Abstracts tagged "pediatric rheumatology and vasculitis"

Abstract Number: 832 • 2018 ACR/ARHP Annual Meeting
Immunoglobuline a Vasculitis: Comparison between Pediatric and Adult Population
Martin Brom¹, Ignacio Javier Gandino², Marina Scolnik³, Valeria Scaglioni³, Maria Britos⁴, Carmen De Cunto⁴ and Enrique R Soriano³, ¹Rheumatology Unit, Internal Medicine Service, Hospital Italiano de Buenos Aires, Instituto Universitario Hospital Italiano de Buenos Aires, and Fundacion PM Catoggio, Buenos Aires, Argentina, ²Rheumatology Unit, Internal Medicine Service, Hospital Italiano de Buenos Aires, Instituto Universitario Hospital Italiano de Buenos Aires, and Fundacion PM Catoggio, Argentina., Buenos Aires, Argentina, ³Rheumatology Unit, Internal Medicine Service. Hospital Italiano Buenos Aires. Argentina, Buenos Aires, Argentina, ⁴Pediatric Rheumatology, Hospital Italiano De Buenos Aires, Buenos Aires, Argentina
Background/Purpose: Immunoglobuline A (IgA) Vasculitis, formerly known as Henoch-Schönlein purpura, is a small-vessel leukocytoclastic vasculitis due to deposition of IgA1, a subclass of IgA. Although…
Abstract Number: 106 • 2017 Pediatric Rheumatology Symposium
Atypical manifestations and main misdiagnoses of Takayasu’s arteritis in childhood: a multicenter study of 71 patients
Gleice Clemente¹, Ana Paula Sakamoto², Silvana B. Sacchetti Sr.³, Virgínia Ferriani⁴, Flavio Sztajnbok⁵, Sheila Oliveira⁶, Blanca Bica⁷, Andre Cavalcanti⁸, Teresa Robazzi⁹, Marcia Bandeira¹⁰ and Maria Teresa Terreri², ¹Pediatric Rheumatology Unit, Federal University of São Paulo (UNIFESP - Univesidade Federal de São Paulo), São Paulo, Brazil, ²Pediatric Rheumatology Unit, Federal University of São Paulo (UNIFESP - Universidade Federal de São Paulo), São Paulo, Brazil, ³Pediatric Rheumatology Unit, Irmandade da Santa Casa de Misericórdia de São Paulo, São Paulo, Brazil, ⁴Department of Pediatrics School of Medicine of Ribeirão Preto, University of São Paulo (USP-RP), Ribeirão Preto, Brazil, ⁵Paediatric Rheumatology International Trials Organization (PRINTO), Istituto Giannina Gaslini, Genoa, Italy, ⁶Pediatric Rheumatology, Universidade F Rio De Janeiro, Rio De Janeiro, Brazil, ⁷Hospital Universitário Clementino Fraga Filho, Rio de Janeiro, Brazil, ⁸Novartis, Sao Paulo, Brazil, ⁹Pediatrics, Universidade Federal da Bahia, Salvador, Brazil, ¹⁰Pediatric Rheumatology Unit, Hospital Pequeno Príncipe, Curitiba, Brazil
Background/Purpose: Takayasu’s arteritis is a chronic inflammatory disease that affects the wall of large and medium-sized blood vessels. At the beginning of the disease, non-specific…
Abstract Number: 108 • 2017 Pediatric Rheumatology Symposium
Characteristics and long-term outcome of children and adolescents with initial diagnosis of Behçet’s disease in a tertiary care center in Brazil
Milagro Raquel Tovar-Avila¹, Francisco Hugo Gomes², Lucenir Da Silva³, Virginia Ferriani⁴ and Luciana Carvalho², ¹Pediatric Reumatology Division, Ribeirão Preto Medical School - University of São Paulo, Rbeirão Preto, Brazil, ²Pediatric Rheumatology Division, Ribeirão Preto Medical School - University of São Paulo, Ribeirão Preto, Brazil, ³Rheumatology Division, Ribeirão Preto Medical School - University of São Paulo, Ribeirão Preto, Brazil, ⁴Pediatric Reumatology Division, Ribeirão Preto Medical School - University of São Paulo, Ribeirão Preto, Brazil
Background/Purpose: Behet's disease (BD) is a rare systemic inflammatory disease with nonspecific clinical presentation that can mimic infections, tumors and other diseases. Diagnostic delay of…
Abstract Number: 2396 • 2016 ACR/ARHP Annual Meeting
Initiation of Dialysis in Pediatric ANCA-Associated Vasculitis
