ACR Meeting Abstracts

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  • Abstract Number: 2261 • 2018 ACR/ARHP Annual Meeting

    Long-Term Outcome of Pulmonary Sarcoidosis: A Population-Based Cohort Study from 1976-2013

    Patompong Ungprasert1,2, Cynthia S. Crowson3, Eva M. Carmona Porquera4 and Eric L. Matteson5, 1Clinical Epidemiology Unit, Department of Research and Development, Faculty of Medicine Siriraj Hospital, Mahidol University, Bangkok, Thailand, 2Rheumatology, Mayo Clinic College of Medicine and Science, Rochester, MN, 3Health Sciences Research, Mayo Clinic College of Medicine and Science, Rochester, MN, 4Pulmonary and Critical Care Medicine, Mayo Clinic College of Medicine and Science, Rochester, MN, 5Division of Rheumatology, Mayo Clinic College of Medicine and Science, Rochester, MN

    Long-term Outcome of Pulmonary Sarcoidosis: A Population-Based Cohort Study from 1976-2013  Background/Purpose: A hallmark of sarcoidosis is lung disease, which has variable expression. This study…
  • Abstract Number: 2262 • 2018 ACR/ARHP Annual Meeting

    Increased Risk of Sarcoidosis Among Patients with Celiac Disease: A Systematic Review and Meta-Analysis

    Patompong Ungprasert1, Karn Wijarnpreecha2, Panadeekarn Panjawatanan3, Ploypin Lertjitbanjong2 and Juan Corral4, 1Clinical Epidemiology Unit, Department of Research and Development, Faculty of Medicine Siriraj Hospital, Mahidol University, Bangkok, Thailand, 2Internal medicine, Bassett medical center, cooperstown, NY, 3Medicine, Chiang Mai University, Chiang Mai, Thailand, 4Internal medicine, Mayo Clinic, Jacksonville, Jacksonville, FL

    Increased Risk of Sarcoidosis among Patients with Celiac Disease: A Systematic Review and Meta-Analysis AbstractBackground/Purpose: Several epidemiologic studies have suggested that patients with celiac disease may…
  • Abstract Number: 2263 • 2018 ACR/ARHP Annual Meeting

    Differentiated Phenotypes at Diagnosis of Sarcoidosis According to the Scadding Classification: Analysis in 1230 Patients

