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  • Abstract Number: 1273 • 2019 ACR/ARP Annual Meeting

    Certolizumab Therapy in Patients with Uveitis During Pregnancy: Multicenter Study

    DIANA PRIETO- PENA1, Vanesa Calvo Río 2, Mónica Calderón-Goercke 3, Olga Maíz Alonso 4, JR Jimenez-Aberasturi 5, Raul Veroz 6, Maria Soledad Blanco 7, José Manuel Santos 8, Francisco Navarro 9, Adela Gallego 10, Rosalia Demetrio 11, Victor Manuel Martínez Taboada 11, Miguel Angel González-Gay 12 and Ricardo Blanco 2, 1Rheumatology, Hospital Universitario Marques de Valdecilla, Santander, Cantabria, Spain, 2Rheumatology, Hospital Universitario Marques de Valdecilla, Santander, Spain, 3Hospital Marqués de Valdecilla, Santander, Cantabria, Spain, 4H. Donostia, San Sebastián, Spain, 5HU Araba, Vitoria, Spain, 6H. Mérida, Merida, Spain, 7H. Galdakano, Bilbao, Spain, 8H. Río Hortega, Valladolid, Spain, 9H.Elche, Alicante, Spain, 10H. Badajoz, Badajoz, Spain, 11Hospital Universitario Marqués de Valdecilla, Santander, Spain, 12Universidad de Cantabria and IDIVAL, Hospital Universitario Marqués de Valdecilla, Santander, Spain

    Background/Purpose: Uveitis often occur in women who are in their reproductive years. The management of uveitis during pregnancy is a challenge, making the physician to…
  • Abstract Number: 1274 • 2019 ACR/ARP Annual Meeting

    New Aspects of Clinical and Immunological Characteristics in Patients with Anti-KS Antibody

    Sho Sasaki1, Akira Ishii 2, Mai Sugiyama 2, Yuto Izumi 2, Yoko Nakagome 2, Kazuki Hirano 3, Takayoshi Kurabayashi 1, Shinichi Nogi 4, Noriko Sasaki 2, Chiho Yamada 2 and Shinji Sato 5, 1Tokai Universitiy School of Medicine, Isehara, Japan, 2Tokai University School of Medicine, Isehara, Japan, 3Tokai University School of Medicine, Isehara, 4National Hospital Organization Sagamihara Hospital, Sagamihara, Japan, 5Division of Rheumatology, Department of Internal Medicine, Tokai University School of Medicine, Yokohama, Japan

    Background/Purpose: Anti-KS antibody, an anti-aminoacyl tRNA synthetase (ARS) antibody, is found mainly in patients with interstitial lung disease (ILD) accompanied by polymyositis/dermatomyositis (PM/DM). Although anti-KS…
  • Abstract Number: 1275 • 2019 ACR/ARP Annual Meeting

    Spectrum of Organ Involvement in Idiopathic Inflammatory Myopathies, Frequency of Comorbidities, and Relationship to Anti-SSA/SSB Positivity

    Ana Valle1, Galina Marder 1, Maria-Louise Barilla-Labarca 1 and Sonali Narain 2, 1Donald and Barbara Zucker School of Medicine at Hofstra/Northwell, Hempstead, NY, 2Northwell Health, Great Neck, Long Island, NY

    Background/Purpose: Idiopathic inflammatory myopathies (IIM) are chronic autoimmune diseases with systemic features and multiple  comorbidities. Of the myositis associated antibodies seen in this population, anti-SSA/SSB…
  • Abstract Number: 1276 • 2019 ACR/ARP Annual Meeting

