ACR Meeting Abstracts

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Abstracts tagged "classification criteria"

  • Abstract Number: 1640 • ACR Convergence 2024

    ACR/EULAR 2022 Classification Criteria Compared to the ACR 1990 Classification Criteria in the ARTESER Registry of Giant Cell Arteritis

    Eugenio De Miguel1, Iñigo Hernández-Rodríguez2, Maite Silva-Diaz3, Joaquin María Belzunegui:4, Patricia Moya5, Marina Tortosa-Cabañas6, Vanessa Andrea Navarro7, Joan Calvet8, Ivette Casafont-Solé9, Jose A Román-Ivorra10, Selene Labrada-Arrabal11, Margarida Vasques Rocha:12, Carlota L Iñiguez:13, Vanesa Hernández-Hernández14, Cristina Campos-Fernández15, María Alcalde Villar:16, Antonio Juan-Mas17, Francisco-Javier Prado-Galbarro18, Itziar Calvo19, Julio Sánchez-Martín20, Javier Narvaez-García21 and Ricardo Blanco-Alonso22, and ARTESER Project Collaborative Group, 1Hospital Universitario La Paz, Madrid, Spain, 2Complejo Hospitalario Universitario de Vigo, Vigo, Spain, 3Complejo Hospitalario Universitario A Coruña, A Coruña, Spain, 4H de Donostia, Donostia-San Sebasti, Spain, 5Hospital de la Santa Creu i Sant Pau, Barcelona, Spain, 6Hospital Universitario Ramón y Cajal, Madrid, Spain, 7Hospital Moisès Broggi, Sant Joan Despí, Spain, 8Parc Taulí Hospital Universitari. Institut d'Investigació i Innovació Parc Taulí (I3PT-CERCA) (UAB), 08208 Sabadell, Spain, Barcelona, Spain, 9Hospital Universitari Germans Trias i Pujol, Badalona, Barcelona, Spain, Barcelona, Spain, 10Hospital Universitari i Politècnic la Fe, Valencia, Comunidad Valenciana, Spain, 11Hospital del Mar, Barcelona, Spain, 12Hospital Universitario Araba, Vitoria, Spain, 13Hospital Universitario Lucus Augusti, Galicia, Spain, Galicia, Spain, 14Hospital Universitario de Canarias, San Cristobal de La Laguna, Canarias, Spain, 15Consorci Hospital General Universitari de València, Comunitat Valenciana, Spain, Valencia, Spain, 16Hospital Universitario Severo Ochoa Leganés, Madrid, Spain, Madrid, Spain, 17Rheumatology Department, Hospital Universitario Severo Ochoa Leganés, Madrid, Spain, Madrid, Cantabria, Spain, 18Departamento de Sistemas Biológicos, Universidad Autónoma Metropolitana-Unidad Xochimilco,, Mexico, Mexico, 19Hospital Universitario de Basurto, Bilbao, Spain, 20Hospital Universitario 12 de Octubre, Madrid, Spain, 21Hospital Universitario de Bellvitge, Barcelona, Spain, 22Division of Rheumatology, Hospital Universitario Marqués de Valdecilla. IDIVAL, Immunopathology group, Santander, Spain

    Background/Purpose: The diagnosis of giant cell arteritis (GCA) has been guided for years by the ACR 1990 classification criteria but the emergence of the image…
  • Abstract Number: 2111 • ACR Convergence 2024

    An International Patient Survey to Identify Candidate Items for Classifying Early-Stage Symptomatic Knee Osteoarthritis

