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  • Abstract Number: 2639 • 2019 ACR/ARP Annual Meeting

    Comparison of Patient Self-reported Data to Physician-driven Cohorts in Patients with Eosinophilic Granulomatosis with Polyangiitis

    Irena Doubelt1, Jason Springer 2, Tanaz Kermani 3, Antoine Sreih 4, Cristina Burroughs 5, David Cuthbertson 5, Simon Carette 1, Nader A. Khalidi 6, Curry L. Koening 7, Carol Langford 8, Carol A. McAlear 9, Larry W. Moreland 10, Paul Monach 11, Dianne Shaw 12, Philip Seo 13, Ulrich Specks 14, Kalen Young 15, Steven Ytterberg 14, Peter A. Merkel 16, Christian Pagnoux 1 and VCRC Vasculitis Clinical Research Consortium 17, 1Mount Sinai Hospital and University Health Network, Toronto, ON, Canada, 2Kansas University Medical Center, Kansas, MO, 3University of California Los Angeles, Los Angeles, CA, 4University of Pennsylvania, Philadelphia, PA, 5University of South Florida, Tampa, FL, 6McMaster University, Hamilton, ON, Canada, 7University of Utah Hospital, Salt Lake City, UT, 8Cleveland Clinic, Cleveland, OH, 9University of Pennsylvania - VCRC Project Manager, Philadelphia, PA, 10University of Pittsburgh, Pittsburgh, PA, 11Brigham and Women's Hospital, Boston, MA, 12Vasculitis Foundation, North Carolina, 13Johns Hopkins Medicine, Baltimore, MD, 14Mayo Clinic College of Medicine, Rochester, MN, 15Vasculitis Foundation, Kansas City, MO, 16Univeristy of Pennsylvania, Philadelphia, PA, 17University of Pennsylvania, Division of Rheumatology, philadelphia

    Background/Purpose: Aligning perspectives of patients and physicians in the diagnosis and management of diseases is imperative, particularly in rare, chronic diseases such as vasculitis. We…
  • Abstract Number: 2640 • 2019 ACR/ARP Annual Meeting

    Performance of Berden’s Classification and ANCA Renal Risk Score for the Prediction of End-Stage Renal Disease in ANCA-associated Vasculitis

    Onay Gercik1, Emre Bilgin 2, Dilek Solmaz 1, Fulya Cakalagaoglu 3, Arzu Saglam 4, Ozge Aybi 5, Riza Kardas 5, Zeki Soypacaci 6, Gokhan Kabadayi 7, Tolga Yildirim 8, İdil Kurut Aysin 9, Omer Karadag 10 and Servet Akar 11, 1Izmir Katip Celebi University, Faculty of Medicine, Department of Internal Medicine, Division of Rheumatology, İzmir, Turkey, 2Hacettepe University Vasculitis Centre, Ankara, Turkey, Ankara, Turkey, 3Izmir Katip Celebi University, Faculty of Medicine, Department of Pathology, Izmir, Turkey, 4Hacettepe University, Faculty of Medicine, Department of Pathology, Ankara, Turkey, 5Hacettepe University, Faculty of Medicine, Department of Internal Medicine, Ankara, Turkey, 6Izmir Katip Celebi University Faculty of Medicine, Department of Internal Medicine, Division of Nephrology, Izmir, Turkey, 7Izmir Katip Celebi University, Faculty of Medicine, Department of Internal Medicine, Division of Rheumatology, İzmir, Turkey, 8Hacettepe University, Faculty of Medicine, Department of Internal Medicine, Division of Nephrology, Ankara, Turkey, 9Izmir Katip Celebi University Faculty of Medicine, Department of Internal Medicine, Division of Rheumatology, İzmir, Turkey, 10Hacettepe University, Faculty of Medicine, Department of Internal Medicine, Division of Rheumatology, Ankara, Turkey, 11Izmir Katip Celebi University, Faculty of Medicine, Division of Rheumatology, İzmir, Turkey