    Myositis Specific Antibodies and Clinical Features in Patients from Argentina

    Amelia Granel1, Maria de Los Angeles Gargiulo 2, Ana Carolina Marcos 3, Ramiro Gomez 4, Andrea Braillard Poccard 5, Carolina Costi 6, Mercedes Garcia 7, Malena Viola 8, Maria de la Vega 9, Belen Barrios 10, Silvia Papasidero 11, Boris Kisluk 12, Guillermo Berbotto 12, Mariana Aciar 13, María Crespo Espíndola 14, Mariano Rivero 15, Maria N Lojo 16, Yessica Ponce Delgado 17, Oscar Rillo 18, Ramiro Puerta 19, Isabel Pineda 20, Dafne Capelusnik 21, Roberto Movia 22, Darío Scublinsky 23, Maria Alicia Lazaro 24 and Graciela Gómez 25, 1Hospital San Roque,Gonnet,La Plata,Buenos Aires.Argentina, La Plata, Buenos Aires, Argentina, 2Instituto de Investigaciones Médicas,Alfredo Lanari.Universidad de Buenos Aires.Argentina, Ciudad de Buenos Aires, Argentina, 3Hospital San Roque,Gonnet,La Plata,Buenos Aires.Argentina, Gonnet, Argentina, 4Hospital de Clínicas José de San Martín, Ciudad Autónoma de Buenos Aires, Buenos Aires, Argentina, 5Hospital de Clínicas José de San Martin, Buenos Aires, Buenos Aires, Argentina, 6Hospital General “San Martín” de la Plata, La Plata, Buenos Aires, Argentina, 7Hospital San Martín, La Plata, Argentina, 8Centro Reumatologia DOM, Buenos Aires, Buenos Aires, Argentina, 9CEIM Investigaciones Medicas, Buenos Aires, Argentina, 10Hospital Enrique Tornu,Ciudad de Buenos Aires.Argentina, Ciudad de Buenos Aires, Argentina, 11Hospital General de Agudos Dr. E. Tornú, Ciudad Autónoma de Buenos Aires, Buenos Aires, Argentina, 12Hospital Escuela Eva Perón.Granadero Baigorria,Santa Fe.Argentina, Granadero Baigorria, Argentina, 13Hospital Ntro Señor del Milagro, Salta.Argentina., Salta, Argentina, 14Hospital Señor del Milagro, Salta, Salta, Argentina, 15Hospital Británico, Buenos Aires, Buenos Aires, Argentina, 16Hospital Rossi,La Plata.Argentina, La Plata, Argentina, 17Hospital Pirovano.Ciudad de Buenos Aires. Argentina, Ciudad de Buenos Aires, Argentina, 18Hospital Pirovano, Buenos Aires, 19Hospital Houssay.Vicente Lopez,Buenos Aires.Argentina., Vicente Lopez, Argentina, 20Consultorios Externos Venado Tuerto.Santa Fe.Argentina., Venado Tuerto, Argentina, 21Instituto de Rehabilitacion Psicofisica, CABA, Ciudad Autonoma de Buenos Aires, Argentina, 22Hospital Evita.Lanus.Pcia Buenos Aires. Argentina, Lanus, Argentina, 23Centros Médicos Ambulatorios SMG, Ciudad Autónoma de Buenos Aires, Buenos Aires, Argentina, 24Consultorio Particular, San Isidro, Argentina, 25Instituto de Investigaciones Médicas,Alfredo Lanari.Universidad de Buenos Aires.Argentina., Buenos Aires, Argentina

    Background/Purpose: To know the frequency of myositis specific antibodies (MSAs) and myositis associated antibodies( MAAs) and their relation with clinical features in patients with idiopathic…
  • Abstract Number: 1277 • 2019 ACR/ARP Annual Meeting

    Damage and Comorbidities in a Cohort of Patients with Idiopathic Inflammatory Myopathy

    Ana Campar1 and Carlos Vasconcelos 2, 1Centro Hospitalar do Porto, Porto, Portugal, 2University of Porto, UMIB Abel Salazar Biomedical Sciences Institute, Porto, Portugal

    Background/Purpose: Idiopathic Inflammatory Myopathies (IIM) remain a major clinical challenge worldwide. The precise aetiopathogenesis of this chronic and disabling disorder remains elusive which precludes the…
  • Abstract Number: 1278 • 2019 ACR/ARP Annual Meeting

    Inpatient Epidemiology of Dermatomyositis and Polymyositis in the United States

    Patompong Ungprasert1, Wisit Cheungpasitporn 2, Charat Thongprayoon 3, Karn Wijarnpreecha 4 and Paul Kroner 5, 1Cleveland Clinic, Cleveland, OH, Bangkok, Thailand, 2University of Mississippi Medical Center, Jackson, MS, 3Mayo Clinic Rochester, Rochester, MN, 4Mayo Clinic Florida, Jacksonville, FL, 5Mayo Clinic Florida, Jacksonville

    Background/Purpose: Dermatomyositis (DM) and polymyositis (PM), collectively known as idiopathic inflammatory myositis (IIM), are autoimmune disorders characterized by inflammation of skeletal muscle, especially in the…
  • Abstract Number: 1279 • 2019 ACR/ARP Annual Meeting

    Response Rate and Sustained Remission in Idiopathic Inflammatory Myopathies Receiving Conventional Immunosuppressive Stepwise Management