    Soledad Retamozo1,2,3, Roberto Pérez-Alvarez4, Pilar Brito-Zerón5,6, Belchin Kostov7, Carlos Feijoo Massó8, Guadalupe Fraile9, A. González-García10, Ricardo Gómez De La Torre11, Begoña De-Escalante12, Miguel Lopez-Dupla13, Ana Alguacil14, Joel Chara-Cervantes15, M. Pérez-Conesa16, Francisco-Javier Rascón17, Jose Salvador Garcia Morillo18, Patricia Perez Guerrero19, Eva Fonseca Aizpuru20, Miriam Akasbi21, Mariona Bonet22, José Luis Callejas23, Gloria De La Red Bellvis24, Eva Calvo Begueria25, Cristina Soler i Ferrer26, Enrique Peral Gutiérrez De Ceballos27, J. F. Gómez-Cerezo28, Gracia Cruz Caparrós29, Sergio Rodríguez Fernández30, Blanca Pinilla31, Alberto Gato Diez32, A. Rolo33, César Morcillo6, Angel Robles34, Inmaculada Ojeda35, M. J. Vives36, Borja de-Miguel37, María Penadés Vidal38, Moisés De Vicente39, Xavier Bosh40, Marta Pérez-de-Lis41, A. González-García9, Carmen Yllera Gutiérrez42, B. Gracia-Tello43, M. Pedrosa44, A. Perez-Gonzalez4, Carles Tolosa45, Antoni Sisó-Almirall46, Lucio Pallarés47 and Manuel Ramos-Casals5, 1Instituto de Investigaciones en Ciencias de la Salud, Universidad Nacional de Córdoba, Consejo Nacional de Investigaciones Científicas y Técnicas (INICSA-UNC-CONICET), Cordoba, Argentina, 2Laboratory of Systemic Autoimmune Diseases “Josep Font”, CELLEX, Institut d’Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), Department of Systemic Autoimmune Diseases, ICMID, Hospital Clinic, Barcelona, Barcelona, Spain, 3Rheumatology Unit, Hospital Privado Universitario de Córdoba, Institute University of Biomedical Sciences University of Córdoba (IUCBC), Cordoba, Argentina, 4Department of Internal Medicine, Hospital Alvaro Cunqueiro, Vigo, Vigo, Spain, 5Laboratory of Autoimmune Diseases Josep Font, IDIBAPS, Department of Autoimmune Diseases, ICMiD, Hospital Clinic, Barcelona, Barcelona, Spain, 6Systemic Autoimmune Diseases Unit, Hospital CIMA-Sanitas, Barcelona, Barcelona, Spain, 7Primary Care Research Group, IDIBAPS, Centre d’Assistència Primària ABS Les Corts, GESCLINIC, Barcelona, Barcelona, Spain, 8Department of Internal Medicine, Hospital Parc Taulí, Sabadell, Sadabell, Spain, 9Hospital Ramon y Cajal, Madrid, Madrid, Spain, 10Internal Medicine, Hospital Ramón y Cajal, Madrid, Madrid, Spain, 11Department of Internal Medicine, Hospital Universitario Central de Asturias, Oviedo, Oviedo, Spain, 12Hospital Clínico, Zaragoza, Zaragoza, Spain, 13Systemic Autoimmune Diseases Unit, Hospital Joan XXIII, Tarragona, Tarragona, Spain, 14Hospital Virgen de la Salud, Toledo, Toledo, Spain, 15Hospital Universitario Miguel Servet, Zaragoza, Zaragoza, Spain, 16Hospital Miguel Servet, Zaragoza, Zaragoza, Spain, 17Hospital Son Espases, Palma de Mallorca, Palma de Mallorca, Spain, 18Department of Internal Medicine, Hospital Virgen del Rocio, Sevilla, Sevilla, Spain, 19Department of Internal Medicine, Hospital Universitario Puerta del Mar, Cádiz, Cadiz, Spain, 20Department of Internal Medicine, Hospital de Cabueñes, Gijón, Gijón, Spain, 21Department of Internal Medicine, Hospital Infanta Leonor, Madrid, Madrid, Spain, 22Department of Internal Medicine, Althaia, Xarxa Assistencial de Manresa, Manresa, Spain, 23Hospital Clínico San Cecilio, Granada, Granada, Spain, 24Department of Internal Medicine, Hospital de Santa Coloma de Gramanet, Barcelona, Barcelona, Spain, 25Hospital Universitario Puerta del Mar, Cádiz, Cádiz, Spain, 26Hospital de Sta Caterina, Girona, Girona, Spain, 27Department of Internal Medicine, Hospital Virgen Macarena, Sevilla, Sevilla, Spain, 28Hospital Infanta Sofía, Madrid, Madrid, Spain, 29Department of Internal Medicine, Hospital de Poniente El Ejido, Almería, Almería, Spain, 30Department of Internal Medicine, Hospital da Barbanza, A Coruña, A Coruña, Spain, 31Systemic Autoimmune Diseases Unit Medicine, Hospital Gregorio Marañón, Madrid, Madrid, Spain, 32Department of Internal Medicine, Complejo Hospitalario Albacete, Albacete, Albacete, Spain, 33Hospital Salamanca, Salamanca, Salamanca, Spain, 34Hospital La Paz, Madrid, Madrid, Spain, 35Department of Internal Medicine, Hospital Valle del Guadiato, Córdoba, Cordoba, Spain, 36Parc Sanitari San Joan de Déu, Sant Boi, Barcelona, Spain, 37Hospital 12 de Octubre, Madrid, Madrid, Spain, 38Department of Internal Medicine, Hospital De Manises, Valencia, Valencia, Spain, 39Department of Internal Medicine, Hospital Nuestra Señora del Prado, Talavera, Talavera, Spain, 40Department of Internal Medicine, ICMiD, Hospital Clinic, Barcelona, Barcelona, Spain, 41Servicio de Anestesiologia y Reanimación. Complejo Hospitalario Universitario de A Coruña, A Coruña, A Coruña, Spain, 42Hospital Universitario Central de Asturias, Oviedo, Oviedo, Spain, 43Hospital Clinico, Zaragoza, Zaragoza, Spain, 44Hospìtal Parc Taulí, Sadabell, Sabadell, Spain, 45Department of Internal Medicine, Corporación Sanitaria Universitaria Parc Taulí, Barcelona, Spain, 46Grup de Recerca Transversal en Atenció Primària, IDIBAPS, Barcelona, Barcelona, Spain, 47Department of Internal Medicine, Hospital Son Espases. Palma de Mallorca, Palma de Mallorca, Spain

    Background/Purpose: To analyse the correlation between Scadding radiological stages and the main phenotypic features at diagnosis (epidemiology, clinical patterns at presentation, extrathoracic disease and need…
  • Abstract Number: 2264 • 2018 ACR/ARHP Annual Meeting

    Methotrexate in the Treatment of Granulomatous Mastitis: A Retrospective Review of 19 Cases

    Anna Postolova1 and Mark C. Genovese2, 1Department of Medicine, Stanford University Medical Center, Palo Alto, CA, 2Department of Medicine, Stanford University, Palo Alto, CA

