ACR Meeting Abstracts

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Abstracts tagged "Vasculitis"

  • Abstract Number: 1534 • ACR Convergence 2023

    ANCA-associated Vasculitis Incidence in a Norther Spanish Health Region

    Salma Al Fazazi1, Fabricio Benavides2, Alba Herrero-Morant3, Vanesa Calvo Río4, monica renuncio garcia2, clara escagedo Cagigas2, maria rodriguez Vidriales2 and Ricardo Blanco5, 1Hospital Universitario Puerta Del Mar, Cádiz, Spain, 2Hospital Universitario Marqués de Valdecilla, Santander, Spain, 3Hospital Universitario Marqués de Valdecilla, Ontinyent, Spain, 4Valdecilla Hospital, Santander, Spain, 5Hospital Universitario Marqués de Valdecilla, IDIVAL, Santander, Spain

    Background/Purpose: Anti-neutrophil cytoplasmic antibodies (ANCA)-associated vasculitis (AAV) includes granulomatosis with polyangiitis (GPA), eosinophilic granulomatosis with polyangiitis (EGPA) or microscopic polyarteritis (MPA). Precise estimation of the…
  • Abstract Number: 1572 • ACR Convergence 2023

    Long-term Efficacy and Retention Rate of Molecular Targeted Drugs in Takayasu Arteritis

    Tsuyoshi Shirai1, Hiroko Sato1, Tomonori Ishii2 and Hiroshi Fujii1, 1Tohoku University, Sendai, Japan, 2Clinical Research, Innovation and Education Center, Tohoku University Hospital, Sendai, Japan

    Background/Purpose: Takayasu arteritis (TAK) is a type of large-vessel vasculitis that predominantly affects young females. The relapse is frequent, accounting for 60% of cases, and…
  • Abstract Number: 2378 • ACR Convergence 2023

    Longitudinal Trajectories of Renal Function in ANCA-Associated Vasculitis: Findings from the Expanded Mass General Brigham Cohort

    Jennifer Hanberg1, Claire Cook1, Xiaoqing Fu1, Hyon K. Choi2, Yuqing Zhang3 and Zachary Wallace4, 1Massachusetts General Hospital, Boston, MA, 2Massachusetts General Hospital and Harvard Medical School, Lexington, MA, 3Division of Rheumatology, Allergy, and Immunology, Department of Medicine, Massachusetts General Hospital, Boston, MA, 4Massachusetts General Hospital, Newton, MA

    Background/Purpose: ANCA-associated vasculitis (AAV) commonly causes renal damage, leading to a spectrum of chronic kidney disease (CKD) and end-stage renal disease (ESRD). Quantitative descriptions of…
  • Abstract Number: 2412 • ACR Convergence 2023

    Evaluation of the Pretest Probability Score, Ultrasound and Biopsy on GCA Diagnose: Data from Real Clinical Practice

    María del Carmen San José Méndez1, Uxía Couto Lareo1, Vanesa Balboa Barreiro2, Francisco J. Blanco1, Bruno de aspe de la iglesia1, Antonio Atanes Sandoval3, Diego Dios Santos1, Jesús Carlos Fernández López1, Mercedes Freire González1, Guillermo González Arribas1, Genaro Graña Gil1, Natividad Oreiro Villar1, Jose Antonio Pinto Tasende1, Francisco Javier De Toro Santos1, Clara Ventin Rodriguez1, Maite silva díaz3 and Ana Lois Iglesias1, 1Rheumatology department, Complexo Hospitalario Universitario A Coruña (CHUAC). Instituto de Investigación Biomédica A Coruña (INIBIC), A Coruña, Spain, 2Clinic epidemiology and biostatistics department. Complejo Hospitalario Universitario A Coruña (CHUAC). Instituto de Investigación Biomédica A Coruña (INIBIC), A Coruña, Spain, 3Rheumatology department, Complexo Hospitalario Universitario A Coruña (CHUAC). Instituto de Investigación Biomédica A Coruña (INIBIC)., A Coruña, Spain

    Background/Purpose: Giant cell arteritis (GCA) affects large and medium size arteries. Biopsy was considered the gold standard in the diagnosis1, but in the last years…
  • Abstract Number: 2561 • ACR Convergence 2023

