ACR Meeting Abstracts

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Abstracts tagged "Myopathies"

  • Abstract Number: 1953 • ACR Convergence 2023

    Mortality Trends in Polymyositis and Dermatomyositis in Mexico: A General Population-based Study from 2000 to 2019

    CLAUDIA MENDOZA PINTO1, Pamela Munguía-Realpozo1, Ivet Etchegaray-Morales2, Mario García-Carrasco2, Paulina Cortés-Hernández1, Roberto Arreguín-Reyes1, Jorge Ayón-Aguilar1 and Gabriel Rodríguez-Castillo2, 1Instituto Mexicano del Seguro Socia, Puebla, Mexico, 2Medicine School, Benemérita Universidad Autónoma de Puebla, Puebla, Mexico

    Background/Purpose: Patients with polymyositis and dermatomyositis (PM/DM) present multiple complications that may lead to increased mortality rates and data on PM/DM mortality in Mexico is…
  • Abstract Number: 0702 • ACR Convergence 2023

    Large Vessel Vasculitis Increases Risk of Acute Myocardial Infarction in Patients Admitted for Congestive Heart Failure : A Nationwide Inpatient Database Study

    Yanint Raksadawan, Sabahat Usmani, Harigopal Sandhyavenu, Thatiana Schulze Goni, Jalpan Patel, Hafiz Muhammad Waqar Younas and Amro Taha, Weiss Memorial Hospital, Chicago, IL

    Background/Purpose: Cardiac disease has been known to be a major morbidity and mortality cause in vasculitis. Large vessel vasculitis is mostly associated with pericarditis, myocarditis…
  • Abstract Number: 1954 • ACR Convergence 2023

    Evaluation of Cancer Screening Methods in Patients Diagnosed with Inflammatory Muscle Disease at Kansas University Medical Center

    Padmini Giri1, Amrita Bath2 and Pooja Bhadbhade2, 1University of Kansas Medical Center, Overland Park, KS, 2University of Kansas Medical Center, Kansas City, MO

    Background/Purpose: Idiopathic inflammatory myopathies (IIM) are characterized by muscle weakness and inflammation. There is an increased risk of developing cancer in patients (pts) with IIM…
  • Abstract Number: 100 • 2023 Pediatric Rheumatology Symposium

    The Brazilian Registry of Juvenile Dermatomyositis (JDM): II – A Longitudinal Assessment of Muscle Strength by Manual Muscle Test (MMT) and Childhood Myositis Assessment Scale (CMAS) Tools

    Darcisio Antonio1, Taciana Fernandes1, Adriana Elias2, Teresa Robazzi3, Ana Julia Moraes4, Sheila Oliveira5, Flavio Sztajnbok6, Luciana Carvalho7, Luciana Marques8, Silvana Sacchetti9, Maria Teresa Terreri10, Simone Appenzelle11, Roberto Marini12, Carlos Rabello Jr13, Cristina Magalhaes14, Melissa Fraga15, Marcia Bandeira16, Iloite Scheibel17, Isabela Daud2, Beatriz Carneiro2, Claudio Len18, Clovis Silva19 and Claudia Magalhaes20, 1Universidade Estadual Paulista (UNESP) Botucatu, Brazil, 2Instituto da Criança - Universidade de São Paulo (USP), São Paulo, Brazil, 3Universidade Federal da Bahia, Brazil, 4Universidade Federal do Para, Brazil, 5Universidade Federal do Rio de janeiro, Rio de Janeiro, 6Universidade Estadual do Rio de Janeiro, Rio de Janeiro, Brazil, 7Universidade de Sao Paulo- Ribeirao Preto, São Paulo, Brazil, 8Hospital Albert Sabin, Brazil, 9Santa Casa de Sao Paulo, Brazil, 10UNIFESP, São Paulo, Brazil, 11University of Campinas, Campinas, Sao Paulo, Brazil, 12UNICAMP, São Paulo, Brazil, 13Hospital Geral de Fortaleza, Brazil, 14Hospital Jose de Alencar - Brasilia, Brazil, 15Hospital Darcy Vargas, Brazil, 16Hospital Pequeno Principe- Curitiba, Brazil, 17Hospital Conceição de Porto Alegre, Brazil, 18Universidade Federal de São Paulo - Unifesp, São Paulo, Brazil, 19Universidade de São Paulo, São Paulo, Brazil, 20São Paulo State University, Pediatric Rheumatology Division, Botucatu, Brazil