    Background/Purpose: Granulomatous Mastitis is a rare, inflammatory disease of the breast. Presenting symptoms in the breast can be unilateral or bilateral pain, masses, skin induration,…
  • Abstract Number: 2265 • 2018 ACR/ARHP Annual Meeting

    Lymphocyte Immunophenotyping and CD4/CD8 Ratio in Cerebrospinal Fluid for the Diagnosis of Sarcoidosis-Related Uveitis

    Romain Paule1, Laure Denis1, Nicolas Chapuis2, Julien Rohmer1, Jonathan London3, Clemence Bonnet4, Anthony Chauvin5, Luc Mouthon1, Dominique Monnet4, Claire Le Jeunne1, Antoine Brezin6 and Benjamin Terrier7, 1National Referral Center for Rare Systemic Autoimmune Diseases, Hôpital Cochin, AP–HP, Université Paris Descartes, Paris, Internal medicine, France, Paris, France, 2Hôpital Cochin, AP–HP, Université Paris Descartes, Paris, Biological Hematology, France, Paris, France, 3Internal Medecine, National Referral Center for Rare Systemic Autoimmune Diseases, Hôpital Cochin, AP–HP, Université Paris Descartes, Paris, France, 4Referral Center for Rare Ophthalmological Diseases, Hôpital Cochin, AP–HP, Université Paris Descartes, Paris, ophtalmology, France, Paris, France, 5Emergency Département, Hôpital Lariboisière, Assistance Publique-Hôpitaux de Paris, Paris, France; Faculté de Médecine, Université Diderot, Paris, France, Paris, France, 6Ophtalmology, Referral Center for Rare Ophthalmological Diseases, Hôpital Cochin, AP–HP, Université Paris Descartes, Paris, ophtalmology, France, Paris, France, 7Internal Medicine, National Referral Center for Rare Systemic Autoimmune Diseases, Hôpital Cochin, AP–HP, Université Paris Descartes, Paris, France

    Background/Purpose: The diagnostic workup of uveitis is a challenge due to the wide range of diagnoses and the lack of a well-codified diagnostic procedure. Underlying…
  • Abstract Number: 2266 • 2018 ACR/ARHP Annual Meeting

    Serum 1,25(OH)2 Vitamin D and 25(OH) Vitamin D Ratio for the Diagnosis of Sarcoidosis-Related Uveitis

    Julien Rohmer1, Jérôme Hadjadj2, Amina Bouzerara3, Sawsen Salah4, Romain Paule5, Matthieu Groh6, Philippe Blanche7, Luc Mouthon8, Dominique Monnet4, Claire Le Jeunne9, Jean Guibourdenche10, Antoine Brezin11 and Benjamin Terrier12, 1National Referral Center for Rare Systemic Autoimmune Diseases, Hôpital Cochin, AP–HP, Université Paris Descartes, Paris, Internal medicine, France, Paris, France, 2Department of Internal Medicine, National Referral Center for Rare Autoimmune and Systemic Diseases, Hospital Cochin, Assistance Publique-Hôpitaux de Paris (AP-HP), Team Neutrophils and Vasculitis, INSERM U1016, Cochin Institute, Paris, France, Paris, France, 3Service d'Hormonologie, Hôpital Cochin, Paris, France, 4Ophtalmology, Cochin Hospital, Paris, France, 5Department of Internal Medicine, Department of Internal Medicine, Cochin University Hospital, Paris, France, 6Internal Medicine, Foch, Suresnes, France, 7Internal Medicine, Cochin Hospital, Paris, France, 8Department of Internal Medicine, INSERM Unité 1016, Centre de Référence pour les Maladies Auto-immunes Rares, National Referral Center for Rare Systemic Autoimmune Diseases, Paris Cochin, France, Paris, France, 9Department of Internal Medicine, National Referral Center for Rare Systemic Autoimmune Diseases, Hôpital Cochin, AP–HP, Université Paris Descartes, Paris, France, 10Hormonology department, Cochin Hospital, Paris, France, 11Ophtalmology, Referral Center for Rare Ophthalmological Diseases, Hôpital Cochin, AP–HP, Université Paris Descartes, Paris, ophtalmology, France, Paris, France, 12National Referral Center for Rare Systemic Autoimmune Diseases, Paris Cochin, France, Paris, France

    Background/Purpose: The diagnostic workup of uveitis is challenging, with 30 to 50% of cases remaining of undetermined etiology despite multiple investigations. Sarcoid granuloma-related increase of…
  • Abstract Number: 2267 • 2018 ACR/ARHP Annual Meeting

    Ocular and Systemic Features in 262 Patients with Systemic Sarcoidosis and Its Correlation with Iwos Criteria

