Abstract Number: 2597 • 2019 ACR/ARP Annual Meeting
Prevalence and Clinical Associations of Degos Lesions in Systemic Sclerosis
Background/Purpose: Degos disease, also known as malignant atrophic papulosis (MAP), is a rare small-vessel vasculopathy that has characteristic cutaneous manifestations consisting of erythematous telangiectatic rims…Abstract Number: 1166 • 2017 ACR/ARHP Annual Meeting
Systemic Degos Disease: Long Term Survival on Combined Therapy with Eculizumab and Treprostinil
Background/Purpose: Degos disease (Malignant Atrophic Papulosis) is a thrombotic microvasculopathy of complement activation, endothelial cell injury and progressive microvascular obliteration. Lesions are marked by vascular…Abstract Number: 2196 • 2014 ACR/ARHP Annual Meeting
Treprostinil Use in Malignant Atrophic Papulosis (Köhlmeier-Degos Disease): Review of Worldwide Experience to Date
Background/Purpose Malignant atrophic papulosis (MAP) is a rare thrombo-occlusive vasculopathy that presents with cutaneous only lesions but can progress after months or years to rapidly fatal systemic…