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Abstracts tagged "Vasculitis"

  • Abstract Number: 1886 • ACR Convergence 2021

    Validation of Angiographic Patterns of Disease in a Turkish Cohort of Patients with Takayasu’s Arteritis

    K. Bates Gribbons1, SEMA KAYMAZ-TAHRA2, Fatma Alibaz3, Ertugrul Cagri bolek4, Omer Karadag5, Burak Ince6, Murat Inanc7, Sinem Kocaer8, Fatos Onen9, KENAN AKSU10, Gokhan Keser11, Askin Ates12, Ayten Yazici13, Ayse Cefle13, Nilufer Alpay Kanitez14, Ahmet Omma15, Onay Gercik16, Servet Akar17, Veli Cobankara18, Nazife Sule Yasar Bilge19, Timucin Kasifoglu20, Mete Kara11, Kaitlin Quinn21, Peter Grayson22, Peter Merkel23 and Haner Direskeneli24, 1McGovern Medical School, Colleyville, TX, 2Marmara University Faculty of Medicine, Rheumatology, Istanbul, Turkey, 3Marmara University, School of Medicine, Rheumatology, Istanbul, Turkey, 4Vasculitis Translational Research Program, NIAMS, NIH, US, Lanham, MD, 5Hacettepe University, Division of Rheumatology, Department of Internal Medicine, Faculty of Medicine, Ankara, Turkey, 6Istanbul Faculty of Medicine, Istanbul University, Division of Rheumatology, İstanbul, Turkey, 7Istanbul University Faculty of Medicine, Istanbul, Turkey, 8Dokuz Eylul University, Izmer, Turkey, 9Dokuz Eylul University, Izmir, Turkey, 10EGE UNIV. FACULTY of MEDICINE, IZMIR, Turkey, 11Ege University, İzmir, Turkey, 12Ankara University, Ankara, Turkey, 13Kocaeli University, Kocaeli, Turkey, 14Koc University School of Medicine, Istanbul, Turkey, 15Ankara City Hospital, Istanbul, Turkey, 16Izmir Katip Celebi University, Izmir, Turkey, 17Izmir Katip Celebi University, Faculty of Medicine, Department of Internal Medicine, Division of Rheumatology, Izmir, Turkey, 18Pamukkale University, Denizli, Turkey, 19Eskisehir Osmangazi University Medical Faculty, Eskisehir, Turkey, 20Osmangazi University Department of Rheumatology, Eskişehir, Turkey, 21National Institute of Arthritis and Musculoskeletal and Skin Diseases (NIAMS), National Institutes of Health (NIH), Washington, DC, 22National Institutes of Arthritis and Musculoskeletal and Skin Diseases (NIAMS), National Institutes of Health (NIH), Bethesda, MD, 23University of Pennsylvania, Philadelphia, PA, 24Marmara University, Istanbul, Turkey

    Background/Purpose: Previous studies using computer-driven methods have identified subsets of patients with Takayasu’s arteritis based on angiographic patterns of disease. These subsets were consistent between…
  • Abstract Number: 0161 • ACR Convergence 2021

    Does 18F-FDG-PET/MRI Add Metabolic Information to Anatomic Image in Childhood-onset Takayasu’s Arteritis Patients? A Multicenter Case Series

    Gleice Clemente1, Alexandre Souza2, Hilton Leão Filho3, Fernando Coelho3, Carlos Buchpiguel4, Marcos Lima4, Daniela Petry Pioto5, Melissa Fraga1, Ana Paula Sakamoto6, Camila Carneiro4, Rosa Pereira7, Nadia Aikawa7, Clovis Artur Silva7, Lucia Campos8, Camilla Astley9, Bruno Gualano10 and Maria Terreri11, 1Universidade Federal de São Paulo, São Paulo, Brazil, 2UNIFESP-EPM, São Paulo, Brazil, 3Universidade de Sao Paulo/Radiology Institute, São Paulo, Brazil, 4Universidade de São Paulo/Department of Radiology and Oncology, São Paulo, Brazil, 5Pediatric Rheumatology Unit, Universidade Federal de São Paulo, São Paulo, SP, Brazil, 6Federal University of So Paulo (UNIFESP), São Paulo, Brazil, 7Hospital das Clinicas da Faculdade de Medicina da Universidade de São Paulo, São Paulo, Brazil, 8children's institute, Sao Paulo, Brazil, 9University of Sao Paulo, Sao Paulo, Brazil, 10Universidade de Sao Paulo/Rheumatology Division, São Paulo, Brazil, 11UNIFESP, São Paulo, Brazil

