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Abstracts tagged "pulmonary"

  • Abstract Number: 1701 • ACR Convergence 2023

    Treatment Regimens and Mortality in Systemic Sclerosis-associated Pulmonary Arterial Hypertension in Light of the 2022 ESC/ERS Guidelines

    Hilde Jenssen Bjørkekjær1, Cosimo Bruni2, Cathrine Brunborg3, Patricia Carreira4, Paolo Airò5, Carmen Pilar Simeon-Aznar6, Marie-Elise Truchetet7, Alessandro Giollo8, Alexandra Balbir-Gurman9, Mickael Martin10, Christopher Denton11, Armando Gabrielli12, Havard Fretheim13, Imon Barua13, Helle Bitter14, Oyvind Midtvedt13, Torhild Garen15, Kaspar Broch16, Arne Andreassen17, Yoshiya Tanaka18, Gabriela Riemekasten19, Ulf Müller-Ladner20, marco Matucci Cerinic21, Iván Castellvi22, Elise Siegert23, Eric Hachulla24, Oliver Distler2 and Anna-Maria Hoffmann-Vold13, 1Department of Rheumatology, Hospital of Southern Norway, Kristiansand & University of Oslo, Institute of Clinical Medicine, Oslo, Norway, 2Department of Rheumatology, University Hospital Zurich, University of Zurich, Zurich, Switzerland, 3Oslo Centre for Biostatistics and Epidemiology, Research Support Services, Oslo University Hospital - Rikshospitalet, Oslo, Norway, 4Hospital Universitario 12 de Octubre, Madrid, Spain, 5Spedali Civili di Brescia, Scleroderma UNIT, UOC Reumatologia ed Immunologia Clinica, Piazzale Spedali Civili 1, 25123, Brescia, Italy, 6Department of Internal Medicine, Systemic Autoimmune Diseases Unit, Hospital Universitario Vall d'Hebronh, Barcelona, Spain, 7Bordeaux University Hospital, Bordeaux, France, 8University of Verona, Rheumatology Section, Department of Medicine, Verona, Italy, Verona, Italy, 9Rheumatology Institute, Rambam Health Care Campus and Rappaport Faculty of |Medicine, Technion, Haifa, Israel, 10Department of Internal Medicine, INSERM U1313, Poitiers University, Poitiers University Hospital, Poitiers, France, 11University College London, London, United Kingdom, 12Ospedali Riuniti Marche, Ancona, Italy, 13Oslo University Hospital, Oslo, Norway, 14Sorlandet sykehus, Kristiansand, Norway, 15Dept of Rheumatology, University Hospital Oslo, Oslo, Norway, 16Oslo University Hospital, Rikshospitalet, Department of Cardiology, Oslo, Norway, KG Jebsen center, Institute for Experimental Medical Research, University of Oslo, Oslo, Norway, 17Oslo University Hospital, Rikshospitalet, Department of Cardiology, Oslo, Norway, 18University of Occupational and Environmental Health, Kitakyushu, Japan, 19University Clinic Schleswit-Holstein (UKSH), Lübeck, Germany, 20Justus Liebig University Gießen, Campus Kerckhoff, Bad Nauheim, Germany, 21Unit of Immunology, Rheumatology, Allergy and Rare diseases, IRCCS San Raffaele Hospital, Milan, Milan, Italy, 22Hospital de Santa Creu i Sant Pau, Barcelona, Spain, 23Department of Rheumatology, Charité University Hospital, Charité Platz 1, D-10117, Berlin, Germany, 24University of Lille, Lille, France

    Background/Purpose: The 2022 ESC/ERS Guidelines recommend upfront combination therapy for low- and intermediate-risk, and triple therapy for high-risk patients with systemic sclerosis (SSc)-associated pulmonary arterial…
  • Abstract Number: 2353 • ACR Convergence 2023

    Role of Insulin-like Growth Factor Binding Protein-7 (IGFBP7) in Pulmonary Hypertension Pathogenesis and as a Biomarker Systemic Sclerosis-Associated Pulmonary Arterial Hypertension (SSc-PAH)

    Ye Jin Jeong1, Soumyaroop Bhattacharya1, Maria de la Luz Garcia-Hernandez2, Javier Rangel-Moreno1, Qingfu Xu3 and Benjamin Korman1, 1University of Rochester, Rochester, NY, 2University of Rochester, West Henrietta, NY, 3CanSino Biologic Inc., Tianjin, China

