ACR Meeting Abstracts

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Abstracts tagged "Systemic JIA and macrophage activation syndrome"

  • Abstract Number: 919 • 2019 ACR/ARP Annual Meeting

    Free Interlukin-18: A New Promising Biomarker for Systemic Juvenile Idiopathic Arthritis and Macrophage Activation Syndrome

    Shima Yasin1, Emiliana Rodriguez 2, Thuy Do 3, Elizabeth Baker 1, Sanjeev Dhakal 3, Scott Canna 4, Cem Gabay 5, Alexei A. Grom 3 and Grant Schulert 3, 1Division of Rheumatology, Cincinnati Children's Hospital Medical Center, Cincinnati, 2Rheumatology, Geneva University Hospitals and University of Geneva, Switzerland, Geneva, Swaziland, 3Division of Rheumatology, Cincinnati Children's Hospital Medical Center, Cincinnati, OH, 4UPMC Children's Hospital of Pittsburgh, Pittsburgh, 5Rheumatology, Geneva University Hospitals and University of Geneva, Switzerland, Geneva, Switzerland

    Background/Purpose: Systemic juvenile idiopathic arthritis (sJIA) is a childhood arthritis with features of autoinflammation, and is associated with high risk of macrophage activation syndrome (MAS).…
  • Abstract Number: 925 • 2018 ACR/ARHP Annual Meeting

    Abortive Viral Infection Becomes Macrophage Activation Syndrome in Mice with Chronically Elevated Interleukin-18: Evidence for Synergy with Cytotoxic Impairment

    Paul Tsoukas1, Corinne Schneider2, Lauren Van Der Kraak2 and Scott Canna3, 1Pediatric Rheumatology, Children’s Hospital of Pittsburgh, Pittsburgh, PA, 2RK Mellon Institute for Pediatric Research, University of Pittsburgh/Children's Hospital of Pittsburgh of UPMC, Pittsburgh, PA, 3RK Mellon Institute for Pediatric Research, University of Pittsburgh/Children's Hospital of Pittsburgh of UPMC, Pittsburrgh, PA

    Background/Purpose: Macrophage Activation Syndrome (MAS) and Hemophagocytic lymphohistiocytosis (HLH) are clinically similar life-threatening hyperinflammatory syndromes, often triggered by viral infection. HLH is associated with cytotoxic…
  • Abstract Number: 2919 • 2018 ACR/ARHP Annual Meeting

    An Epidemic: Severe Lung Disease in Patients with Systemic Juvenile Idiopathic Arthritis, Risk Factors and Predictors

    Shima Yasin1, Christopher Towe2,3, Ndate Fall4, Alexei Grom3,4 and Grant Schulert1,5, 1Rheumatology, Divisions of Rheumatology, Cincinnati Children’s Hospital Medical Center, Cincinnati, OH, 2Pulmonology, Division of Pulmonology, Cincinnati Children’s Hospital Medical Center, Cincinnati, OH, 3Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, OH, 4Division of Rheumatology, Divisions of Rheumatology, Cincinnati Children’s Hospital Medical Center, Cincinnati, OH, 5Pediatrics, Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, OH

    Background/Purpose: There is growing awareness of severe and often fatal chronic lung disease in patients with systemic juvenile idiopathic arthritis (sJIA). However, clinical features and…
  • Abstract Number: 1897 • 2017 ACR/ARHP Annual Meeting

    the Ferritin to ESR Ratio: A Simple Measure to Distinguish Macrophage Activation Syndrome from Systemic Arthritis Flare

    Esraa M. A. Eloseily1,2, Francesca Minoia3, Timothy Beukelman2, Angelo Ravelli4 and Randy Q. Cron2, 1Pediatrics, Assiut University, Assiut, Egypt, 2Pediatric Rheumatology, University of Alabama at Birmingham, Birmingham, AL, 3Istituto Giannina Gaslini, Genoa, Italy, 4University of Genova, Genova, Italy

    Background/Purpose: Macrophage activation syndrome (MAS) is a life threatening complication of systemic juvenile idiopathic arthritis (sJIA). As MAS often shares clinical and laboratory features with…
  • Abstract Number: 75 • 2017 Pediatric Rheumatology Symposium

    Ferritin:ESR, A Predictor of MAS?