    Belén Atienza-Mateo1, José Luis Martín-Varillas1, Rosalía Demetrio-Pablo2, Vanesa Calvo-Río3, Diana Prieto Peña3, Monica Calderón Goercke3, Javier Rueda-Gotor1, Enar Pons1, Miguel Angel González-Gay2 and Ricardo Blanco1, 1Rheumatology, Hospital Universitario Marqués de Valdecilla. IDIVAL. Santander. Universidad de Cantabria. Spain, Santander, Spain, 2Hospital Universitario Marqués de Valdecilla. IDIVAL. Santander. Universidad de Cantabria. Spain, Santander, Spain, 3Rheumatology, Rheumatology. Hospital Universitario Marqués de Valdecilla. IDIVAL. Santander. Universidad de Cantabria. Spain, Santander, Spain

    Background/Purpose: Sarcoidosis is a multisystemic inflammatory disease of unknown origin characterized by non-caseating epitheliod granulomas that can affect any organ system. The three most frequency…
  • Abstract Number: 2268 • 2018 ACR/ARHP Annual Meeting

    Anti-IL6-Receptor Tocilizumab in Graves’ Orbitopathy. Multicenter Study of 46 Patients

    Belén Atienza-Mateo1, José Luis Martín-Varillas1, Vanesa Calvo-Río2, Rosalía Demetrio-Pablo3, Diana Prieto Peña2, Monica Calderón Goercke2, Elia Valls-Pascual4, Beatriz Valls-Espinosa5, Olga Maiz-Alonso6, Ana Blanco7, Ignacio Torre-Salaberri8, Verónica Rodriguez-Mendez9, Angel Garcia-Aparicio10, Raúl Veroz González11, Vega Jovaní12, Diana Peiteado13, Margarita Sanchez Orgaz14, Santos Castañeda15, Eva Tomero16, Francisco J. Toyos Sáenz de Miera17, Valvanera Pinillos18, Elena Aurrecoechea19, Ángel Mora20, Arantxa Conesa21, Manuel Fernández22, Nuria Avilés23, J. Antonio Troyano24, Miguel Angel González-Gay1 and Ricardo Blanco1, 1Rheumatology, Hospital Universitario Marqués de Valdecilla. IDIVAL. Santander. Universidad de Cantabria. Spain, Santander, Spain, 2Rheumatology, Rheumatology. Hospital Universitario Marqués de Valdecilla. IDIVAL. Santander. Universidad de Cantabria. Spain, Santander, Spain, 3Hospital Universitario Marqués de Valdecilla. IDIVAL. Santander. Universidad de Cantabria. Spain, Santander, Spain, 4Hospital Universitario Doctor Peset. Valencia. Spain, Valencia, Spain, 5Rheumatology, Hospital Universitario Doctor Peset. Valencia. Spain, Valencia, Spain, 6Hospital Universitario Donostia. San Sebastian. Spain, Donostia, Spain, 7Ophtamology, Hospital Universitario Donostia. San Sebastian. Spain, San Sebastian, Spain, 8Rheumatology, Hospital Universitario de Basurto. Bilbao. Spain, Bilbao, Spain, 9Ophthalmology, Hospital Universitario de Basurto. Bilbao. Spain, Bilbao, Spain, 10Rheumatology, Hospital de Toledo. Toledo. Spain, Toledo, Spain, 11Rheumatology, Hospital de Mérida. Badajoz. Spain, Mérida, Spain, 12Rheumatology, Hospital General Universitario de Alicante. Spain, Alicante, Spain, 13Rheumatology, Rheumatology, La Paz University Hospital, Madrid, Spain, 14Ophthalmology, Hospital Universitario La Paz. Madrid. Spain, Madrid, Spain, 15Rheumatology, Hospital La Princesa. Madrid. Spain, Madrid, Spain, 16Rheumatology, Hospital de La Princesa. Madrid. Spain, Madrid, Spain, 17Hospital Virgen de La Macarena. Sevilla. Spain, Sevilla, Spain, 18Rheumatology, Hospital San Pedro. Logroño. La Rioja. Spain, Logroño, Spain, 19Rheumatology, Hospital de Sierrallana. Torrelavega. Spain, Torrelavega, Spain, 20Ophthalmology, Hospital de Sierrallana. Torrelavega. Cantabria. Spain, Torrelavega, Spain, 21Rheumatology, Hospital Clínico Universitario de Valencia. Spain, Valencia, Spain, 22Hospital Universitario de Guadalajara. Spain, Guadalajara, Spain, 23Rheumatology, Hospital Puerta del Mar. Cádiz. Spain, Cádiz, Spain, 24Ophthalmology, Hospital Universitario Clínico San Carlos. Madrid. Spain, Madrid, Spain

