ACR Meeting Abstracts

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Abstracts tagged "Vasculitis"

  • Abstract Number: 0412 • ACR Convergence 2020

    2019 Novel Coronavirus Disease (COVID-19) in Patients with Large-Vessels Vasculitis: Single-centre Experience in Paris

    Chloé Comarmond1, Mathilde Leclercq1, Gaëlle Leroux2, Cindy Marques2, Alexandre Le Joncour3, Fanny Domont2, Céline Hatte1, Ségolène Toquet1, Perrine Guillaume-Jugnot1, Anne-Claire Desbois1, Mathieu Vautier1, Aude Rigolet1, Yves Allenbach4, Olivier Benveniste5, David Saadoun2 and Patrice Cacoub2, 1Assistance Publique des Hopitaux de Paris, Paris, France, 2AP-HP, Groupe Hospitalier Pitié-Salpêtrière, Department of Internal Medicine and Clinical Immunology, F-75013, Paris, France, Centre national de références Maladies Autoimmunes et systémiques rares et Maladies Autoinflammatoires rares, Paris, France, 3APHP, paris, France, 4Sorbonne Université, Paris, Ile-de-France, France, 5Sorbonne Université, paris, France

    Background/Purpose: Advanced age and cardiovascular diseases are recognized as major comorbidities associated with severe forms of coronavirus disease 2019 (COVID-19) caused by the severe acute…
  • Abstract Number: 1292 • ACR Convergence 2020

    Frequency and Predictors of Influenza Vaccine Hesitancy in Systemic Autoimmune Rheumatic Diseases

    Valeria Valerio1, Mariana Useche1, Mianbo Wang2, Sasha Bernatsky3, Christian Pineau4 and Ines Colmegna1, 1The Research Institute of the McGill University Health Centre, Montreal, Canada, 2Lady Davis institute for Medical Research, Montreal, QC, Canada, 3The Research Institute of the McGill University Health Centre, Montreal, ON, Canada, 4McGill University Health Center, Montreal, QC, Canada

    Background/Purpose: Patients with systemic autoimmune rheumatic diseases (SARDs) benefit from getting annual inactivated influenza vaccine (IIV). However, vaccine uptake among SARDs is suboptimal.  The delay…
  • Abstract Number: 1589 • ACR Convergence 2020

    An Initiative to Improve Timely Glucocorticoid Tapering in Vasculitis

    Arielle Mendel1, Daniel Ennis2, Shirley Lake3, Simon Carette4 and Christian Pagnoux5, 1Division of Rheumatology, McGill University, Montreal, QC, Canada, 2Division of Rheumatology, Vancouver General Hospital, University of British Columbia, Vancouver, BC, Canada, 3Division of Rheumatology, Sunnybrook Health Sciences Centre, University of Toronto, Toronto, ON, Canada, 4Division of Rheumatology, Mount Sinai Hospital and University Health Network, University of Toronto, Toronto, ON, Canada, 5Division of Rheumatology, Mount Sinai Hospital, University of Toronto, Toronto, ON, Canada

    Background/Purpose: Vasculitis guidelines recommend scheduled glucocorticoid (GC) tapering to avoid toxicity. In an audit of 130 consecutive new patients on GC assessed in our tertiary…
  • Abstract Number: 1939 • ACR Convergence 2020

    Definitions and Reliability Assessment of Chronic Ultrasound Lesions of the Axillary Artery in Giant Cell Arteritis: A Study from the OMERACT Large Vessel Vasculitis Ultrasound Working Group

