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Abstracts tagged "Eosinophilic Granulomatosus with Polyangiitis (Churg-Strauss)"

  • Abstract Number: 0854 • ACR Convergence 2023

    Long-term Efficacy of Remission-induction Regimens for Eosinophilic Granulomatosis with Polyangiitis

    Martin Dutertre1, Gregory Pugnet2, Claire De Moreuil3, Bernard Bonnotte4, YGAL BENHAMOU5, Dominique Chauveau6, Elisabeth Diot7, Pierre Duffau8, Nicolas Limal9, Antoine Néel10, GEOFFREY URBANSKI11, Noémie Jourde-Chiche12, Nicolas MARTIN SILVA13, Francois Maurier14, Arsène Mekinian15, Nicolas Schleinitz16, Felix ackermann17, Anne-Laure Fauchais18, Antoine Froissart19, Thomas Le Gallou20, Yurdagul Uzunhan21, Jean-Francois Viallard22, Alice Berezne23, laurent chiche24, Bruno Crestani25, Guillaume Direz26, Cecile-Audrey DUREL27, Pascal Godmer28, Jean-Emmanuel Kahn29, Marc Lambert30, Mathilde de Menthon1, Thomas Quemeneur31, Jacques Cadranel1, Pierre Charles32, Antoine Dossier1, Loic Guillevin33, Xavier Puéchal34 and Benjamin Terrier35, 1AP-HP, Paris, France, 2CHU Toulouse Rangueil Service de Medecine Interne et Immunologie Clinique, Toulouse, France, 3CHU de Brest, Brest, France, 4Department of Internal Medicine and Clinical Immunology, Dijon University Hospital, Dijon, France, 5rouen university hospital, Rouen, France, 6Hôpital Le Tripode, Bordeaux, France, 7Service de médecine interne et immunologie clinique, CHU Tours, Tours, France, 8CHU Bordeaux, Bordeaux, France, 9AP-HP, Créteil, France, 10CHU de Nantes, Nantes, France, 11CHU Angers, Angers, France, 12AP-HM, Marseille, France, 13CHU Caen, Caen, France, 14Hôpitaux privés de Metz, Vaux / Frankreich, France, 15Department of Internal Medicine, Hôpital Saint-Antoine, AP-HP, Paris, France, 16Aix Marseille university, AP-HM, Marseille, France, 17Hôpital Foch, Suresnes, France, 18Dupuytren Hospital, Limoges, France, 19CHI Créteil, Créteil, France, 20CHU Rennes, Rennes, France, 21AP-HP, Bobigny, France, 22CHU de Bordeaux, Hôpital Haut-Lévêque, Pessac, France, 23CH Annecy, Annecy, France, 24Hopital Europeen, Marseille, France, 25Hopital Bichat, Paris University, Paris, France, 26CH Le Mans, Le Mans, France, 27Hospices Civils de Lyon, Lyon, France, 28CH Bretagne Atlantique, Vannes, France, 29AP-HP, Suresnes Cedex, France, 30CHRU Lille, Lille, France, 31CH Valenciennes, Valenciennes, France, 32Institut Mutualiste Montsouris, Service de Médecine Interne, Paris, France, 33University Paris Descartes, Paris, France, 34National Referral Center for Rare Systemic Autoimmune Diseases, Paris, France, 35Department of Internal Medicine, Hôpital Cochin, AP-HP, Paris, France

    Background/Purpose: The Rituximab in Eosinophilic Granulomatosis With Polyangiitis (REOVAS) trial compared rituximab (RTX) infusions to conventional strategy for remission-induction in eosinophilic granulomatosis with polyangiitis (EGPA).…
  • Abstract Number: 0856 • ACR Convergence 2023

    Dupilumab for Relapsing or Refractory Eosinophilic Granulomatosis with Polyangiitis: A European Retrospective Study

