ACR Meeting Abstracts

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Abstracts tagged "Myopathies"

  • Abstract Number: 0298 • ACR Convergence 2023

    Accuracy of the 2017 European Alliance of Associations for Rheumatology (EULAR)/American College of Rheumatology (ACR) Classification Criteria and Myositis-Specific Autoantibodies-Based Classification Criteria for Classifying Patients with Idiopathic Inflammatory Myopathy

    Tatiana Cobo1, Marta Domínguez2, Anna Pros3, Jose Luís Tandaipán4, Laura Nuño5, JULIA MARTINEZ BARRIO6, Vega Jovani7, Fredeswinda Romero8, Maria Esther Ruiz Lucea9, Eva Tomero Muriel10, Ernesto Trallero Araguás11, Javier Narvaez12, Jordi Camins Fàbregas13, ALBERTO MARIANO RUIZ ROMAN14, Jesus Loarce-Martos15, Annika Nack16, Esmeralda Delgado-Frías17, Francisca Sivera18, carolina Merino19, Antonio Juan Mas20, Alejandro Gómez Gómez1, Jose-Maria Pego-Reigosa21, Maria Martin-Lopez22, Jesús Alejandro Valero23, Carmen carrasco-Cubero24, Mercedes Freire González25, Iñigo Rúa-Figueroa26, Nuria Lozano Rivas27, Julio David Suarez Cuba28, Ana Isabel Turrión Nieves29, María Ángeles Puche Larrubia30 and Patricia Alcocer Amores31, 1Department of Rheumatology, Hospital Universitario Infanta Sofía, Universidad Europea, Madrid, Spain, 2Sociedad Española de Reumatología, Madrid, Spain, 3Department of Rheumatology, Hospital del Mar, Barcelona, Spain, 4Department of Rheumatology, Hospital Universitari de la Santa Creu i Sant Pau, Barcelona, Spain, 5Hospital Universitario La Paz - IdiPAZ, Madrid, Spain, 6Rheumatology, Gregorio Marañon University Hospital, Madrid, Spain, 7Department of Rheumatology, Hospital General Universitario Dr. Balmis, Alicante, Spain, 8IIS-HU Fundación Jiménez Díaz, Madrid, Spain, 9Basurto University Hospital, Bilbao, Spain, 10Rheumatology, Hospital La Princesa, Madrid, Spain, 11Department of Rheumatology, Hospital Universitario Vall d'Hebron, Barcelona, Spain, 12Hospital Universitario de Bellvitge, Barcelona, Spain, 13Department of Rheumatology, Hospital General de Granollers, Barcelona, Spain, 14Department of Rheumatology, Hospital Universitario Virgen del Rocío, Sevilla, Spain, 15Ramón y Cajal University Hospital, Madrid, Spain, 16Department of Rheumatology, Hospital Universitari Germans Trias i Pujol, Barcelona, Spain, 17Department of Rheumatology, Hospital Universitario de Canarias, Tenerife, Spain, 18Department of Rheumatology, Hospital General Universitario de Elda, Alicante, Spain, 19Rheumatology Department Hospital Universitario Puerta de Hierro, Majadahonda (Madrid), Spain, 20Hospital Universitario Son Llàtzer, Mallorca, Spain, 21Rheumatology, Hospital do Meixoeiro, Vigo, Spain, 22Hospital 12 de Octubre, Madrid, Spain, 23Department of Rheumatology, Hospital Universitario Donostia, San Sebastián, Spain, 24Department of Rheumatology, Hospital Universitario de Badajoz, Badajoz, Spain, 25Rheumatology department, Complexo Hospitalario Universitario A Coruña (CHUAC). Instituto de Investigación Biomédica A Coruña (INIBIC), A Coruña, Spain, 26Rheumatology, Hospital de Gran Canaria Doctor Negrin, Las Palmas de Gran Canaria, Spain, 27Department of Rheumatology, Hospital Clínico Universitario Virgen de la Arrixaca, Murcia, Spain, 28Department of Rheumatology, Hospital Universitario Príncipe de Asturias, Madrid, Spain, 29Department of Rheumatology, Hospital Complejo Asistencial Universitario de Salamanca, Salamanca, Spain, 30Department of Rheumatology, Reina Sofia University Hospital, Cordoba, Spain, 31Department of Rheumatology, Hospital Universitario HM Sanchinarro, Madrid, Spain

