Abstracts tagged "CNS Vasculitis"

Abstract Number: 1717 • 2019 ACR/ARP Annual Meeting
Identifying Patterns of Histopathologic Presentation in CNS Vasculitis
Chan Mi Lee¹, Richard Prayson ², Marcia Leon Rabanal ³, Leonard Calabrese ³ and Rula Hajj-ali ³, ¹Cleveland Clinic Lerner College of Medicine of Case Western Reserve University/Cleveland Clinic, Cleveland, OH, ²Anatomic Pathology/Cleveland Clinic, Cleveland, OH, ³Rheumatologic and Immunologic Disease/Cleveland Clinic, Cleveland, OH
Background/Purpose: Primary central nervous system vasculitis (CNS-V) is vasculitis confined to the brain, spinal cord and meninges. It is a rare condition with unknown pathogenesis.…
Abstract Number: 1721 • 2019 ACR/ARP Annual Meeting
Adult Primary Central Nervous System Vasculitis Treatment and Course: A Long-term Follow-up Study
Carlo Salvarani¹, Robert D Brown ², Teresa JH Christianson ², John Huston III ², Caterina Giannini ² and Gene G Hunder ², ¹Division of Rheumatology, Arcispedale Santa Maria Nuova-IRCCS, Reggio Emilia, Italy, ²Mayo Clinic, Rochester
Background/Purpose: To evaluate long-term treatment and outcomes of a large cohort of patients with primary central nervous system vasculitis (PCNSV)Methods: The study cohort consisted of…
Abstract Number: 2838 • 2018 ACR/ARHP Annual Meeting
Comorbid Vasculitis Among Patients in a National Primary Immunodeficiency Database
Kevin Byram¹, Leonard H. Calabrese² and James Fernandez¹, ¹Cleveland Clinic Foundation, Cleveland, OH, ²Rheumatic & Immunologic Disease and Infectious Disease, Cleveland Clinic Foundation, Cleveland, OH
Background/Purpose: Vasculitis has been reported in patients with various forms of primary immunodeficiency (PID) in case reports in the literature. The goal of this study…
Abstract Number: 2730 • 2017 ACR/ARHP Annual Meeting
Clinical Features and Treatment of Central Nervous System Vasculitis Associated with Acute Posterior Multifocal Placoid Pigment Epitheliopathy
Hiromichi Tamaki¹ and Rula A Hajj-Ali², ¹Department of Rheumatic and Immunologic Diseases, Cleveland Clinic Foundation, Cleveland, OH, ²Rheumatic and Immunologic Disease, Cleveland Clinic, Cleveland, OH
Background/Purpose: Acute posterior Multifocal Placoid Pigment Epitheliopathy (APMPPE) is a rare inflammatory eye disease and some appear to develop central nervous system vasculitis (CNSV). This…
Abstract Number: 2731 • 2017 ACR/ARHP Annual Meeting
The Utility of Unbiased Metagenomic Next Generation Sequencing in the Management of Patients with CNS Vasculitis
Hiromichi Tamaki¹, Michael R Wilson², Leonard H. Calabrese³, Joseph L. DeRisi⁴ and Rula A Hajj-Ali⁵, ¹Department of Rheumatic and Immunologic Diseases, Cleveland Clinic Foundation, Cleveland, OH, ²Department of Neurology, UCSF, San Francisco, CA, ³Rheumatic & Immunologic Disease, Cleveland Clinic Foundation, Cleveland, OH, ⁴Biochemistry and Biophysics, UCSF, San Francisco, CA, ⁵Rheumatology, Cleveland Clinic Foundation, Cleveland, OH
Background/Purpose: In the clinical approach to CNS vasculitis, exclusion of infection is of major concern as some microbes can cause vasculitis, and infections can complicate…
Abstract Number: 2951 • 2016 ACR/ARHP Annual Meeting
Patient Outcomes in Primary Angiitis of the Central Nervous System
Elisabeth Ray¹, Didem Saygin², Anabelle Morales-Mena³, William Messner⁴, Leonard H. Calabrese⁵ and Rula A Hajj-Ali⁶, ¹Rheumatology, Cleveland Clinic, Cleveland, OH, ²Cleveland Clinic, Cleveland, OH, ³Rheumatology, Hillcrest Hospital, Mayfield Heights, OH, ⁴Quantitative Health Sciences, Cleveland Clinic, Cleveland, OH, ⁵Rheumatic & Immunologic Disease, Cleveland Clinic, Cleveland, OH, ⁶Rheumatic and Immunologic Dis, Cleveland Clinic, Cleveland, OH
Results: 1855 patient records were identified using the ICD-9 code for cerebral angiitis. 78 patients met inclusion criteria, of which 27 responded to the questionnaires…
Abstract Number: 2952 • 2016 ACR/ARHP Annual Meeting
Differentiation Between Neurosarcoidosis and Primary CNS Vasculitis Based on Clinical and Cerebrospinal Fluid Parameters