    Background/Purpose: Renal involvement in ANCA-associated vasculitides (AAVs) is an important factor for morbidity and mortality. Berden’s histopathologic classification for ANCA-associated glomerulonephritis has been proven to…
  • Abstract Number: 2641 • 2019 ACR/ARP Annual Meeting

    Clinical Characteristics of a Cohort of Patients with a Self-Reported Diagnosis of Granulomatosis with Polyangiitis or Microscopic Polyangiitis

    Jason Springer1, Tanaz Kermani 2, Antoine Sreih 3, Dianne Shaw 4, Kalen Young 5, Cristina Burroughs 6 and Peter Merkel 3, 1Kansas University Medical Center, Kansas, MO, 2University of California Los Angeles, Los Angeles, CA, 3University of Pennsylvania, Philadelphia, PA, 4Vasculitis Foundation, North Carolina, 5Vasculitis Foundation, Kansas City, MO, 6University of South Florida, Tampa, FL

    Background/Purpose: To provide a feasible and sustainable platform for conducting patient-centered research in vasculitis, a prospective, international, internet-based registry of patients with vasculitis has been…
  • Abstract Number: 2642 • 2019 ACR/ARP Annual Meeting

    ANCA Testing: Final Diagnoses in Cases with Positive Immunofluorescence and Negative ELISA

    ‪Gabriel Breuer‬‏1, Bashar Fteiha 1, Alon Benaya 1, Marwan Abu Sneineh‬‏ 1 and Gideon Nesher 1, 1Shaare Zedek Medical Center, Jerusalem, Yerushalayim, Israel

    Background/Purpose: With the widespread availability of anti-neutrophil cytoplasmic antibody (ANCA) testing, interpreting positive results has become increasingly challenging. In addition to ANCA Associated Vasculitis (AAV),…
  • Abstract Number: 2643 • 2019 ACR/ARP Annual Meeting

    Comparative Study of Renal Transplantation Due to Rapidly Progressive Glomerulonephritis (RPGN): Study of 42 Patients from a Single Tertiary Centre

    Lara Sanchez-Bilbao1, Marina De Cos-Gomez 2, Iñigo Gonzalez-Mazon 3, Belén Atienza-Mateo 1, Jose Luis Martín-Varillas 1, Mónica Calderón-Goercke 4, DIANA PRIETO- PENA 3, Juan Carlos Ruiz-San Millan 2, Miguel A Gonzalez-Gay 1 and Ricardo Blanco 1, 1Rheumatology, Hospital Universitario Marques de Valdecilla, Santander, Spain, 2Nephrology, Hospital Universitario Marques de Valdecilla, Santander, Cantabria, Spain, 3Rheumatology, Hospital Universitario Marques de Valdecilla, Santander, Cantabria, Spain, 4Hospital Marqués de Valdecilla, Santander, Cantabria, Spain

    Background/Purpose: Rapidly Progressive Glomerulonephritis (RPGN) is characterized clinically by a rapid and severe decline in kidney function. Thus, this entity may lead to an end…
  • Abstract Number: 2644 • 2019 ACR/ARP Annual Meeting

    Ultrasound to Monitor Treatment Response in Large Vessel Giant Cell Arteritis

    Anne Bull Haaversen1, Viktoria Holt 2, Shagaye Nabizadeh 2, Annicken Slagsvold 2 and Andreas P Diamantopoulos 3, 1Martina Hansens Hospital, Sandvika, Norway, 2Martina Hansens Hospital, Bærum, Norway, 3Martina Hansens Hospital, SANDVIKA, Oslo, Norway

    Background/Purpose: On ultrasound (US) examinations, large vessel vasculitis (LVV) has been reported to be present in up to 55% of Giant cell arteritis (GCA) patients.…
  • Abstract Number: 2645 • 2019 ACR/ARP Annual Meeting

    The Anteromedial Ultrasound Examination of the Large Supraaortic Vessels Identifies Higher Rates of Large Vessel Involvement Than Previous Reported in Patients with Giant Cell Arteritis