    Miriah Gillispie1, Marietta DeGuzman2, Mark Gorelik3 and Tiphanie Vogel4,5, 1Pediatrics, Department of IAR, Baylor College of Medicine, Houston, TX, 2Pediatric Immunology, Allergy and Rheumatology, Baylor College of Medicine, Texas Children's Hospital, Houston, TX, 3Baylor College of Medicine, San Antonio, TX, 4Department of Pediatrics, Division of Immunology, Allergy and Rheumatology and the Center for Human Immunology at Texas Children's Hospital., Baylor College of Medicine, Houston, TX, 5Center for Human Immunobiology, Texas Children's Hospital, Houston, TX

    Background/Purpose: Systemic onset juvenile idiopathic arthritis (SoJIA) is a rare autoinflammatory disorder comprising only 10% of JIA. Macrophage activation syndrome (MAS), an excessive and uncontrolled…
  • Abstract Number: 2375 • 2016 ACR/ARHP Annual Meeting

    Biologic Therapy Modifies Clinical and Laboratory Features of Macrophage Activation Syndrome Associated with Systemic Juvenile Idiopathic Arthritis

    Grant Schulert1, Francesca Minoia2, John F. Bohnsack3, Randy Q. Cron4, Soah Hashad5, Isabelle Koné-Paut6, Mikhail Kostik7, Daniel J Lovell8, Despoina Maritsi9, Peter A. Nigrovic10, Priyankar Pal11, Angelo Ravelli2, Masaki Shimizu12, Valda Stanevicha13, Bas Vastert14, Fabrizio De Benedetti15 and Alexei Grom16, 1Pediatric Rheumatology, Cincinnati Children's Hospital Medical Center, Cincinnati, OH, 2Istituto Giannina Gaslini, Genoa, Italy, 3Division of Allergy, Immunology and Pediatric Rheumatology, University of Utah, Salt Lake City, UT, 4Pediatric Rheumatology, Children's Hospital of Alabama, Birmingham, AL, 5Tripoli Children's Hospital, Tripoli, Libya, 6Hopital Kremlin Bicetre, University of Paris SUD, Paris, France, 7Hospital Pediatrics, State Pediatric Medical University, Saint-Petersburg, Russia, 8PRCSG Cincinnati Children's Hospital Medical Center, Cinncinnati, OH, 92nd Department of Academic Pediatrics, Athens Medical School, university of Athens, Athens, Greece, 10Rheumatology, Immunology, and Allergy, Brigham and Women’s Hospital, Boston, MA, 11Institute of Child Health, Kolkata, India, 12Department of Pediatrics, School of Medicine, Institute of Medical, Pharmaceutical, and Health Sciences, Kanazawa University, Kanazawa, Japan, 13Pediatric cathedra, Riga Stradiņš University, Riga, Latvia, 14Wilhelmina Children's Hospital / UMC Utrecht, Utrecht, Netherlands, 15Division of Rheumatology, Ospedale Pediatrico Bambino Gesù IRCCS, Roma, Italy, Rome, Italy, 16Cincinnati Children's Hospital Medical Center, Cincinnati, OH

    Background/Purpose:  Macrophage activation syndrome (MAS) is a life-threatening episode of hyperinflammation and a substantial cause of morbidity and mortality in pediatric rheumatology. It occurs most…
  • Abstract Number: 2415 • 2016 ACR/ARHP Annual Meeting

    Next Generation Sequencing Analysis of Familial Haemophagocytic Lymphohistiocytosis (HLH) Related Genes in Macrophage Activation Syndrome (MAS) and Secondary HLH (secHLH)

    Chiara Passarelli1, Manuela Pardeo2, Elisa Pisaneschi1, Antonio Novelli1, Fabrizio De Benedetti2 and Claudia Bracaglia2, 1Ospedale Pediatrico Bambino Gesù IRCCS, Unit of Medical Genetics, Laboratory of Cytogenetics and Molecular Genetics, Rome, Italy, 2Division of Rheumatology, Ospedale Pediatrico Bambino Gesù IRCCS, Roma, Italy, Rome, Italy

    Background/Purpose: Macrophage activation syndrome (MAS) is a severe complication of rheumatic disease, particularly of systemic JIA (sJIA). It is currently classified among the secondary forms…
  • Abstract Number: 1456 • 2015 ACR/ARHP Annual Meeting

    Macrophage Activation Syndrome and Familial Hemophagocytic Lymphohistiocytosis: Is Their Clinical Phenotype Really Similar?