    Background/Purpose: Limitations of the 2017 EULAR/ACR classification criteria have been suggested for classifying patients with idiopathic inflammatory myopathies (IIMs) and myositis-specific antibodies (MSAs). On this…
  • Abstract Number: 1948 • ACR Convergence 2023

    The Influence of Specific Myositis Antibodies on the Development of Interstitial Lung Disease

    Ting-Yuan Lan1, Tai-Ju Lee1, Kuan-Yen Lin2, Jui-Hung Kao3, Chiao-Feng Cheng4, Cheng-Hsun Lu4, Chieh-Yu Shen4, Ko-Jen Li4 and Song-Chou Hsieh4, 1National Taiwan University Hospital Hsinchu Branch, Hsinchu City, Taiwan, 2National Taiwan University Hsinchu branch, Hsinchu, Taiwan, 3National Taiwan University Hospital Yunlin branch, Yunlin, Taiwan, 4National Taiwan University Hospital, Taipei, Taiwan

    Background/Purpose: Interstitial Lung Disease (ILD), prevalent in Idiopathic Inflammatory Myositis (IIM) patients, significantly impacts prognosis. Certain myositis-specific antibodies, including anti-MDA5 and anti-aminoacyl-tRNA synthetases (ARS), are…
  • Abstract Number: 2580 • ACR Convergence 2023

    High-intensity Resistance Training Improves Quality of Life, Muscle Endurance and Strength in Patients with Myositis

    Kasper Jensen1, Per Aagaard2, Charlotte Suetta3, Jakob Nielsen2, Rune Bech4, Henrik Schrøder1, Casper Simonsen1, Jan Christensen1 and Louise Pyndt Diederichsen5, 1University Hospital of Copenhagen, Rigshospitalet, Copenhagen, Denmark, 2University of Southern Denmark, Odense, Denmark, 3Bispebjerg Hospital, Copenhagen, Denmark, 4Zealand University Hospital, Koege, Dragør, Denmark, 5University Hospital of Copenhagen, Rigshospitalet, Dragør, Denmark

    Background/Purpose: Myositis is associated with muscle impairment, which impacts quality of life. The purpose of this study was to investigate the effects of high-intensity strength…
  • Abstract Number: 100 • 2023 Pediatric Rheumatology Symposium

    The Brazilian Registry of Juvenile Dermatomyositis (JDM): II – A Longitudinal Assessment of Muscle Strength by Manual Muscle Test (MMT) and Childhood Myositis Assessment Scale (CMAS) Tools

    Darcisio Antonio1, Taciana Fernandes1, Adriana Elias2, Teresa Robazzi3, Ana Julia Moraes4, Sheila Oliveira5, Flavio Sztajnbok6, Luciana Carvalho7, Luciana Marques8, Silvana Sacchetti9, Maria Teresa Terreri10, Simone Appenzelle11, Roberto Marini12, Carlos Rabello Jr13, Cristina Magalhaes14, Melissa Fraga15, Marcia Bandeira16, Iloite Scheibel17, Isabela Daud2, Beatriz Carneiro2, Claudio Len18, Clovis Silva19 and Claudia Magalhaes20, 1Universidade Estadual Paulista (UNESP) Botucatu, Brazil, 2Instituto da Criança - Universidade de São Paulo (USP), São Paulo, Brazil, 3Universidade Federal da Bahia, Brazil, 4Universidade Federal do Para, Brazil, 5Universidade Federal do Rio de janeiro, Rio de Janeiro, 6Universidade Estadual do Rio de Janeiro, Rio de Janeiro, Brazil, 7Universidade de Sao Paulo- Ribeirao Preto, São Paulo, Brazil, 8Hospital Albert Sabin, Brazil, 9Santa Casa de Sao Paulo, Brazil, 10UNIFESP, São Paulo, Brazil, 11University of Campinas, Campinas, Sao Paulo, Brazil, 12UNICAMP, São Paulo, Brazil, 13Hospital Geral de Fortaleza, Brazil, 14Hospital Jose de Alencar - Brasilia, Brazil, 15Hospital Darcy Vargas, Brazil, 16Hospital Pequeno Principe- Curitiba, Brazil, 17Hospital Conceição de Porto Alegre, Brazil, 18Universidade Federal de São Paulo - Unifesp, São Paulo, Brazil, 19Universidade de São Paulo, São Paulo, Brazil, 20São Paulo State University, Pediatric Rheumatology Division, Botucatu, Brazil