    Anne Bull Haaversen1 and Andreas P Diamantopoulos 2, 1Martina Hansens Hospital, Sandvika, Norway, 2Martina Hansens Hospital, SANDVIKA, Oslo, Norway

    Background/Purpose: Giant cell arteritis (GCA) affects both the cranial and large vessels. Ultrasonographic studies have reported that the incidence of large vessel vasculitis (LVV) in…
  • Abstract Number: 2646 • 2019 ACR/ARP Annual Meeting

    Survival of Large Vessel Giant Cell Arteritis in Northern Italy During a 26-year Period : No Correlation with Demographical, Clinical, Laboratory and Imaging Data

    Luigi Boiardi1, Mariagrazia Catanoso 2, Giovanna Restuccia 3, Francesco Muratore 3, Pierluigi Macchioni 4 and Carlo Salvarani 5, 1Division of Rheumatology, Azienda Unita' Sanitaria Locale IRCCS di Reggio Emilia, Reggio Emilia, Italy, 2Arcispedale S Maria Nuova, IRCCS, Reggio Emilia, ITALY, Reggio Emilia, Italy, 3Division of Rheumatology, Azienda Unita’ Sanitaria Locale IRCCS di Reggio Emilia, Reggio Emilia, Italy, 4Azienda USL-IRCCS di Reggio Emilia, Reggio Emilia, 5Division of Rheumatology, Arcispedale Santa Maria Nuova-IRCCS, Reggio Emilia, Italy

    Background/Purpose: To investigate the relationship between demographical, clinical, laboratory and imaging data and survival in patients with large vessel giant cell arteritis (LVGCA) in a…
  • Abstract Number: 2647 • 2019 ACR/ARP Annual Meeting

    Flares and Long-term Remission in Large-vessel Giant Cell Arteritis in Northern Italy: Characteristics and Predictors in a Long-term Follow-up Study

    Carlo Salvarani1, Luigi Boiardi 2, Alberto Cavazza 3, Massimiliano Casali 4, Lucia Spaggiari 5, Luca Cimino 6, Raffaella Aldigeri 7, Francesco Muratore 8, Giovanna Restuccia 8, Nicolò Pipitone 5 and Pierluigi Macchioni 5, 1Azienda USL-IRCCS di Reggio Emilia, REGGIO EMILIA, Emilia-Romagna, Italy, 2Division of Rheumatology, Azienda Unita' Sanitaria Locale IRCCS di Reggio Emilia, Reggio Emilia, Italy, 3Pathology Unit, Azienda Unita' Sanitaria Locale IRCCS di Reggio Emilia, Reggio Emilia, Italy, 4Azienda USL-IRCCS di Reggio Emilia, REGGIO EMILIA, Italy, 5Azienda USL-IRCCS di Reggio Emilia, Reggio Emilia, 6Ophthalmology Unit, Azienda Unita' Sanitaria Locale IRCCS di Reggio Emilia, Reggio Emilia, Italy, 7Università degli Studi di Parma, Parma, 8Division of Rheumatology, Azienda Unita’ Sanitaria Locale IRCCS di Reggio Emilia, Reggio Emilia, Italy

    Background/Purpose: To evaluate the frequency, timing, and characteristics of flares and to evaluate the frequency of long-term remission after glucocorticoids (GCs) suspension in an Italian…
  • Abstract Number: 2648 • 2019 ACR/ARP Annual Meeting

    Association Between Specimen Length and Number of Sections and Diagnostic Yield of Temporal Artery Biopsy: A Retrospective, Single Center Experience over a 21 Years’ Period