    Lauren King1, Armaghan Mahmoudian2, Jean Liew3, Quike Wang4, Ian Stanaitis5, Dieuwke Schiphof6, Leigh Callahan7, David Hunter8, Tom Appleton9, Aleksandra Turkiewicz10, Martin Englund11, Stefan Lohmander11, Ida Kristin Haugen12, Tuhina Neogi13, Gillian Hawker1 and Jos Runhaar6, and OARSI Early-stage Symptomatic Knee Osteoarthritis Initiative, 1University of Toronto, Toronto, ON, Canada, 2University of West Florida, Pensacola, FL, 3Boston University, Boston, MA, 4Shanghai Sixth People's Hospital, Shanghai, China (People's Republic), 5Women's College Hospital, Toronto, ON, Canada, 6Erasmus MC University Medical Center Rotterdam, Rotterdam, Netherlands, 7University of North Carolina Thurston Arthritis Research Center, Chapel Hill, NC, 8Sydney Musculoskeletal Health, University of Sydney, St Leonards, New South Wales, Australia, 9The University of Western Ontario, London, ON, Canada, 10,Lund University, Lund, Sweden, 11Lund University, Lund, Sweden, 12Diakonhjemmet Hospital, Oslo, Norway, 13Boston University Chobanian & Avedisian School of Medicine, Boston, MA

    Background/Purpose: Osteoarthritis Research Society International (OARSI) has launched an initiative to develop classification criteria for early-stage symptomatic knee osteoarthritis (EsSKOA). The goal is to establish…
  • Abstract Number: 2196 • ACR Convergence 2024

    Identifying Specific Criteria for Juvenile Systemic Sclerosis: A Comparison of Adult and Pediatric Ratings

    Suzanne Li1, Natalia Vasquez-Canizares2, Clare Pain3, Marinka Twilt4, Amra Adrovic5, Abdulrahman Alrasheed6, Simone Appenzeller7, ADELE CIVINO8, narendra bagri9, Patricia Costa Reis10, Muserref Cucueoglu11, Fatma Dedeoglu12, samundeeswari Deepak13, Jianghong Deng14, Dalia El-Ghoneimy15, Ivan Foeldvari16, Fernando Garcia-Rodriguez17, Marija Jelusic18, Ankur Jindal19, Ozgur Kasapcopur20, Maria Katsicas21, Archana Khan22, Raju Khubchandani23, Meiping Lu24, Hanna Lythgoe25, edoardo marrani26, Giorgia Martini27, Takako Miyamae28, Tomo Nozawa29, Seza Ozen30, Lidia Rutkowska-Sak31, Sunil Sampath13, Dieneke Schonenberg-Meinema32, Hongmei Song33, Betul Sozeri34, Hayakazu Sumida35, Maria Teresa Terreri36, Kathryn Torok37, Seyma Turkmen38, Dilara Unal38, Gong Yinv39, Emily Willis25, Rongjun Zheng24 and Brian Feldman40, and Pediatric International Consortium for Scleroderma, 1Hackensack Meridian School of Medicine, Joseph M. Sanzari Children's Hospital, Hackensack, NJ, 2Children's Hospital at Montefiore, Bronx, NY, 3Alderhey Children's NHS Foundation Trust, Liverpool, United Kingdom, 4Alberta Children's Hospital, Calgary, AB, Canada, 5Koc University Hospital, Istanbul, Turkey, 6King Abdullah Specialized Children Hospital, Riyadh, Saudi Arabia, 7Unicamp, Campinas, SP, Brazil, 8Pediatric Rheumatology "Vito Fazzi" Hospital LECCE, LECCE, Italy, 9All India Institute of Medical Sciences, New Delhi, Delhi, India, 10Hospital de Santa Maria, Lisbon, Portugal, 11Hacettepe University, Ankara, Turkey, 12Boston Children's Hospital, Boston, MA, 13THE NEWCASTLE UPON TYNE HOSPITALS NHS FOUNDATION TRUST, Newcastle upon Tyne, United Kingdom, 14Beijing Children's Hospital, Beijing, China, 15Children's Hospital, Ain Shams University, Cairo, Egypt, 16Hamburger Zentrum für Kinder- und Jugendrheumatologie, Hamburg, Germany, 17Universidad Autonoma de Nuevo Leon, Monterrey, NL, Mexico, 18University of Zagreb School of Medicine, University Hospital Centre Zagreb, Zagreb, Zagreb, Croatia, 19Postgraduate Institute of Medical Education and Research, Chandigarh, India, 20Istanbul University-Cerrahpasa, Cerrahpasa Medical School, istanbul, Turkey, 21Hospital Garrahan, Buenos Aires, Argentina, 22SRCC Children's Hospital, Mumbai, India, Mumbai, India, 23The SRCC Children's Hospital, Mumbai, India, 24Department of Rheumatology Immunology and Allergy, Children's Hospital of Zhejiang University School of Medicine, National Clinical Research Center for Child Health, Hangzhou, China (People's Republic), 25Royal Manchester Children's Hospital, Manchester, United Kingdom, 26Dipartimento Neurofarba, Università di Firenze, Firenze, Italy, 27University of Udine University Hospital Santa Maria della Misericordia, Udine, Italy, 28Tokyo Women's Medical University, Tokyo, Japan, 29Yokohama City University, Yokohama, Japan, 30Department of Pediatrics, Hacettepe University, Ankara, Turkey, 31National Institute of Geriatrics, Rheumatology and Rehabilitation, Warszawa, Poland, 32Amsterdam University Medical Center, Amsterdam, Netherlands, 33Peking Union Medical College Hospital, Beijing, China, 34University of Health Sciences, Istanbul, Turkey, 35The University of Tokyo, Tokyo, Japan, 36UNIFESP, São Paulo, SP, Brazil, 37Division of Rheumatology, Scleroderma Center, Department of Pediatrics, UPMC Children's Hospital of Pittsburgh, Pittsburgh, PA, USA, Pittsburgh, PA, 38University of Health Sciences, Umraniye Training and Research Hospital, Ankara, Turkey, 39Children's Hospital Affiliated to Fudan University, Shanghai, China (People's Republic), 40Division of Rheumatology, The Hospital for Sick Children; Departments of Pediatrics and Medicine, Faculty of Medicine; The Institute for Health Policy, Management and Evaluation, Dalla Lana School of Public Health, University of Toronto, Toronto, ON, Canada