    Background/Purpose: To assess the efficacy of Tocilizumab (TCZ) in refractory thyroid associated orbitopathy (TAO) due to Grave’s disease.Methods: Multicenter study of 46 patients with TAO…
  • Abstract Number: 2269 • 2018 ACR/ARHP Annual Meeting

    Infliximab Therapy in Refractory Retinal Vasculitis of Behçet’s Disease, Short and Long-Term Follow-up. Multicenter Study of 72 Patients

    José Luis Martín-Varillas1, Belén Atienza-Mateo1, Vanesa Calvo-Río2, Diana Prieto Peña2, Monica Calderón Goercke2, Rosalía Demetrio-Pablo3, Javier Loricera3, M. Victoria Hernández4, Alfredo Adan5, Marina Mesquida5, Diana Peiteado6, David Diaz-Valle7, Lucía Martínez-Costa8, Elia Valls-Pascual8, Miguel A. Caracuel9, Angel Garcia-Aparicio10, Jose M Herreras11, Miguel Cordero-Coma12, Carlos Alberto Montilla-Morales13, Alejandro Fonollosa14, Antonio Atanes15, Félix Francisco16, Ignacio Torre-Salaberri17, Olga Maíz18, Ana Blanco19, Cruz Fernandez-Espartero20, Norberto Ortego Centeno21, Enrique Raya Álvarez22, Myriam Gandía23, Francisco Javier López Longo24, Maria Alcalde-Villar25, Cristina Fernández-Carballido26, Esperanza Pato Cour27, Oscar Ruiz Moreno28, Fernando Jiménez-Zorzo29, Raquel Almodóvar González30, Carmen Carrasco-Cubero31, Luis Francisco Linares32, Fredeswinda I. Romero-Bueno33, Santos Insua34, Senen González-Suárez35, Marisa Hernández36, Emma Beltrán37, Juan Cruz38, Carlos Férnandez Cid39, Elena Aurrecoechea40, Enar Pons1, Miguel Angel González-Gay3 and Ricardo Blanco1, 1Rheumatology, Hospital Universitario Marqués de Valdecilla. IDIVAL. Santander. Universidad de Cantabria. Spain, Santander, Spain, 2Rheumatology, Rheumatology. Hospital Universitario Marqués de Valdecilla. IDIVAL. Santander. Universidad de Cantabria. Spain, Santander, Spain, 3Hospital Universitario Marqués de Valdecilla. IDIVAL. Santander. Universidad de Cantabria. Spain, Santander, Spain, 4Rheumatology, Hospital Clinic. Barcelona. Spain, Barcelona, Spain, 5Hospital Clinic. Barcelona. Spain, Barcelona, Spain, 6Rheumatology, Rheumatology, La Paz University Hospital, Madrid, Spain, 7Hospital Clínico San Carlos. Madrid. Spain, Madrid, Spain, 8Hospital Universitario Doctor Peset. Valencia. Spain, Valencia, Spain, 9Hospital de Córdoba, Córdoba, Spain., Córdoba, Spain, 10Rheumatology, Hospital de Toledo. Toledo. Spain, Toledo, Spain, 11Ophthalmology, Hospital Universitario, IOBA. Valladolid. Spain, Valladolid, Spain, 12Ophthalmology, Hospital de León. Spain, León, Spain, 13Hospital Clínico Universitario de Salamanca. Spain, Salamanca, Spain, 14Ophthalmology, Hospital de Cruces. Bilbao. Spain, Bilbao, Spain, 15Complejo Hospitalario Universitario A Coruña. Spain, A Coruna, Spain, 16Rheumatology, Hospital Doctor Negrín. Las Palmas de Gran Canaria. Spain, Las Palmas de Gran Canaria, Spain, 17Rheumatology, Hospital Universitario de Basurto. Bilbao. Spain, Bilbao, Spain, 18Hospital Universitario Donostia. San Sebastian. Spain, San Sebastián, Spain, 19Ophtamology, Hospital Universitario Donostia. San Sebastian. Spain, San Sebastian, Spain, 20Rheumatology, Hospital de Móstoles. Madrid. Spain, Madrid, Spain, 21Medicine Department, Hospital Universitario San Cecilio. Granada. Spain, Granada, Spain, 22Rheumatology, Hospital Universitario San Cecilio. Granada. Spain, Granada, Spain, 23Rheumatology, Hospital Puerta del Mar. Cádiz. Spain, Cádiz, Spain, 24Rheumatology Department, Hospital General Universitario Gregorio Marañón, Madrid, Spain, 25Hospital Severo Ochoa, Madrid, Spain, Madrid, Spain, 26Rheumatology Division, Hospital General Universitario de Elda, Elda, Spain, 27Rheumatology, Hospital Clínico San Carlos, Madrid, Spain, 28Ophthalmology and Rheumatology, Hospital Miguel Servet. Zaragoza. Spain, Zaragoza, Spain, 29Hospital Miguel Servet. Zaragoza. Spain, Zaragoza, Spain, 30Rheumatology, Hospital Universitario Fundación Alcorcón. Madrid. Spain, Madrid, Spain, 31Hospital de Mérida. Spain, Mérida, Spain, 32Rheumatology, Hospital Virgen de la Arrixaca. Murcia. Spain, Murcia, Spain, 33Section for Autoimmune Diseases, Rheumatology, Fundación Jiménez Díaz University Hospital & Health Research Institute, Madrid, Spain, 34Rheumatology, Hospital Universitario Santiago de Compostela. La Coruña. Spain, La Coruña, Spain, 35Rheumatology, Hospital de Cabueñes. Gijón. Spain, Gijón, Spain, 36Ophthalmology, Hospital General Universitario de Valencia. Spain, Valencia, Spain, 37Rheumatology, Hospital del Mar. Barcelona. Spain, Barcelona, Spain, 38Hospital de Pontevedra. Pontevedra. Spain, Pontevedra, Spain, 39Ophthalmology, Hospital de Pontevedra. Pontevedra. Spain, Pontevedra, Spain, 40Rheumatology, Hospital de Sierrallana, Torrelavega. Cantabria. Spain, Torrelavega, Spain