    Background/Purpose: Systemic sclerosis (SSc, scleroderma) is an autoimmune connective tissue disease that causes autoimmunity, vascular dysfunction, and fibrosis of the skin, lungs, and other organs.…
  • Abstract Number: 059 • 2023 Pediatric Rheumatology Symposium

    Update of Clinical and Laboratory Features of the Childhood Arthritis and Rheumatology Research Alliance (CARRA) Systemic Juvenile Idiopathic Arthritis-Associated Lung Disease (SJIA-LD) Cohort

    Esraa Eloseily1, Min-Lee Chang2, Mary Ellen Riordan3, allan Russell4, Marc Natter2, Yukiko Kimura5 and Grant Schulert1, 1Cincinnati Children's Hospital Medical Center, Cincinnati, OH, 2Boston Children's Hospital, Boston, MA, 3Hackensack Meridian Health/ Joseph M. Sanzari Children's Hospital, Hackensack, NJ, 4Duke Clinical Research Institute, Durham, NC, 5Hackensack Meridian School of Medicine, Hackensack, NJ

    Background/Purpose: Systemic juvenile idiopathic arthritis (SJIA) associated lung disease (SJIA-LD) is an emerging and life-threatening clinical problem. Despite recent advances, there remain key unanswered questions…
  • Abstract Number: 098 • 2023 Pediatric Rheumatology Symposium

    Characterization of Pulmonary Nodules in Juvenile-onset Systemic Sclerosis: A Single Center Case-Series

    Jonathan Li1, Franziska Rosser1, Sameh Tadros1 and Kathryn Torok2, 1UPMC Children's Hospital of Pittsburgh, Pittsburgh, PA, 2University of Pittsburgh, Pittsburgh, PA

    Background/Purpose: Given the high prevalence of intestinal lung disease (ILD) in systemic sclerosis (SSc) and the low sensitivity of pulmonary function testing for diagnosing ILD,…
  • Abstract Number: L16 • ACR Convergence 2022

    Innovative Anti-pneumococcal Vaccine Strategies versus Standard Vaccination Regimen in Patients with ANCA-associated Vasculitides Receiving Rituximab Therapy: A Multicenter Randomized Controlled Trial (PNEUMOVAS)

    Benjamin Terrier1, Laura Richert2, Grégory Pugnet3, Olivier Aumaitre4, Olivier Moranne5, Elisabeth Diot6, Alexandre Karras7, Fabrice Bonnet8, Claire De Moreuil9, Eric Hachulla10, Thomas Le Gallou11, Céline Lebas10, Francois Maurier12, Cédric Rafat7, Maxime Samson13, Jean-Francois Augusto14, Grégoire Couvrat-Devergne15, Cécile Janssen16, Thierry Martin17, Thomas Quemeneur18, Pierre-Louis Caron19, Cécile-Audrey Durel20, Khalil El Karoui7, Aurélie Grados21, Mathieu Puyade22, Virginie Rieu4, Yurdagul Uzunhan23, Jean-Francois Viallard8, Xavier Puéchal7, Loic Guillevin7, Noémie Huchet8, Hendy Abdoul7, Carine Bellera8, Frédéric Batteux7 and Odile Launay7, 1Cochin Hospital, Paris, France, 2EUCLID, Bordeaux, France, 3CHU, Toulouse, France, 4CHU, Clermont-Ferrand, France, 5CHU, Nimes, France, 6CHU, Tours, France, 7CHU, Paris, France, 8CHU, Bordeaux, France, 9CHU, Brest, France, 10CHU, Lille, France, 11CHU, Rennes, France, 12CH, Metz, France, 13CHU, Dijon, France, 14CHU, Angers, France, 15CH, La Roche sur Yon, France, 16CH, Annecy, France, 17CHU, Strasbourg, France, 18CH, Valenciennes, France, 19CHU, Grenoble, France, 20CHU, Lyon, France, 21CH, Niot, France, 22CHU, Poitiers, France, 23CHU, Bobigny, France

    Background/Purpose: Patients receiving glucocorticoids plus rituximab (RTX) show an increased risk of infection, especially invasive pneumococcal infections. Vaccine responses to influenza, Streptococcus pneumoniae and SARS-CoV-2…
  • Abstract Number: 1049 • ACR Convergence 2022

    Risk Stratification of Patients with Systemic Sclerosis-associated Pulmonary Arterial Hypertension in EUSTAR Using the Current and New Proposed Criteria