    Background/Purpose: Despite the high morbidity and mortality risk associated with juvenile systemic sclerosis (jSSc), evidence to guide management is limited.  No jSSc clinical trials have…
  • Abstract Number: 0543 • ACR Convergence 2023

    Sensitivity of the 2019 European Alliance of Associations for Rheumatology /American College of Rheumatology Classification Criteria for Systemic Lupus Erythematosus in a Population-based Cohort; A Study Set in Norway 2000-2015

    Hilde Haukeland1, Sigrid Reppe Moe1, Cathrine Brunborg2, Antonela Botea3, Nenad Damjanic4, Gro Wivestad5, Heidi Øvreås6, Thea Bøe7, Torhild Garen1, Anniken Orre8, Helga Sanner9, Øyvind Molberg10 and Karoline Lerang9, 1Oslo University Hospital, Department of Rheumatology, Oslo, Norway, 2Oslo Centre for Biostatistics and Epidemiology, Research Support Services, Oslo University Hospital - Rikshospitalet, Oslo, Norway, 3Betanien Hospital, Department of Rheumatology, Skien, Norway, 4Ostfold Hospital Trust, Department of Rheumatology,, Grålum, Norway, 5Hospital of Southern Norway Trust, Division of Rheumatology, Department of Medicine, Kristiansand, Norway, 6Lillehammer Hospital for Rheumatic Diseases, Department of Rheumatology, Lillehammer, Norway, 7Vestfold Hospital Trust, Department of Internal Medicine, Tønsberg, Norway, 8Vestre Viken Hospital Trust, Department of Rheumatology, Drammen, Norway, 9Oslo University Hospital, Department of Rheumatology, Nydalen, Norway, 10University of Oslo, Institute of Clinical Medicine, Oslo, Norway

    Background/Purpose: To diagnose Systemic Lupus Erythematosus (SLE), one must understand the phenotype specter and interpret clinical, serological, radiological, and histopathological data, as well as exclude…
  • Abstract Number: 0711 • ACR Convergence 2023