    Berengere Molina1, Roberto Padoan2, Maria Letizia Urban3, Pavel Novikov4, Marco Caminati5, Camille Taillé6, Antoine Néel7, Laurence Bouillet8, Paolo Fraticelli9, Nicolas Schleinitz10, Christine Christides11, Laura Moi12, Bertrand Godeau13, Ann Knight14, Jan Walter Schroeder15, Sylvain Marchand-Adam16, Helder Gil17, Vincent Cottin18, Cécile-Audrey Durel19, Elena Gelain20, Boris Lerais21, Marc Ruivard22, Matthieu Groh23, Maxime Samson24, Luca Moroni25, Jens Thiel26, Anna Kernder27, Jan Willem Cohen Tervaert28, Giulia Costanzo29, Marco Folci30, Sonia Rizzello31, Pascal Cohen32, Giacomo Emmi33 and Benjamin Terrier34, 1Cochin Hospital, Paris, France, 2Department of Medicine DIMED, University of Padova, Padova, Italy, 3Department of Experimental and Clinical Medicine, University of Florence, Florence, Italy, 4Sechenov First Moscow State Medical University, Moscow, Russia, 5University of Verona, Verona, Italy, 6AP-HP, Bichat Hospital, Reference Center for Rare Pulmonary Diseases and University of Paris Cité, Inserm 1152, Paris, France, 7CHU Nantes, Nantes, France, 8Internal medicine department, Grenoble University Hospital, Grenoble, France, 9University Hospital Ospedali Riuniti, Ancona, Italy, 10Aix Marseille university, AP-HM, Marseille, France, 11Avignon Hospital, Avignon, France, 12Valais Hospital, Sion, Switzerland, 13CHU Henri Mondor, Créteil, France, 14Uppsala University, Uppsala, Sweden, 15ASST Grande Ospedale Metropolitano Niguarda, Milan, Italy, 16CHRU Tours, service de pneumologie et d'explorations fonctionnelles respiratoires, Tours, France, 17CHU Besancon, Besançon, France, 18Coordinating Reference Center for Rare Pulmonary Diseases, Louis Pradel Hospital, University of Lyon, INRAE, Lyon, France, 19CHU Lyon, Lyon, France, 20Meyer Children's Hospital, Florence, Italy, 21Brest University Hospital, Brest, France, 22CHU Clermont Ferrand, Clermont Ferrand, France, 23National Referral Center for Hypereosinophilic Syndrome (CEREO), Hôpital Foch, Suresnes, France, 24Department of Internal Medicine and Clinical Immunology, Dijon University Hospital, Dijon, France, 25San Raffaele Scientific Institute, Milan, Italy, 26University Hospital Freiburg, Freiburg, Germany, 27Heinrich-Heine-University Düsseldorf, Dusseldorf, Germany, 28University of Alberta, Edmonton, AB, Canada, 29University of Cagliari, Monserrato, Italy, 30Fondazione Poliambulanza Istituto Ospedaliero, Brescia, Italy, 31Careggi University Hospital, Florence, Italy, 32CHU Cochin, Paris, France, 33University of Florence, Florence, Italy, 34Department of Internal Medicine, Hôpital Cochin, AP-HP, Paris, France

    Background/Purpose: Eosinophilic granulomatosis with polyangiitis (EGPA) is an ANCA-associated vasculitides characterized by asthma, blood and tissue eosinophilia and systemic manifestations. Glucocorticoids (GCs)-dependent asthma and/or disabling…
  • Abstract Number: 1546 • ACR Convergence 2023

    Eosinophilic Granulomatosis with Polyangiitis: Clinical Suspicion Red Flags Identification by a Systematic Literature Review and Multidisciplinary Expert Consensus