    The Prognostic Value of the “2022 ACR/EULAR Classification Criteria for Giant Cell Arteritis”: Data from the Italian Society of Rheumatology Vasculitis Study Group

    Alessandro Tomelleri1, Corrado Campochiaro2, Francesco Muratore3, Sara Monti4, Nicola Farina5, Chiara Marvisi6, Elena Galli7, Alessandra Milanesi8, Naomi Viapiana5, Alvise Berti9, Roberto Bortolotti9, Milena Bond10, Roberto Padoan11, Mara Felicetti9, Franco Schiavon12, Carlotta Nannini13, Fabrizio Cantini13, Alessandro Giollo14, Maurizio Rossini15, Edoardo Conticini16, Bruno Frediani17, Fabrizio Conti18, Roberta Priori18, Marco Sebastiani19, Giulia Cassone20, Luca Quartuccio Quartuccio21, Elena Treppo22, Silvano Bettio23, Ariela Hoxha24, Marco Lovisotto24, Giacomo Emmi25, irene mattioli26, Pietro Leccese27, Roberto F. Caporali28, Lorenza Maria Argolini29, Rosario Foti30, Elisa Visalli30, Michele Colaci31, Carlomaurizio Montecucco32, Lorenzo Dagna33 and Carlo Salvarani34, 1Unit of Immunology, Rheumatology, Allergy and Rare Diseases, San Raffaele Scientific Institute, Milano, Italy, 2IRCCS San Raffaele Hospital, Unit of Immunology, Rheumatology, Allergy and Rare Disease. Vita-Salute San Raffaele University, Milan, Italy, 3IRCCS di Reggio Emilia, Reggio Emilia, Italy, 4Division of Rheumatology, Fondazione IRCCS Policlinico San Matteo, Pavia, Italy; Department of Internal Medicine and Therapeutics, Università di Pavia, Pavia, Italy, 5IRCCS San Raffaele Hospital, Milan, Italy, 6IRCCS di Reggio Emilia, Reggio Emilia, Italy, Reggio Emilia, Italy, 7Azienda Unità Sanitaria Locale-IRCCS Di Reggio Emilia, Reggio Emilia, Italy, 8Fondazione IRCCS Policlinico San Matteo, Pavia, Italy, 9Santa Chiara Hospital of Trento, Trento, Italy, 10Azienda sanitaria dell'Alto Adige, Merano, Italy, 11Department of Medicine DIMED, University of Padova, Padova, Italy, 12University of Padova, Padova, Italy, 13Santo Stefano Hospital Prato, Prato, Italy, 14Rheumatology Unit, Department of Clinical and Experimental Medicine, University of Padova, Padua, Italy, 15Rheumatology Unit, Department of Medicine, University of Verona, Verona, Italy, 16Tallaght University Hospital, Dublin, Ireland, 17University of Siena, Siena, Italy, 18University of Rome La Sapienza, Rome, Italy, 19Azienda Policlinico di Modena, Modena, Italy, 20University of Modena and Reggio Emilia, Modena, Italy, 21Rheumatology Division, Department of Medicine, University of Udine, Udine, Italy, 22Physician, Moimacco, Italy, 23University of Padua, Treviso, Italy, 24San Bortolo Hospital of Vicenza, Vicenza, Italy, 25University of Florence, Florence, Italy, 26University of Florence, Firenze, Italy, 27Regional Hospital San Carlo, Potenza, Italy, 28Department of Clinical Sciences and Community Health, University of Milan, and Department of Rheumatology and Medical Sciences, ASST Gaetano Pini-CTO, Milano, Italy, 29ASST Gaetano Pini, Milano, Italy, 30AOU San Marco, Catania, Catania, Italy, Catania, Italy, 31University of Catania, Catania, Italy, 32Unità Operativa e Cattedra di Reumatologia, IRCCS Policlinico S Matteo, Pavia, Italy, 33Ospedale San Raffaele, Milano, Italy, 34Azienda USL-IRCCS di Reggio Emilia, Reggio Emilia, Italy

    Background/Purpose: The 2022 classification criteria for giant cell arteritis (GCA) have been recently published. The aim of this study is to investigate whether the score…
  • Abstract Number: 0044 • ACR Convergence 2023

    Aberrant Mevalonate Metabolite Farnesyl Pyrophosphate-Induced Neutrophil Hyperactivation in Behçet’s Disease Pathogenesis