    IgA Vasculitis in a Diverse Adult Patient Population

    Michelle Toker1, Urmi Khanna1, Roya Nazarian1, Adhya Mehta2, Bibi Ayesha1, Anand Kumthekar1 and Benedict Wu1, 1Albert Einstein College of Medicine, Montefiore Medical Center, Bronx, NY, 2Jacobi Medical Center, Bronx, NY

    Background/Purpose: Immunoglobulin-A (IgA) Vasculitis (IgAV) is a small-vessel vasculitis that is primarily diagnosed based on the European League Against Rheumatism (EULAR) criteria. There is limited…
  • Abstract Number: 1059 • ACR Convergence 2023

    Identification of Patients with Immune Checkpoint Inhibitor-Associated Inflammatory Arthritis Using Medicare Claims Data

    Anne Bass1, Fenglong Xie2, Alexa Meara3, Deanna Jannat-Khah4 and Jeffrey Curtis2, 1Hospital for Special Surgery, Weill Cornell Medicine, New York, NY, 2University of Alabama at Birmingham, Birmingham, AL, 3The Ohio State University Wexner Medical Center, Columbus, OH, 4Hospital For Special Surgery, New York, NY

    Background/Purpose: Immune checkpoint inhibitor (ICI) associated inflammatory arthritis (ICI-IA) has been suggested to occur in approximately 3-6% of ICI-treated patients with cancer1 but most studies…
  • Abstract Number: 1131 • ACR Convergence 2023

    Clinical Phenotypes of IgG4-related Disease in a Multi-ethnic Singapore Cohort

    Choon Guan Chua1, Weida Chew1, Jeggrey Kay Wee Kam1, Hwee-Pin Phua1, Chengzi Chow1, Carol Yee-Leng Ng1, Wei-Yen Lim1, Ru Sin Lim1, Jereme Yijin Gan1, Mung-Ee Loh1, Tianrong Yeo2, David Zhiwei Law1, Stephrene Seok Wei Chan3, Amanda Francesca Ya-Fang Cheang4, Yong-Howe Ho1 and Charles Kien-Fong Vu1, 1Tan Tock Seng Hospital, Singapore, Singapore, 2National Neurology Institute, Singapore, Singapore, 3National University Hospital, Singapore, Singapore, 4Woodlands Health Campus, Singapore, Singapore

    Background/Purpose: IgG4-related disease (IgG4-RD) is an immune-mediated condition that is heterogenous and can result in organ failure. To understand the disease profile of our local…
  • Abstract Number: 1136 • ACR Convergence 2023

    Challenges in Diagnosing VEXAS Syndrome: Delayed Diagnosis, Misdiagnosis, and Associations with Specific Gene Mutations