    Background/Purpose: Muscle weakness is often progressive and persistent in Juvenile Dermatomyositis (JDM). Muscle strength testing is useful for evaluating severity of muscle weakness. There is…
  • Abstract Number: 120 • 2023 Pediatric Rheumatology Symposium

    The Brazilian Registry of Juvenile Dermatomyositis (JDM): I- Onset Clinical Features and Disease Activity Scores by DAS-20 over 2-Years-Follow Up

    Beatriz Carneiro1, Adriana Elias1, Teresa Robazzi2, Ana Julia Moraes3, Sheila Oliveira4, Flavio Sztajnbok5, Luciana Carvalho6, Luciana Marques7, Silvana Sacchetti8, Maria Teresa Terreri9, Simone Appenzelle10, Roberto Marini11, Andre Cavalcante12, Marcia Bandeira13, Cristina Magalhaes14, Melissa Fraga15, Iloite Scheibel16, Isabela Daud1, Darcisio Antonio17, Claudio Len18, Clovis Silva19, Taciana Fernandes17 and Claudia Magalhaes20, 1Instituto da Criança - Universidade de São Paulo (USP), São Paulo, Brazil, 2Universidade Federal da Bahia, Brazil, 3Universidade Federal do Para, Brazil, 4Universidade Federal do Rio de janeiro, Rio de Janeiro, 5Universidade Estadual do Rio de Janeiro, Rio de Janeiro, Brazil, 6Universidade de Sao Paulo- Ribeirao Preto, São Paulo, Brazil, 7Hospital Albert Sabin, Brazil, 8Santa Casa de Sao Paulo, Brazil, 9UNIFESP, São Paulo, Brazil, 10University of Campinas, Campinas, Sao Paulo, Brazil, 11UNICAMP, São Paulo, Brazil, 12Hospital Materno-Infantil de Goiania, Brazil, 13Hospital Pequeno Principe- Curitiba, Brazil, 14Hospital Jose de Alencar - Brasilia, Brazil, 15Hospital Darcy Vargas, Brazil, 16Hospital Conceição de Porto Alegre, Brazil, 17Universidade Estadual Paulista (UNESP) Botucatu, Brazil, 18Universidade Federal de São Paulo - Unifesp, São Paulo, Brazil, 19Universidade de São Paulo, São Paulo, Brazil, 20São Paulo State University, Pediatric Rheumatology Division, Botucatu, Brazil

    Background/Purpose: A national registry was set up, enrolling new onset JDM cases in 18 hospitals, during 3-years (2015-2018) with 2-years follow up, in a low…
  • Abstract Number: 1871 • ACR Convergence 2022

    Hospitalization Outcomes for Acute Myocardial Infraction and Acute Heart Failure in Patients with Idiopathic Inflammatory Myopathies (IIM) from 2016-2019 National Inpatient Sample (NIS)

    Zi Ying Li1, Siyi Huang2, Kevin Xi3, Deepan Dalal4 and Anthony Reginato5, 1Roger Williams Medical Center, Providence, RI, 2UCSF Fresno, Fresno, CA, 3Brown University, Providence, 4Brown University School of Medicine, Providence, RI, 5Brown University, Providence, RI

    Background/Purpose: Cardiovascular disease was encountered in 15% of hospital admission from 2016-2017 for patients with idiopathic inflammatory myopathies (IIM) based on the National Inpatient Sample…
  • Abstract Number: 1877 • ACR Convergence 2022

    Nailfold Videocapillaroscopic Abnormalities Correlate with Disease Activity Measures and Cutaneous Damage in Patients with Idiopathic Inflammatory Myopathies

