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Abstracts tagged "Behçet’s Syndrome"

  • Abstract Number: 2535 • ACR Convergence 2025

    Behçet’s syndrome: distinct features in 344 pediatric and adult patients in a non-endemic region

    Ricardo Machado1, Thales Souza2, Matheus França3, Vinicius Matias4, Sylvia Farhat1, Carolina Siqueira4, Maria Carolina Santos4, Lia Steuer1, Luisa Forero1, Rafael Bassara Macedo5, Thiago Freitas6, barbara Bayeh7, Carolina Ejnisman8, Pedro Araujo9, Rafael Cordeiro10, Fabio Specian5, Verena Balbi1, Nadia Emi Aikawa11, Katia Kozu1, Clovis Artur Silva12, Lucia Maria Campos13, Adriana Elias14 and Henrique Giardini6, 1Instituto da Criança e do Adolescente, Hospital das Clinicas, Sao Paulo, Sao Paulo, Brazil, 2Faculdade de Medicina da Universidade de Brasilia, Brasilia, Distrito Federal, Brazil, 3Instituto da Criança e do Adolescente, Hospital das Clinicas, University of Sao Paulo Medical School, Sao Paulo, Sao Paulo, Brazil, 4Faculdade de Ciências Medicas da Santa Casa de Sao Paulo, Sao Paulo, Sao Paulo, Brazil, 5Rheumatology Division, Hospital das Clinicas da Faculdade de Medicina da Universidade de Sao Paulo (USP), Sao Paulo, Sao Paulo, Brazil, 6Rheumatology Division, Hospital das Clinicas HCFMUSP, Faculdade de Medicina, Universidade de Sao Paulo, Sao Paulo, SP, Brazil, São Paulo, Brazil, 7Hospital das Clínicas, University of Sao Paulo Medical School, Sao Paulo, Sao Paulo, Brazil, 8Rheumatology Division, Hospital das Clinicas HCFMUSP, Faculdade de Medicina, Universidade de Sao Paulo, Sao Paulo, SP, Brazil, Sao Paulo, Brazil, 9Universidade de São Paulo, Sao Paulo, São Paulo, Brazil, 10Rheumatology Division, Hospital das Clinicas HCFMUSP, Faculdade de Medicina, Universidade de Sao Paulo, Sao Paulo, SP, Brazil, São Paulo, Sao Paulo, Brazil, 11Rheumatology Division and Pediatric Rheumatology Unit, Hospital das Clinicas HCFMUSP, Faculdade de Medicina, Universidade de Sao Paulo, Sao Paulo, SP, Brazil, Sao Paulo, São Paulo, Brazil, 12University of São Paulo, São Paulo, São Paulo, Brazil, 13Instituto da Criança e do Adolescente, São Paulo, São Paulo, Brazil, 14Pediatric Rheumatology Unit, Instituto da Criança e do Adolescente, Hospital das Clinicas, University of Sao Paulo Medical School, São Paulo, São Paulo, Brazil

    Background/Purpose: Behçet’s syndrome (BS) is a chronic inflammatory disorder characterized by a heterogeneous clinical presentation, occurring primarily in young adults and very rarely in children…
  • Abstract Number: 2527 • ACR Convergence 2025

    Safety Profile and Impaired Humoral Response to the Recombinant Herpes Zoster Vaccine in Behçet’s Syndrome Patients under Immunosuppression: a Prospective, Randomized, Placebo-Controlled Trial

