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Abstracts tagged "neurology"

  • Abstract Number: 1114 • ACR Convergence 2021

    Pachymeningitis: The Mayo Clinic Experience

    Emily Gilbert1, Mina Al-Awqati2, Tina Gunderson3 and Florentina Berianu1, 1Mayo Clinic, Jacksonville, FL, 2University of Illinois, Chicago, IL, 3Mayo Clinic, Rochester, MN

    Background/Purpose: Pachymeningitis is a rare disorder defined by localized or generalized inflammatory thickening of the dura. It can be associated with infections, malignancy, autoimmune disorders,…
  • Abstract Number: 1883 • ACR Convergence 2021

    Neuro-Behcet’s Disease: 20 Years Single Center Experience of Cyclophosphamide for Induction of Remission

    Pablo Vinicius da Fonseca, Henrique Ayres Mayrink Giardini,, Célio Roberto Gonçalves and Leandro Lara do Prado, Faculdade de Medicina da Universidade de São Paulo, São Paulo, Brazil

    Background/Purpose: Behçet's disease (BD) is a systemic vasculitis. Neurological involvement, also known as Neuro-Behçet's disease (NBD), leads to great morbimortality. Diagnosis is challenging, since clinical…
  • Abstract Number: 1885 • ACR Convergence 2021

    Biological Therapy in Refractory Neurobehçet’s Disease. Multicenter Study of 42 Patients

    Alba Herrero-Morant1, José Luis Martin-Varillas2, Vanesa Calvo-Río3, Santos Castañeda4, Olga Maíz5, Ana Blanco6, Julio Sánchez7, Norberto Ortego8, Enrique Raya9, Anahy Maria Brandy-Garcia10, Alejandro Olive-Marques11, Agueda Prior-Español12, Clara Moriano13, Elvira Díez14, Rafael Melero15, Jenaro Enrique Grana Gil16, Álvaro Seijas-López17, Ana Urruticoechea-Arana18, Ángel Ramos-Calvo19, Concepcion Delgado-Beltran20, Marta Loredo-Martinez20, Eva Salgado21, Francisca Sivera22, Ignacio Torre23, Javier Narvaez24, Jose Luis Andreu25, Olga Martinez26, Ricardo Gómez de la Torre27, Sabela Fernandez-Aguado28, Susana Romero-Yuste29, Gerard Espinosa30, Miguel Ángel gonzalez-Gay31 and Ricardo Blanco3, 1Hospital Universitario Marqués de Valdecilla, Santander, Spain, 2Hospital Sierrallana, Torrelavega, Spain, 3Hospital Universitario Marqués de Valdecilla, IDIVAL, Santander, Spain, 4Hospital Universitario de la Princesa, Madrid, Spain, 5Hospital Universitario de Donostia, San Sebastián, Spain, 6Hospital Universitario de Donostia, San Sebastián, 7Hospital Universitario 12 de Octubre, Madrid, Spain, 8Medicine Department, Universidad de Granada, Granada, Spain, 9Hospital San Cecilio, Granada, Spain, 10Hospital Germans Trias i Pujol, Badalona, Spain, 11Rheumatology Service. Hospital Germans Trias i Pujol, Barcelona, Spain, 12Department of Rheumatology, Germans Trias i Pujol. University Hospital, Badalona, Spain, 13Hospital Universitario de León, León, Spain, 14Hospital de León, León, Spain, 15Complexo Hospitalario Universitario de Vigo, Vigo, Galicia, Spain, 16Hospital Universitario de A Coruña, A Corua, Spain, 17Hospital Universitario de A Coruña, A Coruña, Spain, 18H. Can Misses, Elvissa, Spain, 19Complejo Hospitalario de Soria, Soria, Spain, 20Hospital Clínico Lozano Blesa, Zaragoza, Spain, 21Complejo Hospitalario Universitario de Ourense, Ourense, Spain, 22Hospital Universitario de Elda, Alicante, Spain, 23Hospital Universitario de Basurto, Bilbao, Spain, 24Division of Rheumatology, Hospital Universitario de Bellvitge, Barcelona, Spain, 25Hospital Universitario Puerta de Hierro, Madrid, Spain, 26H. Salamanca, Zamora, Spain, 27H. Asturias, Oviedo, Spain, 28Hospital Universitario de Cabueñes, Gijón, Spain, 29Complejo Hospitalario Universitario de Pontevedra, Pontevedra, Spain, 30Hospital Clinic, Barcelona, Spain, 31Research group on Genetic Epidemiology and Atherosclerosis in Systemic Diseases and in Metabolic Bone Diseases of the Musculoskeletal System, IDIVAL, Division of Rheumatology, Hospital Universitario Marqués de Valdecilla; School of Medicine, Universidad de Cantabria, Santander, Spain. Cardiovascular Pathophysiology and Genomics Research Unit, School of Physiology, Faculty of Health Sciences, University of the Witwatersrand, Johannesburg, South Africa