    Paula García Escudero1, Marta López i Gómez2, Marta López Maraver3, PALOMA VELA4, María Rodríguez Laguna5, carolina Merino6, Ana Victoria Orenes Vera7, Clara García Belando8, Diego Dios Santos9, Jose Alberto Miranda Filloy10, Francisco Javier Toyos Sáenz de Miera11, Alicia Garcia Dorta12, Ignacio Vázquez13, José Ángel Hernández Beriain14, MARIA ELVIRA DIEZ ALVAREZ15, Marta Ibáñez Martínez16, Beatriz Frade Sosa17, Judit Font Urgelles18, Meritxell Salles Lizarzaburu19, Elena Riera Alonso20, Ernesto Trallero Araguás21, Berta Magallanes López22, Joaquín Belzunegui Otano23, Carlos de Miguel Sánchez24, Zuriñe Ortiz de Zárate Caballero25 and Jaime Calvo Alén26, 1Hospital Universitario Araba, Bilbao, Spain, 2Hospital Universitario de Araba, Pamplona, Spain, 3Hospital Universitario de Araba, Vitoria, Spain, 4Rheumatology, Hospital General Universitario Alicante, Alicante, Spain, 5H. Clínico San Carlos, Madrid, Spain, 6Rheumatology Department Hospital Universitario Puerta de Hierro, Majadahonda (Madrid), Spain, 7H. Arnau de Vilanova, Valencia, Spain, 8Hospital Los Arcos del Mar Menor, Murcia, Spain, 9Rheumatology department, Complexo Hospitalario Universitario A Coruña (CHUAC). Instituto de Investigación Biomédica A Coruña (INIBIC), A Coruña, Spain, 10C. H. U. Lucus Augusti, Lugo, Spain, 11Hospital Virgen Macarena, Sevilla, Spain, 12Rheumatology Unit, Hospital Universitario de Canarias, Santa Cruz de Tenerife, Spain, 13H. U. Dr. Peset, Valencia, Spain, 14Rheumatology, Hospital Insular de Gran Canaria, Las Palmas de Gran Canaria, Spain, 15Rheumatology, Hospital Universitario de León, León, Spain, 16C. A. U. de Salamanca, Salamanca, Spain, 17Hospital Clínic de Barcelona, Barcelona, Spain, 18Hospital Universitario Germans Trías i Pujol, Barcelona, Spain, 19C. H. de Manresa - Fundació Althaia, Barcelona, Spain, 20Hospital Universitario Mútua Terrassa, Barcelona, Spain, 21Department of Rheumatology, Hospital Universitario Vall d'Hebron, Barcelona, Spain, 22Hospital de la Santa Creu i Sant Pau, Barcelona, Spain, 23Hospital Universitario Donosti, Donosti, Spain, 24Hospital Universitario de Araba, Hematology, VItoria, Spain, 25Hospital Universitario de Araba, Internal Medicine, Vitoria, Spain, 26Hospital Universitario Araba, Vitoria, Spain

    Background/Purpose: The newly described VEXAS syndrome is a very heterogenous disease with rheumatologic and hematologic manifestations, caused by somatic mutations affecting UBA1 gene, that still…
  • Abstract Number: 1175 • ACR Convergence 2023

    Inclusion of All Myositis Specific Autoantibodies or Other Rashes Leads to Better Sensitivity but Lower Specificity of 2017 EULAR/ACR Myositis Classification Criteria for Dermatomyositis

    Yusra Hasan1, Katharine Ching Chung2, Dana Ascherman3, Siamak Moghadam-Kia4, Chester V. Oddis3 and Rohit Aggarwal3, 1CHI Health Creighton University Medical Center, Omaha, NE, 2University of Pittsburgh Medical Center, Mckeesport, PA, 3University of Pittsburgh, Pittsburgh, PA, 4University of Pittsburgh Medical Center, Pittsburgh, PA

    Background/Purpose: Idiopathic Inflammatory Myopathies (IIM), collectively known as myositis, are heterogeneous disorders characterized by muscle weakness and muscle inflammation. ACR/EULAR classification criterion for IIM was…
  • Abstract Number: 1228 • ACR Convergence 2023

    Validation of the PEDiatric Behçet’s Disease Classification Criteria (PEDBD): An International Consensus-based Approach