    Eduardo Borba1, Caio Carvalho2, Nadia E Aikawa3, Ana C Medeiros-Ribeiro2, Sandra G Pasoto2, Carla Saad4, Henrique Giardini5, Thiago Freitas5, Rafael Cordeiro6, Eloisa Bonfa1 and Clovis Artur Silva7, 1Faculdade de Medicina da Universidade de São Paulo, São Paulo, Brazil, São Paulo, Brazil, 2Rheumatology Division, Hospital das Clinicas HCFMUSP, Faculdade de Medicina, Universidade de Sao Paulo, Sao Paulo, SP, Brazil, Sao Paulo, Brazil, 3Pediatric Rheumatology Unit, Instituto da Criança e do Adolescente, Hospital das Clinicas HCFMUSP, Sao Paulo, Brazil., Sao Paulo, Sao Paulo, Brazil, 4Rheumatology Division, Hospital das Clinicas HCFMUSP, Faculdade de Medicina, Universidade de Sao Paulo, Sao Paulo, SP, Brazil, Sao Paulo, Sao Paulo, Brazil, 5Rheumatology Division, Hospital das Clinicas HCFMUSP, Faculdade de Medicina, Universidade de Sao Paulo, Sao Paulo, SP, Brazil, São Paulo, Brazil, 6Rheumatology Division, Hospital das Clinicas HCFMUSP, Faculdade de Medicina, Universidade de Sao Paulo, Sao Paulo, SP, Brazil, São Paulo, Sao Paulo, Brazil, 7University of São Paulo, São Paulo, São Paulo, Brazil

    Background/Purpose: Although rare, new-onset Behçet’s syndrome (BS) and disease flares have been reported following vaccination. In this context, the recommendation of the Recombinant Herpes Zoster…
  • Abstract Number: 2045 • ACR Convergence 2025

    Malignancy in Behçet’s Syndrome: A 24-Year Cohort Study In a Non-Endemicand Multiethnic Country

    Pedro Araujo1, Rafael Bassara Macedo2, Fabio Specian2, Carolina Ejnisman3, Barbara Bayeh3, Percival Sampaio-Barros4, Thiago Freitas4, Rafael Cordeiro5 and Henrique Giardini4, 1Universidade de São Paulo, Sao Paulo, São Paulo, Brazil, 2Rheumatology Division, Hospital das Clinicas da Faculdade de Medicina da Universidade de Sao Paulo (USP), Sao Paulo, Sao Paulo, Brazil, 3Rheumatology Division, Hospital das Clinicas HCFMUSP, Faculdade de Medicina, Universidade de Sao Paulo, Sao Paulo, SP, Brazil, Sao Paulo, Brazil, 4Rheumatology Division, Hospital das Clinicas HCFMUSP, Faculdade de Medicina, Universidade de Sao Paulo, Sao Paulo, SP, Brazil, São Paulo, Brazil, 5Rheumatology Division, Hospital das Clinicas HCFMUSP, Faculdade de Medicina, Universidade de Sao Paulo, Sao Paulo, SP, Brazil, São Paulo, Sao Paulo, Brazil

    Background/Purpose: Behçet’s syndrome (BS) has been associated with an increased risk of malignancy, particularly in studies from endemic regions such as East Asia and the…
  • Abstract Number: 2037 • ACR Convergence 2025

    The Largest International Cohort Study of HA20 Reveals Novel Genetic Architecture and Age-Dependent Phenotypic Evolution

    Manuel Carpio Tumba1, Tingyan He2, Jun Wang3, Elizabeth Kairis1, Kyr Goyette1, Akuti Kethri1, Urekha Karri4, Atif Towheed1, Jun Yang5, Qing Zhou6 and Daniella Schwartz1, 1University of Pittsburgh, Pittsburgh, PA, 2Shenzhen Children's Hospital, Shenzhen, China (People's Republic), 3Zhejiang University School of Medicine, Zhejiang, China (People's Republic), 4School of public health, Pittsburgh, PA, 5Rheumatology and Immunology Department of Shenzhen Children's Hospital, Shenzhen, 518100, China., Shenzhen, China (People's Republic), 6Zhejiang University School of Medicine, Hangzhou, China (People's Republic)

    Background/Purpose: Haploinsufficiency of A20 (HA20) is a monogenic autoinflammatory disease caused by loss-of-function (LOF) mutations in TNFAIP3. HA20 was initially described as an early-onset form…
  • Abstract Number: 2028 • ACR Convergence 2025