    Ricardo Blanco1, Iñigo Rúa-Figueroa2, Roser Solans3, Maria C Cid4, Marina Blanco5, Ismael Garcia Moguel6, Francisco Perez Grimaldi7, Ana Noblejas8, Moises Labrador3, Cristian Domingo9, Georgina espigol10, Fernando Sanchez Toril11, Francisco Ortiz-Sanjuán12, Ebymar Arismendi13 and Jose María Alvaro-Gracias14, 1Hospital Universitario Marqués de Valdecilla, IDIVAL, Santander, Spain, 2Rheumatology, Hospital de Gran Canaria Doctor Negrin, Las Palmas de Gran Canaria, Spain, 3Internal Medicine Department, H. Universitari Vall d’Hebron, Universitat Autònoma de Barcelona, Barcelona, Spain, 4Hospital Clinic Barcelona, Barcelona, Spain, 5Pneumology Department, Hospital Universitario de A Coruña, Madrid, Spain, 6Allergy Department, Hospital Universitario 12 de Octubre, Madrid, Spain; Instituto de Investigación Sanitaria Hospital 12 de Octubre (imas12), Madrid, Spain, 7Pneumology Department, H. University of Jerez, Cádiz, Spain, 8Internal Medicine Department, Hospital Universitario La Paz, Madrid, Spain, 9Pneumology Department, Corporació Sanitaria Parc Taulí, Universitat Autònoma de Barcelona, Barcelona, Spain, 10Autoimmune Diseases Department, Hospital Clínic, FCRB-IDIBAPS, Universitat de Barcelona, Barcelona, Spain, 11Pneumology Department, Hospital Arnau Vilanova, Valencia, Spain;, Valencia, Spain, 12Hospital Universitario y Politécnico La Fe, Valencia, Spain, 13Pneumology Department, Hospital Clínic de Barcelona, Barcelona, Spain, Universitat de Barcelona, Spain and CIBERES, Barcelona, Spain, 14Hospital General Universitario Gregorio Marañon, Madrid, Spain

    Background/Purpose: Eosinophilic Granulomatosis with Polyangiitis (EGPA) is a rare ANCA-associated vasculitis, characterized histologically by eosinophilic tissue infiltration, necrotizing vasculitis, and eosinophil-rich granulomatous inflammation. The diagnosis…
  • Abstract Number: 1547 • ACR Convergence 2023

    Disease Burden of Eosinophilic Granulomatosis with Polyangiitis (EGPA): A Retrospective Analysis of US Health Insurance Claims Data

    Paul Dolin1, Danuta Kielar1, Anat Shavit1, Karina Keogh2, Jennifer Rowell1, Chris Edmonds3, Juliana Meyers4, Elizabeth Esterberg4, Tram Nham4 and Stephanie Chen5, 1AstraZeneca, Cambridge, United Kingdom, 2Mayo Clinic, Rochester, MN, 3AstraZeneca, Gaithersburg, MD, 4RTI Health Solutions, Research Triangle Park, NC, 5BioPharmaceuticals Medical, AstraZeneca, Gaithersburg, MD

    Background/Purpose: Eosinophilic granulomatosis with polyangiitis (EGPA) is a rare necrotizing small-to-medium vessel vasculitis with a relapsing-remitting course involving prodromal (various allergic reactions), eosinophilic (infiltration into…
  • Abstract Number: 1548 • ACR Convergence 2023

    Diagnosis Pathways in Patients with Eosinophilic Granulomatosis with Polyangiitis (EGPA): A Retrospective Analysis of US Health Insurance Claims Data

    Paul Dolin1, Danuta Kielar1, Anat Shavit1, Karina Keogh2, Jennifer Rowell1, Chris Edmonds3, Juliana Meyers4, Elizabeth Esterberg4, Tram Nham4 and Stephanie Chen5, 1AstraZeneca, Cambridge, United Kingdom, 2Mayo Clinic, Rochester, MN, 3AstraZeneca, Gaithersburg, MD, 4RTI Health Solutions, Research Triangle Park, NC, 5BioPharmaceuticals Medical, AstraZeneca, Gaithersburg, MD

    Background/Purpose: Raising awareness of eosinophilic granulomatosis with polyangiitis (EGPA), a rare necrotizing small-to-medium vessel vasculitis, amongst clinicians is important to ensure timely diagnosis and treatment.…
  • Abstract Number: 1549 • ACR Convergence 2023

    Treatment Patterns for Eosinophilic Granulomatosis with Polyangiitis (EGPA): A Retrospective Analysis of US Health Insurance Claims Data