    Francesca Minoia1, AnnaCarin Horne2, Sergio Davì1, Francesca Bovis1, Silvia Rosina1, Kai Lehmberg3, Sheila Weitzman4, Antonella Insalaco5, Carine Wouters6, Susan Shenoi7, Graciela Espada8, Seza Ozen9, Jordi Anton10, Raju Khubchandani11, Ricardo Russo12, Nicolino Ruperto13, Alberto Martini1, Randy Q. Cron14 and Angelo Ravelli1, 1Istituto Giannina Gaslini, Genoa, Italy, 2Karolinska University Hospital Solna, Stockholm, Sweden, 3University Medical Center, Hamburg, Germany, 4The Hospital for Sick Children, Toronto, ON, Canada, 5Ospedale Pediatrico Bambino Gesù, Rome, Italy, 6University Hospital Gasthuisberg, Leuven, Belgium, 7Seattle Children's Hospital, Seattle, WA, 8Hospital de Ninos Ricardo Gutierrez, Buenos Aires, Argentina, 9Hacettepe University, Ankara, Turkey, 10Unitat de Reumatologia Pediàtrica, Hospital Sant Joan de Déu, Barcelona, Spain, 11Jaslok Hospital and Research Center, Mumbai, India, 12Hospital de Pediatria Garrahan, Buenos Aires, Argentina, 13Istituto G. Gaslini, Pediatria II, PRINTO, Genoa, Italy, 14University of Alabama at Birmingham, Birmingham, AL

    Background/Purpose: Macrophage activations syndrome (MAS) is a potentially life-threatening complication of systemic juvenile idiopathic arthritis (sJIA). It is common view that sJIA associated MAS bears…
  • Abstract Number: 2281 • 2014 ACR/ARHP Annual Meeting

    Dissecting the Heterogeneity of  Macrophage Activation Syndrome

    Francesca Minoia1, Sergio Davì1, AnnaCarin Horne2, Francesca Bovis3, Erkan Demirkaya4, Alessandro Consolaro5, Jonathan Akikusa6, Nuray Aktay Ayaz7, Patrizia Barone8, Bianca Bica9, Isabel Bolt10, Luciana Breda11, Zane Davidsone12, Carmen De Cunto13, Jaime De Inocencio14, Sandra Enciso15, Romina Gallizzi16, Thomas Griffin17, Teresa Hennon18, Gerd Horneff19, Maka Ioseliani20, Michael Jeng21, Agneza Marija Kapovic22, Bianca Lattanzi5, Jeffrey M Lipton23, Silvia Magni-Manzoni24, Clarissa Nassif25, Ingrida Rumba-Rozenfelde26, Claudia Saad-Magalhães27, Sulaiman Almayouf28, Wafaa Al-Suwairi29, Kimo C Stine30, Olga Vougiouka31, Lehn K. Weaver32, Nicolino Ruperto33, Alberto Martini5,34, Randy Q. Cron35 and Angelo Ravelli34, 1Pediatria II, Istituto Giannina Gaslini, Genova, Italy, 2Karolinska Institutet, Karolinska University Hospital Solna, Stockholm, Sweden, 3Pediatria II, PRINTO, PRINTO - Istituto Giannina Gaslini, Genoa, Italy, 4Gulhane Military Medical Faculty, Ankara, Turkey, 5Istituto Giannina Gaslini, Genova, Italy, 63 West Clinical Offices, Royal, Royal Children's Hospital, Melbourne, Australia, 7Bakırkoy Maternity and Childrens Education and Research Hospital, Istanbul, Turkey, 8Azienda Policlinico Università di Catania, Catania, Italy, 9Hospital Universitário Clementino Fraga Filho, Rio de Janeiro, Brazil, 10Kinderspital Zuerich, Universitaetskinderklinik, Zurich, Switzerland, 11Department of Paediatrics, University of Chieti G. D'Annunzio, Chieti, Italy, 12Children's University Hospital, Riga, Latvia, 13Hospital Italiano de Buenos Aires, Buenos Aires, Argentina, 14Hospital 12 de Octubre, Madrid, Spain, 15Hospital Infantil de Mexico Federico Gomez in Mexico City, Mexico City, Mexico, 16University of Messina, Messina, Italy, 17Pediatrics, Division of Rheumatology, Levine Children's Hospital, Carolinas Medical Ctr, Charlotte, NC, 18Division of Pediatric Allergy/Immunology/Rheumatol, Women & Children's Hospital of Buffalo, Buffalo, NY, 19Asklepios Klinik Sankt Augustin, Sankt Augustin, Germany, 20M. Iashvili Children's Central Clinic, Tbilisi, Georgia, 21Stanford University, Stanford, CA, 22Children's Hospital Zagreb, Zagreb, Croatia, 23Steven and Alexandra Cohen Children's Hospital of New York, New York, NY, 24Ospedale Pediatrico Bambino Gesù, Roma, Italy, 25Hospital das Clínicas da Universidade Federal de Minas Gerais, Belo Horizonte, Brazil, 26University of Latvia, Riga, Latvia, 27Alameda Das Hortensias 868, Botucatu Medical School, Botucatu, Brazil, 28King Faisal Specialist H.,Riyadh, Riyadh, Saudi Arabia, 29Pediatric, King AbdulAziz Medical City, Riyadh, Saudi Arabia, 30Arkansas Children's Hospital, Little Rock, AR, 31P. A. Kyriakou Childrens Hospital of Athens University, Athens, Greece, 32Pediatric Rheumatology, Children's Hospital of Philadelphia, Philadelphia, PA, 33Pediatria II,, Istituto Giannina Gaslini, Genoa, Italy, 34University of Genova, Genova, Italy, 35Pediatric Rheumatology, University of Alabama at Birmingham, Birmingham, AL