    Valentin Schaefer1, Stavros Chrysidis2, Greta Carrara3, Wolfgang Schmidt4, George A. Bruyn5, Bhaskar Dasgupta6, Eugenio De Miguel7, Andreas Diamantopoulos8, Christina Duftner9, Ulrich Fredberg10, Berit Nielsen11, Wolfgang Hartung12, Alojzija Hocevar13, Annamaria Iagnocco14, Aaron Juche4, Tanaz Kermani15, Tove Lorenzen16, Pierluigi Macchioni17, Marcin Milchert18, Uffe Døhn19, Sara Monti20, Chetan Mukhtyar21, Cristina Ponte22, Carlo Scire23, Lene Terslev24, Luca Seitz25 and Christian Dejaco26, 1Clinic of Internal Medicine III, Department of Oncology, Hematology and Rheumatology, University Hospital Bonn, Germany, Bonn, Nordrhein-Westfalen, Germany, 2Sydvestjysk Sygehus Esbjerg, Esbjerg, Denmark, 3Epidemiology Unit, Italian Society for Rheumatology, Milan, Italy, 4Immanuel Krankenhaus Berlin Buch, Berlin, Germany, 5Rheumatology, Reumakliniek Lelystad, Lelystad, Netherlands, 6Rheumatology, Mid and South Essex University Hospital NHS Foundation Trust, Southend University Hospital, United Kingdom, Westcliff on sea, England, United Kingdom, 7Rheumatology Department, Hospital Universitario La Paz, Madrid, Spain, 8Martina Hansens Hospital, Baerum, Norway, 9Medical University Innsbruck, Innsbruck, Austria, 10Silkeborg Regional Hospital, Silkeborg, Denmark, 11Aarhus University Hospital, Aarhus, Denmark, 12Asklepios Klinik Bad Abbach, Bad Abbacg, Germany, 13University Medical Center, Rheumatology, Ljubljana, LJUBLJANA, Slovenia, 14Università degli Studi di Torino, Academic Rheumatology Centre, Turin, Italy, 15David Geffen School of Medicine / University of California, Los Angeles, CA, 16Copenhagen Center for Arthritis Research, Copenhagen, Denmark, 17Unità Operativa di Reumatologia/Arcispedale S. Maria Nuova, Reggio Emilia, Italy, 18Pomeranian Medical University, Szczecin, Poland, 19Center for Rheumatology and Spine Diseasesand COPECARE, Copenhagen, Denmark, 20Fondazione IRCCS Policlinico S Matteo, University of Pavia, Pavia, Italy, 21Norfolk and Norwich University Hospitals NHS Foundation Trust, Norwich, United Kingdom, 22Rheumatology Department, Hospital de Santa Maria, Centro Hospitalar Universitário Lisboa Norte, Lisboa, Portugal, 23University of Ferrara, Ferrara, Italy, 24Copenhagen Center for Arthritis Research, Center for Rheumatology and Spine Diseases, Rigshospitalet, Glostrup., Copenhagen, Denmark, 25Department of Rheumatology, Immunology and Allergology, University of Bern, Inselspital, Switzerland, Bern, Switzerland, 26South Tyrol Health Trust, Hospital of Bruneck, Bruneck, Italy

    Background/Purpose: The OMERACT Ultrasound (US) large vessel vasculitis task force has recently defined the US appearance of normal axillary arteries (AA) and the key elementary…
  • Abstract Number: 0413 • ACR Convergence 2020

    Coronavirus Infection and Vasculitis: Identifying Associations Mining the Biomedical Literature

    Alicia Rodriguez Pla1 and Rodrigo Cartin-Ceba2, 1Rheumatology. Mayo Clinic Arizona, Scottsdale, 2Pulmonary. Mayo Clinic Arizona, Scottsdale, AZ

    Background/Purpose: Based on recent publications suggesting an association between COVID-19 and vascular inflammation, our aim was to explore new associations between coronavirus infections and vasculitis…
  • Abstract Number: 1416 • ACR Convergence 2020