    Background/Purpose: Retinal vasculitis is a serious complication of uveitis due to Behçet’s disease (BD). The treatment is based on corticosteroids, conventional immunosuppressants (IS) and anti-TNF-α…
  • Abstract Number: 2270 • 2018 ACR/ARHP Annual Meeting

    Treatment of Refractory Cystoid Macular Edema to Conventional Immunosuppressive Therapy: Tocilizumab Vs Anti-TNF-Alpha. Multicenter Study of 59 Patients

    José Luis Martín-Varillas1, Belén Atienza-Mateo1, Vanesa Calvo-Río2, Monica Calderón Goercke2, Diana Prieto Peña2, Rosalía Demetrio-Pablo3, Javier Loricera3, Eva Peña Sainz-Pardo3, M. Victoria Hernández4, Alfredo Adan5, Marina Mesquida5, Santos Insua6, Jose M Herreras7, Olga Maíz8, Ana Blanco9, Myriam Gandía10, David Diaz-Valle11, Lucía Martínez-Costa12, Elia Valls-Pascual12, Gisela Díaz-Cordovés13, Manuel Díaz-Llopis14, Inmaculada Calvo15, Ignacio Torre-Salaberri16, Antonio Atanes17, Luis Francisco Linares18, Marisa Hernández19, Emma Beltrán20, Miguel Cordero-Coma21, Elena Aurrecoechea22, Félix Francisco23, Raquel Almodóvar González24, Oscar Ruiz Moreno25, Fernando Jiménez-Zorzo26, Joan Miquel Nolla27, Consuelo Modesto28, Enar Pons1, Miguel Angel González-Gay3 and Ricardo Blanco1, 1Rheumatology, Hospital Universitario Marqués de Valdecilla. IDIVAL. Santander. Universidad de Cantabria. Spain, Santander, Spain, 2Rheumatology, Rheumatology. Hospital Universitario Marqués de Valdecilla. IDIVAL. Santander. Universidad de Cantabria. Spain, Santander, Spain, 3Hospital Universitario Marqués de Valdecilla. IDIVAL. Santander. Universidad de Cantabria. Spain, Santander, Spain, 4Rheumatology, Hospital Clinic. Barcelona. Spain, Barcelona, Spain, 5Hospital Clinic. Barcelona. Spain, Barcelona, Spain, 6Rheumatology, Hospital Universitario Santiago de Compostela. La Coruña. Spain, La Coruña, Spain, 7Ophthalmology, Hospital Universitario, IOBA. Valladolid. Spain, Valladolid, Spain, 8Hospital Universitario Donostia. San Sebastian. Spain, San Sebastián, Spain, 9Ophtamology, Hospital Universitario Donostia. San Sebastian. Spain, San Sebastian, Spain, 10Rheumatology, Hospital Puerta del Mar. Cádiz. Spain, Cádiz, Spain, 11Hospital Clínico San Carlos. Madrid. Spain, Madrid, Spain, 12Hospital Universitario Doctor Peset. Valencia. Spain, Valencia, Spain, 13Rheumatology, Hospital Regional Universitario de Málaga. Spain, Málaga, Spain, 14Hospital Universitario La Fe. Valencia. Spain, Valencia, Spain, 15Hospital Universitario La Fe, Valencia, Spain, 16Rheumatology, Hospital Universitario de Basurto. Bilbao. Spain, Bilbao, Spain, 17Complejo Hospitalario Universitario A Coruña. Spain, A Coruna, Spain, 18Rheumatology, Hospital Virgen de la Arrixaca. Murcia. Spain, Murcia, Spain, 19Ophthalmology, Hospital General Universitario de Valencia. Spain, Valencia, Spain, 20Rheumatology, Hospital del Mar. Barcelona. Spain, Barcelona, Spain, 21Ophthalmology, Hospital de León. Spain, León, Spain, 22Rheumatology, Hospital de Sierrallana, Torrelavega. Cantabria. Spain, Torrelavega, Spain, 23Rheumatology, Hospital Doctor Negrín. Las Palmas de Gran Canaria. Spain, Las Palmas de Gran Canaria, Spain, 24Rheumatology, Hospital Universitario Fundación Alcorcón. Madrid. Spain, Madrid, Spain, 25Ophthalmology and Rheumatology, Hospital Miguel Servet. Zaragoza. Spain, Zaragoza, Spain, 26Hospital Miguel Servet. Zaragoza. Spain, Zaragoza, Spain, 27Rheumatology, Hospital Universitario de Bellvitge, Barcelona, Spain, 28Hospital Universitari Vall d'Hebron. Barcelona. Spain, Barcenola, Spain