    Behçet’s Syndrome Beyond Endemic Borders: A 24-Year Longitudinal Analysis of Mortality in a Diverse South American Cohort

    Fabio Specian1, Carolina Ejnisman2, Rafael Bassara Macedo1, Pedro Araujo3, Barbara Bayeh2, Thiago Freitas4, Rafael Cordeiro5 and Henrique Giardini4, 1Rheumatology Division, Hospital das Clinicas da Faculdade de Medicina da Universidade de Sao Paulo (USP), Sao Paulo, Sao Paulo, Brazil, 2Rheumatology Division, Hospital das Clinicas HCFMUSP, Faculdade de Medicina, Universidade de Sao Paulo, Sao Paulo, SP, Brazil, Sao Paulo, Brazil, 3Universidade de São Paulo, Sao Paulo, São Paulo, Brazil, 4Rheumatology Division, Hospital das Clinicas HCFMUSP, Faculdade de Medicina, Universidade de Sao Paulo, Sao Paulo, SP, Brazil, São Paulo, Brazil, 5Rheumatology Division, Hospital das Clinicas HCFMUSP, Faculdade de Medicina, Universidade de Sao Paulo, Sao Paulo, SP, Brazil, São Paulo, Sao Paulo, Brazil

    Background/Purpose: Behçet’s syndrome (BS) is a chronic, relapsing vasculitis that contributes substantially to morbidity and mortality, primarily due to vascular and neurological complications. Most of…
  • Abstract Number: 1292 • ACR Convergence 2025

    Childhood-onset Behçet’s disease: HLA alleles role on diagnosis and treatment in a Latin American tertiary center

    Matheus França1, Thales Souza2, Ricardo Machado3, Vinicius Matias4, Sylvia Farhat3, Lia Steuer3, Luisa Forero3, Verena Balbi3, Nadia Emi Aikawa5, Katia Kozu3, Clovis Artur Silva6, Adriana Elias7 and Lucia Maria Campos8, 1Instituto da Criança e do Adolescente, Hospital das Clinicas, University of Sao Paulo Medical School, Sao Paulo, Sao Paulo, Brazil, 2Faculdade de Medicina da Universidade de Brasilia, Brasilia, Distrito Federal, Brazil, 3Instituto da Criança e do Adolescente, Hospital das Clinicas, Sao Paulo, Sao Paulo, Brazil, 4Faculdade de Ciências Medicas da Santa Casa de Sao Paulo, Sao Paulo, Sao Paulo, Brazil, 5Rheumatology Division and Pediatric Rheumatology Unit, Hospital das Clinicas HCFMUSP, Faculdade de Medicina, Universidade de Sao Paulo, Sao Paulo, SP, Brazil, Sao Paulo, São Paulo, Brazil, 6University of São Paulo, São Paulo, São Paulo, Brazil, 7Pediatric Rheumatology Unit, Instituto da Criança e do Adolescente, Hospital das Clinicas, University of Sao Paulo Medical School, São Paulo, São Paulo, Brazil, 8Instituto da Criança e do Adolescente, São Paulo, São Paulo, Brazil

    Background/Purpose: Behçet’s disease (BD) is a rare pediatric vasculitis with limited epidemiological data in Latin America centers, especially in children where initial symptoms can be…
  • Abstract Number: 1180 • ACR Convergence 2025

    Gender-Based Clinical Differences in Behçet’s Syndrome: Findings from a 24-Year Cohort in a Non-Endemic and Multiethnic Country