    Effects of the COVID-19 Pandemic on Patients Living with Vasculitis

    Shubhasree Banerjee1, Michael George2, Kalen Young3, Shilpa Venkatachalam4, Jennifer Gordon5, Cristina Burroughs6, David Curtis7, Marcela Ferrada8, Kelly Gavigan9, Peter C. Grayson10, Joyce Kullman11, Jeffrey R Curtis12, Dianne Shaw3, William Nowell13 and Peter Merkel2, 1University of Pennsylvania, Philadelphia, 2University of Pennsylvania, Philadelphia, PA, 3Vasculitis Foundation, Kansas City, 4Global Healthy Living Foundation, Upper Nyack, 5Temple University, Philadelphia, 6University of South Florida, Tampa, 7Global Healthy Living Foundation, New York City, 8Systemic Autoimmunity Branch, Vasculitis Translational Research Program, National Institute of Arthritis and Musculoskeletal and Skin Diseases, National Institutes of Health, Bethesda, MD, 9Global Healthy Living Foundation, Upper Nyack, NY, 10Systemic Autoimmunity Branch, National Institutes of Health, NIAMS, Bethesda, MD, 11Vasculitis Foundation, Kansas City, MO, 12Division of Clinical Immunology and Rheumatology, University of Alabama at Birmingham, Birmingham, AL, 13Global Healthy Living Foundation, New York City, NY

    Background/Purpose: The COVID-19 pandemic has the potential to impact how patients with vasculitis interact with health care systems due to concerns about infections. This study…
  • Abstract Number: 1638 • ACR Convergence 2020

    Systemic Treatment in Behçet’s Disease According to Clinical Phenotypes. Study of 111 Patients

    David Martinez-Lopez1, Lara Sanchez-Bilbao2, Carmen Alvarez-Reguera2, Alba Herrero Morant2, Inigo Gonzalez-Mazon3, José Luis Martín-Varillas4, Guillermo Suarez-Amorin2, Patricia Setien-Preciados2, Cristina Mata-Arnaiz5, Miguel Ángel González-Gay6 and Ricardo Blanco2, 1Hospital Universitario Marques de Valdecilla, Santander (SPAIN), Spain, 2Hospital Universitario Marques de Valdecilla, Santander, Spain, 3Hospital Universitario Marques de Valdecilla, Bezana, Spain, 4Hospital Sierrallana, Torrelavega, Spain, 5Hospital de Laredo, Santander, Spain, 6Hospital Universitario Marques de Valdecilla, Santander, Cantabria, Spain

    Background/Purpose: Behçet’s disease (BD) is a multisystemic vasculitis. Different clinical phenotypes can be distinguished. Systemic corticosteroids are the most used drugs in BD. Conventional and…
  • Abstract Number: 1943 • ACR Convergence 2020

    The Prevalence of Anxiety and Depression in Patients with Giant Cell Arteritis

    Joana Martinho1, André Ponte2, Eduardo Dourado3, Nikita Khmelinskii1, Sara Dias4, Sofia Barreira5, Ana Rita Cruz-Machado1, Carla Macieira1, Vítor Teixeira6, Ana Rodrigues4, Diogo Telles-Correia7, João Eurico Fonseca8 and Cristina Ponte1, 1Rheumatology Department, Hospital de Santa Maria, Centro Hospitalar Universitário Lisboa Norte, Lisboa, Portugal, 2Centro Hospitalar Psiquiátrico de Lisboa, Lisboa, Portugal, Lisbon, Portugal, 3Rheumatology Department, Hospital de Santa Maria, Centro Hospitalar Universitário Lisboa Norte, Lisboa, Lisboa, Portugal, 4EpiDoC Unit, Centro de Estudos de Doenças Crónicas (CEDOC), NOVA Medical School, Universidade NOVA de Lisboa (NMS/UNL), Lisbon, Portugal, 5Rheumatology Department, Hospital de Santa Maria, Centro Hospitalar Universitário Lisboa Norte, Lisbon, Portugal, 6Rheumatology Department, Centro Hospitalar Universitário do Algarve, Faro, Portugal, 7Serviço de Psiquiatria, Hospital de Santa Maria, CHULN, Lisboa, Portugal, Lisbon, Portugal, 8Instituto de Medicina Molecular, Faculdade Medicina Universidade de Lisboa and Centro Hospitalar Universitário Lisboa Norte., Lisboa, Portugal

    Background/Purpose: Giant cell arteritis (GCA) is the most common primary vasculitis of the elderly causing blindness if left untreated. However, its hallmark treatment with glucocorticoids…
  • Abstract Number: 0414 • ACR Convergence 2020

    Clinical Characteristics of an Internet-Based Cohort of Participants with a Self-Reported Diagnosis of Cryoglobulinemic Vasculitis or IgA Vasculitis