    Menghao Zhang1, Na Kang2, Xin Yu1, Wanli Liu2 and Wenjie Zheng1, 1Department of Rheumatology and Clinical Immunology, Peking Union Medical College Hospital, Beijing, China, 2Beijing Key Lab for Immunological Research on Chronic Diseases, School of Life Sciences, Institute for Immunology, Tsinghua University, Beijing, China

    Background/Purpose: Behçet’s disease (BD) is a chronic vasculitis characterized by polymorphonuclear neutrophils (PMNs) hyperactivation with unknown etiology. The over-productions of neutrophil extracellular traps (NETs) and…
  • Abstract Number: 0697 • ACR Convergence 2023

    Alterations in Composition and Function of Gut Microbiota in Patients with Large-Vessel Vasculitis

    Adam Mayer1, Weiming Hu2, Kyle Bittinger2, Rui Liang3, Naomi Amudala3, Shubhasree Banerjee3, Peter Merkel3 and Rennie Rhee3, 1University of Pennsylvania/Children's Hospital of Philadelphia, Philadelphia, PA, 2Children's Hospital of Philadelphia, Philadelphia, PA, 3University of Pennsylvania, Philadelphia, PA

    Background/Purpose: The gut microbiome has a critical role in immune homeostasis and there is growing interest in understanding the relationship between the microbiome and autoimmunity.…
  • Abstract Number: 0747 • ACR Convergence 2023

    Clinical Phenotype of Patients with Subclinical Giant Cell Arteritis in Polymyalgia Rheumatica

    Sharon Cowley1, Colm Kirby2, Patricia Harkins3, Richard Conway4 and David Kane5, 1Tallaght University Hospital, Dublin, Dublin, Ireland, 2Tallaght University Hospital, Dublin, Ireland, 3St James's Hospital, Dublin, Ireland, 4Trinity College Dublin, Dublin, Ireland, 5Tallaght University Hospital & Trinity College Dublin, Dublin, Ireland

    Background/Purpose: It has been reported that more than a quarter of patients with polymyalgia rheumatica (PMR) have subclinical giant cell arteritis (GCA). It remains unclear…
  • Abstract Number: 1538 • ACR Convergence 2023

    Large Vessel Involvement in Antineutrophil Cytoplasmic Antibody- Associated Vasculitis: A Single Center Experience over Two Decades

    Mahmut Kaymakci1, Mohanad Elfishawi1, Hannah Langenfeld2, Andrew Hanson2, Cynthia Crowson1, Melanie Bois1, Umar Ghaffar1, Ulrich Specks1, Matthew Koster1 and Kenneth Warrington1, 1Mayo Clinic, Rochester, MN, 2Department of Quantitative Health Sciences, Mayo Clinic, Rochester, MN

    Background/Purpose: Anti-neutrophil cytoplasmic antibody (ANCA) associated vasculitis (AAV) is currently categorized under the small vessel vasculitides and includes granulomatosis with polyangiitis (GPA), microscopic polyangiitis (MPA),…
  • Abstract Number: 1573 • ACR Convergence 2023

    Inpatient Prevalence and Comorbidity of Takayasu’s Arteritis: Nationwide Inpatient Sample 2016-2020

    Husam el Sharu1, Sukhvir Singh1, Omar Alwahadneh2, Mohammad Alqaisieh3 and Laksmi Subramanian1, 1East Carolina University, Greenville, NC, 2Carle Foundation Hospital, Urbana, IL, 3Hamilton Medical Center, Dalton, GA

    Background/Purpose: Takayasu’s Arteritis (TAK) is a granulomatous large-vessel vasculitis that affects the aorta and its branches, and it is more commonly observed in women. We…
  • Abstract Number: 2381 • ACR Convergence 2023

    ANCA-associated Vasculitis and Renal Disease in a Multidisciplinary Outpatient Clinic in Northern Spain

    Salma Al Fazazi1, Fabricio Benavides2, Vanesa Calvo Río3, maria rodriguez Vidriales2, clara escagedo Cagigas2, monica renuncio garcia2, luis martin penagos4 and Ricardo Blanco5, 1Hospital Universitario Puerta Del Mar, Cádiz, Spain, 2Hospital Universitario Marqués de Valdecilla, Santander, Spain, 3Valdecilla Hospital, Santander, Spain, 4Division of Nephrology, Immunopathology Group, Hospital Universitario Marqués de Valdecilla-DIVAL, Santander, Spain, 5Hospital Universitario Marqués de Valdecilla, IDIVAL, Santander, Spain