    Paul Dolin1, Danuta Kielar1, Anat Shavit1, Karina Keogh2, Jennifer Rowell1, Chris Edmonds3, Juliana Meyers4, Elizabeth Esterberg4, Tram Nham4 and Stephanie Chen5, 1AstraZeneca, Cambridge, United Kingdom, 2Mayo Clinic, Rochester, MN, 3AstraZeneca, Gaithersburg, MD, 4RTI Health Solutions, Research Triangle Park, NC, 5BioPharmaceuticals Medical, AstraZeneca, Gaithersburg, MD

    Background/Purpose: Eosinophilic granulomatosis with polyangiitis (EGPA) is a rare, immune-inflammatory disorder characterized by asthma, eosinophilia, eosinophil-rich granulomatous inflammation, and chronic necrotizing vasculitis of small-to-medium-sized blood…
  • Abstract Number: 1552 • ACR Convergence 2023

    Epidemiology and Outcome of Eosinophilic Granulomatosis with Polyangiitis in France

    Benjamin Terrier1, Camille Taillé2, Alice Brouquet3, Solenne Tauty3, Francoise Bugnard3, Loic Guillevin4, Xavier Puéchal5 and Vincent Cottin6, 1Department of Internal Medicine, Hôpital Cochin, AP-HP, Paris, France, 2AP-HP, Bichat Hospital, Reference Center for Rare Pulmonary Diseases and University of Paris Cité, Inserm 1152, Paris, France, 3Steve Consultant, Lyon, France, 4University Paris Descartes, Paris, France, 5National Referral Center for Rare Systemic Autoimmune Diseases, Paris, France, 6Coordinating Reference Center for Rare Pulmonary Diseases, Louis Pradel Hospital, University of Lyon, INRAE, Lyon, France

    Background/Purpose: Eosinophilic granulomatosis with polyangiitis (EGPA, formerly Churg-Strauss) belongs to the group of anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitides (AAV). There are no recent data on…
  • Abstract Number: 1553 • ACR Convergence 2023

    Central Nervous System Involvement and Mimickers in ANCA Associated Vasculitis

    Yeliz Yagiz Ozogul1, Sinem Nihal Esatoglu2, Murat Ozogul3, Osman Kizilkilic4, Yesim Ozguler5, Ugur Uygunoglu6, Vedat Hamuryudan2 and Gulen Hatemi2, 1Istanbul University-Cerrahpasa, Cerrahpasa Medical School, Department of Internal Medicine, Istanbul, Turkey, 2Istanbul University-Cerrahpasa, Cerrahpasa Medical School, Department of Internal Medicine, Division of Rheumatology, Istanbul, Turkey, 3Haydarpasa Numune Training and Research Hospital, Department of Radiology, Istanbul, Turkey, 4Istanbul University-Cerrahpasa, Cerrahpasa Medical School, Department of Radiology, Istanbul, Turkey, 5Istanbul University-Cerrahpasa, Cerrahpasa Medical School, Department of Internal Medicine, Division of Rheumatology, İstanbul, Turkey, 6Istanbul University-Cerrahpasa, Cerrahpasa Medical School, Department of Neurology, Istanbul, Turkey

    Background/Purpose: Central nervous system (CNS) involvement is rare in ANCA associated vasculitis (AAV). On the other hand, AAV patients may develop complications or other conditions…
  • Abstract Number: 1074 • ACR Convergence 2022

    Safety and Efficacy of Dupilumab in Patients with Relapsing and/or Refractory Eosinophilic Granulomatosis with Polyangiitis