    Background/Purpose: The disease activity assessment in c-TA is a challenge in clinical practice, especially in patients who are under immunosuppression. Our aim was to perform…
  • Abstract Number: 1391 • ACR Convergence 2021

    Rituximab Is Superior to Placebo in Polymyalgia Rheumatica Patients: A Double Blind Randomized Controlled Proof of Principle Trial

    Diane Marsman1, Nathan den Broeder2, Frank van den Hoogen3, Alfons den Broeder1 and Aatke van der Maas4, 1Sint Maartenskliniek, Nijmegen, Gelderland, Netherlands, 2Radboud University Medical Centre, Nijmegen, Gelderland, Netherlands, 3Sint Maartenskliniek, Ubbergen, Gelderland, Netherlands, 4St Maartenskliniek, Nijmegen, Gelderland, Netherlands

    Background/Purpose: Corticosteroids remain the cornerstone of polymyalgia rheumatica treatment, but their use has several disadvantages such as long treatment duration and glucocorticoid-related adverse events.1,2 Data…
  • Abstract Number: 1564 • ACR Convergence 2021

    Nailfold Capillaroscopy Characterization in COVID-19: A Case Control Study

    Paola Estefania Bermudez Bermejo1, RODOLFO JIMENEZ-SOTO1, Alain Sanchez-Rodríguez1, Alonso Turrent1, Daniela Mercado- Velasco1, Ian Bravo-Lee1, Mariana Berenice Colli-Cortés2, Everardo Alvarez Hernandez3 and MaryCarmen Amigo1, 1CENTRO MEDICO ABC, Mexico City, Mexico, 2Hospital Regional "General Ignacio Zaragoza" ISSSTE, Mexico City, Mexico, 3HOSPITAL GENERAL DE MEXICO, Mexico City, Mexico

    Background/Purpose: Nailfold capillaroscopy is a relatively easy-to-access, low-cost clinical tool that could help identify early coagulopathy in subjects with SARS-CoV-2, but specific findings vs. controls…
  • Abstract Number: 1887 • ACR Convergence 2021

    Evidence-Based Behçet’s Disease Activity Scale (EBDA) – A New Instrument with Improved Acuity for Major Organ Disease Activity and Remission Depth Assessment

    Maria Caterina Lagdameo1, Hyungrok Do2 and Johannes Nowatzky1, 1Division of Rheumatology, New York University School of Medicine, New York, NY, 2Department of Population Health, NYU School of Medicine, New York

    Background/Purpose: Most current Behçet’s disease (BD) activity assessment tools are strongly based on patient-reported symptoms and findings allowing a wide range of observer-dependent interpretations and…
  • Abstract Number: 0163 • ACR Convergence 2021