    Background/Purpose: Muscle weakness is often progressive and persistent in Juvenile Dermatomyositis (JDM). Muscle strength testing is useful for evaluating severity of muscle weakness. There is…
  • Abstract Number: 120 • 2023 Pediatric Rheumatology Symposium

    The Brazilian Registry of Juvenile Dermatomyositis (JDM): I- Onset Clinical Features and Disease Activity Scores by DAS-20 over 2-Years-Follow Up

    Beatriz Carneiro1, Adriana Elias1, Teresa Robazzi2, Ana Julia Moraes3, Sheila Oliveira4, Flavio Sztajnbok5, Luciana Carvalho6, Luciana Marques7, Silvana Sacchetti8, Maria Teresa Terreri9, Simone Appenzelle10, Roberto Marini11, Andre Cavalcante12, Marcia Bandeira13, Cristina Magalhaes14, Melissa Fraga15, Iloite Scheibel16, Isabela Daud1, Darcisio Antonio17, Claudio Len18, Clovis Silva19, Taciana Fernandes17 and Claudia Magalhaes20, 1Instituto da Criança - Universidade de São Paulo (USP), São Paulo, Brazil, 2Universidade Federal da Bahia, Brazil, 3Universidade Federal do Para, Brazil, 4Universidade Federal do Rio de janeiro, Rio de Janeiro, 5Universidade Estadual do Rio de Janeiro, Rio de Janeiro, Brazil, 6Universidade de Sao Paulo- Ribeirao Preto, São Paulo, Brazil, 7Hospital Albert Sabin, Brazil, 8Santa Casa de Sao Paulo, Brazil, 9UNIFESP, São Paulo, Brazil, 10University of Campinas, Campinas, Sao Paulo, Brazil, 11UNICAMP, São Paulo, Brazil, 12Hospital Materno-Infantil de Goiania, Brazil, 13Hospital Pequeno Principe- Curitiba, Brazil, 14Hospital Jose de Alencar - Brasilia, Brazil, 15Hospital Darcy Vargas, Brazil, 16Hospital Conceição de Porto Alegre, Brazil, 17Universidade Estadual Paulista (UNESP) Botucatu, Brazil, 18Universidade Federal de São Paulo - Unifesp, São Paulo, Brazil, 19Universidade de São Paulo, São Paulo, Brazil, 20São Paulo State University, Pediatric Rheumatology Division, Botucatu, Brazil

    Background/Purpose: A national registry was set up, enrolling new onset JDM cases in 18 hospitals, during 3-years (2015-2018) with 2-years follow up, in a low…
  • Abstract Number: 0166 • ACR Convergence 2022

    Detection of the Novel Autoantibodies Against Transcription Factor Sp4 Is Related with Low Risk of Cancer in Idiopathic Inflammatory Myopathy Patients

    Yuji Hosono1, Azusa Kojima1, Akira Ishii1, Mai Sugiyama1, Yuto Izumi1, Noriko Sasaki2, Chiho Yamada1 and Shinji Sato1, 1Tokai University School of Medicine, Isehara Kanagawa, Japan, 2Tokai University School of Medicine, sagamihara-city, Japan

    Background/Purpose: In idiopathic inflammatory myopathy (IIM), many kinds of autoantibodies are often detected and associated with each clinical phenotype. Recently, autoantibody against transcription factor Sp4…
  • Abstract Number: 1886 • ACR Convergence 2022

    Statin-induced Immune-mediated Miopathy: Treatment with Glucocorticoid-free Protocols and Role of Muscle Biopsy in the Follow-up