    Background/Purpose: Neurobehçet’s disease (NBD) is a severe complication of Behcet's disease (BD). Despite well-established therapies, with glucocorticoids and conventional immunosuppressants (cIS) a significant proportion of…
  • Abstract Number: 0123 • ACR Convergence 2021

    Vestibulocortical Stimulation with Caloric Irrigation Reduces Pain and Improves Subjective Well-Being in Fibromyalgia: An Open-Label Pilot Trial

    Michael Kaplan1, Celine Zhou1, Emily Carroll1, Alan Weinberg2, Daniel Clauw3, Trung Thanh Ngo4 and Ioannis Tassiulas5, 1The Mount Sinai Hospital, Manhattan, NY, 2The Mount Sinai Hospital, New York, NY, 3University of Michigan, Ann Arbor, MI, 4University of Queensland & Translational Research Institute, Woolloongabba, Australia, 5Icahn School of Medicine at Mount Sinai, New York, NY

    Background/Purpose: Safe and effective therapies for fibromyalgia (FM) remain a major unmet clinical need. Vestibulocortical stimulation (VCS) via caloric irrigation is a safe, inexpensive, non-invasive…
  • Abstract Number: 0417 • ACR Convergence 2021

    Neurologic Involvement in ANCA-associated Vasculitis: Data from Multicenter Longitudinal Observational Study

    Rula Hajj-Ali1, Robert Butler2, Carol Langford3, Leonard Calabrese2, David Cuthbertson4, Nader Khalidi5, CURRY LEE MD KOENING6, Carol McAlear7, Paul Monach8, Larry Moreland9, Christian Pagnoux10, Philip Seo11, Ulrich Specks12, Antoine Sreih7, Kenneth Warrington13 and Peter Merkel7, 1Cleveland Clinic, Hunting Valley, OH, 2Cleveland Clinic, Cleveland, OH, 3Cleveland Clinic, Moreland Hills, OH, 4University of South Florida, Tampa, FL, 5McMaster University, Hamilton, ON, Canada, 6LIMITED TO OFFICIAL UNIVERSITY DUTIES ONLY, Salt Lake City, UT, 7University of Pennsylvania, Philadelphia, PA, 8Brigham and Women's Hospital, Boston, MA, 9University of Colorado, Denver, CO, 10Mount Sinai Hospital, Toronto, ON, Canada, 11Johns Hopkins University, Baltimore, MD, 12Mayo Clinic, Rochester, MN, 13Mayo Clinic, Rochester, Minnesota

    Background/Purpose: The prevalence of neurologic involvement (NI) in ANCA-associated vasculitis (AAV), especially central nervous system (CNS) involvement, is not well characterized. This project aimed to…
  • Abstract Number: 0431 • ACR Convergence 2021

    Clinical Characteristics and Outcomes of ANCA-Associated and Non Immune-Mediated Hypertrophic Pachymeningitis: A Comparative Study

    Eduardo Martin-Nares, Lilian Guadalupe Cano Cruz and Andrea Hinojosa-Azaola, Department of Immunology and Rheumatology, Instituto Nacional de Ciencias Médicas y Nutrición Salvador Zubirán, Mexico City, Mexico

    Background/Purpose: Hypertrophic pachymeningitis (HP) is an infrequent manifestation in autoimmune and non-autoimmune conditions. The differences in clinical characteristics and outcomes of ANCA-associated and non-immune-mediated HP…
  • Abstract Number: 0651 • ACR Convergence 2021