    Francesco Muratore1, Luigi Boiardi 2, Alberto Cavazza 3, Giacomo Tiengo 4, Raffaella Aldigeri 5, Luca Cimino 6 and Carlo Salvarani 7, 1Division of Rheumatology, Azienda Unita’ Sanitaria Locale IRCCS di Reggio Emilia, Reggio Emilia, Italy, 2Division of Rheumatology, Azienda Unita' Sanitaria Locale IRCCS di Reggio Emilia, Reggio Emilia, Italy, 3Pathology Unit, Azienda Unita' Sanitaria Locale IRCCS di Reggio Emilia, Reggio Emilia, Italy, 4Division of Rheumatology, University of Modena and Reggio Emilia, Modena, Italy, 5Department of Medicine and Surgery, University of Parma, Parma, Italy, 6Ophthalmology Unit, Azienda Unita' Sanitaria Locale IRCCS di Reggio Emilia, Reggio Emilia, Italy, 7Division of Rheumatology, Arcispedale Santa Maria Nuova-IRCCS, Reggio Emilia, Italy

    Background/Purpose: To investigate the association between specimen length and number of sections and the diagnostic yield of temporal artery biopsy (TAB) for giant cell arteritis…
  • Abstract Number: 2649 • 2019 ACR/ARP Annual Meeting

    Comparison of Biopsy Proven Giant Cell Arteritis in North America and South Europe: A Population-Based Study

    Francesco Muratore1, Cynthia Crowson 2, Luigi Boiardi 3, Ambra Pinelli 4, Matthew Koster 5, Giovanna Restuccia 1, Tanaz Kermani 6, Eric Matteson 7, Carlo Salvarani 8 and Kenneth Warrington 5, 1Division of Rheumatology, Azienda Unita’ Sanitaria Locale IRCCS di Reggio Emilia, Reggio Emilia, Italy, 2Mayo Clinic Rochester, Rochester, 3Division of Rheumatology, Azienda Unita' Sanitaria Locale IRCCS di Reggio Emilia, Reggio Emilia, Italy, 4Division of Rheumatology, University of Modena and Reggio Emilia, Reggio Emilia, Italy, 5Mayo Clinic Rochester, Rochester, MN, 6University of California Los Angeles, Los Angeles, CA, 7Mayo Clinic College of Medicine and Science, Rochester, Minnesota, USA, Rochester, 8Division of Rheumatology, Arcispedale Santa Maria Nuova-IRCCS, Reggio Emilia, Italy

    Background/Purpose: To compare clinical characteristics, treatment, long-term follow-up and prognosis of two population-based cohorts of patients with biopsy-proven giant cell arteritis (GCA) from North America…
  • Abstract Number: 2650 • 2019 ACR/ARP Annual Meeting

    Predictors of Relapse in Giant Cell Arteritis: Data from an International Collaboration

    Laure Delaval 1, Raphael Porcher 2, Kenneth Warrington 3, Francesco Muratore 4, Cynthia Crowson 5, Daniel Blockmans 6, Christian Agard 7, Alexis Régent 8, Maxime Samson 9, Loic Guillevin 8, Carlo Salvarani 10 and Benjamin Terrier8, 1Department of Internal Medicine, Hôpital Cochin, Université Paris Descartes, Sorbonne Paris Cité, INSERM Unité 1016, Centre de Référence pour les Maladies Auto-immunes Rares, Paris, France, Paris, France, 2Hotel Dieu Hospital, Paris, France, 3Mayo Clinic Rochester, Rochester, MN, 4Division of Rheumatology, Azienda Unita’ Sanitaria Locale IRCCS di Reggio Emilia, Reggio Emilia, Italy, 5Mayo Clinic Rochester, Rochester, 6Department of General Internal Medicine, University Hospitals Gasthuisberg, Leuven, Belgium, 7CHU Nantes, Nantes, France, 8National Referral Center for Rare Systemic Autoimmune Diseases Paris Cochin, Paris, France, 9Service de Médecine Interne et Immunologie Clinique, CHU Dijon Bourgogne, Hôpital François Mitterrand, Dijon ; Université Bourgogne-Franche Comté, INSERM, EFS BFC, UMR1098, F-21000 Dijon, Dijon, France, 10Division of Rheumatology, Arcispedale Santa Maria Nuova-IRCCS, Reggio Emilia, Italy

    Background/Purpose: Roughly half of giant-cell arteritis (GCA) patients taking only glucocorticoids (GCs) relapse. The relapse rate seems to reflect, in part, the duration of GC intake, more…
  • Abstract Number: 2651 • 2019 ACR/ARP Annual Meeting

    Are There Phenotypic Overlaps Between Giant Cell Arteritis Subgroups?