    Rafael Bassara Macedo1, Pedro Araujo2, Fabio Specian1, Carolina Ejnisman3, Barbara Bayeh3, Percival Degrava Sampaio Barros3, Thiago Freitas4, Rafael Cordeiro5 and Henrique Giardini4, 1Rheumatology Division, Hospital das Clinicas da Faculdade de Medicina da Universidade de Sao Paulo (USP), Sao Paulo, Sao Paulo, Brazil, 2Universidade de São Paulo, Sao Paulo, São Paulo, Brazil, 3Rheumatology Division, Hospital das Clinicas HCFMUSP, Faculdade de Medicina, Universidade de Sao Paulo, Sao Paulo, SP, Brazil, Sao Paulo, Brazil, 4Rheumatology Division, Hospital das Clinicas HCFMUSP, Faculdade de Medicina, Universidade de Sao Paulo, Sao Paulo, SP, Brazil, São Paulo, Brazil, 5Rheumatology Division, Hospital das Clinicas HCFMUSP, Faculdade de Medicina, Universidade de Sao Paulo, Sao Paulo, SP, Brazil, São Paulo, Sao Paulo, Brazil

    Background/Purpose: Behçet’s syndrome (BS) is a multisystemic inflammatory condition that affects both genders, although gender-related differences in disease manifestations may vary across regions. Studies report…
  • Abstract Number: L14 • ACR Convergence 2024

    A Withdrawal Study of Colchicine in Behçet Syndrome

    Basak Sirin1, Sinem Nihal Esatoglu2, Hasan Yazıcı3 and Gulen Hatemi4, 1Istanbul University- Cerrahpaşa, Cerrahpaşa Medical Faculty, Department of Internal Medicine, Istanbul, Turkey, 2Istanbul University- Cerrahpaşa, Cerrahpaşa Medical Faculty, Department of Internal Medicine, Division of Rheumatology, Istanbul,Türkiye/Istanbul University- Cerrahpaşa, Behcet's Disease Research Center, Istanbul, Turkey, 3Academic Hospital, Istanbul, Turkey, 4Istanbul University- Cerrahpaşa, Cerrahpaşa Medical Faculty, Department of Internal Medicine, Division of Rheumatology, Istanbul,Türkiye/Istanbul University- Cerrahpaşa, Behcet's Disease Research Center, Istanbul,Türkiye, Istanbul, Turkey

    Background/Purpose: Previous randomized controlled studies reported conflicting results regarding the effectiveness of colchicine on oral ulcers in Behçet syndrome (BS). A randomized drug discontinuation design…
  • Abstract Number: 2524 • ACR Convergence 2024

    Metabolite Profiling of Saliva for the Discrimination of Behcet’s Disease, Sjogren’s Syndrome, and Recurrent Aphthous Stomatitis

    Sooah Kim1, Ye Ji Jung2, Joong Kyong Ahn3 and Jiwon Hwang4, 1Environment Science & Biotechnology, Jeonju University, Jeonju, Republic of Korea, 2Division of Rheumatology, Department of Internal Medicine, Kyung Hee University Hospital, Seoul, Republic of Korea, 3Internal Medicine, Kangbuk Samsung Hospital, Sungkyunkwan University School of Medicine, Seoul, Republic of Korea, 4Internal Medicine, Kyung Hee University Hospital, Seoul, Republic of Korea

    Background/Purpose: Oral manifestations can be the initial indicators of systemic diseases such as Behcet’s disease (BD) and Sjogren’s syndrome (PSS). The frequency and presentation of…
  • Abstract Number: 0150 • ACR Convergence 2024

    The Characteristics of a Northern Israeli Cohort of Patients with Behcet’s Syndrome

    Firas Sabbah1, Fadi Hassan2, Rula Daood2, Helana Jeries3, Tamar Hareuveni4, Nimer Abed5 and Mohammad E Naffaa2, 1Rheumatology Unit, Tzafon Medical Center, Poria, Israel, Tiberias, Israel, 2Rheumatology Unit, Galilee Medical Center, Naharyia, Israel, Naharyia, Israel, 3Rheumatology Unit, Galilee Medical Center, Naharyia, Israel, Naharyia, HaZafon, Israel, 4Ophthalmology department, Galilee Medical Center, Naharyia, Israel, Nahariya, Israel, 5Internal Medicine "B", Galilee Medical Center, Naharyia, Israel, Nahariya

    Background/Purpose: Behcet's syndrome (BS) is a multisystem disease that typically manifests as recurrent oral and genital ulcers, along with skin, eye, gastrointestinal, neurologic and vascular…
  • Abstract Number: 1111 • ACR Convergence 2024