    Diagnostic Approach to Identifying Small Fiber Neuropathy in Patients with Sarcoidosis

    Bassel Bou Dargham1, Nima Madanchi2, Kelsey Satkowiak1, Huzaefah Syed1 and Kelly Gwathmey3, 1Virginia Commonwealth University Medical Center, RICHMOND, VA, 2Virginia CommonHealth University Medical Center, Richmond, VA, 3Virginia Commonwealth University Health system, Richmond, VA

    Background/Purpose: Sarcoidosis is a multisystem granulomatous disease that can affect the nervous system in about 5% of patients. Sarcoidosis associated small fiber neuropathy (SSFN) presents…
  • Abstract Number: 0703 • ACR Convergence 2021

    CD8 Positron Emission Tomography (PET/CT) Imaging with 89Zr-Df-IAB22M2C in Patients with Inclusion Body Myositis

    Colin Quinn1, Kelsey Moulton1, Ron Korn2, William Le3, Niti Goel4, Michael Farwell5 and Steven Greenberg6, 1Department of Neurology, University of Pennsylvania, Philadelphia, PA, 2ImaginAb, Inglewood, CA, 3ImaginAb, Inc, Inglewood, CA, 4Abcuro, Inc., Newton,, MA, 5Department of Radiology, University of Pennsylvania, Philadelphia, PA, 6Brigham and Women's Hospital Department of Neurology, Boston, MA

    Background/Purpose: Inclusion body myositis (IBM) is a slowly progressive autoimmune skeletal muscle disease for which no effective pharmacological therapy is available. A prominent feature of…
  • Abstract Number: 0712 • ACR Convergence 2021

    Immune Checkpoint Inhibitor-related Myotoxicity : Musculoskeletal and/or Neuromuscular Junction Disorder ?

    Hortense Chassepot1, Lotta Plomp2, Dimitri Psimaras3, Thierry Maisonobe3, Sarah Leonard Louis4, Isabelle Plu4, Mehdi Touat3, Celine Anquetil5, Nadege Wesner5, Nicolas Champtiaux5, Aude Rigolet5, Sophie Demeret3, Nicolas Weiss3, Baptiste Abbar6, Marie-Claire Bretagne7, Bruno Pinna7, Capucine Morelot8, Martin Dres8, Thomas Similowski8, Stephane Ederhy9, Joe-Elie Salem7, Olivier Benveniste5 and Yves Allenbach5, 1Universite de Picardie Jules Verne UPJV - Amiens Picardie Hospital, Department of Clinical Immunology and Internal Medicine, Fourqueux, France, 2Amsterdam University Medical Center (AUMC), Amsterdam, Netherlands, 3Sorbonne University - AP-HP, Pitié-Salpêtrière Hospital, Department of Neurology, Paris, France, 4Sorbonne University - AP-HP, Pitié-Salpêtrière Hospital, Department of Neuropathology, Paris, France, 5Sorbonne University - AP-HP, Pitié-Salpêtrière Hospital, Department of Clinical Immunology and Internal Medicine, Paris, France, 6Sorbonne University - AP-HP, Pitié-Salpêtrière Hospital, Department of Oncology, Paris, France, 7Sorbonne University - AP-HP, Pitié-Salpêtrière Hospital, Department of Pharmacology, Paris, France, 8Sorbonne University - AP-HP, Pitié-Salpêtrière Hospital, Department of Pneumology - R3S, Paris, France, 9Sorbonne University - AP-HP, Pitié-Salpêtrière Hospital, Department of Cardiology, Paris, France

    Background/Purpose: Immune checkpoint inhibitor (ICI)-related adverse events (irAE) recently emerged as new diseases in the field of auto-immunity. Among them, ICI-related myotoxicity has the highest…
  • Abstract Number: 1096 • ACR Convergence 2021