    Diane Zisa1, Aliza Bloostein1, Deanna Jannat-Khah, DrPH, MSPH1, Maurizio Cutolo2, Vanessa Smith3 and David Fernandez1, 1Hospital for Special Surgery, New York, NY, 2Laboratory of Experimental Rheumatology and Academic Division of Clinical Rheumatology, Department of Internal Medicine, University of Genova, IRCCS San Martino Polyclinic Hospital, Genova, Italy, 3Department of Rheumatology, Ghent University Hospital – Department of Internal Medicine, Ghent University, Belgium – Unit for Molecular Immunology and Inflammation, VIB Inflammation Research Center (IRC), Gent, Belgium

    Background/Purpose: Nailfold videocapillaroscopy (NVC) is a non-invasive tool used to evaluate the microcirculation of patients with connective tissue diseases (CTDs). A specific combination of NVC…
  • Abstract Number: 0156 • ACR Convergence 2022

    Impact of Polymyositis and Dermatomyositis in Patients Admitted with Congestive Heart Failure: An Insight from the National Database

    Brinda Basida1, Sanket Basida2, Jasleen Kaur3, Urja Nagadia2, mahmoud mansour2, Palak Shah4 and Monil Majmundar5, 1DMC/Sinai Grace Hospital, Detroit, MI, 2University of Missouri, Columbia, MO, 3DMC/WSU, Saginaw, MI, 4Metropolitan Hospital Center, New York Medical College, New York, NY, 5University of Kansas Medical Center, Kansas City, KS

    Background/Purpose: Polymyositis (PM) and Dermatomyositis (DM) are systemic autoimmune diseases of inflammatory infiltrates in skeletal muscle resulting in chronic muscle weakness. Systemic involvement of the…
  • Abstract Number: 1882 • ACR Convergence 2022

    Efficacy of Immune-apheresis in Patients with Inflammatory Myopathies: A Case Series

    Kastriot Kastrati1, Hanien Rajab2, Anna Rader2, Elisabeth Anna Aichner2, Thomas Karonitsch2, Hans-Peter Kiener2, Michael Bonelli3, Daniel Aletaha4 and Helga Radner3, 1Division of Rheumatology, Vienna, Austria, 2Medical University Vienna, Vienna, Austria, 3Division of Rheumatology, Department of Internal Medicine III, Medical University of Vienna, Vienna, Austria, 4Medical University Vienna, Wien, Austria

    Background/Purpose: Idiopathic inflammatory myopathies (IIM) comprise a heterogenous group of acquired autoimmune diseases characterised by inflammation of muscle and affection of other organs, including lung…
  • Abstract Number: 0164 • ACR Convergence 2022

    Anti-SSa/SSb and Ro52 Status and Pulmonary Function Tests in Patients with Interstitial Lung Disease and Idiopathic Inflammatory Myopathies

    Abdullah Ahmed1, Sonali Narain2, Ivana Ilic1, Can Hu3, Jaspreet Bhatti4 and Galina Marder5, 1Donald and Barbara Zucker School of Medicine at Hofstra/Northwell, Manhasset, NY, 2Donald and Barbara Zucker School of Medicine at Hofstra/Northwell, Great Neck, NY, 3Donald and Barbara Zucker School of Medicine at Hofstra/Northwell, Fort Lee, NJ, 4Donald and Barbara Zucker School of Medicine at Hofstra/Northwell, New York, NY, 5Donald and Barbara Zucker School of Medicine at Hofstra/ Northwell, Great Neck, NY

    Background/Purpose: Interstitial lung disease (ILD) is a major cause of morbidity and mortality in patients with idiopathic inflammatory myositis (IIM). Anti-SSa/SSb and Ro52 are frequently…
  • Abstract Number: 1884 • ACR Convergence 2022

    Idiopathic Inflammatory Myopathies in Alaska Native/American Indian People in Alaska

    Vivek Mehta and Elizabeth Ferucci, Alaska Native Tribal Health Consortium, Anchorage, AK

    Background/Purpose: Racial disparities have been in noted in various autoimmune disorders. Indigenous North American populations have higher prevalence and severity of a number of autoimmune…
  • Abstract Number: 0166 • ACR Convergence 2022

    Detection of the Novel Autoantibodies Against Transcription Factor Sp4 Is Related with Low Risk of Cancer in Idiopathic Inflammatory Myopathy Patients