    Diagnosis of Giant Cell Arteritis in Spain: Data from the ARTESER Registry

    Eugenio De Miguel1, Jesús T. Sánchez-Costa2, Javier Narvaez3, Miguel Ángel gonzalez-Gay4, Noemí Garrido-Puñal5, Paula V. Estrada-Alarcon6, Iñigo Hernández-Rodríguez7, Elisa Fernández-Fernández8, María T. Silva-Diaz9, Jesús A. Valero-Jaimes10, Ismael González-Fernández11, Julio Sánchez12, Judit Lluch13, Eva Galindez-Agirregoikoa14, Javier Mendizábal-Mateos15, Luis Rodriguez Rodriguez16, Javier Loricera García17, Alejandro Muñoz18, Santos Castañeda19, Patricia Moya20, Patricia Morán-Álvarez21, Vanessa A. Navarro-Angeles6, Joan Calvet-Fontova22, Ivette Casafont23, Francisco Ortiz-Sanjuán24, Selene Labrada-Arrabal25, Cristina Campos-Fernández26, María Alcalde-Villar27, Antonio Juan-Mas28 and Ricardo Blanco29, 1Hospital Universitario La Paz, Madrid, Spain, 2Spanish Society of Rheumatology, Madrid, Spain, 3Division of Rheumatology, Hospital Universitario de Bellvitge, Barcelona, Spain, 4Research group on Genetic Epidemiology and Atherosclerosis in Systemic Diseases and in Metabolic Bone Diseases of the Musculoskeletal System, IDIVAL, Division of Rheumatology, Hospital Universitario Marqués de Valdecilla; School of Medicine, Universidad de Cantabria, Santander, Spain. Cardiovascular Pathophysiology and Genomics Research Unit, School of Physiology, Faculty of Health Sciences, University of the Witwatersrand, Johannesburg, South Africa, 5Hospital Universitario Virgen del Rocío, Sevilla, Spain, 6Hospital de Sant Joan Despí Moisès Broggi. Sant Joan Despí, Barcelona, Spain, 7Complejo Hospitalario Universitario de Vigo, Vigo, Spain, 8Rheumatology department, La Paz University Hospital, Madrid, Spain, 9Complejo Hospitalario Universitario de La Coruña, Coruña, Spain, 10Hospital Universitario Donostia, Donostia-San Sebasti, Spain, 11Hospital Universitario de León, León, Spain, 12Hospital Universitario 12 de Octubre, Madrid, Spain, 13Hospital Universitari Bellvitge, Hospitalet de Llobregat, Spain, 14Hospital Universitario de Basurto, Bilbao, Spain, 15H. Navarra, Navarra, Spain, 16Hospital Clinico San Carlos, Madrid, Spain, 17Hospital Universitario Marqués de Valdecilla, Santander, Spain, 18Hospital Universitario Virgen del Rocío, Sevial, Spain, 19Hospital Universitario de la Princesa, Madrid, Spain, 20Hospital Sant Pau, Barcelona, Spain, 21Hospital Universitario Ramón y Cajal, Madrid, Spain, 22Hospital Universitari Parc Tauli, Sabadell, Spain, 23Hospital Universitari Germans Trias i Pujol, Barcelona, Badalona, Spain, 24H. La Fe, Valencia, Spain, 25Hospital del Mar, Barcelona, Spain, 26Consorci Hospital General Universitari de Valencia, Valencia, Spain, 27Hospital Universitario Severo Ochoa, Leganés, Spain, 28Hospital Universitario Son Llàtzer, Palma de Mallorca, Spain, 29Hospital Universitario Marqués de Valdecilla, IDIVAL, Santander, Spain

    Background/Purpose: To standardize research studies different classification systems are used. Currently, the ACR Giant Cell Arteritis (GCA) 19901 classification criteria is probably the most widely…
  • Abstract Number: 1393 • ACR Convergence 2021

    All-cause Mortality in a Hospital Ascertained Cohort with Giant Cell Arteritis: A Longitudinal Population-level Data Linkage Cohort Study

    Helen Keen1, Warren Raymond2, Susan Lester3, David Preen2, Charles Inderjeeth4, Catherine Hill5 and Johannes Nossent2, 1University of Western Australia, Daglish, Australia, 2University of Western Australia, Perth, Australia, 3Rheumatology Department, The Basil Hetzel Institute, The Queen Elizabeth Hospital, Adelaide, Australia, 4University of Western Australia, Nedlands, Perth, Australia, 5Queen Elizabeth Hospital, Woodville, Australia

    Background/Purpose: Giant Cell Arteritis (GCA) is the most common primary vasculitis in high income countries and ischemic complications of GCA include blindness and stroke. The…
  • Abstract Number: 1625 • ACR Convergence 2021

    Clinical Characteristics of Multisystem Inflammatory Syndrome in Children: A Provincial Cohort

    Herman Tam1, Alison Lopez2, Mona Patel2, Jonathan Rayment3, Lori Tucker4 and Catherine Biggs5, 1Stollery Children's Hospital, University of Alberta, Edmonton, AB, Canada, 2British Columbia Children's Hospital, University of British Columbia, Vancouver, BC, Canada, 3British Columbia Children’s Hospital, University of British Columbia, Vancouver, BC, Canada, 4BC Children's Hospital, Vancouver, BC, Canada, 5[email protected], Vancouver, BC, Canada

    Background/Purpose: Multisystem Inflammatory Syndrome in Children (MIS-C) is a post-infectious complication of COVID-19 infection with overlapping features of Kawasaki Disease (KD) and Toxic Shock Syndrome…
  • Abstract Number: PP10 • ACR Convergence 2021

    Discovering ‘I’ Through Interaction with Support Group Members: A Place of Empathy That Transcends the Limitations of Words

    Noriko Okochi1, Eiji Oishi2 and Mika Ishiguro1, 1Rheumatic Disease and Vasculitis Support Network Japan, Tokyo, Japan, 2Rheumatic Disease and Vasculitis Support Network Japan, Yamaguchi, Japan

    Background/Purpose: Since 5-year-old, I have had unexplained symptoms. At the age of 13, my whole body became inflamed. The pain was so intense that I…
  • Abstract Number: 0418 • ACR Convergence 2021