    Berengere Molina1, Maria Letizia Urban2, Roberto Padoan3, Pavel Novikov4, Camille Taillé5, Marco Caminati6, Christine Christides7, nicolas schleinitz8, Laura Moi9, Vincent Cottin10, bertrand godeau11, Laurence Bouillet12, Paolo Fraticelli13, Ann Knight14, Jan Walter Schroeder15, Sylvain Marchand-Adam16, Helder Gil17, Elena Gelain18, Giacomo Emmi2 and Benjamin Terrier19, 1Department of Internal Medicine, Cochin Hospital, Paris, France, 2Department of Experimental and Clinical Medicine, University of Florence, Florence, Italy, 3University of Padova, Padova, Italy, 4Tareev’s Clinic, Sechenov First Moscow State Medical University, Moscow, Russia, 5Pulmonology department, Bichat Hospital, Paris, Ile-de-France, France, 6Verona University Hospital, University of Verona, Verona, Italy, 7Avignon hospital, Avignon, France, 8Aix Marseille university, AP-HM, Marseille, France, 9Centre hospitalier universitaire vaudois, Lausanne, Lausanne, Switzerland, 10Coordinating Reference Center for Rare Pulmonary Diseases, Louis Pradel Hospital, University of Lyon, INRAE, Lyon, France, 11Department of Internal Medicine, National Referral Center for Adult's Immune Cytopenias, Mondor Hospital, Créteil, France, 12Grenoble University Hospital, Grenoble, France, 13Department of Internal Medicine, Ospedali Riuniti di Ancona, Ancona, Italy, 14Akademiska sjukhuset, Uppsala, Sweden, 15ASST GOM Niguarda, Milano, Italy, 16Tours University Hospital, Tours, France, 17Besancon University Hospital, Besançon, France, 18Meyer Children’s University Hospital of Firenze, Florence, Italy, 19National Referral Center for Rare Systemic Autoimmune Diseases, Cochin Hospital, Paris, France

    Background/Purpose: Eosinophilic granulomatosis with polyangiitis (EGPA) is an ANCA-associated vasculitides characterized by asthma, blood and tissue eosinophilia and systemic manifestations. Glucocorticosteroids (GCs)-dependent asthma and/or disabling…
  • Abstract Number: 1075 • ACR Convergence 2022

    Efficacy of Mepolizumab in Patients with Eosinophilic Granulomatosis with Polyangiitis and a Vasculitic Phenotype

    Benjamin Terrier1, David Jayne2, Bernhard Hellmich3, Jane Bentley4, Jonathan Steinfeld5, Steven Yancey6, Namhee Kwon7, Praveen Akuthota8, Paneez Khoury9, Lee Baylis10 and Michael Wechsler11, 1National Referral Center for Rare Systemic Autoimmune Diseases, Cochin Hospital, Paris, France, 2University of Cambridge, Cambridge, United Kingdom, 3Klinik für Innere Medizin, Rheumatologie & Immunologie, Medius Kliniken, Universität Tübingen, Plochingen, Germany, 4Clinical Statistics, GlaxoSmithKline, Brentford, United Kingdom, 5Clinical Sciences, Respiratory, GSK (affiliation at time of research), Philadelphia, PA, 6Respiratory Therapeutic Area, GSK (affiliation at the time of research), Research Triangle Park, NC, 7Clinical Sciences, Respiratory, GSK, Brentford, United Kingdom, 8Division of Pulmonary, Critical Care, and Sleep Medicine, Department of Medicine, University of California, San Diego, CA, 9Human Eosinophil Section, Laboratory of Parasitic Diseases, National Institute of Allergy and Infectious Diseases, National Institutes of Health, Bethesda, MD, 10Global Medical Affairs, GlaxoSmithKline, Durham, NC, 11Department of Medicine, National Jewish Health, Denver, CO

    Background/Purpose: Patients with eosinophilic granulomatosis with polyangiitis (EGPA) can have vasculitic or eosinophilic phenotypes. The MIRRA study demonstrated that patients with EGPA spent more time…
  • Abstract Number: 1767 • ACR Convergence 2022

    Epidemiology of Eosinophilic Granulomatosis with Polyangiitis (EGPA) and Hypereosinophilic Syndrome (HES) in Germany: A Claims Database Study