Karen James¹, Rui Xiao^2,3, Peter A. Merkel^4,5 and Pamela F. Weiss⁶, ¹Pediatric Rheumatology, The Children's Hospital of Philadelphia, Philadelphia, PA, ²Department of Pediatrics, Division of Biostatistics, Children's Hospital of Philadelphia, Philadelphia, PA, ³Department of Biostatistics and Epidemiology, University of Pennsylvania, Philadelphia, PA, ⁴Penn Vasculitis Center, Division of Rheumatology, University of Pennsylvania, Philadelphia, PA, ⁵Division of Rheumatology, University of Pennsylvania, Philadelphia, PA, ⁶Division of Rheumatology, Center for Pediatric Clincial Effectiveness, Children's Hospital of Philadelphia, Philadelphia, PA
Background/Purpose: ANCA-associated vasculitis (AAV) is a group of rare systemic vasculitidies with significant morbidity and mortality. There have been no comparative effectiveness studies of AAV…
Abstract Number: 876 • 2015 ACR/ARHP Annual Meeting
Damage Develops Early and Is Common in Children with Chronic Systemic Vasculitis
Lorraine O'Neill¹, Marinka Twilt², Susanne Benseler³, Dirk Föll⁴, David A. Cabral⁵ and Raashid Luqmani⁶, ¹University of Oxford, Oxford, United Kingdom, ²Division of Rheumatology, The Hospital for Sick Children, Toronto, ON, Canada, ³Pediatrics, University of Calgary, Toronto, ON, Canada, ⁴University of Muenster, Muenster, Germany, ⁵Pediatrics/Rm K4-121, BC Children's Hospital, Vancouver, BC, Canada, ⁶Nuffield Department of Orthopaedics Rheumatology and Musculoskeletal Sciences, University of Oxford, Oxford, United Kingdom
Background/Purpose: The chronic primary systemic vasculitides are a group of rare conditions with affected patients subject to a significant burden of morbidity from both the…
Abstract Number: 2415 • 2015 ACR/ARHP Annual Meeting
Use of Plasma Exchange for Children Hospitalized with ANCA-Associated Vasculitis in the United States
Karen James¹, Rui Xiao², Peter A. Merkel³ and Pamela F. Weiss¹, ¹Rheumatology, Children's Hospital of Philadelphia, Philadelphia, PA, ²Department of Biostatistics and Epidemiology, University of Pennsylvania, Philadelphia, PA, ³Division of Rheumatology, University of Pennsylvania, Philadelphia, PA
Background/Purpose: ANCA-associated vasculitis (AAV) is a group of rare systemic vasculitidies with significant morbidity and mortality. Plasma exchange (PLEX) has been shown to decrease risk…
Abstract Number: 3179 • 2015 ACR/ARHP Annual Meeting
Diagnosing Childhood Small Vessel CNS Vasculitis
Marinka Twilt¹, Maryam Nabavi Nouri², Pascal N. Tyrrell³, Anastasia Dropol¹, Shehla Sheikh⁴, Cynthia Hawkins⁵ and Susanne Benseler^6,7, ¹Rheumatology, Alberta Children's Hospital, Calgary, AB, Canada, ²Neurology, The Hospital for Sick Childern, Toronto, ON, Canada, ³Department of Medical Imaging, University of Toronto, Toronto, ON, Canada, ⁴Rheumatology, The Hospital for Sick Children, Toronto, ON, Canada, ⁵Paediatric Laboratory Medicine, The Hospital for Sick Children, Toronto, ON, Canada, ⁶Alberta Children's Hospital Research Institute/University of Calgary, Calgary, AB, Canada, ⁷Pediatrics/Alberta Children's Hospital, Department of Pediatrics/University of Calgary, Calgary, AB, Canada
Background/Purpose: Childhood primary small vessel CNS vasculitis (SVcPACNS) is an increasingly recognized inflammatory brain disease with high morbidity and mortality mandating an elective brain biopsy…
Abstract Number: 2903 • 2014 ACR/ARHP Annual Meeting
Early Outcomes in Pediatric Antineutrophil Cytoplasmic Antibody (ANCA) Associated Vasculitis (AAV)
