Abstract Number: 245 • 2016 ACR/ARHP Annual Meeting
Efficacy of Cyclophosphamide Therapy in Idiopathic Retroperitoneal Fibrosis in a Retrospective Monocentric Analysis
Background/Purpose: Ormond’s disease (idiopathic retroperitoneal fibrosis ,IRF) is a rare disease. Main clinical symptom is compression of the ureters leading to renal failure. A majority…Abstract Number: 246 • 2016 ACR/ARHP Annual Meeting
Efficacy of Colchicine and IL-1 Inhibitors in Amyloidosis Associated with Familial Mediterranean Fever: A Retrospective Analysis
Background/Purpose: Familial Mediterranean fever (FMF), the most common form of hereditary autoinflammatory diseases, is associated with increased risk for secondary (AA) amyloidosis. We herein aimed…Abstract Number: 247 • 2016 ACR/ARHP Annual Meeting
ANTI-Interleukin 1 Therapy in FMF Amyloidosis: A Single Center Experience
Background/Purpose: Recently there is increasing number of reports pointing out the efficacy of anti-interleukin 1(anti-IL1)therapy to control AA amyloidosis secondary to autoinflammatory diseases. Here we…Abstract Number: 248 • 2016 ACR/ARHP Annual Meeting
Disease Severity and High Attack Frequency Under Colchicine Treatment Is Associated with Increased Carotid Intima Media Thickness in FMF
Background/Purpose: Cardiovascular (CV) risk assessment is infrequently performed in Familial Mediterranean Fever (FMF), an autoinflammatory disorder with only acute attacks of inflammation. As a surrogate…Abstract Number: 249 • 2016 ACR/ARHP Annual Meeting
MiR-204-3p Associates with an Increased Level of IL-6 in Familial Mediterranean Fever By Targeting the PIK3 Signaling Pathway
Background/Purpose: Familial Mediterranean fever (FMF) is caused by a number of mutations of the MEFV gene, coding for a protein named pyrin that acts as…Abstract Number: 250 • 2016 ACR/ARHP Annual Meeting
Application of the 2016 European Leage Against Rheumatism (EULAR) /American College of Rheumatology (ACR)/Paediatric Rheumatology International Trials Organisation (PRINTO) Classification Criteria of Macrophage Activation Syndrome in Patients with Adult Onset Still’s Disease
Background/Purpose: Macrophage activation syndrome (MAS) is acute systemic inflammation arising in the context of various autoimmune and autoinflammatory conditions, which is often life-threatening. In 2016,…Abstract Number: 251 • 2016 ACR/ARHP Annual Meeting
Persistent Pruritic Skin Lesions with Dyskeratotic Cells in Upper Layer of Epidermis Are Specific and Associated with High Levels of Serum IL-18 in Adult-Onset Still’s Disease
Background/Purpose: Adult-onset Still’s disease (AOSD) is an acute and systemic inflammatory disorder that is characterized by high spiking fever, evanescent rash, arthralgia/arthritis and hyperferritinemia. However,…Abstract Number: 252 • 2016 ACR/ARHP Annual Meeting
Cytokine Profiles of Korean Patients with Adult Onset Still’s Disease Treated with Biologic Agents
Background/Purpose: Adult onset Still’s disease (AOSD) is a rare inflammatory disorder of unknown etiology. Several studies have reported that pro-inflammatory cytokines including interleukin (IL)-1, IL-6,…Abstract Number: 253 • 2016 ACR/ARHP Annual Meeting
Corticosteroid-Free Tocilizumab Monotherapy for Adult Onset Still’s Disease: Results in Six Month
Background/Purpose: To assess the efficacy and safety of tocilizumab (TCZ) monotherapy for the induction therapy of adult onset Still’s disease (AOSD) in a prospective, single-arm, single-center, cohort,…Abstract Number: 254 • 2016 ACR/ARHP Annual Meeting
NLRP12 Autoinflammatory Disease: A Chinese Case Series and Literature Review
Background/Purpose: Systemic autoinflammatory diseases (SAIDs) are a genetically heterogeneous group of rheumatic diseases that are driven by abnormal activation of the innate immune system.…Abstract Number: 255 • 2016 ACR/ARHP Annual Meeting
Safety and Efficacy of Long-Term Canakinumab Therapy in Patients with CAPS: Final Results from Beta-Confident Registry
Background/Purpose: Cryopyrin-associated periodic syndrome (CAPS) is a rare auto-inflammatory disease encompassing a spectrum of 3 phenotypes: familial cold auto-inflammatory syndrome (FCAS), Muckle–Wells syndrome (MWS), and…Abstract Number: 256 • 2016 ACR/ARHP Annual Meeting
Muckle-Wells Syndrome in Chinese Adult Patients
Background/Purpose: Muckle-Wells syndrome (MWS) is a rare autoinflammatory disease, which is categorized as one of the three cryopyrin-associated periodic syndromes (CAPS). MWS is characterized by…Abstract Number: 257 • 2016 ACR/ARHP Annual Meeting
CNS Manifestations of Patients with Muckle-Wells Syndrome
Background/Purpose: CAPS is a rare autoinflammatory disease associated with mutations in the NLRP3 gene that result in overactivation of the inflammasome, increased secretion of IL-1beta…Abstract Number: 258 • 2016 ACR/ARHP Annual Meeting
Unmet Psychosocial Needs in Patients with CAPS
Background/Purpose: Cryopyrin-associated periodic syndrome (CAPS) is a rare autoinflammatory disease. Generalized manifestations like recurrent fever and fatigue and organ disease like reduced vision, hearing loss,…Abstract Number: 259 • 2016 ACR/ARHP Annual Meeting
Rituximab in Refractory Cardiac Sarcoidosis – Single Center Experience
Background/Purpose: Cardiac sarcoidosis is a life threatening condition for which there is limited data to guide optimal steroid-sparing agents. B-cells have been reported to…
ACR Meeting Abstracts