    Yuji Hosono1, Azusa Kojima1, Akira Ishii1, Mai Sugiyama1, Yuto Izumi1, Noriko Sasaki2, Chiho Yamada1 and Shinji Sato1, 1Tokai University School of Medicine, Isehara Kanagawa, Japan, 2Tokai University School of Medicine, sagamihara-city, Japan

    Background/Purpose: In idiopathic inflammatory myopathy (IIM), many kinds of autoantibodies are often detected and associated with each clinical phenotype. Recently, autoantibody against transcription factor Sp4…
  • Abstract Number: 1886 • ACR Convergence 2022

    Statin-induced Immune-mediated Miopathy: Treatment with Glucocorticoid-free Protocols and Role of Muscle Biopsy in the Follow-up

    David Martínez-López1, Piotr Szczęsny2, Inger Nennesmo3, Karina Gheorghe4, Antonella Notarnicola5, Helene Alexanderson6, Ingrid Lundberg7 and Maryam Dastmalchi8, 1Hospital Universitario Marqués de Valdecilla, Santander, Spain, 2Department of Rheumatology, National Institute of Geriatrics, Rheumatology and Rehabilitation, Warsaw, Poland. Department of Neurology, Medical University of Warsaw, Warsaw, Poland, 3Department of Pathology, Karolinska University Hospital,Pathology, Karolinska University Hospital., Stockholm, Sweden, 4Division of Rheumatology, Department of Medicine, Solna, Karolinska Institutet. Rheumatology, Karolinska University Hospital Stockholm, Sweden. Center for Molecular Medicine, Karolinska Institutet, Karolinska University Hospital, Stockholm, Sweden, 5Division of Rheumatology, Department of Medicine, Solna, Karolinska Institutet, Karolinska University Hospital, Stockholm, Sweden, 6Karolinska Institutet, Stockholm, Sweden, 7Karolinska Universitetssjukhuset, Karolinska Institutet, Stockholm, Sweden, 8Karolinska University Hospital, Stockholm, Sweden

    Background/Purpose: Statin-induced immune mediated necrotizing myopathy (IMNM) is a recently identified autoimmune condition associated with anti-3-hydroxy-3-methylglutaryl-CoA reductase (HMGCR) antibodies, characterized by progressive muscle weakness leading…
  • Abstract Number: 0171 • ACR Convergence 2022

    Cardiac Involvement in Idiopathic Inflammatory Myopathies: When Should We Look for It?