Didem Saygin¹, Leonard H. Calabrese², Elisabeth Ray¹, William Messner³, Jinny Tavee⁴ and Rula A Hajj-Ali⁵, ¹Rheumatology, Cleveland Clinic, Cleveland, OH, ²Rheumatic & Immunologic Disease, Cleveland Clinic, Cleveland, OH, ³Quantitative Health Sciences, Cleveland Clinic, Cleveland, OH, ⁴Neuromuscular diseases, Cleveland Clinic, Cleveland, OH, ⁵Rheumatic and Immunologic Dis, Cleveland Clinic, Cleveland, OH
Background/Purpose: Neurosarcoidosis is one of the great mimickers of primary angiitis of central nervous system (PACNS) in terms of disease presentation, imaging and pathologic findings.…
Abstract Number: 2953 • 2016 ACR/ARHP Annual Meeting
Comparison of Patient Outcomes in Primary Angiitis of the Central Nervous System and Reversible Cerebral Vasoconstriction Syndrome
Elisabeth Ray¹, Didem Saygin¹, Seby John², William Messner³, Ken Uchino⁴, Leonard H. Calabrese⁵ and Rula A Hajj-Ali⁶, ¹Rheumatology, Cleveland Clinic, Cleveland, OH, ²Cleveland Clinic, Cleveland, OH, ³Quantitative Health Sciences, Cleveland Clinic, Cleveland, OH, ⁴Cerebrovascular Center, Cleveland Clinic Foundation, Cleveland, OH, ⁵Rheumatic & Immunologic Disease, Cleveland Clinic, Cleveland, OH, ⁶Rheumatic and Immunologic Dis, Cleveland Clinic, Cleveland, OH
Background/Purpose: Reversible Cerebral Vasoconstriction Syndrome (RCVS) is an important mimic of Primary Angiitis of the Central Nervous System (PACNS). Distinct clinical and diagnostic features differentiate…
Abstract Number: 3179 • 2015 ACR/ARHP Annual Meeting
Diagnosing Childhood Small Vessel CNS Vasculitis
Marinka Twilt¹, Maryam Nabavi Nouri², Pascal N. Tyrrell³, Anastasia Dropol¹, Shehla Sheikh⁴, Cynthia Hawkins⁵ and Susanne Benseler^6,7, ¹Rheumatology, Alberta Children's Hospital, Calgary, AB, Canada, ²Neurology, The Hospital for Sick Childern, Toronto, ON, Canada, ³Department of Medical Imaging, University of Toronto, Toronto, ON, Canada, ⁴Rheumatology, The Hospital for Sick Children, Toronto, ON, Canada, ⁵Paediatric Laboratory Medicine, The Hospital for Sick Children, Toronto, ON, Canada, ⁶Alberta Children's Hospital Research Institute/University of Calgary, Calgary, AB, Canada, ⁷Pediatrics/Alberta Children's Hospital, Department of Pediatrics/University of Calgary, Calgary, AB, Canada
Background/Purpose: Childhood primary small vessel CNS vasculitis (SVcPACNS) is an increasingly recognized inflammatory brain disease with high morbidity and mortality mandating an elective brain biopsy…
Abstract Number: 1993 • 2015 ACR/ARHP Annual Meeting
Imaging Findings of Cerebral Amyloid Angiopathy, Abeta-Related Angiitis (ABRA) and Cerebral Amyloid Angiopathy-Related Inflammation: A Single Institution 25 Year Experience
Carlo Salvarani¹, Jonathan M Morris², Caterina Giannini², Teresa J. H. Christianson³, Robert D. Brown Jr.⁴ and Gene G. Hunder⁵, ¹Rheumatology, Arcispedale S Maria Nuova-IRCCS, Reggio Emilia, Italy, ²Mayo Clinic, Rochester, MN, ³Division of Biomedical Statistics & Informatics, Mayo Clinic, Rochester, MN, ⁴Department of Neurology, Mayo Clinic, Rochester, MN, ⁵Dept Internal Med/Rheum, Mayo Clinic, Rochester, MN
Background/Purpose: To investigate the role of imaging in differentiating cerebral amyloid angiopathy (CAA) with and without inflammation. Methods: We studied 54 patients seen over 25…
Abstract Number: 2766 • 2014 ACR/ARHP Annual Meeting
Mycophenolate Mofetil in the Treatment of Primary Central Nervous System Vasculitis
Carlo Salvarani¹, Robert D. Brown Jr.², Teresa J. H. Christianson², John Huston III², Francesco Muratore¹, Caterina Giannini² and Gene G. Hunder³, ¹Rheumatology Unit, Arcispedale S Maria Nuova, Reggio Emilia, Italy, ²Mayo Clinic, Rochester, MN, ³Rheumatology, Mayo Clinic, Rochester, MN
Background/Purpose . The optimal management of primary central nervous system vasculitis (PCNSV) remains unclear. Cyclophosphamyde (CYC) in combination with glucocorticoids (GCs) or GCs alone are…
Abstract Number: 1661 • 2013 ACR/ARHP Annual Meeting