    Background/Purpose: The severity of clinical features and outcomes in previous series of patients reported with renal disease related to ANCA-associated vasculitis (AAV) vary greatly, probably…
  • Abstract Number: 2415 • ACR Convergence 2023

    Giant Cell Arteritis Is Associated with Worse Hospital Outcomes in Aortic Aneurysm/Dissection Hospitalizations: A Nationwide United States Population-Based Study

    Artem Minalyan1, Christopher Hino1, Emily He1, Osahon Idolor2, Chinenye Osuorji3, Nneka Chukwu4, Ehizogie Edigin1 and Vaneet Sandhu5, 1Loma Linda University Health, Loma Linda, CA, 2Piedmont Athens Regional Hospital, Atlanta, GA, 3Montefiore Medical Center/Albert Einstein College of Medicine, Bronx, NY, 4Nuvance Health Internal Medicine Residency, Poughkeepsie, NY, 5Loma Linda University, Loma Linda, CA

    Background/Purpose: Giant Cell Arteritis (GCA) is a known risk factor for Aortic Aneurysm/Dissection (AAD). However, it is unclear if patients with GCA have worse hospital…
  • Abstract Number: 2562 • ACR Convergence 2023

    Immune Checkpoint Inhibitors-Induced Large Vessel Vasculitis: Data from a Multicenter Study

    Adrien Cottu1, Alessandro Tomelleri2, Corrado Campochiaro3, Alexandra Forestier4, Jérémie Dion5, Milena Bond6, Ariane Laparra-ramakichenin7, Aline Gury8, Xavier Savary9, Robin Dhote10, Albrecht Betrains11, Laurence Bouillet12, Eric Liozon13, Eva Bories14, Arthur Petitdemange1, Paul Legendre15, Benjamin Crichi16, Philippe Kerschen17, Lucie Carneiro-Esteves18, Lucile Grange18 and Benjamin Terrier19, 1Department of Internal Medicine, Hôpital Cochin, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France, 2Unit of Immunology, Rheumatology, Allergy and Rare Diseases, San Raffaele Scientific Institute, Milano, Italy, 3IRCCS San Raffaele Hospital, Unit of Immunology, Rheumatology, Allergy and Rare Disease. Vita-Salute San Raffaele University, Milan, Italy, 4Department of Medical Oncology, Centre Oscar Lambret, Lille, France, 5Internal Medicine Department, Toulouse University Hospital, Toulouse, France, 6Azienda sanitaria dell'Alto Adige, Merano, Italy, 7Department of Therapeutic Innovations and Early Trials, Gustave Roussy, Université Paris-Saclay, Villejuif, France, 8Department of Internal Medicine, Arras GHAT, Arras, France, 9Department of Internal Medicine, Brest CHU Hospital, Brest, France, 10Department of Internal Medicine, Centre Hospitalier Avicenne, Bobigny, France, 11Department of General Internal Medicine, University Hospitals Leuven, Department of Microbiology, Immunology, and Transplantation, KU Leuven, Leuven, Belgium, 12Internal medicine department, Grenoble University Hospital, Grenoble, France, 13Department of Internal Medicine, University Hospital of Limoges, Limoges Cedex, Limoges, France, 14Department of Internal Medicine, Purpan CHU Hospital, Toulouse, France, 15Department of Clinical Immunology, Centre hospitalier du Mans, Le Mans, France, 16Department of Internal Medicine, Saint Louis Hospital, Assistance Publique-Hôpitaux de Paris (AP-HP), Paris, France, 17Department of Neurology, Luxembourg Hospital Center, Luxembourg City, Luxembourg, 18Department of Internal Medicine, Centre Hospitalier Universitaire de Saint-Etienne, Saint-Etienne, France, 19Department of Internal Medicine, Hôpital Cochin, AP-HP, Paris, France

    Background/Purpose: Immune checkpoint inhibitors (ICIs) have dramatically improved the prognosis for many cancers. The therapeutic effect of ICIs is based on their ability to release…
  • Abstract Number: 0139 • ACR Convergence 2023

    Systemic Vasculitides in Portugal and Brazil: Preliminary Results from the Reuma.pt/vasculitis Registry