    Alain Sánchez-Rodríguez1, Citlallyc Josefina Gómez-Ruiz 2, Abril Montes-Yanes 2 and Gabriel Medrano-Ramírez 2, 1Hospital General de Mexico, Mexico City, Distrito Federal, Mexico, 2Hospital General de Mexico, Rheumatology Department, Ciudad de Mexico, Distrito Federal, Mexico

    Background/Purpose: Information regarding response rate and sustained remission in patients with idiopathic inflammatory myopathies (IIM), polymyositis (PM), dermatomyositis (DM), in Hispanics with non-biological treatment is…
  • Abstract Number: 1280 • 2019 ACR/ARP Annual Meeting

    JAK Inhibitors: A Promising Molecular-targeted Therapy in Dermatomyositis

    Océane Landon-Cardinal1, Perrine Guillaume-Jugnot 2, Lois Bolko 2, Ségolène Toquet 2, Aude Rigolet 2, Baptiste Hervier 3, Nicolas Champtiaux 2, Mathieu VAUTIER 4, Olivier Benveniste 5 and Yves Allenbach 5, 1Centre Hospitalier de l'Université de Montréal, Montréal, Canada, 2Pitié-Salpêtrière University Hospital, Paris, France, 3Hopital Pitie-Salpetriere, Paris, France, 4Paris - Pitié salpétrière, Paris, France, 5Sorbonne Université, Paris, France

    Background/Purpose: We previously observed in vitro that IFN-I reproduces dermatomyositis (DM) pathological findings, that pathogenic effects may be prevented in vitro by JAK inhibitor (JAKinh) therapy and an improvement…
  • Abstract Number: 1281 • 2019 ACR/ARP Annual Meeting

    Maintenance Therapy for anti-MDA5-Positive Dermatomyositis Patients with Interstitial Lung Disease: Can They Achieve Drug-Free Remission?

    Tsuneo Sasai1, Ran Nanashima 1, Tsuneyo Mimori 2, Hideaki Tsuji 1, Shuji Akizuki 1, Kosaku Murakami 3, Motomu Hashimoto 3, Hajime Yoshifuji 1, Masao Tanaka 2 and Koichiro Ohmura 2, 1Kyoto University, Kyoto, Japan, 2Graduate School of Medicine, Kyoto University, Kyoto, Japan, 3Department of Advanced Medicine for Rheumatic Diseases, Kyoto University Graduate School of Medicine, Kyoto, Japan

    Background/Purpose: Interstitial lung disease (ILD) accompanied by anti-melanoma differentiation associated gene 5 (MDA5)-positive dermatomyositis (DM) is often rapidly progressive and associated with poor life prognosis…
  • Abstract Number: 1282 • 2019 ACR/ARP Annual Meeting

    Female Sex Is a Risk Factor for Failure to Achieve Remission in Polymyositis

    Prasanth Lingamaneni1, Carrie Richardson 2, Soumyasri Kambhatla 3 and Augustine Manadan 2, 1John H. Stroger Hospital of Cook County, Chicago, IL, 2Rush University Medical Center, Chicago, IL, 3John H. Stroger Hospital of Cook County, Chicago

    Background/Purpose: Adults with polymyositis demonstrate wide variability in responses to treatment, and the risk factors for failure to achieve remission in polymyositis are largely unknown. …
  • Abstract Number: 1283 • 2019 ACR/ARP Annual Meeting

    Risk Factors of Cancer-Associated Inflammatory Myopathies: A Multicenter Study

    Nantakarn Pongtarakulpanit1, Khemmapop Yongchairat 2, Wanruchada Kachamart 2, Charungthai Dejthevaporn 1, Natta Rajatanavin 1 and Parawee Chevaisrakul 1, 1Ramathibodi hospital, Mahidol University, Bangkok, Thailand, 2Siriraj Hospital, Mahidol university, Bangkok, Thailand

    Background/Purpose: The association between idiopathic inflammatory myopathies (IIMs) and malignancies in Thai population has been rarely reported. The objective of our study was to determine…
  • Abstract Number: 1284 • 2019 ACR/ARP Annual Meeting

    Idiopathic Inflammatory Myopathies: Are Muscle Biopsies Still Needed?

