Abstract Number: 2274 • 2014 ACR/ARHP Annual Meeting
TNF Inhibitors Provide Long-Term Clinical Benefits in 6 Patients with Early-Onset Sarcoidosis
Background/Purpose: Early-onset sarcoidosis (EOS) is a NOD2 gene-associated chronic autoinflammatory disease, characterized by the triad of arthritis, rash, and uveitis, which usually occurs in children…Abstract Number: 2275 • 2014 ACR/ARHP Annual Meeting
Immunization Status and Barriers in Childhood Rheumatic Diseases
Background/Purpose To determine the vaccination status of children with rheumatic diseases, and identify immunization knowledge of families and potential barriers to vaccination. Methods A cross-sectional…Abstract Number: 2276 • 2014 ACR/ARHP Annual Meeting
Consensus Statement on the Transition Process from Pediatric Care to Adult Care in Patients with Chronic Inflammatory Rheumatic Diseases with Childhood-Onset
Background/Purpose: many young people with childhood-onset diseases, including rheumatic diseases, continue to require medical care into adult life. There are many differences between pediatric and…Abstract Number: 2277 • 2014 ACR/ARHP Annual Meeting
Inpatient Pediatric Rheumatic Diseases: Characteristics, Cost and Trends
Background/Purpose: Childhood rheumatic diseases (cRD) have wide spectrum of complexity and disease course from mild disease to acute fulminate disease and even sudden death. Physicians…Abstract Number: 2278 • 2014 ACR/ARHP Annual Meeting
Orbital Pseudotumor As the Presenting Symptom of Pediatric ANCA-Associated Vasculitis
Background/Purpose: Ocular involvement, particularly orbital pseudotumor, has been reported as the initial manifestation of ANCA-associated vasculitis (AAV) in the adult population, predominantly in granulomatosis with…Abstract Number: 2279 • 2014 ACR/ARHP Annual Meeting
Evidence Based Recommendations for Diagnosis and Management of Tumor Necrosis Factor Receptor-1 Associated Periodic Syndrome (TRAPS)
Background/Purpose Tumor necrosis factor receptor-1 associated periodic syndrome (TRAPS) is a rare hereditary autoinflammatory syndrome that can lead to significant morbidity. Evidence-based guidelines are lacking…Abstract Number: 2280 • 2014 ACR/ARHP Annual Meeting
Evidence Based Recommendations for the Management of Cryopyrin Associated Periodic Syndromes (CAPS)
Background/Purpose Cryopyrin-associated periodic syndromes (CAPS) is a group of rare monogenetic autoinflammatory disorders. Evidence-based guidelines are lacking and management is mostly based on physician’s experience. Consequently,…Abstract Number: 2281 • 2014 ACR/ARHP Annual Meeting
Dissecting the Heterogeneity of Macrophage Activation Syndrome
Background/Purpose Macrophage activations syndrome (MAS) occurring in the context of systemic juvenile idiopathic arthritis (sJIA) can pursue a rapidly fatal course. However, the diagnosis of…Abstract Number: 2282 • 2014 ACR/ARHP Annual Meeting
Evidence Based Recommendatinos for Diagnosis and Management of Mevalonate Kinase Deficiency (MKD)
Background/Purpose Mevalonate kinase deficiency (MKD) is a rare hereditary autoinflammatory syndrome that can lead to significant morbidity. Evidence-based guidelines are lacking and management is mostly…Abstract Number: 2283 • 2014 ACR/ARHP Annual Meeting
Steroid-Sparing Effect of Anakinra (Kineret®) in the Treatment of Patients with Severe Cryopyrin-Associated Periodic Syndrome
Background/Purpose Cryopyrin-Associated Periodic Syndromes (CAPS) include a group of rare inherited autoinflammatory diseases consisting of FCAS, Muckle-Wells Syndrome and the most severe form, NOMID. Reduction…Abstract Number: 2284 • 2014 ACR/ARHP Annual Meeting
Joint Involvement in Pediatric Crohn’s Disease Is Related to Higher Disease Activity and Worse Quality of Life
Background/Purpose: The incidence of arthritis and arthralgia in pediatric patients with Crohn's disease (CD) is reported to be 2–15% and 22%, respectively. The aim of our…Abstract Number: 2285 • 2014 ACR/ARHP Annual Meeting
Safety and Efficacy of Rilonacept in Patients with Deficiency of Interleukin-1 Receptor Antagonist (DIRA)
Background/Purpose: Deficiency of interleukin-1 receptor antagonist (DIRA) is a neonatal-onset autoinflammatory syndrome caused by recessive mutations in IL1RN gene, the gene encoding the interleukin-1-receptor antagonist.…Abstract Number: 2286 • 2014 ACR/ARHP Annual Meeting
Food Allergy and Celiac Disease in Children with Juvenile Idiopathic Arthritis
Background/Purpose: There are multiple strong associations between gut pathology and rheumatologic diseases. This connection, between primary GI disease and rheumatologic diseases, is manifest in both…Abstract Number: 2287 • 2014 ACR/ARHP Annual Meeting
Cartilage Thickness and Bone Health in Children with Juvenile Idiopathic Arthritis
Background/Purpose Although treatment options have increased and morbidity has decreased in the last decade Juvenile Idiopathic Arthritis (JIA) may still result in disability. Increasingly ultrasonography…Abstract Number: 2288 • 2014 ACR/ARHP Annual Meeting
The Research in Arthritis in Canadian Children Emphasizing Outcomes (ReACCh Out) Cohort: Independent Risk Factors and Medication Use in New Onset Uveitis in Juvenile Idiopathic Arthritis
Background/Purpose: The Research in Arthritis in Canadian Children emphasizing Outcomes (ReACCh Out) cohort is a multi-centre prospective inception cohort of newly diagnosed Juvenile Idiopathic Arthritis…