Abstract Number: 2192 • 2014 ACR/ARHP Annual Meeting
Successful Therapy with Intravenous Sodium Thiosulfate for Adult Dermatomyositis Associated Calcinosis
Background/Purpose: Calcinosis cutis is the deposition of insoluble calcium salts in skin or subcutaneous tissue. In cases related to CTD, presents with normal calcium/phosphorus metabolism,…Abstract Number: 2193 • 2014 ACR/ARHP Annual Meeting
Prevalence of Raynaud’s Phenomenon and Nailfold Capillaroscopic Abnormalities in Fabry’s Disease: A Cross-Sectional Study
Background/Purpose: Fabry's disease (FD) is a lysosomal disorder leading to progressive systemic involvement, including neurologic and vascular. We hypothesize that the microangiopathy observed in FD…Abstract Number: 2194 • 2014 ACR/ARHP Annual Meeting
Blue Digit Syndrome: The Rheumatologist’s Perspective
Background/Purpose: Blue or purple digit syndrome (or sign) is a cutaneous manifestation of multiple diseases that produce acute or subacute ischemic compromise in one or…Abstract Number: 2195 • 2014 ACR/ARHP Annual Meeting
Eculizumab Treatment of Malignant Atrophic Papulosis (Köhlmeier-Degos Disease): World Experience to Date
Background/Purpose Malignant atrophic papulosis (MAP) is an obliterative vasculopathy which presents with distinctive cutaneous lesions but can progress over months to years to systemic disease…Abstract Number: 2196 • 2014 ACR/ARHP Annual Meeting
Treprostinil Use in Malignant Atrophic Papulosis (Köhlmeier-Degos Disease): Review of Worldwide Experience to Date
Background/Purpose Malignant atrophic papulosis (MAP) is a rare thrombo-occlusive vasculopathy that presents with cutaneous only lesions but can progress after months or years to rapidly fatal systemic…Abstract Number: 2197 • 2014 ACR/ARHP Annual Meeting
Malignant Atrophic Papulosis (MAP) Complicating Connective Tissue Diseases (CTDs)
Background/Purpose Malignant Atrophic Papulosis (MAP) is a rare vasculopathy of unknown etiology commonly presenting with cutaneous lesions, but can progress to multisystem disease with a…Abstract Number: 2198 • 2014 ACR/ARHP Annual Meeting
The Aromatase Inhibitor Induced Musculoskeletal Syndrome: Is There a Potential Role of Osteoporosis Therapy and Menopause Timing?
Background/Purpose: Aromatase Inhibitor (AI) therapy is the most effective hormonal treatment in post-menopausal estrogen receptor (ER) positive breast cancer. These patients may be seen by…Abstract Number: 2199 • 2014 ACR/ARHP Annual Meeting
Intravenous Immunoglobulin Therapy for Secondary Hemophagocytic Lymphohistiocytosis : A Retrospective Study of 46 Patients
Background/Purpose Intravenous Immunoglobulins (IVIg) have been reported as giving good results in infectious, but also auto-immune related forms of hemophagocytic lymphohistiocytosis (HLH), but only in…Abstract Number: 2200 • 2014 ACR/ARHP Annual Meeting
Elevated Serum Ferritin Levels in Adult Inpatients As a Predictor of in-Hospital Mortality and Association with Macrophage Activation Syndrome
Background/Purpose Macrophage Activation Syndrome (MAS) is a syndrome similar to Familial Hemophagocytic Lymphohistiocytosis (HLH) characterized by increased proliferation and activity of T-cells and macrophages leading…Abstract Number: 2201 • 2014 ACR/ARHP Annual Meeting
Haematological Complications in Rheumatic Diseases: Not Only Lymphomas
Background/Purpose Several immunological abnormalities have been reported among patients affected by myelodisplastic syndrome (MDS). On the other hand, a relatively limited number of studies have…Abstract Number: 2202 • 2014 ACR/ARHP Annual Meeting
Pilot Study of Tocilizumab in Patients with Erdheim-Chester Disease
Background/Purpose Erdheim-Chester disease (ECD) is a rare, systemic disorder of unknown etiology, characterized by tissue infiltration with CD68+, CD1a- foamy histiocytes. ECD is a chronic,…Abstract Number: 2203 • 2014 ACR/ARHP Annual Meeting
Adalimumab Therapy Improves Insulin Sensitivity in Non-Diabetic Psoriatic Patients: A 6-Month Prospective Study
Background/Purpose: psoriasis is a systemic inflammatory condition that shares similarities with other inflammatory immune disorders. In this context, patients with psoriasis are at an increased…Abstract Number: 2204 • 2014 ACR/ARHP Annual Meeting
New Onset Vitiligo Under Biological Agents: A Case Series
Background/Purpose: biological agents are now widely used in clinical practice for the treatment of chronic cutaneous, rheumatic and gastro-intestinal inflammatory diseases. Various cutaneous lesions have…Abstract Number: 2205 • 2014 ACR/ARHP Annual Meeting
Management of Asymptomatic Coccidioidomycosis in Patients with Rheumatic Disease
Background/Purpose: In the Southwestern United States, coccidioidomycosis (valley fever) is an endemic fungal infection which typically causes a self-limited pulmonary illness. Immunosuppressed patients, including those…Abstract Number: 2206 • 2014 ACR/ARHP Annual Meeting
The Incidence of Zoster in Patients with Cutaneous Lupus Erythematosus and Dermatomyositis Is Increased Compared to the Average U.S. Population
Background/Purpose: Herpes zoster is a common condition that causes significant pain and, often, post-herpetic neuralgia. In the United States the incidence of zoster per 1,000…
ACR Meeting Abstracts