ACR Meeting Abstracts

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Abstracts tagged "interstitial lung disease and vasculitis"

  • Abstract Number: 804 • 2019 ACR/ARP Annual Meeting

    STING-associated Vasculopathy with Onset in Infancy (SAVI Syndrome) Can Mimic Juvenile Idiopathic Arthritis

    Jose Luis Tandaipan1, Mireia Lopez Corbeto 2 and Estefania Moreno Ruzafa 3, 1Hospital Universitari Mutua Terrassa, Terrassa, Spain, 2Hospital Universitari Vall d'Hebron, Barcelona, Catalonia, Spain, 3Hospital Universitari Vall d'Hebron, Barcelona, Spain

    Background/Purpose: Gain-of-function mutations in TMEM173 encoding STING (Stimulator of Interferon Genes) underlie a novel type I INF termed SAVI syndrome. It is characterized by a…
  • Abstract Number: 1746 • 2018 ACR/ARHP Annual Meeting

    Impact of Interstitial Lung Disease on the Long-Term Survival in 76 Japanese Patients with Microscopic Polyangiitis

    Hiromi Matsushita1, Yoshioki Yamasaki2, Yukiko Takakuwa3, Hidehiro Yamada4 and Kimito Kawahata3, 1Internal Medicine, St. Marianna University School of Medicine, Kawasaki, Japan, 2Internal Medicie, St. Marianna University School of Medicine, Kawasaki, Japan, 3Division of Rheumatology and Allergology, Department of Internal Medicine, St. Marianna University School of Medicine, Kawasaki, Japan, 4Rheumatology, Seirei Yokohama Hospital, Yokohama, Japan

    Background/Purpose: ANCA-associated vasculitis including microscopic polyangiitis (MPA) involves multiple organs including lungs. Clinical characteristics and impact on long-term survival in MPA patients with interstitial lung disease (ILD) have not…
  • Abstract Number: 1748 • 2018 ACR/ARHP Annual Meeting

    Interstitial Lung Disease in ANCA-Positive Vasculitis Patients

    Andy Abril1, Minkyung Kwon,2, Isabel Mira-Avendano3, Carlos Rojas4 and Andras Khoor5, 1Rheumatology, Mayo Clinic Florida, Jacksonville, FL, 2Pulmonary and Critical Care, Mayo Clinic, Jacksonville, FL, 3Pulmonary and Critical Care, Mayo Clinic Florida, Jacksonville, FL, 4Radiology, Mayo Clinic, Jacksonville, FL, 5Pathology, Mayo Clinic, Jacksonville, FL

    Background/Purpose: Rarely, ANCA-positive vasculitis patients are found to have interstitial lung disease (ILD). Clinical characteristics and prognosis are not well known in these patients. The…
  • Abstract Number: 878 • 2015 ACR/ARHP Annual Meeting

    Significance of Interstitial Pneumonitis in Microscopic Polyangiitis

    Kensuke Nakanishi and Mitsuyo Kinjo, Rheumatology, Okinawa Chubu Hospital, Uruma, Japan

    Background/Purpose: Microscopic polyangiitis (MPA) is often associated with lung involvement, including alveolar hemorrhage and interstitial pneumonitis (IP). Clinical characteristics of IP in MPA have not…
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