    Mariana de Aguiar1, Alexandre wagner Silva de Souza2, Joana Martinho3, Adriana Carones4, Ana Beatriz Bacchiega de Freitas5, Ana Catarina Duarte6, Ana Filipa Águeda7, Camila Souto Oliveira Elias8, Catarina Cortesão9, Catarina Soares10, Carla Macieira11, Carlos Eduardo Garcez Teixeira12, Daniela Peixoto13, Duarte Vinha3, Estela Nogueira3, Fabricia Simil14, Francisca Guimarães13, Frederico Rajão Martins15, Gilda Ferreira16, Helena Assunção4, Heloisa Rulff8, Jorge Pestana Lopes6, José Costa3, Julia Medeiros17, Lilian Santos Porto18, Luiz Felipe Adsuara17, Manuella Ochtrop8, Maria João Gonçalves19, Mariana Diz Lopes20, Matheus Vieira21, Nikita Khmelinskii11, Rita Torres22, Sarah Neaime1, Vitor Teixeira23, Zoraida Sachetto12 and Cristina Ponte24, 1Universidade Federal de São Paulo (UNIFESP), São Paulo, Brazil, 2Division of Rheumatology, Medical School, Universidade Federal de São Paulo, São Paulo, Brazil, 3Centro Hospitalar Universitario Lisboa Norte, Lisboa, Portugal, 4Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal, 5Faculdade de Ciências da Saúde de Barretos, Barretos, Brazil, 6Hospital Garcia de Orta, Almada, Portugal, 7Centro Hospitalar Universitário Cova da Beira, Covilhã, Portugal, 8Universidade Estadual do Rio de Janeiro, Rio de Janeiro, Brazil, 9Instituto Português de Reumatologia, Lisboa, Portugal, 10Centro Unidade Local de Saúde do Alto Minho, Viana do Castelo, Portugal, 11Centro Hospitalar Universitário Lisboa Norte, Lisboa, Portugal, 12Universidade Estadual de Campinas, Campinas, Brazil, 13Centro Unidade Local de Saúde do Alto Minho, Ponte de Lima, Portugal, 14Universidade Federal de Minas Gerais, Belo Horizonte, Brazil, 15Department of Rheumatology, University Hospital Centre of Algarve, Faro, Portugal, 16Federal University of Minas Gerais, Belo Horizonte, Brazil, 17Santa Casa de Misericórdia de São Paulo, São Paulo, Brazil, 18Santa Casa de Misericórdia de Belo Horizonte, Belo Horizonte, Brazil, 19Centro Hospitalar de Lisboa Ocidental, Lisboa, Portugal, 20Centro Hospitalar Universitário de São João, Porto, Portugal, 21Universidade Federal de São Paulo; Universidade Federal do Rio de Janeiro, Rio de Janeiro, Brazil, 22Hospital Egas Moniz, Lisboa, Portugal, 23Hospital de Faro, CHUA, Lisbon, Portugal, 24Department of Rheumatology, Centro Hospitalar Universitário Lisboa Norte, Centro Académico de Medicina de Lisboa, Lisbon, Portugal; Rheumatology Research Unit, Instituto de Medicina Molecular, Faculdade de Medicina, Universidade de Lisboa, Centro Académico de Medicina de Lisboa, Lisbon, Portugal

    Background/Purpose: The epidemiology of vasculitis varies widely across different geographic areas of the world which may be due to different ethnic and environmental factors. Brazil…
  • Abstract Number: 0698 • ACR Convergence 2023

    Differentiating Large Vessel Vasculitis from Vasculitis Mimickers in a Real World Setting: Clinical Presentation, Laboratory Tests and Radiographic Findings

    James haigney1, Laura Fandino1 and Vasileios Kyttaris2, 1Beth Israel Deaconess Medical Center, Boston, MA, 2BIDMC, Boston, MA

    Background/Purpose: As the resolution of Computed Tomography Angiography (CTA) has improved, rheumatologists have faced an increased volume of consults to evaluate patients for the presence…
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All abstracts accepted to ACR Convergence are under media embargo once the ACR has notified presenters of their abstract’s acceptance. They may be presented at other meetings or published as manuscripts after this time but should not be discussed in non-scholarly venues or outlets. The following embargo policies are strictly enforced by the ACR.

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