    Caterina Matucci-Cerinic1, helene Palluy2, Sulaiman Al-Mayouf3, Paul Brogan4, Luca Cantarini5, Ahmet Gul6, Ozgur Kasapcopur7, Jasmin B. Kuemmerle-Deschner8, Seza Ozen9, david saadoun10, Farhad Shahram11, Francesca Bovis12, Eugenia mosci13, Nicolino Ruperto14, Marco Gattorno15 and Isabelle Kone-Paut16, 1DINOGMI, University of Genoa; IRCCS Istituto Giannina Gaslini, UOC Rheumatology and autoinflammatory diseases, Genova, Italy, 2Pediatric rheumatology and CEREMAIA, Bicêtre hospital, APHP, University of Paris Saclay, Paris, France, 3King Faisal Specialist Hospital & Research Centre, Riyadh, Saudi Arabia, 4UCL Institute of Child Health and Great Ormond Street Hospital NHS Foundation Trust, London, United Kingdom, 5Rheumatology Unit, Department of Medical Sciences, Surgery and Neurosciences, University of Siena, Siena, Italy, 6Istanbul University, Istanbul Faculty of Medicine, Department of Internal Medicine, Division of Rheumatology, Istanbul, Turkey, 7Department of Pediatric Rheumatology, Cerrahpasa Medical School, Istanbul University-Cerrahpasa, Istanbul, Turkey, 8med.uni-tuebingen, Tübingen, Germany, 9Hacettepe University Medical Faculty, Ankara, Turkey, 10Sorbonne Universités, Department of Internal Medicine and Clinical Immunology, Centre de Référence des Maladies Auto-Inflammatoires et de l’Amylose inflammatoire, F-75013, Paris, France; AP-HP, Groupe Hospitalier Pitié-Salpêtrière., Neuilly sur Seine, France, 11Rheumatology Research Center, Shariati Hospital, Tehran University of Medical Sciences, Tehran, Iran, 12Dept of Health Sciences (DISSAL), University of Genoa, Genova, Italy, 13UOC Servizio di Sperimentazioni Cliniche Pediatriche, PRINTO, IRCCS Istituto Giannina Gaslini, Genova, Italy, 14IRCCS Istituto Giannina Gaslini, UOSID Centro Trial, Genova, Italy, 15UOC Reumatologia e Malattie Autoinfiammatorie, Genoa, Italy, 16Department of Pediatric Rheumatology, Reference Centre for Autoinflammatory Disorders CEREMAIA, Bicêtre Hospital, APHP, University of Paris Saclay, Paris, France

    Background/Purpose: Behçet's disease (BD) is an autoinflammatory disease characterized by a variable vessel vasculitis. In the past, several criteria have been created for adult BD…
  • Abstract Number: 1545 • ACR Convergence 2023

    Validation of the 2022 American College of Rheumatology/European Alliance of Associations for Rheumatology Classification Criteria in Patients with ANCA-associated Vasculitis

    Liubov Petelytska, Vladyslav Kravchenko and Oleg Iaremenko, Bogomolets National Medical University, Kyiv, Ukraine

    Background/Purpose: The early diagnosis of ANCA-associated vasculitis (AAV) and treatment initiation may prevent progression to end organ damage, particularly renal disease. Based on the Vasculitis…
  • Abstract Number: 1901 • ACR Convergence 2023

    Which ASDAS-ESR Cut-offs for Disease Activity Correspond to ASDAS-CRP Cut-offs in Axial Spondyloarthritis? – Results from the EuroSpA Collaboration

    Stylianos Georgiadis1, Lykke Ørnbjerg1, Brigitte Michelsen2, Tore Kvien3, Daniela Di Giuseppe4, Johan Karlsson Wallman5, Jakub Zavada6, Sella Provan7, Ana Maria Rodrigues8, Maria Jose Santos9, Ziga Rotar10, Dan Nordstrom11, Anna-Mari Hokkanen12, Gary Macfarlane13, Gareth T. Jones13, Irene van der Horst-Bruinsma14, Pasoon Hellamand15, Mikkel Østergaard16 and Merete Hetland1, 1Copenhagen Center for Arthritis Research, Rigshospitalet, Copenhagen, Denmark, 2Rigshospitalet Glostrup; Diakonhjemmet Hospital; Sørlandet Hospital, Copenhagen, Denmark, 3Center for Treatment of Rheumatic and Musculoskeletal Diseases (REMEDY), Diakonhjemmet Hospital, Oslo, Norway, 4Karolinska Institutet, Stockholm, Sweden, 5Lund University and Skåne University Hospital, Lund, Sweden, 6Institute of Rheumatology; Charles University, Prague, Czech Republic, 7Diakonhjemmet Hospital, Oslo, Norway, 8Sociedade Portuguesa de Reumatologia; Nova Medical School; Hospital dos Lusíadas, Lisbon, Portugal, 9Hospital Garcia de Orta, Almada, Lisboa, Portugal, 10University Medical Centre Ljubljana, Ljubljana, Slovenia, 11Helsinki University Hospital, Helsinki, Finland, 12Helsinki University and Helsinki University Hospital, Helsinki, Finland, 13Aberdeen Centre for Arthritis and Musculoskeletal Health (Epidemiology Group), University of Aberdeen, Aberdeen, United Kingdom, 14Radboud University Medical Centre, Department of Rheumatology, Nijmegen, Netherlands, 15Amsterdam University Medical Centers, University of Amsterdam, Amsterdam, Netherlands, 16Copenhagen Center for Arthritis Research, Center for Rheumatology and Spine Diseases, Centre for Head and Orthopaedics, Rigshospitalet; University of Copenhagen, Copenhagen, Denmark