    David Martínez-López1, Piotr Szczęsny2, Inger Nennesmo3, Karina Gheorghe4, Antonella Notarnicola5, Helene Alexanderson6, Ingrid Lundberg7 and Maryam Dastmalchi8, 1Hospital Universitario Marqués de Valdecilla, Santander, Spain, 2Department of Rheumatology, National Institute of Geriatrics, Rheumatology and Rehabilitation, Warsaw, Poland. Department of Neurology, Medical University of Warsaw, Warsaw, Poland, 3Department of Pathology, Karolinska University Hospital,Pathology, Karolinska University Hospital., Stockholm, Sweden, 4Division of Rheumatology, Department of Medicine, Solna, Karolinska Institutet. Rheumatology, Karolinska University Hospital Stockholm, Sweden. Center for Molecular Medicine, Karolinska Institutet, Karolinska University Hospital, Stockholm, Sweden, 5Division of Rheumatology, Department of Medicine, Solna, Karolinska Institutet, Karolinska University Hospital, Stockholm, Sweden, 6Karolinska Institutet, Stockholm, Sweden, 7Karolinska Universitetssjukhuset, Karolinska Institutet, Stockholm, Sweden, 8Karolinska University Hospital, Stockholm, Sweden

    Background/Purpose: Statin-induced immune mediated necrotizing myopathy (IMNM) is a recently identified autoimmune condition associated with anti-3-hydroxy-3-methylglutaryl-CoA reductase (HMGCR) antibodies, characterized by progressive muscle weakness leading…
  • Abstract Number: 0171 • ACR Convergence 2022

    Cardiac Involvement in Idiopathic Inflammatory Myopathies: When Should We Look for It?

    Matilde Bandeira1, Eduardo Dourado1, Ana Teresa Melo1, Patricia Martins2, Vanessa Fraga3, José Luís Ferraro4, André Saraiva5, Marlene Sousa6, Hugo Parente7, Catarina Soares8, Ana Margarida Correia9, Diogo Esperança Almeida9, Sara Paiva Dinis10, Ana Pinto11, Filipe Pinheiro12, Maria Rato12, Tiago Beirão13, Beatriz Samões13, Bernardo Santos14, Carolina Mazeda15, Ana Teodósio Chícharo16, Margarida Faria17, Agna Neto17, Helena Lourenço18, Luísa Brites19, Marília Rodrigues19, Joana Silva-Dinis20, João Madruga-Dias21, Filipe Araújo22, Nádia Martins23, Maura Couto23, Ana Valido24, Maria José Santos25, Sofia Barreira1, João Eurico Fonseca1 and Raquel Campanilho-Marques1, 1Serviço de Reumatologia, Centro Hospitalar Universitário Lisboa Norte, Centro Académico de Medicina de Lisboa (CAML), Lisboa, Portugal; Unidade de Investigação em Reumatologia, Instituto de Medicina Molecular, Faculdade de Medicina, Universidade de Lisboa, CAML, Lisboa, Portugal, 2Rheumatology department, Centro Hospitalar e Universitário de Lisboa Norte, Centro Académico de Medicina de Lisboa, Lisboa, Portugal, 3Serviço de Reumatologia, Hospital Beatriz Ângelo, Almada, Portugal, 4Serviço de Reumatologia, Hospital Beatriz Ângelo, Loures, Portugal, 5Rheumatology department, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal, 6Serviço de Reumatologia, Centro Hospitalar Universitário de Coimbra, Coimbra, Portugal, 7Rheumatology department, Unidade Local de Saúde do Alto Minho, Ponte de Lima, Portugal, 8Rheumatology department, Unidade Local de Saúde do Alto Minho, Ponte de Lima, Viana do Castelo, Portugal, 9Serviço de Reumatologia, Hospital de Braga, Braga, Portugal, Braga, Portugal, 10Rheumatology department, Unidade Local de Saúde da Guarda - Hospital Sousa Martins, Guarda, Portugal, 11Local Health Unit of Guarda, Barcelos, Portugal, 12Rheumatology Department, Centro Hospitalar Universitário de São João, Porto, Portugal, 13Rheumatology Department, Centro Hospitalar de Vila Nova de Gaia / Espinho, Vila Nova de Gaia, Portugal, 14Serviço de Reumatologia, Centro Hospitalar do Baixo Vouga, Aveiro, Portugal, 15Centro Hospitalar Baixo Vouga, Ovar, Portugal, 16Serviço de Reumatologia, Centro Hospitalar Universitário do Algarve, Faro, Portugal, 17Serviço de Reumatologia, Hospital Nélio Mendonça, Serviços de Saúde da Região Autónoma da Madeira, Funchal, Portugal, 18Serviço de Reumatologia, Centro Hospitalar de Lisboa Ocidental, Lisboa, Portugal, 19Serviço de Reumatologia, Centro Hospitalar de Leiria, Leiria, Portugal, Leiria, Portugal, 20Serviço de Reumatologia, Centro Hospitalar Universitário de Lisboa Central, Lisboa, Portugal, 21Rheumatology Service, Centro Hospitalar Médio Tejo, Tomar, Portugal, 22Rheumatology and Osteoporosis Unit, Hospital de Sant´Ana, SCML, Lisboa, Portugal, 23Rheumatology department, Centro Hospitalar Tondela-Viseu, Viseu, Portugal, 24Serviço de Reumatologia, Unidade Local de Saúde do Litoral Alentejano, Santiago do Cacém, Portugal, 25Hospital Garcia de Orta, Almada, Charneca da Caparica, Portugal