    Bernhard Hellmich1, Konstantin Neukirch2, Marco Lukas2, Martin Wernitz2, Dominik Beier3 and Dennis Häckl4, 1Department of Internal Medicine, Rheumatology and Immunology, Medius Kliniken, University of Tübingen, Kirchheim Teck, Germany, 2GlaxoSmithKline GmbH & Co. KG, Munich, Germany, 3InGef - Institute for Applied Health Research Berlin GmbH, Berlin, Germany, 4WIG2 GmbH, Leipzig, Germany

    Background/Purpose: EGPA and HES are rare multisystemic diseases associated with eosinophilia. Robust data on the epidemiology and treatment of HES and EGPA are scarce. The…
  • Abstract Number: 0125 • ACR Convergence 2022

    Baseline Characteristics in Patients with Eosinophilic Granulomatosis with Polyangiitis in the U.S. Initiating Mepolizumab

    Jared Silver1, Arijita Deb2, Elizabeth Packnett3, Donna McMorrow3, Cynthia Morrow3 and Michael Bogart1, 1GlaxoSmithKline, Research Triangle Park, NC, 2GlaxoSmithKline, Upper Providence, PA, 3IBM Watson Health, Cambridge, MA

    Background/Purpose: EGPA is a multisystem disorder often characterized clinically by asthma, chronic rhinosinusitis, and prominent eosinophilia, and histopathologically by eosinophil-rich, necrotizing , granulomatous vasculitis of…
  • Abstract Number: 0432 • ACR Convergence 2022

    Predictive Factors of Eosinophilic Granulomatosis with Polyangiitis Long-term Evolution: Data from a European Cohort

    Matthias Papo1, Pauline Martinot2, Renato A. Sinico3, Vitor Teixeira4, Nils Venhoff5, Maria-Letizia Urban6, Juliane Mahrhold7, Francesco Locatelli8, Giulia Cassone9, Franco Schiavon10, Benjamin Seeliger11, Thomas Neumann12, Claus Kroegel13, Matthieu Groh14, Chiara Marvisi15, Maxima Samson16, Thomas Barba17, David Jayne18, Arianna Troilo19, Jens Thiel20, Bernhard Hellmich21, Sara Monti22, Carlomaurizio Montecucco8, Carlo Salvarani23, Jean-Emmanuel Kahn24, Cecile-Audrey DUREL25, Luc Mouthon26, Loïc Guillevin26, Giacomo Emmi27, Augusto Vaglio28, Raphaël Porcher29 and Benjamin Terrier26, 1Service De Médecine Interne - Hôpital Cochin, Paris, France, 2Centre of Research in Epidemiology and Statistics, Université de Paris, Paris, Île-de-France, France, Paris, 3Department of Medicine and Surgery, Università degli Studi di Milano – Bicocca, Italy, Milano, Italy, 4Hospital de Faro, CHUA, Lisbon, Portugal, 5Department of Rheumatology and Clinical Immunology, Medical Center, Faculty of Medicine, University of Freiburg, Freiburg, Germany, 6Department of Experimental and Clinical Medicine, University of Firenze, Firenze, Italy, 7Department of Internal Medicine, Rheumatology and Immunology, Medius Kliniken, University of Tübingen, Kirchheim Teck, Germany, 8Department of Rheumatology, IRCCS Policlinico S. Matteo Foundation, University of Pavia, Pavia, Italy, 9Università di Modena e Reggio Emilia, Modena, Italy, 10Operative Unit of Rheumatology, Department of Medicine DIMED, University of Padova, Padova, Italy, 11Department of Respiratory Medicine, Hannover Medical School, Wermsdorf, Germany, 12Kantonsspital St. Gallen, St. Gallen, Switzerland, 13Department of Pneumology and Allergology, Clinic of Internal Medicine I, Jena University Hospital, Jena, Germany, 14Service de Médecine Interne, Centre de Référence des Syndromes Hyperéosinophiliques-CEREO, Hôpital Foch, Université Versailles–Saint-Quentin-en-Yvelines, Suresnes, France, 15Università di Modena e Reggio Emilia and National Institute of Arthritis & Musculoskeletal & Skin Diseases, National Institutes of Health, Bethesda, MD, 16Dijon University Hospital, Dijon, France, 17Department of Internal Medicine, Hôpital Edouard Herriot, Lyon, France, 18University of Cambridge, Cambridge, United Kingdom, 19Department of Rheumatology and Clinical Immunology, Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany, 20University Hospital Freiburg, Freiburg, Germany, 21Klinik für Innere Medizin, Rheumatologie & Immunologie, Medius Kliniken, Universität Tübingen, Plochingen, Germany, 22Rheumatology, Fondazione IRCCS Policlinico S. Matteo, University of Pavia, Pavia, Italy, 23Azienda USL -IRCCS di Reggio Emilia and Università di Modena e Reggio Emilia, Reggio Emilia, Reggio Emilia, Italy, 24Service de médecine interne - Hôpital Ambroise Paré, AP-HP, Boulogne-Billancourt, France, 25CHU Lyon, Lyon, France, 26National Referral Center for Rare Systemic Autoimmune Diseases, Cochin Hospital, Paris, France, 27Azienda Ospedaliero Universitaria Careggi, Firenze, Italy, 28Azienda Ospedaliero Universitaria Meyer, Parna, Italy, 29Université Paris Cité, Hôtel-Dieu, Paris, France