The Spectrum of childhood Inflammatory Brain Diseases; An Increasingly Recognised Field
Marinka Twilt¹, Eyal Muscal², Tania Cellucci³, Pavla Dolezalova⁴, Rob Forsyth⁵, Susan Kim⁶, David A. Cabral⁷, Johannes Roth⁸, Adam Kirton⁹, Rolando Cimaz¹⁰, Jasmin Kummerle-Deschner¹¹, Annet van Royen-Kerkhof¹², Jürgen Brunner¹³, Gaelle Chedeville¹⁴, Jordi Anton¹⁵, Angela Robinson¹⁶, Mary Toth¹⁷, Tilmann Kallinich¹⁸, Claudia Bracaglia¹⁹, Alexis Boneparth²⁰, Shehla Sheikh²¹ and Susanne M. Benseler²¹, ¹Division of Rheumatology, The Hospital for Sick Children, Toronto, ON, Canada, ²TCH Pediatric Rheum Center, Baylor College of Medicine, Houston, TX, ³Rheumatology, Hamilton Health Sciences, McMaster, Hamilton, ON, Canada, ⁴Pediatric Rheumatology Unit, Department of Pediatrics and Adolescent Medicine, General University Hospital in Prague, Prague, Czech Republic, ⁵Newcastle upon Tyne's NHS foundation Trust, Newcastle upon Tyne, United Kingdom, ⁶Division of Immunology, Boston Children's Hospital, Boston, MA, ⁷University of British Columbia, Vancouver, BC, Canada, ⁸University of Ottawa, Ottawa, ON, Canada, ⁹Neurology, Alberta Children's Hospital, Calgary, AB, Canada, ¹⁰Rheumatology Unit, A. Meyer Children's Hospital, Florence, Italy, ¹¹University Childrens Clinic Tuebingen, Tuebingen, Germany, ¹²Department of Pediatric Immunology & Rheumatology, Wilhelmina Children’s Hospital, University Medical Center Utrecht, Utrecht, Netherlands, ¹³pediatric Rheumatology, University Children's Hospital, Innsbruck, Austria, ¹⁴Pediatric Rheumatology, Montreal Children's Hospital, Montreal, QC, Canada, ¹⁵Rheumatology, Hospital Sant Joan de Deu, Barcelona, Spain, ¹⁶Pediatrics, Rainbow Babies & Children's Hospital / Case Medical Center, Cleveland, OH, ¹⁷Rheumatology, Akron Children's Hospital, Akron, OH, ¹⁸Charite, University Medicine Berlin, Berlin, Germany, ¹⁹Department of Pediatric Medicine, Division of Rheumatology, Ospedale Pediatrico Bambino Gesù, IRCCS, Rome, Italy, ²⁰Pediatrics, The Children's Hospital at Montefiore, Bronx, NY, ²¹Rheumatology, The Hospital for Sick Children, Toronto, ON, Canada
Background/Purpose: Childhood Inflammatory Brain diseases are potentially life-threatening diseases leading to severe neurological deficits if not treated. The spectrum of childhood inflammatory brain diseases is…
Abstract Number: 741 • 2013 ACR/ARHP Annual Meeting
Granulomatosis With Polyangiitis Central Nervous System Involvement: Presentation and Management
Gonzalo De Luna^1,2, Benjamin Terrier³, Pierre Kaminsky⁴, Francois Maurier⁵, Roser Solans⁶, Raphaèle Seror⁷, Xavier Puéchal⁸, Luc Mouthon⁹ and Loic Guillevin¹⁰, ¹Medecine Interne, Cochin University Hospital, Paris, France, ²Internal Medicine, Hospital Ramon y Cajal, Madrid, Spain, ³Internal Medicine, Cochin University Hospital, Paris, France, ⁴Université de Lorraine, Nancy, F-54000, France; CHU de Nancy, Orphan disease unit, Nancy, F-54000, France;, Nancy, France, ⁵HP Metz Belle Isle Hospital, Department of Internal Medicine, Metz, France, ⁶Autoimmune Systemic Diseases Unit, Department of Internal Medicine, Hospital Vall d'Hebron, Autonomous University of Barcelona, Barcelona, Spain, ⁷Rheumatology, Bicetre university hospital, LE Kremlin-Bicetre, France, ⁸National Referral Center for Rare Systemic Auto-immune Diseases, Hôpital Cochin, AP-HP, Université Paris Descartes, Sorbonne Paris Cité, Paris, France, ⁹Department of Internal Medicine, Referral Center for Rare Autoimmune and Systemic Diseases, Hôpital Cochin, AP–HP, Université Paris Descartes, Paris, France, Paris, France, ¹⁰Department of Internal Medicine, Referral Center for Rare Autoimmune and Systemic Diseases, Hôpital Cochin, AP–HP, Université Paris Descartes, Paris, France
Background/Purpose: Granulomatosis with polyangiitis (GPA), a small-sized–vessel vasculitis, commonly involves ear, nose & throat (ENT), lungs and kidneys, and, more rarely, the central nervous system…

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