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Abstracts tagged "inflammation and registry"

  • Abstract Number: 2841 • 2017 ACR/ARHP Annual Meeting

    Infection Is the Major Trigger of Adult Hemophagocytic Syndrome, an Orphan Systemic Hyperinflammatory, Life-Threatening Disease: Analysis in 147 Patients (GEAS-SEMI Registry)

    Pilar Brito-Zerón1, Alejandra Flores-Chavez2,3,4, Pedro Moral Moral5, A. Martínez-Zapico6, Pilar Hernández-Jimenez7, Guadalupe Fraile Rodriguez8, Patricia Perez Guerrero9, Eva Fonseca10, Angel Robles11, María Vaquero Herrero12, Angela Ruiz de Temiño de la Peña13, Maria José Forner14, José Ramón Larrañaga15, Mónica Rodriguez Carballeira16, Luis Fernando Viejo Llorente17, Manuel Ruiz Muñoz18, Roberto Hurtado19, César Morcillo20, Soledad Retamozo21 and Manuel Ramos-Casals22,23, 1Laboratory of Systemic Autoimmune Diseases “Josep Font”, CELLEX, Institut d’Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), Department of Systemic Autoimmune Diseases, ICMID, Hospital Clinic, Barcelona, Barcelona, Spain, 2Department of Autoimmune Diseases, ICMiD, Hospital Clínic Barcelona, Spain., Barcelona, Spain, 3Programa de Doctorado en Ciencias Médicas, Centro Universitario de Investigaciones Biomédicas (CUIB), Universidad de Colima, Colima, Mexico, Mexico, Mexico, 4Unidad de Investigación Biomédica 02 (Unidad de Investigación en Epidemiología Clínica), UMAE, Hospital de Especialidades, Centro Médico Nacional de Occidente, Instituto Mexicano del Seguro Social, Jalisco, Mexico, 5Hospital La Fé Valencia, Valencia, Spain, 6Hospital Universitario de Asturias, Oviedo, Oviedo, Spain, 7Internal Medicine, Hospital 12 de Octubre, Madrid, Spain, 8Internal Medicine, Hospital Ramón y Cajal, Madrid, Madrid, Spain, 9Department of Internal Medicine, Hospital Universitario Puerta del Mar, Cádiz, Cadiz, Spain, 10Internal Medicine, Hospital de Cabueñes, Gijón, Gijón, Spain, 11Internal Medicine, Hospital La Paz, Madrid, Madrid, Spain, 12Complejo Asistencial Universitario de Salamanca, Salamanca, Spain, 13Hospital Rio Hortega Valladolid, Valladolid, Spain, 14Department of Internal Medicine, Hospital Clínico de Valencia, Valencia, Spain, 15Department of Internal Medicine, Hospital Xeral, Vigo, Vigo, Spain, 16Hospital Mutua de Terrasa, Terrasa, Spain, 17Hospital Virgen de la Salud Toledo, Toledo, Spain, 18Department of Internal Medicine, Hospital Universitario Fundacion Alcorcón, Madrid, Spain, 19Hospital Vega Baja de Orihuela, Alicante, Spain, 20Department of Medicine, Hospital CIMA-Sanitas, Barcelona, Barcelona, Spain, 21Rheumatology Unit, Hospital Privado Universitario de Córdoba, Institute University of Biomedical Sciences University of Córdoba (IUCBC), Cordoba, Argentina, 22Laboratory of Systemic Autoimmune Diseases “Josep Font”, CELLEX, Institut d’Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), Department of Systemic Autoimmune Diseases, ICMID, Hospital Clinic, Barcelona, Spain, Barcelona, Spain, 23Department of Medicine, University of Barcelona, Barcelona, Spain., Barcelona, Spain

    Background/Purpose: Hemophagocytic syndrome or hemophagocytic lymphohistiocytosis (HLH) is an increasingly-recognized condition in adults, characterized by a wide range of etiologies, symptoms and outcomes, but with…
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