    Jason Springer1, Tanaz Kermani2, Dianne Shaw3, Kalen Young4, Cristina Burroughs5 and Peter Merkel6, 1University of Kansas Medical Center, Overland Park, KS, 2David Geffen School of Medicine / University of California, Los Angeles, CA, 3Vasculitis Foundation, North Carolina, 4Vasculitis Foundation, Kansas City, 5University of South Florida, Tampa, 6University of Pennsylvania, Philadelphia, PA

    Background/Purpose: Cyroglobulinemic vasculitis (CV) and IgA vasculitis are forms of small-vessel vasculitis characterized by immune complex deposition. The purpose of this study was to a)…
  • Abstract Number: 1420 • ACR Convergence 2020

    Characterization of ANCA-Associated Vasculitis Among African American Patients

    Sehris Khawaja1, Saloni Godbole1, Maryann Kimoto2, Virginia Steen3 and Kaitlin Quinn4, 1Georgetown University, Washington, DC, 2UCLA, Los Angeles, CA, 3Division of Rheumatology, Department of Medicine, MedStar Georgetown University Hospital, Washington, DC, 4National Institutes of Health, Washington, DC

    Background/Purpose: ANCA-associated vasculitis (AAV) comprises a group of disorders characterized by inflammation of small and medium-sized arteries.  Prevalence and phenotype of these diseases appear to…
  • Abstract Number: 1686 • ACR Convergence 2020

    The COV-ASAKI Survey from the Pediatric Tuscany Network During COVID-19 Era

    Maria Vincenza Mastrolia1, Rino Agostiniani2, Chiara Azzari3, Roberto Bernardini4, Ugo Bottone5, Giovanni Battista Calabri6, Flavio Civitelli7, Rita Consolini8, Roberto Danieli9, Rosalia Di Silvio10, Susanna Falorni11, Luigi Gagliardi12, Salvatore Grosso13, Marco Martini14, Graziano Memmini15, Marco Pezzati16, Giovanni Suriano17, Luca Tafi18, Angelina Vaccaro19, Pier Luigi Vasarri20 and Gabriele Simonini21, 1Rheumatology Unit, Meyer Children's University Hospital, Firenze, Italy, Florence, Toscana, Italy, 2Paediatric Unit, San Jacopo Hospital, Pistoia, Italy, Pistoia, Toscana, Italy, 3Paediatric Immunology Unit, Department of Health Sciences, Meyer Children’s University Hospital, Firenze, Italy, Florence, Toscana, Italy, 4Paediatric Unit, San Giuseppe Hospital, Empoli, Italy, Empoli, Toscana, Italy, 5Division of Neonatology and Pediatrics, Lotti Hospital, Pontedera, AUSL Toscana Nord Ovest, Pisa, Italy, Pisa, Toscana, Italy, 6Cardiologic Unit, Meyer Children’s University Hospital, Firenze, Italy, Florence, Toscana, Italy, 7Division of Neonatology and Pediatrics, Montepulciano Hospital, Montepulciano, AUSL Sud Est Toscana, Siena, Italy., Siena, Toscana, Italy, 8Section of clinical and laboratory Immunology, Department of clinical and experimental Medicine, University of Pisa, Italy, Pisa, Italy, 9Division of Neonatology and Pediatrics, Spedali Riuniti di Livorno, Livorno, AUSL Toscana Nord Ovest, Pisa, Italy, Livorno, Toscana, Italy, 10Paediatric Unit, Mugello Hospital, Borgo San Lorenzo, Firenze, Italy, Florence, Toscana, Italy, 11Paediatric Unit, Misericordia Hospital, Grosseto, Italy, Grosseto, Italy, 12Division of Neonatology and Pediatrics, Ospedale Versilia Hospital, Viareggio, AUSL Toscana Nord Ovest, Pisa, Italy, Viareggio, Toscana, Italy, 13Clinical Pediatrics, Department of Molecular Medicine and Development, University of Siena, Siena, Italy, Siena, Toscana, Italy, 14Paediatric Unit, San Donato Hospital, Arezzo, Italy, Arezzo, Toscana, Italy, 15Division of Neonatology and Pediatrics, Apuane Hospital, Massa Carrara, AUSL Toscana Nord Ovest, Pisa, Italy, Massa Carrara, Toscana, Italy, 16Paediatric Unit, Santa Maria Annunziata Hospital, Bagno a Ripoli, Firenze, Italy, Florence, Toscana, Italy, 17Division of Neonatology and Pediatrics, Cecina Hospital, Cecina, AUSL Toscana Nord Ovest, Pisa, Italy, Cecina, Toscana, Italy, 18Paediatric and Neonatal Unit, Valdarno Hospital, Montevarchi, Arezzo, Italy, Arezzo, Toscana, Italy, 19Division of Neonatology and Pediatrics, San Luca Hospital, Lucca, AUSL Toscana Nord Ovest, Pisa, Italy, Lucca, Toscana, Italy, 20Paediatric and Neonatologic Unit, Santo Stefano Hospital, Prato, Italy, Prato, Toscana, Italy, 21Rheumatology Unit, Meyer Children's University Hospital, Florence; NEUROFARBA Department, University of Florence, Italy, Florence, Italy