Kimberly Morishita¹, Susanne Benseler², Rae S.M. Yeung³, Thomas Mason II⁴, Dawn Wahezi⁵, Kenneth N. Schikler⁶, Erica F. Lawson⁷, Susan Nielsen⁸, Sirirat Charuvanij⁹, Paul Dancey¹⁰, Susan Shenoi¹¹, Linda Wagner-Weiner¹², Angelyne Sarmiento¹, David A. Cabral¹³ and For the PedVas Initiative¹, ¹BC Children's Hospital and University of British Columbia, Vancouver, BC, Canada, ²Pediatrics/Alberta Children's Hospital, Department of Pediatrics/University of Calgary, Calgary, AB, Canada, ³Rheumatology, The Hospital for Sick Children and University of Toronto, Toronto, ON, Canada, ⁴Division of Rheumatology - Department of Medicine, Mayo Clinic, Rochester, MN, ⁵Pediatric Rheumatology, Children's Hospital at Montefiore, Bronx, NY, ⁶Department of Pediatrics, Univ of Louisville Schl of Med, Louisville, KY, ⁷Pediatrics, University of California, San Francisco, San Francisco, CA, ⁸Pediatric rheumatology, Rigshospitalet, Copenhagen, Denmark, ⁹Pediatrics, Siriraj Hospital, Bangkok, Thailand, ¹⁰Pediatrics, Janeway Children's Hospital, St. John's, NL, Canada, ¹¹Pediatric Rheumatology, Seattle Childrens Hospital, seattle, WA, ¹²Pediatric Rheumatology, University of Chicago Hospital, Chicago, IL, ¹³Pediatrics, BC Children's Hospital and University of British Columbia, Vancouver, BC, Canada
Background/Purpose: Childhood AAV is rare and outcome studies are limited. The PedVas Study is an international initiative collecting clinical data (to A Registry of Childhood…
Abstract Number: 2195 • 2013 ACR/ARHP Annual Meeting
Expanding The Spectrum Of Recombination Activating Gene-1 Deficiency To Include Early Onset Autoimmunity
Lauren A. Henderson¹, Francesco Frugoni¹, Gregory Hopkins², Helen de Boer², Sung-Yun Pai^2,3, Yu Nee Lee¹, Jolan E. Walter⁴, Melissa M. Hazen¹ and Luigi D Notarangelo^5,6, ¹Division of Immunology, Boston Children's Hospital, Boston, MA, ²Division of Hematology and Oncology, Boston Children's Hospital, Boston, MA, ³Division of Pediatric Oncology, Dana-Farber Cancer Institute, Boston, MA, ⁴Division of Allergy/Immunology, Massachusetts General Hospital for Children, Boston, MA, ⁵Division of Immunology and The Manton Center for Orphan Disease Research, Boston Children's Hospital, Boston, MA, ⁶Harvard Stem Cell Institute, Boston, MA
Background/Purpose: We sought to identify the etiology of early onset autoimmunity and T cell lymphopenia in two siblings through genetic and functional studies. Newborn screening…
Abstract Number: 1661 • 2013 ACR/ARHP Annual Meeting
The Spectrum of childhood Inflammatory Brain Diseases; An Increasingly Recognised Field
Marinka Twilt¹, Eyal Muscal², Tania Cellucci³, Pavla Dolezalova⁴, Rob Forsyth⁵, Susan Kim⁶, David A. Cabral⁷, Johannes Roth⁸, Adam Kirton⁹, Rolando Cimaz¹⁰, Jasmin Kummerle-Deschner¹¹, Annet van Royen-Kerkhof¹², Jürgen Brunner¹³, Gaelle Chedeville¹⁴, Jordi Anton¹⁵, Angela Robinson¹⁶, Mary Toth¹⁷, Tilmann Kallinich¹⁸, Claudia Bracaglia¹⁹, Alexis Boneparth²⁰, Shehla Sheikh²¹ and Susanne M. Benseler²¹, ¹Division of Rheumatology, The Hospital for Sick Children, Toronto, ON, Canada, ²TCH Pediatric Rheum Center, Baylor College of Medicine, Houston, TX, ³Rheumatology, Hamilton Health Sciences, McMaster, Hamilton, ON, Canada, ⁴Pediatric Rheumatology Unit, Department of Pediatrics and Adolescent Medicine, General University Hospital in Prague, Prague, Czech Republic, ⁵Newcastle upon Tyne's NHS foundation Trust, Newcastle upon Tyne, United Kingdom, ⁶Division of Immunology, Boston Children's Hospital, Boston, MA, ⁷University of British Columbia, Vancouver, BC, Canada, ⁸University of Ottawa, Ottawa, ON, Canada, ⁹Neurology, Alberta Children's Hospital, Calgary, AB, Canada, ¹⁰Rheumatology Unit, A. Meyer Children's Hospital, Florence, Italy, ¹¹University Childrens Clinic Tuebingen, Tuebingen, Germany, ¹²Department of Pediatric Immunology & Rheumatology, Wilhelmina Children’s Hospital, University Medical Center Utrecht, Utrecht, Netherlands, ¹³pediatric