    Longitudinal Patterns of Renal Function in ANCA-Associated Vasculitis

    Jennifer Hanberg1, Xiaoqing Fu1, Claire Cook2, John Stone3, Hyon K. Choi4 and Zachary Wallace5, 1Massachusetts General Hospital, Boston, MA, 2Division of Rheumatology, Allergy, and Immunology, Mass General Hospital, Boston, MA, 3Massachusetts General Hospital Rheumatology Unit, Harvard Medical School, Boston, MA, 4Massachusetts General Hospital, Lexington, MA, 5Massachusetts General Hospital, Newton, MA

    Background/Purpose: Renal involvement is common in ANCA-associated vasculitis (AAV). Prior analyses show that end stage renal disease (ESRD) in AAV may be multifactorial. Little is…
  • Abstract Number: 1395 • ACR Convergence 2021

    Utility and Validity of the Southend Pretest Probability Score (SPTPS) in a Giant Cell Arteritis Fast Track Clinic: Analysis in a Spanish Cohort of 297 Patients

    Elisa Fernández-Fernández1, Irene Monjo2 and Eugenio De Miguel3, 1Rheumatology department, La Paz University Hospital, Madrid, Spain, 2Hospital La Paz - IdiPAZ, Madrid, Spain, 3Hospital Universitario La Paz, Madrid, Spain

    Background/Purpose: The implementation of fast track clinics (FTC) has enabled quick diagnosis and reduced the blindness rate of giant cell arteritis (GCA). Recently, the Southend…
  • Abstract Number: 1641 • ACR Convergence 2021

    Long-term Cardiovascular Disease and Mortality Following Kawasaki Disease in Childhood: A Systematic Review

    Francis Lao1, Cal Robinson2, Megan Schlorff1, Jocelyne Ewusie3, Karen Beattie1 and Michelle Batthish1, 1McMaster University, Hamilton, ON, Canada, 2The Hospital for Sick Children, Hamilton, ON, Canada, 3St Joseph's Healthcare, Hamilton, ON, Canada

    Background/Purpose: Kawasaki Disease (KD) is a common vasculitis of childhood, with an annual North American incidence of 20-26 per 100,000 children (< 5 years of…
  • Abstract Number: 0420 • ACR Convergence 2021

    Development and Validation of a Simulation Model for Maintenance Treatment in ANCA-Associated Vasculitis

    Zachary Wallace1, John Stone2, Hyon K. Choi3 and Emily Hyle4, 1Massachusetts General Hospital, Newton, MA, 2Massachusetts General Hospital Rheumatology Unit, Harvard Medical School, Boston, MA, 3Massachusetts General Hospital, Lexington, MA, 4Infectious Diseases, Department of Medicine, Massachusetts General Hospital, Boston, MA

    Background/Purpose: ANCA-associated vasculitis (AAV) care has evolved over the last two decades with several approaches to remission maintenance. However, these approaches have trade-offs regarding the…
  • Abstract Number: 1396 • ACR Convergence 2021

    Baricitinib in Relapsing Giant Cell Arteritis: A Prospective Open-Label Single-Institution Study

    Matthew Koster1, Cynthia Crowson2, Rachel Giblon1, Ali Duarte-Garcia1, Jane Jaquith1, Cornelia M. Weyand1 and Kenneth Warrington3, 1Mayo Clinic, Rochester, MN, 2Mayo Clinic, Eyota, MN, 3Mayo Clinic, Rochester, Minnesota

    Background/Purpose: Pre-clinical giant cell arteritis (GCA) mouse models have demonstrated effective suppression of arterial wall lesional T-cells through inhibition of Janus kinase 3 (JAK3) and…
  • Abstract Number: 1720 • ACR Convergence 2021

    Cervical Dysplasia and HPV Infection in Women with Vasculitis

    Taylor Koenig1, Ambra Burrell2, Hilary Kleppel3, Ashlee Weaver4, Veronica Mruk5, Lynn Fussner1, Salem Almaani6 and Alexa Meara1, 1Ohio State University Wexner Medical Center, Columbus, OH, 2Division of Rheumatology, The Ohio State University Wexner Medical Center, Columbus, OH, 3Wright State University, Blacklick, OH, 4Ohio State University College of Medicine, Columbus, OH, 5Ohio State University / Nationwide Children's Hospital, Columbus, OH, 6Ohio State University Medical Center, Columbus, OH

    Background/Purpose: The most common cause of cervical cancer is persistent human papillomavirus (HPV) infection in the cervical epithelium, causing precancerous cervical dysplasia and ultimately cervical…
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