    Matilde Bandeira1, Eduardo Dourado1, Ana Teresa Melo1, Patricia Martins2, Vanessa Fraga3, José Luís Ferraro4, André Saraiva5, Marlene Sousa6, Hugo Parente7, Catarina Soares8, Ana Margarida Correia9, Diogo Esperança Almeida9, Sara Paiva Dinis10, Ana Pinto11, Filipe Pinheiro12, Maria Rato12, Tiago Beirão13, Beatriz Samões13, Bernardo Santos14, Carolina Mazeda15, Ana Teodósio Chícharo16, Margarida Faria17, Agna Neto17, Helena Lourenço18, Luísa Brites19, Marília Rodrigues19, Joana Silva-Dinis20, João Madruga-Dias21, Filipe Araújo22, Nádia Martins23, Maura Couto23, Ana Valido24, Maria José Santos25, Sofia Barreira1, João Eurico Fonseca1 and Raquel Campanilho-Marques1, 1Serviço de Reumatologia, Centro Hospitalar Universitário Lisboa Norte, Centro Académico de Medicina de Lisboa (CAML), Lisboa, Portugal; Unidade de Investigação em Reumatologia, Instituto de Medicina Molecular, Faculdade de Medicina, Universidade de Lisboa, CAML, Lisboa, Portugal, 2Rheumatology department, Centro Hospitalar e Universitário de Lisboa Norte, Centro Académico de Medicina de Lisboa, Lisboa, Portugal, 3Serviço de Reumatologia, Hospital Beatriz Ângelo, Almada, Portugal, 4Serviço de Reumatologia, Hospital Beatriz Ângelo, Loures, Portugal, 5Rheumatology department, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal, 6Serviço de Reumatologia, Centro Hospitalar Universitário de Coimbra, Coimbra, Portugal, 7Rheumatology department, Unidade Local de Saúde do Alto Minho, Ponte de Lima, Portugal, 8Rheumatology department, Unidade Local de Saúde do Alto Minho, Ponte de Lima, Viana do Castelo, Portugal, 9Serviço de Reumatologia, Hospital de Braga, Braga, Portugal, Braga, Portugal, 10Rheumatology department, Unidade Local de Saúde da Guarda - Hospital Sousa Martins, Guarda, Portugal, 11Local Health Unit of Guarda, Barcelos, Portugal, 12Rheumatology Department, Centro Hospitalar Universitário de São João, Porto, Portugal, 13Rheumatology Department, Centro Hospitalar de Vila Nova de Gaia / Espinho, Vila Nova de Gaia, Portugal, 14Serviço de Reumatologia, Centro Hospitalar do Baixo Vouga, Aveiro, Portugal, 15Centro Hospitalar Baixo Vouga, Ovar, Portugal, 16Serviço de Reumatologia, Centro Hospitalar Universitário do Algarve, Faro, Portugal, 17Serviço de Reumatologia, Hospital Nélio Mendonça, Serviços de Saúde da Região Autónoma da Madeira, Funchal, Portugal, 18Serviço de Reumatologia, Centro Hospitalar de Lisboa Ocidental, Lisboa, Portugal, 19Serviço de Reumatologia, Centro Hospitalar de Leiria, Leiria, Portugal, Leiria, Portugal, 20Serviço de Reumatologia, Centro Hospitalar Universitário de Lisboa Central, Lisboa, Portugal, 21Rheumatology Service, Centro Hospitalar Médio Tejo, Tomar, Portugal, 22Rheumatology and Osteoporosis Unit, Hospital de Sant´Ana, SCML, Lisboa, Portugal, 23Rheumatology department, Centro Hospitalar Tondela-Viseu, Viseu, Portugal, 24Serviço de Reumatologia, Unidade Local de Saúde do Litoral Alentejano, Santiago do Cacém, Portugal, 25Hospital Garcia de Orta, Almada, Charneca da Caparica, Portugal

    Background/Purpose: Idiopathic inflammatory myopathies (IIM) are a group of rare disorders that can affect the heart. It is unclear which patients are at higher risk.…
  • Abstract Number: 2237 • ACR Convergence 2022

    Randomized Placebo-Controlled Trial to Evaluate Efficacy and Safety of Subcutaneous Abatacept in Adults with Active Idiopathic Inflammatory Myopathy: Results of the 24-Week Double-Blind and 28-Week Open-Label Periods

    Rohit Aggarwal1, Ingrid Lundberg2, Yeong-Wook Song3, Aziz Shaibani4, Victoria Werth5 and Michael Maldonado6, 1Division of Rheumatology and Clinical Immunology, Department of Medicine, University of Pittsburgh, Pittsburgh, PA, 2Karolinska Universitetssjukhuset, Karolinska Institutet, Stockholm, Sweden, 3Seoul National University, Seoul, Republic of Korea, 4Nerve and Muscle Center of Texas, Houston, TX, 5Philadelphia VAMC, Philadelphia, PA, USA and Department of Dermatology, Perelman School of Medicine at the University of Pennsylvania, Philadelphia, 6Bristol Myers Squibb, Princeton, NJ

    Background/Purpose: A 52-week (wk), randomized, placebo (PBO)-controlled phase 3 trial of subcutaneous (SC) abatacept (ABA) and standard of care (SOC) was performed in patients (pts)…
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All abstracts accepted to ACR Convergence are under media embargo once the ACR has notified presenters of their abstract’s acceptance. They may be presented at other meetings or published as manuscripts after this time but should not be discussed in non-scholarly venues or outlets. The following embargo policies are strictly enforced by the ACR.

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Accepted abstracts are made available to the public online in advance of the meeting and are published in a special online supplement of Arthritis & Rheumatology. Information contained in those abstracts may not be released until the abstracts appear online. Academic institutions, private organizations and companies with products whose value may be influenced by information contained in an abstract may issue a press release to coincide with the availability of an ACR abstract on the ACR website. However, the ACR continues to require that information that goes beyond that contained in the abstract (e.g., discussion of the abstract done as part a scientific presentation or presentation of additional new information that will be available at the time of the meeting) is under embargo until Saturday, November 11, 2023.

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