    Background/Purpose: Cystoid macular edema (CME) is the main cause of irreversible visual loss in patients with uveitis. Our aim objective was to determine the efficacy…
  • Abstract Number: 2271 • 2018 ACR/ARHP Annual Meeting

    Long-Term Efficacy and Safety of Adalimumab By Immunosuppressant Use in Patients with Non-Infectious Uveitis

    Yan Guex-Crosier1, C. Stephen Foster2, Kei Nakai3, Hiroshi Goto4, Kevin Douglas5, Sophia Pathai6, Martina Kron7, Alexandra P. Song5, Joachim Van Calster8 and Alfredo Adan9, 1Jules Gonin Eye Hospital, University of Lausanne, Lausanne, Switzerland, 2Massachusetts Eye Research and Surgery Institution (MERSI), Ocular Immunology & Uveitis Foundation (OIUF), Waltham, MA, USA and Harvard Medical School, Boston, MA, 3Yodogawa Christian Hospital, Osaka, Japan, 4Tokyo Medical University, Tokyo, Japan, 5AbbVie Inc., North Chicago, IL, 6AbbVie Ltd, Maidenhead, United Kingdom, 7AbbVie Deutschland GmbH & Co. KG, Ludwigshafen, Germany, 8University Hospitals Leuven, Leuven, Belgium, 9Hospital Clinic. Barcelona. Spain, Barcelona, Spain

    Background/Purpose: To evaluate the long-term safety and efficacy of adalimumab in patients with non-infectious intermediate, posterior, or panuveitis, by immunosuppressant (IMM) use. Methods: Adult patients…
  • Abstract Number: 2272 • 2018 ACR/ARHP Annual Meeting

    Missed Opportunity? Evaluation for Systemic Autoimmune Diseases in Patients with Uveitis May Not be Optimal: 5-Year Analysis of Patients Being Seen in a Tertiary Medical Center

    Nancy Harrison1, Swetha Boddeda2, Shweta Kishore2 and Vikas Majithia3, 1Rheumatolody, University of Mississippi Medical Center, Jackson, MS, 2Rheumatology, University of Mississippi Medical Center, Jackson, MS, 3Division of Rheumatology, University of Mississippi Medical Center, Jackson, MS

    Background/Purpose: Uveitis is the most common inflammatory eye disease and is frequently associated with secondary systemic autoimmune diseases (SSAID) excluding infection in 40-55% of cases.…
  • Abstract Number: 2273 • 2018 ACR/ARHP Annual Meeting

    High Dose Intravenous Methylorednisolone Induces Rapid Improvement in Severe Non-Infectious Uveitis. a Multicenter Study of 120 Patients