    Background/Purpose: Idiopathic inflammatory myopathies (IIM) are a group of rare disorders that can affect the heart. It is unclear which patients are at higher risk.…
  • Abstract Number: 2237 • ACR Convergence 2022

    Randomized Placebo-Controlled Trial to Evaluate Efficacy and Safety of Subcutaneous Abatacept in Adults with Active Idiopathic Inflammatory Myopathy: Results of the 24-Week Double-Blind and 28-Week Open-Label Periods

    Rohit Aggarwal1, Ingrid Lundberg2, Yeong-Wook Song3, Aziz Shaibani4, Victoria Werth5 and Michael Maldonado6, 1Division of Rheumatology and Clinical Immunology, Department of Medicine, University of Pittsburgh, Pittsburgh, PA, 2Karolinska Universitetssjukhuset, Karolinska Institutet, Stockholm, Sweden, 3Seoul National University, Seoul, Republic of Korea, 4Nerve and Muscle Center of Texas, Houston, TX, 5Philadelphia VAMC, Philadelphia, PA, USA and Department of Dermatology, Perelman School of Medicine at the University of Pennsylvania, Philadelphia, 6Bristol Myers Squibb, Princeton, NJ

    Background/Purpose: A 52-week (wk), randomized, placebo (PBO)-controlled phase 3 trial of subcutaneous (SC) abatacept (ABA) and standard of care (SOC) was performed in patients (pts)…
  • Abstract Number: 0175 • ACR Convergence 2022

    Extracorporeal Membrane Oxygenation for Acute Lung Injury in Idiopathic Inflammatory Myopathies – a Potential Lifesaving Intervention

    boyang zheng1, Ellen Eline2, Lilian Xu3, Kun Huang4, Greet Hermans5, michael Perch6, gordan Samoukovic1, ellen De Langhe5, Maryam Dastmalchi7, Lisa Christopher-Stine2, Louise Diederichsen8 and Valerie Leclair1, 1McGill University, Montréal, QC, Canada, 2Johns Hopkins University, Baltimore, MD, 3Johns Hopkins University School of Medicine, Baltimore, MD, 4University of British Columbia, Vancouver, BC, Canada, 5University Hospitals Leuven, Leuven, Belgium, 6Righospitalet, University of Copenhagen, Copenhagen, Denmark, 7Karolinska University Hospital, Stockholm, Sweden, 8Copenhagen University Hospital, Rigshospitalet, Dragør, Denmark

    Background/Purpose: Idiopathic inflammatory myopathies (IIM) can present with acute IIM-related lung injury and respiratory failure, leading to a high mortality risk in intensive care units…
  • Abstract Number: 2242 • ACR Convergence 2022

    Metabolomics-based Identification of Metabolic Dysfunction in Inclusion Body Myositis

    Jemima Albayda1, Cissy Zhang1, Pratik Khare1, Brittany Adler1, Erika Darrah1, Lisa Christopher-Stine1, Thomas E Lloyd2 and Anne Le1, 1Johns Hopkins University, Baltimore, MD, 2Johns Hopkins University School of Medicine, Baltimore, MD

