Abstract Number: 1166 • 2017 ACR/ARHP Annual Meeting
Systemic Degos Disease: Long Term Survival on Combined Therapy with Eculizumab and Treprostinil
Background/Purpose: Degos disease (Malignant Atrophic Papulosis) is a thrombotic microvasculopathy of complement activation, endothelial cell injury and progressive microvascular obliteration. Lesions are marked by vascular…