    Background/Purpose: At the end of April 2020, national and international Pediatrics scientific societies diffused an alert about a rise in the number of pediatric severe,…
  • Abstract Number: 1945 • ACR Convergence 2020

    Characterization of Visual Manifestations and Identification of Risk Factors for Permanent Vision Loss in Patients with Giant Cell Arteritis

    Hussein Baalbaki1, Darya Jalaledin2, Catherine Lachance2 and Jean-Paul Makhzoum3, 1Hopital du Sacre-Coeur de Montreal, Montreal, QC, Canada, 2Universite de Montreal, Montreal, QC, Canada, 3Vasculitis Clinic, Canadian Network for Research on Vasculitides (CanVasc), Hopital du Sacre-Coeur de Montreal, Montreal, QC, Canada

    Background/Purpose: Permanent vision loss (PVL) is a feared complication and a leading cause of morbidity in Giant Cell Arteritis (GCA). Multiple risk factors for ocular…
  • Abstract Number: 0415 • ACR Convergence 2020

    Characteristics of Arthritis in Adult IgA Vasculitis

    Alojzija Hocevar1, Vesna Jurcic2, Matija Tomsic1 and Ziga Rotar1, 1University Medical Center Ljubljana, LJUBLJANA, Slovenia, 2Institute of Pathology, Medical Faculty, University of Ljubljana, LJUBLJANA, Slovenia

    Background/Purpose: Arthritis is one of the main clinical features in IgA vasculitis (IgAV). In children, joint involvement represents the second most common manifestation with the…
  • Abstract Number: 1421 • ACR Convergence 2020

    Clinical Features, Disease Activity and Prognosis of ANCA-Associated Vasculitis in US African Americans

    Luis Palomino1, Angelo Gaffo2, Sebastian Sattui3 and Dongmei Sun2, 1University of Alabama at Birmingham Hospital, Birmingham, AL 2University of Alabama at Birmingham, Birmingham, AL, 3Hospital for Special Surgery, New York, NY

    Background/Purpose: ANCA-associated vasculitis (AAV), including Granulomatosis with Polyangiitis (GPA), Eosinophilic Granulomatosis with Polyangiitis (EGPA) and Microscopic Polyangiitis (MPA), affect mostly Caucasians of European descent. Clinical…
  • Abstract Number: 1687 • ACR Convergence 2020

    Kawasaki Disease Shock Syndrome in the Intensive Care Unit: A Single Center Cohort

    Monica Bray1, Jennifer Rammel2, Andrea Ramirez1, Kristen Sexson1, Fong Lam1, Eyal Muscal3 and Marietta DeGuzman3, 1Baylor College of Medicine, Houston, TX, 2University of Florida Health Jacksonville, Jacksonville, FL, 3Baylor College of Medicine, Houston

    Background/Purpose: Kawasaki disease (KD), a well described vasculitis of childhood, is the leading cause of acquired heart disease in developed countries. Kawasaki disease shock syndrome…
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