    Background/Purpose: Sporadic Inclusion Body Myositis (IBM) is the most common myopathy over the age of 50 and is currently refractory to treatment. The pathogenesis of…
  • Abstract Number: 0176 • ACR Convergence 2022

    Diagnostic Accuracy and Clinical Relevance of Muscle Biopsy in Patients with Suspected Myositis

    Kastriot Kastrati1, Nasim NAKHOST LOTFI2, Marwa Tawfik3, Ellen Gelpi2, Romana Hoeftberger2, Hans-Peter Kiener2, Daniel Aletaha4, Michael Bonelli5 and Helga Radner5, 1Division of Rheumatology, Vienna, Austria, 2Medical University Vienna, Vienna, Austria, 3Suez Canal University, Ismailia, Egypt, 4Medical University Vienna, Wien, Austria, 5Division of Rheumatology, Department of Internal Medicine III, Medical University of Vienna, Vienna, Austria

    Background/Purpose: Diagnosis of idiopathic inflammatory myopathies (IIM) represents a clinical challenge and muscle biopsy is regarded as a fundamental procedure for confirming diagnosis. However, the…
  • Abstract Number: 0177 • ACR Convergence 2022

    COVID-19 Vaccination-related Short-term Adverse Events in Patients with Idiopathic Inflammatory Myositis and Autoimmune Multimorbidity: Results from the COVID-19 Vaccination in Autoimmune Diseases Survey

    Mrinalini Dey1, Naveen R2, Elena Nikiphorou3, Parikshit Sen4, James B. Lilleker5, Vishwesh Agarwal6, Sinan Kardes7, Jessica Day8, Marcin Milchert9, Mrudula Joshi10, Tamer A Gheita11, Babur Salim12, Tsvetelina Velikova13, Abraham Edgar Gracia-Ramos14, Ioannis Parodis15, Albert Selva O’Callaghan16, Minchul Kim17, Tulika Chatterjee17, Ai Lyn Tan18, Ashima Makol19, Arvind Nune20, Lorenzo Cavagna21, Miguel Angel Saavedra Salinas22, Samuel Shinjo23, Nelly Ziade24, Johannes Knitza25, Masataka Kuwana26, Oliver Distler27, Hector Chinoy28, John Pauling29, Chris Wincup30, Vikas Agarwal2, Rohit Aggarwal31 and Latika Gupta32, 1Institute of Life Course and Medical Sciences, University of Liverpool, Liverpool, United Kingdom, 2Sanjay Gandhi Postgraduate Institute of Medical Sciences, Lucknow, India, 3Leiden University Medical Center & King's College London, London, United Kingdom, 4Maulana Azad Medical College, New Delhi, India, 5The University of Manchester, Manchester, United Kingdom, 6Mahatma Gandhi Missions Medical College, Lucknow, India, 7Istanbul University, Istanbul, Turkey, 8Walter and Eliza Hall Institute, Melbourne, Australia, 9Pomeranian Medical University in Szczecin, Szczecin, Poland, 10Byramjee Jeejeebhoy Government Medical College and Sassoon General Hospitals, Pune, India, 11Rheumatology Department, Faculty of Medicine, Cairo University, Cairo, Egypt, 12Fauji foundation hospital Rawalpindi, Rawalpindi, Pakistan, 13Sofia University St. Kliment Ohridski, Sofia, Bulgaria, 14Instituto Mexicano del Seguro Social, Ciudad de México, Mexico, 15Karolinska Institutet, Stockholm, Sweden, 16Hospital Universitari Vall d'Hebron, Barcelona, Spain, 17University of Illinois College of Medicine Peoria, Peoria, IL, 18University of Leeds, Leeds, United Kingdom, 19Mayo Clinic, Rochester, MN, Rochester, MN, 20Southport and Ormskirk Hospital NHS Trust, Southport, United Kingdom, 21Università di Pavia, Fondazione IRCCS Policlinico San Matteo, Pavia, Italy, Pavia, Italy, 22IMSS, Ciudad de México, Mexico, 23Faculdade de Medicina FMUSP, Universidade de São Paulo, São Paulo, Brazil, 24Saint-Joseph University, Beirut, Lebanon, 25Department of Internal Medicine 3 – Rheumatology and Immunology, Friedrich-Alexander-University Erlangen-Nürnberg and Universitätsklinikum Erlangen, 91054 Erlangen, Germany; Deutsches Zentrum Immuntherapie, Friedrich-Alexander-UniversityErlangen-Nürnberg and Universitätsklinikum Erlangen, Erlangen, Germany, 26Nippon Medical School Graduate School of Medicine, Tokyo, Japan, 27Department of Rheumatology, University Hospital Zurich, University of Zurich, Zürich, Switzerland, 28The University of Manchester, Sale, United Kingdom, 29North Bristol NHS Trust, Bristol, United Kingdom, 30Rayne Institute, University College London, London, United Kingdom, 31Division of Rheumatology and Clinical Immunology, Department of Medicine, University of Pittsburgh, Pittsburgh, PA, 32Royal Wolverhampton Trust, Wolverhampton/University of Manchester, United Kingdom