    Background/Purpose: When assessing disease activity in patients with axial spondyloarthritis (axSpA), the Ankylosing Spondylitis Disease Activity Score with C-reactive protein (ASDAS-CRP) is recommended over ASDAS…
  • Abstract Number: 1943 • ACR Convergence 2023

    IgG4-related Disease: 2010-2022 Case Review and Comparative Evaluation of Diagnostic Criteria

    Pablo Martínez Calabuig1, Jorge Juan Fragio1, Roxana Gonzalez Mazarío2, Amalia Rueda Cid3, Mireia Lucía Sanmartín Martínez1, Laura Salvador Maicas1, Laura Abenza Barberá1, María Cristina Sabater Abad1, Antonio Sierra Rivera1, Inmaculada Castelló Miralles1, Juan José Lerma Garrido1, Clara Molina Almela3, Isabel Balaguer Trull1 and Cristina Campos Fernández1, 1Hospital General Universitario Valencia, Valencia, Spain, 2Hospital de Sagunto, Valencia, Spain, 3Hospital General de Valencia, Valencia, Spain

    Background/Purpose: IgG4 immunoglobulin-related disease (IgG4-RD) is a rare, systemic immune-mediated fibro-inflammatory process with an unclear etiology and pathophysiology with the capacity of affecting multiple organs.…
  • Abstract Number: 2264 • ACR Convergence 2023

    Proposal for Defining Moderate and Severe Activity States in Systemic Lupus Erythematosus. Impact on Flares and Other Outcomes

