients with Juvenile Idiopathic Inflammatory Myopathies of Adult Age: A Referral Population Study

    Sam Serafi1, Vladislav Tsaltskan2, Anna Yakovleva3, Heidi Sami1, Frederick W. Miller4, Rodolfo Curiel1, Olcay Y. Jones1,5 and Lisa G. Rider1,4, 1Rheumatology, George Washington University, Washington, DC, 2Internal Medicine, George Washington University, Washington, DC, 3Department of Microbiology, Immunology, and Tropical Medicine., George Washington University, Washington, DC, 4Environmental Autoimmunity Group, National Institute of Environmental Health Sciences, NIH, Bethesda, MD, 5Pediatrics, Walter Reed National Military Medical Center, Bethesda, MD

    Background/Purpose:  To investigate the long-term outcomes and prognostic factors for pts with juvenile-onset idiopathic inflammatory myopathies (JIIM) who are currently adults. Methods: Adults with JIIM…
  • Abstract Number: 1368 • 2016 ACR/ARHP Annual Meeting

    Clinical Course of Juvenile Dermatomyositis Presenting As Skin Predominant Disease

    Edward J. Oberle1,2, Dominic O. Co3,4, Yvonne Chiu3,4, Michelle Bayer4,5, Adam Huber6, Hatice Ezgi Baris7 and Susan Kim8, 1Pediatric Rheumatology, Nationwide Children's Hospital, Columbus, OH, 2Pediatrics, Ohio State University, Columbus, OH, 3Pediatrics, Medical College of Wisconsin, Milwaukee, WI, 4Children's Hospital of Wisconsin, Milwaukee, WI, 5Dermatology, Medical College of Wisconsin, Milwaukee, WI, 6Pediatric rheumatology, IWK Health Centre, Halifax, NS, Canada, 7Boston Children's Hospital, Boston, MA, 8Division of Immunology, Boston Children's Hospital, Boston, MA

    Background/Purpose:  Juvenile dermatomyositis (JDM) is a chronic inflammatory disorder of the skin and striated muscle. A subset of patients can present with rash only, labeled…
  • Abstract Number: 1369 • 2016 ACR/ARHP Annual Meeting

    Features Distinguishing Clinically Hypo- and Amyopathic Juvenile Dermatomyositis (CAJDM) from Juvenile Dermatomyositis (JDM)  

    Gulnara Mamyrova1, Takayuki Kishi2, Nastaran Bayat2, Ira N. Targoff3, Lan Wu2, Olcay Y. Jones1,4, Rodolfo Curiel1, Frederick W. Miller2 and Lisa G. Rider1,2, 1Rheumatology, George Washington University, Washington, DC, 2Environmental Autoimmunity Group, National Institute of Environmental Health Sciences, NIH, Bethesda, MD, 3University of Oklahoma, Oklahoma City, OK, 4Pediatrics, Walter Reed National Military Medical Center, Bethesda, MD

    Background/Purpose:   Clinically Amyopathic Juvenile Dermatomyositis (CAJDM) is a distinct clinical phenotype of JDM in which patients (pts) often have characteristic JDM rashes with little…
  • Abstract Number: 1370 • 2016 ACR/ARHP Annual Meeting

    Development and Validation of a Composite Disease Activity Score for Juvenile Dermatomyositis

    Silvia Rosina1, Alessandro Consolaro1, Pieter van Dijkhuizen1, Kiran Nistala2, Nicola Ruperto1, Clarissa Pilkington3 and Angelo Ravelli1, 1Rheumatology, Giannina Gaslini Institute, Genova, Italy, 2Centre for Rheumatology, University College London, London, United Kingdom, 3Paediatric Rheumatology, Great Ormond Street Hospital NHS Trust, London, United Kingdom

    Background/Purpose: JDM is a multisystem vasculopathic disease that primarily affects the skin and muscles. Most tools for assessment of disease activity in JDM are lenghty,…
  • Abstract Number: 1371 • 2016 ACR/ARHP Annual Meeting

    Comparison of Patient and Physician Reported Global Disease Activity Measures in Juvenile Dermatomyositis

    Heather Tory1, David Zurakowski2, Susan Kim3 and CARRA JDM Quality Measures Workgroup, 1Rheumatology, Connecticut Children's Medical Center, Hartford, CT, 2Departments of Anesthesia and Surgery, Boston Children’s Hospital, Boston, MA, 3Division of Immunology, Boston Children's Hospital, Boston, MA

    Background/Purpose: Patient reported outcomes (PROs) are becoming increasingly recognized as important in the care of patients with chronic diseases, such as Juvenile Dermatomyositis (JDM); however,…
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