    Background/Purpose: COVID-19 vaccines are safe and effective, though patients with rare rheumatic diseases like idiopathic inflammatory myositis (IIMs), and those with multiple comorbidities continue to…
  • Abstract Number: 0940 • ACR Convergence 2022

    Effect of an 8-week Tailored Physical Therapy Program on Sexual Function in Women with Systemic Sclerosis and Idiopathic Inflammatory Myopathies: A Pilot Controlled Study

    Barbora Hermankova1, Maja Spiritovic1, Sabina Oreska2, Hana Storkanova2, Karel Pavelka3, Ladislav Šenolt4, Jiří Vencovský4, Radim Becvar2 and Michal Tomcik2, 1Institute of Rheumatology, Department of Physiotherapy, Faculty of Physical Education and Sport, Charles University, Prague, Czech Republic, Prague, Czech Republic, 2Institute of Rheumatology, Department of Rheumatology, 1st Faculty of Medicine, Charles University, Prague, Czech Republic, Prague, Czech Republic, 3Institute of Rheumatology, Department of Rheumatology, 1st Faculty of Medicine, Charles University, Prague, Czech Republic, Praha, Czech Republic, 4Institute of Rheumatology and Department of Rheumatology, First Faculty of Medicine, Charles University, Prague, Czech Republic

    Background/Purpose: Systemic rheumatic diseases like systemic sclerosis (SSc) and idiopathic inflammatory myopathies (IIM) may affect all aspects of life, including sexual health. However, no non-pharmacological…
  • Abstract Number: 1233 • ACR Convergence 2022

    Ultrasound Is Reliable in the Assessment of Muscle Echogenicity in Patients with Rheumatic Diseases: Results of a Multicenter International Web-based Study