    Nuria Vegas-Revenga1, Vanesa Calvo-Río1, Íñigo González-Mazón2, Lara Sánchez-Bilbao2, Emma Beltrán3, Alejandro Fonollosa4, Olga Maiz-Alonso5, Ana Blanco6, Miguel Cordero-Coma7, Norberto Ortego Centeno8, Ignacio Torre-Salaberri9, Félix Francisco10, Santiago Muñoz-Fernández11, Maria del Mar Esteban Ortega12, Manuel Díaz-Llopis13, Mario Agudo2, Joaquin Cañal1, Juan Antonio Ventosa1, Rosalía Demetrio-Pablo1, Lucia C. Domínguez-Casas1, Miguel Angel González-Gay14 and Ricardo Blanco2, 1Hospital Universitario Marqués de Valdecilla. IDIVAL. Santander. Universidad de Cantabria. Spain, Santander, Spain, 2Rheumatology, Hospital Universitario Marqués de Valdecilla. IDIVAL. Santander. Universidad de Cantabria. Spain, Santander, Spain, 3Rheumatology, Hospital General Universitario de Valencia. Spain, Valencia, Spain, 4Ophthalmology, Hospital de Cruces. Bilbao. Spain, Bilbao, Spain, 5Hospital Universitario Donostia. San Sebastian. Spain, Donostia, Spain, 6Ophtamology, Hospital Universitario Donostia. San Sebastian. Spain, San Sebastian, Spain, 7Ophthalmology, Hospital de León. Spain, León, Spain, 8Medicine Department, Hospital Universitario San Cecilio. Granada. Spain, Granada, Spain, 9Rheumatology, Hospital Universitario de Basurto. Bilbao. Spain, Bilbao, Spain, 10Rheumatology, Hospital Doctor Negrín. Las Palmas de Gran Canaria. Spain, Las Palmas de Gran Canaria, Spain, 11Hospital Universitario Infanta Sofia. Madrid. Spain, Mardid, Spain, 12Hospital Universitario Infanta Sofia. Madrid. Spain, Madrid, Spain, 13Hospital Universitario La Fe. Valencia. Spain, Valencia, Spain, 14Rheumatology. Hospital Universitario Marqués de Valdecilla. IDIVAL. Santander. Universidad de Cantabria. Spain, Santander, Spain

    Background/Purpose: In uveitis rapid and effective remission-inducing therapy is mandatory to avoid irreversible structural and functional damage.Our aim was to evaluate the efficacy and safety…
  • Abstract Number: 2274 • 2018 ACR/ARHP Annual Meeting

    Refractory and Severe Uveitic Cystoid Macular Edema Improves with Tocilizumab in Different Immune Mediated Diseases

    Nuria Vegas-Revenga1, Vanesa Calvo-Río1, Marina Mesquida2, Alfredo Adan2, M. Victoria Hernández2, Emma Beltrán3, Elia Valls Pascual4, David Diaz-Valle5, Gisela Díaz-Cordovés6, Marisa Hernandez Grafella7, Lucía Martínez-Costa8, Inmaculada Calvo9, Antonio Atanes10, Luis Francisco Linares11, Consuelo Modesto12, Elena Aurrecoechea13, Miguel Cordero-Coma14, Rosalía Demetrio-Pablo1, Lucia C. Domínguez-Casas15, José Luis Hernández1, Miguel Angel González-Gay1 and Ricardo Blanco15, 1Hospital Universitario Marqués de Valdecilla. IDIVAL. Santander. Universidad de Cantabria. Spain, Santander, Spain, 2Hospital Clinic. Barcelona. Spain, Barcelona, Spain, 3Rheumatology, Hospital del Mar. Barcelona. Spain, Barcelona, Spain, 4Hospital Universitario de Valencia. Spain, Valencia, Spain, 5Hospital Clínico San Carlos. Madrid. Spain, Madrid, Spain, 6Rheumatology, Hospital Regional Universitario de Málaga. Spain, Málaga, Spain, 7Hospital Doctor Peset. Valencia. Spain, Valencia, Spain, 8Hospital Doctor Peset. Valencia. Spain, Valencia., Spain, 9Hospital Universitario La Fe, Valencia, Spain, 10Complejo Hospitalario Universitario A Coruña. Spain, A Coruna, Spain, 11Rheumatology, Hospital Virgen de la Arrixaca. Murcia. Spain, Murcia, Spain, 12Hospital Universitari Vall d'Hebron. Barcelona. Spain, Barcenola, Spain, 13Rheumatology, Hospital de Sierrallana. Torrelavega. Spain, Torrelavega, Spain, 14Ophthalmology, Hospital de León. Spain, León, Spain, 15Rheumatology, Hospital Universitario Marqués de Valdecilla. IDIVAL. Santander. Universidad de Cantabria. Spain, Santander, Spain

     Background/Purpose: Cystoid macular edema (CME) represents the leading cause of blindness in uveitis of different immune mediated diseases (IMD). Our aim was to evaluate the…
  • Abstract Number: 2275 • 2018 ACR/ARHP Annual Meeting

    Autoimmune Encephalitis with Concomitant Systemic Rheumatologic Auto-Antibodies

    Nicole Droz1, Alexander Rae-Grant2 and Rula A Hajj-Ali3, 1Rheumatology, Cleveland Clinic Foundation, Cleveland, OH, 2Neurology, Cleveland Clinic Foundation, Cleveland, OH, 3Rheumatic and Immunologic Disease, Cleveland Clinic Foundation, Cleveland, OH

    Background/Purpose: Autoimmune encephalitis (AE) is a rapidly progressive encephalopathy presenting with neurologic and psychiatric manifestations and is often associated with antibodies targeting neuronal cell-surface or…
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