Rheumatology, University Children's Hospital, Innsbruck, Austria, ¹⁴Pediatric Rheumatology, Montreal Children's Hospital, Montreal, QC, Canada, ¹⁵Rheumatology, Hospital Sant Joan de Deu, Barcelona, Spain, ¹⁶Pediatrics, Rainbow Babies & Children's Hospital / Case Medical Center, Cleveland, OH, ¹⁷Rheumatology, Akron Children's Hospital, Akron, OH, ¹⁸Charite, University Medicine Berlin, Berlin, Germany, ¹⁹Department of Pediatric Medicine, Division of Rheumatology, Ospedale Pediatrico Bambino Gesù, IRCCS, Rome, Italy, ²⁰Pediatrics, The Children's Hospital at Montefiore, Bronx, NY, ²¹Rheumatology, The Hospital for Sick Children, Toronto, ON, Canada
Background/Purpose: Childhood Inflammatory Brain diseases are potentially life-threatening diseases leading to severe neurological deficits if not treated. The spectrum of childhood inflammatory brain diseases is…
Abstract Number: 750 • 2013 ACR/ARHP Annual Meeting
Maintenance Treatment In Childhood Granulomatosis With Polyangiitis
Marinka Twilt¹, Rayfel Schneider², Diane Hebert³, Elizabeth Harvey³, Ronald M. Laxer², Sharon Dell⁴, Christoph Licht³ and Susanne M. Benseler², ¹Division of Rheumatology, The Hospital for Sick Children, Toronto, ON, Canada, ²Rheumatology, The Hospital for Sick Children, Toronto, ON, Canada, ³Nephrology, The Hospital for Sick Children, Toronto, ON, Canada, ⁴Respiratory Medicine, The Hospital for Sick Children, Toronto, ON, Canada
Background/Purpose: Granulomatosis with Polyangiitis (GPA) is a rare but life threatening disease. Most children present with pulmonary bleeds and/or renal failure. Most treatment regimens are…
Abstract Number: 295 • 2012 ACR/ARHP Annual Meeting
Brain Biopsy Diagnosis in Magnetic Resonance Imaging Negative Childhood Primary Angiitis of the Central Nervous System
Senq-J Lee¹, Cynthia Hawkins², Suzanne Laughlin³, Shehla Sheikh⁴ and Susanne M. Benseler⁴, ¹Division of Rheumatology, The Hospital for Sick Children, Toronto, ON, Canada, ²Paediatric Laboratory Medicine, The Hospital for Sick Children, Toronto, ON, Canada, ³Diagnostic Imaging, The Hospital for Sick Children, Toronto, ON, Canada, ⁴Rheumatology, The Hospital for Sick Children, Toronto, ON, Canada
Background/Purpose: Primary CNS vasculitis in childhood (cPACNS) is a devastating inflammatory brain disease mandating rapid and accurate diagnostic evaluation, in order to optimize neurologic outcomes. …
Abstract Number: 304 • 2012 ACR/ARHP Annual Meeting
Burden of Childhood Central Nervous System Vasculitis: Identifying High Risk Factors for Poor Cognitive Outcome
Peter J. Gowdie¹, Marinka Twilt¹, Pascal N. Tyrrell¹, Robyn Westmacott², Tania Cellucci¹, Shehla Sheikh¹, Nick Blancette¹ and Susanne M. Benseler¹, ¹Rheumatology, The Hospital for Sick Children, Toronto, ON, Canada, ²Psychology, The Hospital for Sick Children, Toronto, ON, Canada
Background/Purpose: Childhood primary angiitis of the CNS (cPACNS) is an increasingly recognized, reversible cause of severe neurological and psychiatric deficit such as stroke, refractory seizures…
Abstract Number: 279 • 2012 ACR/ARHP Annual Meeting
Distribution of Vasculitides in Childhood Arthritis and Rheumatology Research Alliance-Affiliated Pediatric Rheumatology Centers in the United States
Melissa A. Lerman¹, Peter A. Merkel² and for the CARRA Registry Investigators³, ¹Division of Rheumatology, Children's Hospital of Philadelphia, Philadelphia, PA, ²University of Pennsylvania, Philadelphia, PA, ³Stanford, CA
Background/Purpose: The epidemiology of pediatric vasculitis is poorly described. Two studies in the 1990s described the frequency in pediatric rheumatology centers in the United States…

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