Abstract Number: 1311 • 2018 ACR/ARHP Annual Meeting
A Multidisciplinary Cohort of Patients with Interstitial Pneumonia with Autoimmune Features
Background/Purpose: Interstitial Lung Disease (ILD) remains a significant diagnostic and therapeutic challenge, especially for patients who do not meet criteria for a connective tissue disease…Abstract Number: 1312 • 2018 ACR/ARHP Annual Meeting
Interstitial Pneumonia with Autoimmune Features (IPAF)-Nsip: Hurdles to Reclassification of Overlapping Ilds
Background/Purpose: Interstitial lung disease (ILD) may occur in the presence of autoimmune elements without meeting criteria for a distinctive Connective Tissue Disease. The European Respiratory…Abstract Number: 1313 • 2018 ACR/ARHP Annual Meeting
Clinical Features and Timing of Studies in Interstitial Lung Disease with Autoimmune Disease Features: Do Autoantibody Panels Improve Diagnostic Yields and/or Increase Costs?
Background/Purpose: The entity of interstitial lung disease with autoimmune disease features (ILD-AF) is increasingly gaining traction as condition that is best co-managed by pulmonologists and…Abstract Number: 1314 • 2018 ACR/ARHP Annual Meeting
Autoantibodies and Clinical Outcomes in Pulmonary Arterial Hypertension Associated with Connective Tissue Diseases
Background/Purpose: Pulmonary arterial hypertension (PAH) associated with SSc (SSc-PAH) has a substantially worse prognosis as compared to other connective tissue diseases (CTD)-PAH. Although SSc-PAH are…Abstract Number: 1315 • 2018 ACR/ARHP Annual Meeting
Japanese Relapsing Polychondritis Patients with Airway Involvement Were Mutually Exclusive with Those with Ear Involvement in the Clinical Characteristics
Background/Purpose: Relapsing polychondritis (RP) is a multisystem disorder of cartilaginous tissues. We previously found that, in a Japanese cohort study, RP patients with airway involvement…Abstract Number: 1316 • 2018 ACR/ARHP Annual Meeting
Respiratory Involvement in Relapsing Polychondritis – a Single Centre Study
Background/Purpose: Relapsing Polychondritis (RP) is a rare immune mediated inflammatory disorder that may result in destruction of cartilaginous tissues. Diagnostic delay is common due to…Abstract Number: 1317 • 2018 ACR/ARHP Annual Meeting
Tracheomalacia in Coventry in UK
Background/Purpose: Tracheomalacia (TM) is pathological diffuse or segmental narrowing of the tracheal lumen, caused by softening of the supporting cartilage and reduction in stiffness of…Abstract Number: 1318 • 2018 ACR/ARHP Annual Meeting
Clinical Utility of Ultrasonography (US) in Diagnosing and Monitoring Disease Activity of Relapsing Polychondritis (RP) and Comparison of Cartilaginous US Findings between RP, Repeated Trauma and Healthy Subjects
Background/Purpose: Relapsing polychondritis (RP) is a rare systemic inflammatory disorder, and the diagnosis and treatment evaluation are often difficult. Therefore, the discovery of more convenient…Abstract Number: 1319 • 2018 ACR/ARHP Annual Meeting
Familial Mediterranean Fever Related Damage Assessed By Auto-Inflammatory Disease Damage Index (ADDI) and Associated Factors with Damage
Background/Purpose: Familial Mediterranean Fever (FMF) is the most frequent auto-inflammatory disease caused by MEFV gene mutations. Although FMF is characterized by intermittent inflammatory attacks some…Abstract Number: 1320 • 2018 ACR/ARHP Annual Meeting
Activity Tracker Bracelets Captures Familial Mediterranean Fever Attacks and Their Impact on Daily Physical Activities
Activity Tracker bracelets captures Familial Mediterranean Fever attacks and their impact on daily physical activities Background/Purpose: Familial Mediterranean fever (FMF) is a recessively inherited systemic…Abstract Number: 1321 • 2018 ACR/ARHP Annual Meeting
Clinical and Genetic Analysis of the Patients Mimicking Familial Mediterranean Fever
Clinical and genetic analysis of the patients mimicking familial Mediterranean feverBackground/Purpose: Familial Mediterranean fever (FMF) is an auto-inflammatory disease characterized by recurrent episodes of fever…Abstract Number: 1322 • 2018 ACR/ARHP Annual Meeting
Comparison of Serum Hepcidin and Calprotectin Levels in Patients with Familial Mediterranean Fever (FMF) and Healthy Subjects
Background/Purpose: Familial Mediterranean fever (FMF) is an autoinflammatory disease which has self-limiting inflammatory attacks placing in polyserositis. Hepcidin is a protein in peptide structure and…Abstract Number: 1323 • 2018 ACR/ARHP Annual Meeting
Evaluation of Prolidase and HIF-1α Levels in Patients with Familial Mediterranean Fever (FMF)
Background/Purpose: Familial Mediterranean Fever(FMF) is an autoinflammatory disease characterized by recurrent fever attacks, sterile peritonitis, pleural inflammation, arthritis and / or erysipelas like rash. Prolidase…Abstract Number: 1324 • 2018 ACR/ARHP Annual Meeting
Anakinra Treatment in Refractory Cases of Adult-Onset Still Disease: Case Series
Background/Purpose: Despite methotrexate and steroid treatment, in cases of Adult-onset Still’s disease (AOSD) it is usually difficult to maintain clinic stability. In refractory cases, Anakinra…Abstract Number: 1325 • 2018 ACR/ARHP Annual Meeting
Canakinumab Treatment in Adult-Onset Still’s Disease: Case Series
Background/Purpose: In Adult-onset Still’s disease (AOSD), cases refractory to typical DMARDs, Canakinumab (an anti-IL-1ß monoclonal antibody) has been reported to be effective in a limited…