    Ivonne Lourdes Mamani Velarde1, Iñigo Rúa-Figueroa2, Sara García Pérez1, Irene Altabás González3, CORAL Mourino Rodriguez4, Norman Jiménez5, JULIA MARTINEZ BARRIO6, Maria Galindo-Izquierdo7, Jaime Calvo- Alén8, Celia Eurasquin9, Belen Serrano Benavente10, Esther Uriarte Isacelaya11, Eva Tomero Muriel12, Mercedes Freire González13, Ricardo Blanco14, Eva Salgado-Pérez15, Paloma Vela16, Antonio Fernandez-Nebro17, Alejandro Olivé-Marqués18, Clara Sanguesa Gomez19, Javier Narvaez20, Raúl Menor-Almagro21, Jose Rosas22, José Ángel Hernández Beriain23, JAVIER MANERO24, Elena Aurrecoechea Aguinaga25, Oihane Ibarguengoitia-Barrena26, Carlos Montilla-Morales27, Gema Bonilla28, Vicente Torrente-Segarra29, Ana Paula Cacheda30, Maria J. García-Villanueva31, Clara Moriano Morales32, Concepción Fito Manteca33, Nuria Lozano Rivas34, Cristina Bohórquez35 and Jose-Maria Pego-Reigosa36, 1University Hospital of Vigo, Department of Rheumatology. IRIDIS Group (Investigation in Rheumatology and Immune-Diseases), Galicia Sur Health Research Institute (IISGS), Vigo, Spain, 2Rheumatology, Hospital de Gran Canaria Doctor Negrin, Las Palmas de Gran Canaria, Spain, 3Department of Rheumatology, University Hospital of Vigo. IRIDIS Group (Investigation in Rheumatology and Immune-Diseases), Vigo, Spain, 4Complejo Hospitalario Universitario de Vigo. IRIDIS (Investigation in Rheumatology and Immune-Mediated Diseases) Group, Galicia Sur Health Research Institute, Vigo, Spain, 5IIRIDIS (Investigation in Rheumatology and Immune-Mediated Diseases) Group, Galicia Sur Health Research Institute., Vigo, Spain, 6Rheumatology, Gregorio Marañon University Hospital, Madrid, Spain, 7Rheumatology, University Hospital of 12 de Octubre, Madrid, Spain, 8Rheumatology, Bioaraba Research Unit, Hospital Universitario Araba, Vitoria, Spain, 9Department of Rheumatology, Doctor Negrín University Hospital, Las Palmas de Gran Canaria, Spain, 10Rheumatology Department Hospital Gregorio Marañón, Madrid, Spain, 11Rheumatology, University Hospital of Donosti, San Sebastián, Spain, 12Rheumatology, Hospital La Princesa, Madrid, Spain, 13Rheumatology department, Complexo Hospitalario Universitario A Coruña (CHUAC). Instituto de Investigación Biomédica A Coruña (INIBIC), A Coruña, Spain, 14Hospital Universitario Marqués de Valdecilla, IDIVAL, Santander, Spain, 15Department of Rheumatology, University Hospital of Ourense, Ourense, Spain, 16Department of Rheumatology, University Hospital of Alicante, Alicante, Spain, 17Hospital Regional Universitario de Málaga, Malaga, Spain, 18Department of Rheumatology, Hospital Germans Trias i Pujol, Badalona, Spain, 19Severo Ochoa Hospital, Madrid, Spain, 20Hospital Universitario de Bellvitge, Barcelona, Spain, 21Rheumatology, Hospital Jerez, Puerto De Santa María, Spain, 22Department of Rheumatology, Hospital Villajoyosa, Alicante, Spain, 23Rheumatology, Hospital Insular de Gran Canaria, Las Palmas de Gran Canaria, Spain, 24Department of Rheumatology, Hospital Universitario Miguel Servet, Zaragoza, Spain, 25Department of Rheumatology, Hospital Sierrallana, Torrelavega, Spain, 26Galdakao-Usansolo University Hospital, Bilbao, Spain, 27Rheumatology, University Hospital of Salamanca, Salamanca, Spain, 28Department of Rheumatology, Hospital Clínico Universitario La Paz, Madrid, Spain, 29Department of Rheumatology, Hospital de Sant Joan Despí Moises Broggi,, Sant Joan Despí, Spain, 30Department of Rheumatology, Hospital Son Llatzer, Palma de Mallorca, Spain, 31Hospital Ramón y Cajal, Madrid, Spain, 32Rheumatology, Hospital Universitario de León, León, Spain, 33Complejo Universitario de Navarra, Pamplona, Spain, 34Department of Rheumatology, Hospital Clínico Universitario Virgen de la Arrixaca, Murcia, Spain, 35Department of Rheumatology, University Hospital Príncipe de Asturias, Alcalá de Henares, Spain, 36Rheumatology, Hospital do Meixoeiro, Vigo, Spain

    Background/Purpose: In systemic lupus erythematosus (SLE), there is no definition of states of moderate and severe SLE activity. How these states may influence different disease…
  • Abstract Number: 0108 • ACR Convergence 2023

    Decoding Antiphospholipid Syndrome Laboratory Test Outcomes in a Large Multicenter Electronic Health Record Database

    Emily Balczewski, Wenying Liang, Amala Ambati, Yu Zuo, Karandeep Singh and Jason Knight, University of Michigan, Ann Arbor, MI

    Background/Purpose: Electronic health record (EHR) data provide an inexpensive, information-rich tool to study rare diseases like antiphospholipid syndrome (APS). Many such studies rely on structured…
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