    Belén Virasoro1, Ramiro Gomez 2, Andrea Braillard Poccard 3, Dafne Capelusnik 4, Emilce Schneeberger 5, Silvia Papasidero 6, Juan Bande 6, Malena Viola 7, Maria de la Vega 8, Carolina Costi 9, Mercedes Garcia 10, Cecilia Asnal 11, Ana Cappuccio 12, Demelza Yucra 13, Linda Vergel Orduz 14, Natalia Tamborenea 15, Mariano Rivero 16, Amelia Granel 17, Carolina Segura Escobar 16, Marina Dalpiaz 15 and Cecilia Pisoni 18, 1CEMIC, buenos aires, Buenos Aires, Argentina, 2Hospital de Clínicas José de San Martín, Ciudad Autónoma de Buenos Aires, Buenos Aires, Argentina, 3Hospital de Clínicas José de San Martin, Buenos Aires, Buenos Aires, Argentina, 4Instituto de Rehabilitacion Psicofisica, CABA, Ciudad Autonoma de Buenos Aires, Argentina, 5Instituto de Rehabilitación Psicofísica, Buenos Aires, Argentina, 6Hospital General de Agudos Dr. E. Tornú, Ciudad Autónoma de Buenos Aires, Buenos Aires, Argentina, 7Hospital Argerich, Argentina, Buenos Aires, Argentina, 8CEIM Investigaciones Medicas, Buenos Aires, Argentina, 9Hospital General “San Martín” de la Plata, La Plata, Buenos Aires, Argentina, 10Hospital San Martín, La Plata, Argentina, 11Instituto Centenario, Buenos Aires, Buenos Aires, Argentina, 12Hospital Francés, Buenos Aires, Buenos Aires, Argentina, 13Sanatorio Güemes, Buenos Aires, Buenos Aires, Argentina, 14Sanatorio Gúemes, Buenos Aires, Buenos Aires, Argentina, 15Hospital Rivadavia, Buenos Aires, Buenos Aires, Argentina, 16Hospital Británico, Buenos Aires, Buenos Aires, Argentina, 17Hospital San Roque,Gonnet,La Plata,Buenos Aires.Argentina, La Plata, Buenos Aires, Argentina, 18Centro de Educación Médica e Investigaciones Clínicas Norberto Quirno (CEMIC), Ciudad Autónoma de Buenos Aires, Buenos Aires, Argentina

    Background/Purpose: Inflammatory myopathies (IM) are a heterogeneous group of diseases characterized by muscle inflammation. In Argentina, there are few pathologists specialized in muscle biopsies and…
  • Abstract Number: 1285 • 2019 ACR/ARP Annual Meeting

    Changes in Nail-fold Capillary Abnormalities, and Serum FGF and VEGF Levels in Dermatomyositis Patients with anti-MDA5 Antibody During the Clinical Course

    Yasuhito Hamaguchi1, Takashi Matsushita 1, Naoki Mugii 2 and Kazuhiko Takehara 1, 1Department of Dermatology, Kanazawa University, Kanazawa, Japan, 2Kanazawa University Hospital, Kanazawa, Japan

    Background/Purpose: Capillary abnormalities in the nail-fold are a characteristic finding of microangiopathy in autoimmune connective tissue diseases, including dermatomyositis and systemic sclerosis. A previous study…
  • Abstract Number: 1286 • 2019 ACR/ARP Annual Meeting

    Patients with Anti-tRNA Synthetase Syndrome Are More Likely to Present to Pulmonary Clinic and Have a Higher Prevalence and Severity of Lung Disease Than Patients with Other Types of Myositis or Systemic Sclerosis

    Bret Sohn1, Erin Wilfong 1 and Leslie Crofford 1, 1Vanderbilt University, Nashville

    Background/Purpose: Interstitial lung disease (ILD) is a significant cause of morbidity and mortality in idiopathic inflammatory myopathies (IIM) as well as systemic sclerosis (SSc). The…
  • Abstract Number: 1287 • 2019 ACR/ARP Annual Meeting

    Anti-mitochondrial Autoantibodies in Idiopathic Inflammatory Myopathies

    Sara Sabbagh1, Iago Pinal-Fernandez 2, Maria Casal-Dominguez 3, Frederick W. Miller 4, Andrew L Mammen 3 and Lisa G. Rider 5, 1National Institute of Arthritis and Musculoskeletal and Skin Diseases, National Institutes of Health (NIH), Bethesda, MD, 2National Institute of Arthritis and Musculoskeletal and Skin Diseases, National Institutes of Health (NIH), Bethesda, 3National Institutes of Health, Bethesda, 4NIEHS, NIH, Bethesda, MD, 5Environmental Autoimmunity Group, Clinical Research Branch, NIEHS, NIH, Bethesda, MD

    Background/Purpose: Autoantibodies found in adult and juvenile myositis patients are often associated with specific clinical features.  Prior reports have suggested that the myositis-associated autoantibody, anti-mitochondrial…
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