    Berkan Armagan 1, Abdullah Yildirim 2, Alper Sarı 3, Bayram Farisoğulları 3, Emre Bilgin 3, Levent Kilic 4, Umut Kalyoncu 5, Şule Apras Bilgen 4 and Omer Karadag6, 1Department of Internal Medicine, Hacettepe University, Faculty of Medicine, Ankara, Turkey., Ankara, Turkey, 2Hacettepe University, Faculty of Medicine, Department of Internal Medicine, Ankara, Turkey, 3Hacettepe University Vasculitis Centre, Ankara, Turkey, Ankara, Turkey, 4Hacettepe University, Faculty of Medicine, Department of Internal Medicine, Division of Rheumatology, Ankara, Turkey, 5Hacettepe University Department of Rheumatology, Ankara, Turkey, 6Hacettepe University Vasculitis Centre, Ankara, Turkey / Vasculitis and Lupus Clinic, Addenbrooke’s Hospital, University of Cambridge, UK, Ankara, Turkey

    Background/Purpose: In parallel to the improvements in imaging, increasing data is accumulated regarding phenotypes of primary vasculitides. Giant cell arteritis (GCA) is a large vessel…
  • Abstract Number: 2652 • 2019 ACR/ARP Annual Meeting

    Comparison Between Transmural and Isolated Periadventitial And/or Adventitial Inflammation at Temporal Artery Biopsy: A Single Center Cohort of Biopsy-Positive GCA with Long Term Follow-up

    Elena Galli1, Francesco Muratore 2, Luigi Boiardi 3, Alberto Cavazza 4, Giovanna Restuccia 2, Luca Cimino 5 and Carlo Salvarani 6, 1Division of Rheumatology, University of Modena and Reggio Emilia, Modena, Italy, 2Division of Rheumatology, Azienda Unita’ Sanitaria Locale IRCCS di Reggio Emilia, Reggio Emilia, Italy, 3Division of Rheumatology, Azienda Unita' Sanitaria Locale IRCCS di Reggio Emilia, Reggio Emilia, Italy, 4Pathology Unit, Azienda Unita' Sanitaria Locale IRCCS di Reggio Emilia, Reggio Emilia, Italy, 5Ophthalmology Unit, Azienda Unita' Sanitaria Locale IRCCS di Reggio Emilia, Reggio Emilia, Italy, 6Division of Rheumatology, Arcispedale Santa Maria Nuova-IRCCS, Reggio Emilia, Italy

    Background/Purpose: Temporal artery biopsy (TAB) showing transmural inflammation is considered the gold standard for the diagnosis of giant cell arteritis (GCA). In some cases, inflammation…
  • Abstract Number: 2653 • 2019 ACR/ARP Annual Meeting

    Adventitial Fibroblast, an Important Actor in Giant Cell Arteritis

    Simon Parreau1, Nicolas Vedrenne 2, Alexis Régent 3, Laurence Richard 4, Philippe Sindou 2, Luc Mouthon 3, Anne-Laure Fauchais 4, Marie-Odile Jauberteau 2 and Kim Heang Ly 1, 1Limoges University Hospital, Limoges, France, 2EA3842-CaPTuR, Limoges, 3National Referral Center for Rare Systemic Autoimmune Diseases Paris Cochin, Paris, France, 4Limoges University Hospital, Limoges

    Background/Purpose: Giant cell arteritis (GCA) is a systemic vasculitis affecting large vessels. The diagnosis is based on temporal artery biopsy (TAB) which shows an arterial…
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