    Andrea Di Matteo1, Erica Moscioni2, Maria Giovanna Lommano1, Edoardo Cipolletta1, Gianluca Smerilli1, Sonia Farah1, Carla Airoldi3, Sibel Aydin4, Becciolini Andrea5, Karina Bonfiglioli6, Marina Carotti7, Greta Carrara8, Tomas Cazenave9, Davide Corradini10, Micaela Ana Cosatti11, Juan Josè de Agustin12, Giulia Maria Destro Castaniti13, Marco Di Carlo1, Eleonora Di Donato5, Luca Di geso14, Ashley Elliott15, Daniela Fodor16, Francesca Francioso1, Alessandra Gabba17, Cristina Hernández-Díaz18, Rudolf Horvath19, Jana Hurnakova19, Diogo Jesus20, Josefina Marin21, Maria Victoria Martire22, Riccardo Mashadi-Mirza23, Marco Massarotti24, Alice Andreea Musca25, Jagdish Nair26, Tadashi Okano27, Ioannis Papalopoulos28, Javier Eduardo Rosa21, Marcos Rosemffet29, João Rovisco30, Davide Rozza8, Fausto Salaffi1, Crescenzio Scioscia31, Carlo Alberto Scirè8, Maria-Magdalena Tamas32, Shun Tanimura33, Lucio Ventura-Rios18, Catalina Villota-Eraso34, Orlando Villota35, Paraksevi V Voulgari36, Florentin Ananu Vreju37, Gentiana Vukatana37, Johana Zacariaz Hereter21, Anna Zanetti8, Walter Grassi1 and Emilio Filippucci1, 1Polytechnic University of Marche, Rheumatology Unit, Department of Clinical and Molecular Sciences, "Carlo Urbani" Hospital, Jesi, Italy, 2Polytechnic University of Marche, Jesi, Italy, 3Hospital Provincial, Rosario, Argentina, 4University of Ottawa, Rheumatology, Ottawa, Canada, Ottawa, ON, Canada, 5Department of Medicine, Internal Medicine and Rheumatology Unit, Azienda Ospedaliero Universitaria di Parma, Parma, Italy, 6Hospital das Clínicas, Faculdade de Medicina da Universidade de São Paulo, São Paulo, Brazil, 7Department of Radiology, Ospedali Riuniti, Università Politecnica delle Marche, Ancona, Italy, 8Epidemiology Unit, Italian Society of Rheumatology, Milano, Italy, 9Rheumatology Unit, Instituto de Rehabilitación Psicofísica, Buenos Aires, Argentina, 10Rheumatology Unit, University Clinic AOU Cagliari, Cagliari, Italy, 11CEMIC, Centro de educación médica e investigaciones médicas "Norberto Quirno", Buenos Aires, Argentina, 12Vall D'hebron University Hospital, Barcelona, Spain, 13Department of Health Promotion, Mother and Child Care, Internal Medicine and Medical Specialties, Rheumatology section, University of Palermo, Palermo, Italy, 14Ospedale Madonna del Soccorso, Department of Internal Medicine, San Benedetto del Tronto, Italy, 15Centre for Experimental Medicine, Queen's University, Belfast, Northern Ireland, United Kingdom, 162nd Internal Medicine Department, "Iuliu Hatieganu" University of Medicine and Pharmacy, Cluj-Napoca, Romania, 17Local Health Unit (ASL), Oristano, Italy, 18Division de Reumatologia. Instituto Nacional de Rehabilitacion "Luis Guillermo Ibarra Ibarra", Ciudad de México, Mexico, 19Department of Paediatric and Adult Rheumatology, University Hospital Motol, Prague, Czech Republic, 20Rheumatology Department, Centro Hospitalar de Leiria, Leira, Portugal, 21Hospital Italiano de Buenos Aires, Buenos Aires, Argentina, 22San Roque Hospital, La Plata, Buenos Aires, Argentina, 23Radiology Department, A.O. Ospedali Riuniti Marche Nord, Pesaro, Italy, 24Department of Rheumatology, University Hospitals Dorset NHS Foundation Trust, Christchurch Hospital, Christchurch, United Kingdom, 25Department of Rheumatology - Colentina Clinical Hospital, Bucharest, Romania, 26Rheumatology, Liverpool University Hospitals Foundation Trust, Liverpool, United Kingdom, 27Department of Orthopedic Surgery, Osaka Metropolitan University Graduate School of Medicine, Osaka, Japan, 28Department of Rheumatology, Clinical Immunology and Allergy, University Hospital of Heraklion, Heraklion, Greece, 29Rheumatology Unit, Instituto de Rehabilitación Psicofísica, Capital Federal, Argentina, 30Rheumatology Department, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal, 31Department of Emergency and Organ Transplantations-Rheumatology Unit, University of Bari "Aldo Moro", Bari, Italy, 32Department of Rheumatology, "Iuliu Hatieganu" University of Medicine and Pharmacy, Cluj-Napoca, Romania, 33Rheumatology Department, Hokkaido Medical Center for Rheumatic Diseases, Sapporo, Japan, 34IPS Servicio integral de reumatología e inmunología Dr Orlando Villota, Pasto, Colombia, 35Division of Rheumatology, Fundación Hospital San Pedro, Pasto, Colombia, 36Department of Rheumatology, School of Health Science, Faculty of Medicine, University of Ioannina, Ioannina, Greece, 37Rheumatology Department, University of Medicine and Pharmacy of Craiova, Craiova, Romania, 37Rheumatology Unit; IRCCS Policlinico S. Orsola Malpighi, Bologna, Italy

    Background/Purpose: Studies have showed that an increased ultrasound (US) muscle echogenicity indicating fatty replacement/fibrosis of muscle tissue may represent an early indicator of muscle involvement associated…
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