Methods:  For the pediatric rheumatology specialist who belongs to PRAJ (68 hospitals and medical institutes), web-based registry system was constructed. After review and approval by the ethics committee of PRAJ and each hospital, PRICURE survey has started since January 2017. The survey covered juvenile idiopathic arthritis (JIA), systemic lupus erythematosus (SLE), juvenile dermatomyositis (JDM), Sjögren’s syndrome (SS), mixed connective tissue disease (MCTD), systemic sclerosis (SSc), Behçet’s disease (BD), vasculitis syndrome and autoinflammatory diseases. Patient data included age, sex, date of disease onset, diagnosis, diagnostic criteria, treatment, complication and adverse effect.

Results:  One medical institute and 3 hospitals were accepted by each ethics committee and had started to register patients. Sixty one patients were registered initially (JIA patients 25, SLE patients 8, JDM patients 3, Sjögren’s syndrome patients 6, systemic sclerosis patients 3, Behçet’s disease patients 6, vasculitis syndrome patients 3 and autoinflammatory patients 6). Planned number of enrollment is more than 500 in first year.

Conclusion:  PRICURE survey is the exclusive survey by the pediatric rheumatologist in Japan. We hope to collaborate with other registry such as CARRA registry.