    Impact of Scleroderma, Antiphospholipid Syndrome, Behçet’s Disease, and Dermatomyositis on Mortality Among Hospitalized Patients with Pulmonary Embolism

    Kessiena Aomreore, Lincoln Medical Center, New york, NY

    Background/Purpose: Autoimmune diseases are associated with a high prevalence of pulmonary embolism due to the inflammation-induced hyper coagulable state.This study aimed to analyze trends in…
  • Abstract Number: 1118 • ACR Convergence 2024

    The Performance of Behcet’s Disease Clinical Diagnostic Criteria in a Low Prevalence Region. A Retrospective Single Center Cohort Study

    Muhammad Shamim1, Mazen Allouni2, Haseeb Chaudhary3 and Omer Pamuk4, 1University Hospitals/ Case Western Reserve University, Cuyahoga Falls, OH, 2Case Western Reserve, University Hospitals, Cleveland Medical Center, Cleveland, OH, 3Case Western Reserve University, Westlake, OH, 4University Hospitals Cleveland Medical Center/ Case Western Reserve University, Cleveland, OH

    Background/Purpose: The diagnosis of Behcet’s Disease (BD) is particularly challenging in non-endemic areas because of milder disease presentations and lack of specific tests. Prior studies…
  • Abstract Number: 1633 • ACR Convergence 2024

    Arthritis Activity Significantly Affects Quality of Life in Behcet’s Disease Patients

    Koichi Sugihara1, Risa Wakiya2, Hiromi Shimada2, Taichi Miyagi2, Yusuke Ushio2, Rina Mino2, Mao Mizusaki3, Hayamasa yamaguchi3, Naoto Manabe3, Shusaku Nakashima2 and Hiroaki dobashi2, 1Department of Internal Medicine, Division of Hematology, Rheumatology and Respiratory Medicine, Faculty of Medicine, Kagawa University, Miki-cho, Kita-gun, Kagawa Prefecture, Japan, 2Kagawa University, Miki-cho, Kita-gun, Japan, 3Department of Internal Medicine, Division of Hematology, Rheumatology and Respiratory Medicine, Faculty of Medicine, Kagawa University, Miki-cho, Kita-gun, Japan

    Background/Purpose: Arthritis associated with Behcet's disease (BD) has been reported to be related to patients' quality of life and associated with skin and mucosal lesions.…
  • Abstract Number: 1896 • ACR Convergence 2024

    The Prevalence, Incidence, Risk Factors and Time to Diagnosis of Behcet’s Syndrome in England: A Retrospective Nested Case Control Study in Clinical Practice Research Datalink and Hospital Episode Statistics

    Priyanka Chandratre1, Joht Chandan2, Ben Hammond3, Rasiah Thayakaran3, Samuel Cusworth3, Nicola Adderley3 and Deva Situnayake4, 1The Ottawa Hospital and Ottawa Hospital Research Institute (OHRI), Ottawa, ON, Canada, 2Institute of Applied Health Research, Birmingham, United Kingdom, 3Institute of Applied Health Research, University of Birmingham, Birmingham, United Kingdom, 4Sandwell and West Birmingham NHS Trust, Birmingham, United Kingdom

    Background/Purpose: The prevalence and incidence of Behcet’s syndrome (BS) in the UK is unknown at an unselected population level. BS may be associated with phenotypically…
  • Abstract Number: 2515 • ACR Convergence 2024

    Upadacitinib for Refractory Behçet’s Syndrome: A Multi-center, Prospective, Open-label, Pilot Study

    Weiyi Xia1, Jiachen Li1, Tian Liu1 and Yuhui Li2, 1Peking University People’s Hospital, Beijing, China, 2Peking University, BeiJing, China

    Background/Purpose: The aim of this prospective cohort study is to evaluate the efficacy and safety of Janus kinase (JAK) inhibitor upadacitinib in refractory Behçet’s Syndrome…
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