    Background/Purpose Macrophage activations syndrome (MAS) occurring in the context of systemic juvenile idiopathic arthritis (sJIA) can pursue a rapidly fatal course. However, the diagnosis of…
  • Abstract Number: 321 • 2014 ACR/ARHP Annual Meeting

    Mutations of Familial Hemophagocytic Lymphohistiocytosis (FHL) Related Genes and Abnormalities of Cytotoxicity function tests in Patients with Macrophage Activation Syndrome (MAS) Occurring in Systemic Juvenile Idiopathic Arthritis (sJIA)

    Claudia Bracaglia1, Elena Sieni2, Martina Da Ros2, Carmela De Fusco3, Concetta Micalizzi4, Valentina Cetica2, Benedetta Ciambotti2, Maria Luisa Coniglio2, Antonella Insalaco5, Fabrizio De Benedetti Sr.1 and Maurizio Arico' Sr.6, 1Department of Pediatric Medicine, Division of Rheumatology, Ospedale Pediatrico Bambino Gesù, IRCCS, Rome, Italy, 2Department of Pediatric Hematology-Oncology, Meyer Children’s Hospital, Florence, Italy, 3Department of Pediatric Hematology-Oncology, Pausillipon Children’s Hospital, Naple, Italy, 4Department of Pediatric Hematology-Oncology, G. Gaslini Children' s Hospital, Genoa, Italy, 5Department of Pediatric Medicine,, Division of Rheumatology, Ospedale Pediatrico Bambino Gesù, IRCCS, Rome, Italy, 6Istituto Toscano Tumori (I.T.T.), Florence, Italy

    Background/Purpose: MAS is a severe complication of rheumatic diseases, mostly sJIA. Clinical and laboratory features are similar to those of FHL resulting from mutations in…
  • Abstract Number: 2171 • 2013 ACR/ARHP Annual Meeting

    Identification Of Best Cutoff Points and Clinical Signs Specific For Early Recognition Of Macrophage Activation Syndrome In Active Systemic Juvenile Idiopathic Arthritis

    Mikhail Kostik1, Margarita Dubko2, Ludmila Snegireva1, Vera Masalova1, Tatyana Kornishina2, Natalya Abramova3, Irina Chikova2, Natalya Glebova3, Ekaterina Kuchinskaya3, Eugenia Balbotkina3, Olga Kalshnikova3 and Vyacheslav Chasnyk4, 1Hospital Pediatrics, State Pediatric Medical University, Saint-Petersburg, Russia, 2State Pediatric Medical University, Saint-Petersburg, Russia, 3Saint-Petersburg State Pediatric Medical University, Saint-Petersburg, Russia, 4Hospital Pediatry, State Pediatric Medical University, Saint-Petersburg, Russia

    Background/Purpose: Macrophage activation syndrome (MAS) – is a severe life-threatening hematological condition, mostly complicated systemic juvenile idiopathic arthritis (SJIA). Early detection of MAS can lead…
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