    Hilde Jenssen Bjørkekjær1, cosimo bruni2, PATRICIA E CARREIRA3, Paolo Airò4, CARMEN PILAR SIMEON5, Marie-Elise Truchetet6, Alessandro Giollo7, Alexandra Balbir-Gurman8, Mickaël MARTIN9, Chris Denton10, Armando Gabrielli11, Håvard Fretheim12, Imon Barua12, Helle Bitter13, Øyvind Midtvedt12, Kaspar Broch14, Arne Andreassen12, Yoshiya Tanaka15, Gabriela Riemekasten16, Ulf Müller-Ladner17, Marco Matucci-Cerinic2, Ivan Castellvi18, Elise Siegert19, Eric Hachulla20, Oliver Distler21 and Anna-Maria Hoffmann-Vold12, 1Department of Rheumatology, Hospital of Southern Norway, Kristiansand, Norway, Kristiansand, Norway, 2University of Florence, Florence, Italy, 3HOSPITAL 12 DE OCTUBRE, Madrid, Spain, 4Rheumatology and Clinical Immunology Unit, ASST Spedali Civili, Brescia, Italy, 5Hospital Vall D'Hebron, Barcelona, Spain, 6CHU de Bordeaux, Bordeaux, France, 7Rheumatology Section, Department of Medicine, University of Verona, Italy, Verona, Italy, 8Rheumatology Institute, Rambam Health Care Campus, Haifa, Israel, 9Poitiers's Universatory Hospital, Department of Internal Medicine, Poitiers, France, Mignaloux-Beauvoir, France, 10University College London, London, United Kingdom, 11Università Politecnica delle Marche, Ancona, Italy, 12Oslo University Hospital, Oslo, Norway, 13Sorlandet sykehus, Kristiansand, Norway, 14Oslo University Hospital, Rikshospitalet, Department of Cardiology, Oslo, Norway, Oslo, Norway, 15University of Occupational and Environmental Health, Kitakyusyu Fukuoka, Japan, 16University Clinic Schleswit-Holstein (UKSH), Luebeck, Germany, 17JLU Campus KK, Bad Nauheim, Germany, 18Hospital Universitari de la Santa Creu i Sant Pau, Vilafranca del Pened, Spain, 19Charité Hospital, Berlin, Germany, 20University of Lille, LILLE, France, 21Department of Rheumatology, University Hospital Zurich, University of Zurich, Zürich, Switzerland

    Background/Purpose: Pulmonary arterial hypertension (PAH) is a major clinical challenge in systemic sclerosis (SSc). A new definition for precapillary PH is proposed. Risk stratification is…
  • Abstract Number: 1941 • ACR Convergence 2022

    Pediatric Idiopathic Pulmonary Hemosiderosis – a Single-Center, Retrospective Study Comparing Use of Commonly Used Steroid-Sparing Agents

    Melissa Argraves1, Melissa Lerman1, Julie Chase2 and Samuel Goldfarb3, 1Children's Hospital of Philadelphia, Philadelphia, PA, 2University of Kentucky, Lexington, KY, 3University of Minnesota, Minneapolis, MN

    Background/Purpose: Idiopathic Pulmonary Hemosiderosis (IPH) is a rare, pediatric predominant condition causing episodic diffuse alveolar hemorrhage, which can be recurrent and life-threatening. Chronic steroid use…
  • Abstract Number: 1057 • ACR Convergence 2022

    Usefulness of REVEAL 2.0 Score as a Prognosis Tool of All-Cause Pulmonary Hypertension in Systemic Sclerosis Patients: A Multicentric Study

    Ivette Casafont-Solé1, Laura Calvo2, Anne Riveros-Frutos3, Carlos De la Puente Bujidos4, Pau Alcubilla5, Lourdes Mateo1 and Ivan Castellví6, 1Hospital Universitari Germans Trias i Pujol, Badalona, Spain, 2Hospital Universitario Ramon y Cajal, Madrid, Spain, 3Hospital Universitari Germans Trias i Pujol, Barcelona, Spain, 4Ramon y Cajal University Hospital, Madrid, Spain, 5Hospital Clínic de Barcelona, Barcelona, Spain, 6Hospital Universitari de la Santa Creu i Sant Pau, Barcelona, Spain

    Background/Purpose: Pulmonary arterial hypertension (PAH) leads to a progressive right heart failure and death.PAH is a leading cause of death in Systemic Sclerosis (SSc). To…
  • Abstract Number: 2160 • ACR Convergence 2022