    Background/Purpose: Eosinophilic granulomatosis with polyangiitis (EGPA) is a small vessel necrotizing vasculitis characterized by blood and tissue eosinophilia and asthma. Glucocorticoids (GCs) frequently control the…
  • Abstract Number: 0453 • ACR Convergence 2022

    Validation of the 2022 – American College of Rheumatology/European Alliance of Associations for Rheumatology Classification Criteria in Patients with ANCA Associated Vasculitis

    Aman Sharma1, Prateek Deo1, Shankar Naidu2, Joydeep Samanta3, Sakshi Mittal3, Kusum Sharma3, Ritambhra Nada3, Varun Dhir4, sanjay jain2 and Ranjana Minz2, 1PGIMER, Chandigarh, India, Chandigarh, India, 2Postgraduate Institute of Medical Education and Research, Chandigarh, India, 3PGIMER, Chandigarh, India, 4PGIMER, CHD, INDIA, Chandigarh, India

    Background/Purpose: The purpose of this study was to validate the recently published 2022 American College of Rheumatology/European Alliance of Associations for Rheumatology Classification Criteria for…
  • Abstract Number: 0455 • ACR Convergence 2022

    Performance of 2022 American College of Rheumatology/European Alliance of Associations for Rheumatology Classification Criteria in Turkish Vasculitis Patients

    Ummugulsum Gazel1, Sevinc Can Sandikci2, Ahmet Omma3, Sinem Burcu Kocaer4, Fatoş Onen5, Onay Gercik6, Servet Akar7, Kerem Abacar8, Ebru Asicioglu9, Serhan Tuglular9, Fatma Alibaz-Oner8 and Haner Direskeneli10, 1University of Ottawa, Rheumatology, Ottawa, Canada, Ottawa, ON, Canada, 2Ankara Numune Education and Research Hospital, Rheumatology, Ankara, Turkey, 3Ankara Numune Education and Research Hospital, Rheumatology, Ankara, Turkey, Istanbul, Turkey, 4Dokuz Eylul University, Faculty of Medicine, Rheumatology, Izmir, Turkey, 5Dokuz Eylul University, Faculty of Medicine, Rheumatology, İzmir, Turkey, 6Izmir Tepecik Research Hospital, Izmir, Turkey, 7Izmir Katip Celebi University School of Medicine, Izmir, Turkey, 8Marmara University, Rheumatology, Istanbul, Turkey, 9Marmara University, Faculty of Medicine, Nephrology, Istanbul, Turkey, 10Marmara University, Rheumatology, Istanbul, Istanbul, Turkey

    Background/Purpose: The American College of Rheumatology (ACR)-1990 criteria is the most used method for the classification of ANCA Associated Vasculitis (AAV). However, with ACR-1990 criteria,…
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