    CSF-specific CD8 T Cell Clonal Expansion in Neurosarcoidosis

    Michael Paley1, Brandi Baker2, Steven Dunham3, Nicole Linskey3, Elisha Roberson3, David Clifford3 and Wayne Yokoyama3, 1Washington University in St. Louis, Olivette, MO, 2Washington University in St. Louis, St. Louis, MO, 3Washington University School of Medicine, St. Louis, MO

    Background/Purpose: Neuroinflammation is a severe manifestation of the systemic inflammatory disorders. Sarcoidosis, which leads to neurologic disease in 5-10 % of cases, has traditionally been…
  • Abstract Number: 0090 • ACR Convergence 2020

    110 Patients with Monoclonal Gammopathy of Undetermined Significance (MGUS) in a Rheumatology Disease Unit: Fracture, Neuropathy, and Pernicious Anemia Are Clues to Recognition

    Michael Lovy1 and Andrew Dulalia1, 1Desert Oasis Healthcare, Palm Springs, CA

    Background/Purpose: Monoclonal gammopathy of undetermined significance (MGUS) has been associated with osteoporosis, neuropathy, pernicious anemia, and low vitamin B12, and may precede multiple myeloma and…
  • Abstract Number: 0259 • ACR Convergence 2020

    Guillain-Barré Syndrome in Systemic Lupus Erythematosus – Results of a Nationwide Analysis

    Shilpa Arora1, Ehizogie Edigin2 and Augustine Manadan1, 1Rush University Medical Center, Chicago, IL, 2John H Jr. Stroger Hospital of Cook County, Chicago, IL

    Background/Purpose: Guillain-Barré Syndrome (GBS) is a rare autoimmune polyneuropathy well described following viral illness, vaccination, or surgery. Systemic Lupus Erythematosus (SLE) has been associated with several…
  • Abstract Number: 1434 • ACR Convergence 2020

    The Role of Sural Nerve Biopsy in the Diagnosis of Systemic Vasculitis – a Retrospective Study from Two Specialized Centres

    Karl Gisslander1, Lars Dahlin2, Rona Smith3, David Jayne3 and Aladdin Mohammad4, 1Lund University, Lund, Sweden, Lund, Sweden, 2Department of Translational Medicine – Hand Surgery, Lund University, Malmö, Sweden, Malmö, Sweden, 3Department of Medicine, Vasculitis and Lupus Research Group, University of Cambridge, Cambridge, UK, Cambridge, United Kingdom, 4Lund University, Lund, Sweden. Department of Medicine, Vasculitis and Lupus Research Group, University of Cambridge, Cambridge, UK, Lund, Sweden

    Background/Purpose: Vasculitis of the peripheral nervous system is seen mainly in systemic vasculitis involving small and medium sized vessels and in cases of single-organ vasculitis…
  • Abstract Number: 1436 • ACR Convergence 2020

    Incidence Rate, Predictors and Outcome of Stroke in Patients with ANCA Associated Vasculitis – A Population-based Study

    Dennis Tabakovic1, Rona Smith2, David Jayne3 and Aladdin Mohammad4, 1Lund University, Lund, Skane Lan, Sweden, 2University of Cambridge, Cambridge, United Kingdom, 3Department of Medicine, Vasculitis and Lupus Research Group, University of Cambridge, Cambridge, UK, Cambridge, United Kingdom, 4Lund University, Lund, Sweden. Department of Medicine, Vasculitis and Lupus Research Group, University of Cambridge, Cambridge, UK, Lund, Sweden

    Background/Purpose: To study the incidence rate, predictors and outcome of stroke in patients with ANCA-associated vasculitis (AAV) within a defined population in southern Sweden.Methods: The…
  • Abstract Number: 1636 • ACR Convergence 2020

    8 Years Follow-Up of a Novel Autoinflammatory Disease: CD59 Malfunction Causes Hemolytic Anemia, Recurrent Guillain-Barre Syndrome, and Strokes in Pediatric Populations and Respond Well to Eculizumab and Pozelimab

    Dror Mevorach1 and Netanel Karbian1, 1Hadassah-University Hospital, Jerusalem, Yerushalayim, Israel

    Background/Purpose: In 2013 we have described the first patients with a novel autoinflammatory disease manifested in 4 children with recurrent Guillain-Barre syndrome and hemolytic anemia…
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