    The Role of CCL21 in Serum Samples from Systemic Sclerosis Patients

    Henriette Didriksen1, Øyvind Molberg2, Adi Mehta3, Suzana Jordan4, Håvard Fretheim3, Einar Gude3, Thor Ueland3, Cathrine Brunborg3, Vyacheslav Palchevskiy5, Torhild Garen3, Øyvind Midtvedt3, Arne Andreassen3, Fridtjof Lund-Johansen3, Oliver Distler4, John Belperio5 and Anna-Maria Hoffmann-Vold3, 1Oslo University Hospital, Moss, Norway, 2Department of Rheumatology, Oslo University Hospital, Oslo, Norway, Oslo, Norway, 3Oslo University Hospital, Oslo, Norway, 4Department of Rheumatology, University Hospital Zurich, University of Zurich, Zürich, Switzerland, 5University of California Los Angeles, Los Angeles, CA

    Background/Purpose: Chemokines appear to be important for the pathogenesis of autoimmune diseases. Humans may generate antibodies targeting chemokines leading to inhibition of signaling and driving…
  • Abstract Number: 1058 • ACR Convergence 2022

    Clinical Characteristics and Survival of Combined Pulmonary Arterial Hypertension and Interstitial Lung Disease in Systemic Sclerosis

    Jessica Fairley1, Dylan Hansen2, Laura Ross3, Susanna Proudman4, Jo Sahhar5, Gene-Siew Ngian6, Jenny Walker7, Lauren Host8, Kathleen Morrisroe2, Diane Apostolopoulos9, Nava Ferdowsi2, Michelle Wilson9, Maryam Tabesh2, Wendy Stevens2 and Mandana Nikpour10, 1The University of Melbourne, Melbourne, Australia, 2St Vincent's Hospital Melbourne, Melbourne, Australia, 3The University of Melbourne at St. Vincent's Hospital, Brunswick, Australia, 4University of Adelaide, Medindie, Australia, 5Monash Health, Melbourne, Australia, 6Melbourne Health, Northcote, Australia, 7Royal Adelaide Hospital, Adelaide, Australia, 8Fiona Stanley Hospital, London, United Kingdom, 9Monash University, Melbourne, Australia, 10The University of Melbourne at St. Vincent's Hospital Melbourne, Melbourne, Australia

    Background/Purpose: Pulmonary arterial hypertension (PAH) and interstitial lung disease (ILD) are the leading causes of systemic sclerosis (SSc) associated death. There is increasing interest in…
  • Abstract Number: 2172 • ACR Convergence 2022

    Pulmonary Function in Patients Diagnosed of Early Systemic Sclerosis: 10 Years-Experience

    Samuel Leal Rodriguez1, Francisco Miguel Ortiz Sanjuan2, José Ivorra Cortés3, Laura Mas Sanchez3, Pablo Muñoz Martinez4, Carmen Riesco Bárcena5, Anderson Huaylla Quispe6, Cristobal Pavez Perales3, Inés Cánovas Olmos3, Luis Gonzalez Puig7, Elena Grau García3, Isabel Martínez-Cordellat3, Carmen Nájera Herranz3, Rosa Negueroles Albuixech3, JOSE ELOY OLLER RODRIGUEZ8, Elvira Vicens Bernabeu2, Alba Torrat Novés5, Daniel Ramos Castro3 and José andrés Román ivorra1, 1Hospital Universitari i Politécnic La Fe, València, Spain, 2Hospital Universitario de La Fe, València, 3Rheumatology Department. Hospital Universitario y Politécnico La Fe, València, Spain, 4Rheumatology Department. Hospital Universitario y Politécnico La Fe, Sagunto, Spain, 5Rheumatology Department. Hospital Universitario y Politécnico La Fe, València, 6Medicina, València, Spain, 7Hospital La Fe, Torrente, Valencia, Spain, 8Hospital Universitario de La Fe, València, Spain

    Background/Purpose: Interstitial lung disease (ILD) is a frequent complication of systemic sclerosis (SSc), often progressive and has a poor prognosis. A restrictive ventilatory defect could…
  • Abstract Number: 1090 • ACR Convergence 2022

    Pulmonary Function Testing (PFT) in Patients with Antineutrophil Cytoplasmic Antibodies (ANCA)-associated Vasculitis (AAV): Correlation with Radiologic Imaging

    Johannes Dieterich1, You-Shan Feng2, Juliane Mahrhold1, Abdallah El Rai3 and Bernhard Hellmich1, 1Department of Internal Medicine, Rheumatology and Immunology, Medius Kliniken, University of Tübingen, Kirchheim Teck, Germany, 2Institute for clinical Epidemiology and Biometry, University of Tübingen, Tübingen, Germany, 3Department of Radiology und Nuclear Medicine, Medius Kliniken, University of Tübingen, Nürtingen, Germany

    Background/Purpose: Although pulmonary manifestations occur frequently in AAV, empirical evidence of their impact on pulmonary function is scarce. This project analyzed PFT data from a…
  • Abstract Number: 2175 • ACR Convergence 2022

    Evaluation of the Distribution of Haemodynamic Parameters and Prognostic Impact in a Cohort of Patients with Systemic Sclerosis

    Zoe Brown1, Dylan Hansen2, Wendy Stevens2, Laura Ross1, Nava Ferdowsi2, Susanna Proudman3, Jenny Walker4, Jo Sahhar5, Gene-Siew Ngian6, Lauren Host7, Gabor Major8, Mandana Nikpour9 and Kathleen Morrisroe2, 1St Vincent's Hospital, Melbourne, Australia, 2St Vincent's Hospital Melbourne, Melbourne, Australia, 3University of Adelaide, Medindie, Australia, 4Flinders Medical Centre, Flinders University, Daw Park, Australia, 5Monash Health, Melbourne, Australia, 6Melbourne Health, Northcote, Australia, 7Fiona Stanley Hospital, London, United Kingdom, 8Hunter New England Health Service, Rankin Park - Newcastle, New South Wales, Australia, 9The University of Melbourne at St. Vincent's Hospital Melbourne, Melbourne, Australia

    Background/Purpose: Scleroderma (SSc) is a complex multisystem autoimmune disease, characterised by vasculopathy and fibrosis of skin and organs. Involvement of the cardiovascular system occurs frequently…
  • Abstract Number: 1108 • ACR Convergence 2022

    Abnormal Baseline Chest CT Shows Increased Risk for Immune Checkpoint Inhibitor Associated Pneumonitis

    Danielle Stahlbaum1, Renea Jablonski1, Mary Strek2 and Pankti Reid1, 1University of Chicago Medical Center, Chicago, IL, 2University of Chicago, Chicago, IL

    Background/Purpose: Immune checkpoint inhibitors (ICIs) have revolutionized cancer therapy but can result in off-target toxicities known as immune-related adverse events (irAEs). With increased use of…
  • Abstract Number: 2176 • ACR Convergence 2022

    Novel Tissue Turnover Blood Markers Are Associated with Pulmonary Arterial Hypertension and NYHA Stages in Patients with Systemic Sclerosis

    Signe Holm Nielsen1, Sine Søndergaard Korsholm2, Axel Diederichsen3, Morten Karsdal1, John Bonde Knudsen4, Anne-Christine Bay-Jensen1, Louise Diederichsen5 and Christoffer Tandrup Nielsen6, 1Nordic Bioscience, Herlev, Denmark, 2Center for Rheumatology and Spine Diseases, Rigshospitalet, Copenhagen, Denmark, Dept of Rheumatology, Odense University Hospital (OUH), Odense, Denmark, 3Dept of Cardiology, OUH, Odense, Denmark, Odense, 4Dept of Rheumatology, OUH, Odense, Denmark., Odense, 5Copenhagen University Hospital, Rigshospitalet, Dragør, Denmark, 6Center for Rheumatology and Spine Diseases, Rigshospitalet, Copenhagen, Denmark

    Background/Purpose: Systemic sclerosis (SSc) is characterized by vasculopathy and fibrosis of the skin and internal organs. Cardiac involvement, pulmonary arterial hypertension (PAH), and interstitial lung…
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All abstracts accepted to ACR Convergence are under media embargo once the ACR has notified presenters of their abstract’s acceptance. They may be presented at other meetings or published as manuscripts after this time but should not be discussed in non-scholarly venues or outlets. The following embargo policies are strictly enforced by the ACR.

Accepted abstracts are made available to the public online in advance of the meeting and are published in a special online supplement of our scientific journal, Arthritis & Rheumatology. Information contained in those abstracts may not be released until the abstracts appear online. In an exception to the media embargo, academic institutions, private organizations, and companies with products whose value may be influenced by information contained in an abstract may issue a press release to coincide with the availability of an ACR abstract on the ACR website. However, the ACR continues to require that information that goes beyond that contained in the abstract (e.g., discussion of the abstract done as part of editorial news coverage) is under media embargo until 10:00 AM CT on October 25. Journalists with access to embargoed information cannot release articles or editorial news coverage before this time. Editorial news coverage is considered original articles/videos developed by employed journalists to report facts, commentary, and subject matter expert quotes in a narrative form using a variety of sources (e.g., research, announcements, press releases, events, etc.).

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